Behcet syndrome

doi:10.1016/j.medcli.2025.106983

2025-07-01

PRE

Gerard Espinosa *

DOI：10.1016/j.medcli.2025.106983

原文链接

原文求助

摘要

En 中文

白塞综合征（BS）是一种系统性血管炎，可影响各种口径的血管。它具有几个标志性特征，例如其随时间缓解的倾向和典型的地域分布。临床上，静脉血栓与动脉瘤、炎性实质脑受累、伴有视网膜血管炎的典型后葡萄膜炎模式，以及已知的口咽溃疡和结节性红斑三联征是该疾病的独特特征。尽管在BS的发病机制方面取得了一些进展，并且生物药物的使用改善了预后，但某些方面仍存在争议，例如皮试（pathergy test）或HLA-B*51在疾病诊断中的作用，以及抗凝治疗在BS合并血管血栓患者中的实际价值。

Keyword:

Behcet's syndrome

Vasculo-Behcet

HLA-B*51

Pathergy

Anticoagulation

Anti-TNF agents

期刊

Medicina Clinica

IF:

2.1

论文数:

513

被引数:

3.7K

机构

ctr referencia uec csur enfermedades autoinmunes s

学者数:

论文数: 1

被引数: 0

引用论文

Biologic therapy in refractory neurobehçet’s disease: a multicentre study of 41 patients and literature review 生物制剂治疗难治性神经白塞病：一项包含41例患者的多中心研究及文献综述

Rheumatology

IF0

2022-02-15

PREAI

Alba Herrero-Morant; José Luis Martín-Varillas; Santos Castañeda; Olga Maíz; Julio Sánchez; Norberto Ortego; Enrique Raya; Águeda Prior-Español; Clara Moriano; Rafael B Melero-González; Jenaro Graña-Gil; Ana Urruticoechea-Arana; Ángel Ramos-Calvo; Marta Loredo-Martínez; Eva Salgado-Pérez; Francisca Sivera; Ignacio Torre; Javier Narváez; José Luis Andreu; Olga Martínez-González; Ricardo Gómez-de la Torre; Sabela Fernández-Aguado; Susana Romero-Yuste; Íñigo González-Mazón; Carmen Álvarez-Reguera; José Luis Hernández; Miguel Ángel González-Gay; Ricardo Blanco; Ana Blanco; José Luis Callejas; Anahy Brandy-García; Alejandro Olivé; Elvira Díez; Álvaro Seijas-López; Concepción Delgado-Beltrán

Clinical and Ultrasonographic Evaluation of Lower-extremity Vein Thrombosis in Behcet Syndrome

Medicine

IF0

2015-11-01

OAAI

Emire Seyahi; Osman Serdal Cakmak; Burcin Tutar; Caner Arslan; Atilla Suleyman Dikici; Necdet Sut; Fatih Kantarci; Hasan Tuzun; Melike Melikoglu; Hasan Yazici

Clinical course of acute deep vein thrombosis of the legs in Behçet’s syndrome

Rheumatology

IF0

2019-08-29

OAAI

Yesim Ozguler; Gulen Hatemi; Firat Cetinkaya; Koray Tascilar; Vedat Hamuryudan; Serdal Ugurlu; Emire Seyahi; Hasan Yazici; Melike Melikoglu

Pathogenesis of Beh‡et's disease: autoinflammatory features and beyond

SEMINARS IN IMMUNOPATHOLOGY

IF9.2

2015-06-12

110

PREAI

Gul, Ahmet

Vascular Behcet syndrome: from pathogenesis to treatment

NATURE REVIEWS RHEUMATOLOGY

IF32.7

2022-12-21

PREAI

Bettiol, Alessandra; Alibaz-Oner, Fatma; Direskeneli, Haner; Hatemi, Gulen; Saadoun, David; Seyahi, Emire; Prisco, Domenico; Emmi, Giacomo

Apremilast for Behcet's Syndrome - A Phase 2, Placebo-Controlled Study

NEW ENGLAND JOURNAL OF MEDICINE

IF78.5

2015-04-16

188

OAAI

Hatemi, Gulen; Melikoglu, Melike; Tunc, Recep; Korkmaz, Cengiz; Ozturk, Banu Turgut; Mat, Cem; Merkel, Peter A.; Calamia, Kenneth T.; Liu, Ziqi; Pineda, Lilia; Stevens, Randall M.; Yazici, Hasan; Yazici, Yusuf

The Long-Term Mortality and Morbidity of Behçet Syndrome

Medicine

IF0

2003-01-01

OAAI

Emire Kural-Seyahi; Izzet Fresko; Nurhan Seyahi; Yilmaz Ozyazgan; Cem Mat; Vedat Hamuryudan; Sebahattin Yurdakul; Hasan Yazici

Immunosuppressants reduce venous thrombosis relapse in Behçet's disease

Arthritis & Rheumatism

IF0

2012-07-27

PREAI

A. C. Desbois; B. Wechsler; M. Resche‐Rigon; J. C. Piette; D. Le Thi Huong; Z. Amoura; F. Koskas; K. Desseaux; P. Cacoub; D. Saadoun

Criteria for Behcet's disease with reflections on all disease criteria

JOURNAL OF AUTOIMMUNITY

IF7

2014-02-01

PREAI

Yazici, Hasan; Yazici, Yusuf

The International Criteria for Behcet's Disease (ICBD): a collaborative study of 27 countries on the sensitivity and specificity of the new criteria

JOURNAL OF THE EUROPEAN ACADEMY OF DERMATOLOGY AND VENEREOLOGY

IF8

2013-02-26

1.0K

PREAI

Davatchi, F.; Assaad-Khalil, S.; Calamia, K. T.; Crook, J. E.; Sadeghi-Abdollahi, B.; Schirmer, M.; Tzellos, T.; Zouboulis, C. C.; Akhlagi, M.; Al-Dalaan, A.; Alekberova, Z. S.; Ali, A. A.; Altenburg, A.; Arromdee, E.; Baltaci, M.; Bastos, M.; Benamour, S.; Ben Ghorbel, I.; Boyvat, A.; Carvalho, L.; Chen, W.; Ben-Chetrit, E.; Chams-Davatchi, C.; Correia, J. A.; Crespo, J.; Dias, C.; Dong, Y.; Paixao-Duarte, F.; Elmuntaser, K.; Elonakov, A. V.; Grana Gil, J.; Haghdoost, A-A.; Hayani, R. M.; Houman, H.; Isayeva, A. R.; Jamshidi, A. R.; Kaklamanis, P.; Kumar, A.; Kyrgidis, A.; Madanat, W.; Nadji, A.; Namba, K.; Ohno, S.; Olivieri, I.; Vaz Patto, J.; Pipitone, N.; de Queiroz, M. V.; Ramos, F.; Resende, C.; Rosa, C. M.; Salvarani, C.; Serra, M. J.; Shahram, F.; Shams, H.; Sharquie, K. E.; Sliti-Khanfir, M.; Tribolet de Abreu, T.; Vasconcelos, C.; Vedes, J.; Wechsler, B.; Cheng, Y. K.; Zhang, Z.; Ziaei, N.

查看更多内容