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Pulmonary Hypertension in Adults with Congenital Heart Disease (ACHD) - Novel Aspects from the 7th World Symposium on Pulmonary Hypertension 2024
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DOI：10.1055/a-2625-5000.png)
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Abstract
En 中文
The number of adults with congenital heart defects (ACHD, CHD) is constantly rising, with more than 360,000 affected individuals in Germany and 50 million worldwide. Many patients with congenital heart defects (CHD) develop pulmonary hypertension (PH), often as pulmonary arterial hypertension (PAH) associated with congenital heart defects (P[A]H-CHD). P(A)H-CHD may occur early in life or develop long-term, even decades after repair, which is associated with significant morbidity and mortality. Due to the anatomical and hemodynamic complexity of CHD, PH in this population, especially among ACHD, often requires a more differentiated nuanced approach to diagnosis and treatment compared to most forms of PH. The European society of Cardiology (ESC) guidelines provide diagnostic and treatment approaches to P(A)H-CHD, but do not cover all aspects. The current contributions from the 7 th World Symposium on Pulmonary Hypertension (7 th WSPH, Barcelona 2024) provides an update of the diagnosis and an overview of the optimization of PH treatment to improve care of affected individuals, but primarily focuses on children and adolescents with CHD, while recommendations for adults with P(A)H-CHD are scarce. This article comments on specific aspects covering all contents of the 7 th WSPH, in the context of existing guidelines, as well as regarding gaps in recommendations and future perspectives from the standpoint of congenital cardiology for ACHD.
Keywords:
WSPH
pulmonary hypertension
pulmonary arterial hypertension
congenital heart disease
adult congenital heart disease
ACHD
Eisenmenger syndrome
pulmonary hypertension
pulmonary arterial hypertension
congenital heart disease
adult congenital heart disease
ACHD
Eisenmenger syndrome
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