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High-intensity immunosuppression versus modern standard care in poor-prognosis diffuse cutaneous systemic sclerosis: A propensity-matched study

delete2026-06-26
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OA
AI
L
Lucas Khellaf
R
Rémi Khellaf
P
Pierre Pinson
Y
Yannick Allanore
Z
Zahir Amoura
J
Jérôme Avouac
T
Tiphaine Goulenok
B
Bertrand Dunogué
A
Anuxcy Kanagaratnam
S
Sébastien Rivière
G
Guillaume Bussone
R
Robin Dhôte
J
Jean‐Emmanuel Kahn
O
Olivier Lidove
A
Arsène Mékinian
D
Didier Bouscary
L
Luc Mouthon
B
Benjamin Chaigne *
DOI:10.1016/j.jaut.2026.103594delete
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Abstract

Abstract

En 中文
• Five-year overall survival was similar with HI-IS/HSCT and standard care. • HI-IS/HSCT improved 5-year EFS versus modern standard care (76% vs 46%). • HI-IS/HSCT improved 5-year PFS versus standard care (82% vs 40%). • HI-IS/HSCT stabilized lung function and improved skin fibrosis at 24 months. • Older age and cardiac involvement predicted poorer outcomes after HI-IS/HSCT.

Journal

Journal of Autoimmunity cover
Journal of Autoimmunity
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7
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3.1K
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university paris cité
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A
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8
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A
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9
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2
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764
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96
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2
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M
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112
Papers: 51
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A
assistance publique-hôpitaux de paris
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208
Papers: 77
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