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Transjugular intrahepatic portosystemic shunt for variceal bleeding due to hereditary hemorrhagic telangiectasia with cirrhosis: A case report
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DOI：10.3748/wjg.v32.i12.119002.png)
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Abstract
En 中文
BACKGROUND The co-occurrence of hereditary hemorrhagic telangiectasia (HHT) and hepatitis C cirrhosis represents an exceptionally rare clinical entity, which can pose a diagnostic and therapeutic challenge. CASE SUMMARY We reported a patient with portal hypertension-induced esophageal and gastric variceal rupture due to HHT-hepatic arterioportal fistula and hepatitis C cirrhosis. Computed tomography confirmed hepatic diffuse arteriovenous fistula. Following initial embolization of arterioportal fistula, persistent gastrointestinal bleeding recurred, indicating suboptimal embolization efficacy. Subsequent transjugular intrahepatic portosystemic shunt (TIPS) treatment was performed and resulted in significant portal hypertension reduction. Endoscopic evaluation demonstrated marked improvement in esophageal and gastric varices, achieving remarkable therapeutic outcomes. CONCLUSION TIPS is an effective treatment option for esophageal and gastric variceal bleeding secondary to portal hypertension in patients with both HHT and liver cirrhosis.
Keywords:
Transjugular intrahepatic portosystemic shunt
Hereditary hemorrhagic telangiectasia
Hepatic arterioportal fistula
Portal hypertension
Variceal bleeding
Case report
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5.4
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2.1W
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5.1W
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