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SaveInterferon-γ causes myogenic cell dysfunction and senescence in immune myopathies
Hou, Cyrielle; Periou, Baptiste; Gervais, Marianne; Martin, Ludovic; Berthier, Juliette; Baba-Amer, Yasmine; Souvannanorath, Sarah; Lechapt-Zalcman, Emmanuele; Malfatti, Edoardo; Gherardi, Romain K.; Relaix, Frederic; Bencze, Maximilien; Authier, Francois-Jerome
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SaveProgressive cardiomyopathy with intercalated disc disorganization in a rat model of Becker dystrophy
Taglietti, Valentina; Kefi, Kaouthar; Mirciloglu, Busra; Bastu, Sultan; Masson, Jean-Daniel; Bronisz-Budzynska, Iwona; Gouni, Vassiliki; Ferri, Carlotta; Jorge, Alan; Gentil, Christel; Pietri-Rouxel, France; Malfatti, Edoardo; Lafuste, Peggy; Tiret, Laurent; Relaix, Frederic
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SaveReceptor interacting protein kinase-3 mediates both myopathy and cardiomyopathy in preclinical animal models of Duchenne muscular dystrophy
Bencze, Maximilien; Periou, Baptiste; Punzon, Isabel; Barthelemy, Ines; Taglietti, Valentina; Hou, Cyrielle; Zaidan, Louai; Kefi, Kaouthar; Blot, Stephane; Agbulut, Onnik; Gervais, Marianne; Derumeaux, Genevieve; Authier, Francois-Jerome; Tiret, Laurent; Relaix, Frederic
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SaveMyopathologic trajectory in Duchenne muscular dystrophy (DMD) reveals lack of regeneration due to senescence in satellite cells
Cardone, Nastasia; Taglietti, Valentina; Baratto, Serena; Kefi, Kaouthar; Periou, Baptiste; Gitiaux, Ciryl; Barnerias, Christine; Lafuste, Peggy; Pharm, France Leturcq; Pharm, Juliette Nectoux; Panicucci, Chiara; Desguerre, Isabelle; Bruno, Claudio; Authier, Francois-Jerome; Fiorillo, Chiara; Relaix, Frederic; Malfatti, Edoardo
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SaveGlucose oxidation drives trunk neural crest cell development and fate
Nekooie Marnany, Nioosha; Fodil, Redouane; Fereol, Sophie; Dady, Alwyn; Depp, Marine; Relaix, Frederic; Motterlini, Roberto; Foresti, Roberta; Duband, Jean-Loup; Dufour, Sylvie
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SaveInhibitory SMAD6 interferes with BMP-dependent generation of muscle progenitor cells and perturbs proximodistal pattern of murine limb muscles
Asfour, Hasan; Hirsinger, Estelle; Rouco, Raquel; Zarrouki, Faouzi; Hayashi, Shinichiro; Swist, Sandra; Braun, Thomas; Patel, Ketan; Relaix, Frederic; Andrey, Guillaume; Stricker, Sigmar; Duprez, Delphine; Stantzou, Amalia; Amthor, Helge
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SaveClinical and functional characterization of a long survivor congenital titinopathy patient with a novel metatranscript-only titin variant
Cardone, Nastasia; Moula, Melissa; Baelde, Rianne J.; Biquand, Ariane; Villanova, Marcello; Metay, Corinne; Fiorillo, Chiara; Baratto, Serena; Merlini, Luciano; Sabatelli, Patrizia; Romero, Norma B.; Relaix, Frederic; Authier, Francois Jerome; Taglietti, Valentina; Savarese, Marco; de Winter, Josine; Ottenheijm, Coen; Richard, Isabelle; Malfatti, Edoardo
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