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SaveInactivation of ceramide synthase 2 catalytic activity in mice affects transcription of genes involved in lipid metabolism and cell division
Bickert, Andreas; Kern, Paul; van Uelft, Martina; Herresthal, Stefanie; Ulas, Thomas; Gutbrod, Katharina; Breiden, Bernadette; Degen, Joachim; Sandhoff, Konrad; Schultze, Joachim L.; Doermann, Peter; Hartmann, Dieter; Bauer, Reinhard; Willecke, Klaus
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SaveUnbalanced lipolysis results in lipotoxicity and mitochondrial damage in peroxisome-deficient Pex19 mutants
Buelow, Margret H.; Wingen, Christian; Senyilmaz, Deniz; Gosejacob, Dominic; Sociale, Mariangela; Bauer, Reinhard; Schulze, Heike; Sandhoff, Konrad; Teleman, Aurelio A.; Hoch, Michael; Sellin, Julia
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SaveCeramide Synthase Schlank Is a Transcriptional Regulator Adapting Gene Expression to Energy Requirements
Sociale, Mariangela; Wulf, Anna-Lena; Breiden, Bernadette; Klee, Kathrin; Thielisch, Melanie; Eckardt, Franka; Sellin, Julia; Buelow, Margret H.; Loebbert, Sinah; Weinstock, Nadine; Voelzmann, Andre; Schultze, Joachim; Sandhoff, Konrad; Bauer, Reinhard
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SaveSynthetic Glycoforms Reveal Carbohydrate-Dependent Bioactivity of Human Saposin D
Graf, Christopher G. F.; Schulz, Christian; Schmaelzlein, Marina; Heinlein, Christian; Moennich, Manuel; Perkams, Lukas; Puettner, Markus; Boos, Irene; Hessefort, Markus; Sanchez, Jose Nelson Lombana; Weyand, Michael; Steegborn, Clemens; Breiden, Bernadette; Ross, Kerstin; Schwarzmann, Guenter; Sandhoff, Konrad; Unverzagt, Carlo
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SaveIdentification of a feedback loop involving β-glucosidase 2 and its product sphingosine sheds light on the molecular mechanisms in Gaucher disease
Schonauer, Sophie; Koerschen, Heinz G.; Penno, Anke; Rennhack, Andreas; Breiden, Bernadette; Sandhoff, Konrad; Gutbrod, Katharina; Dormann, Peter; Raju, Diana N.; Haberkant, Per; Gerl, Mathias J.; Bruegger, Britta; Zigdon, Hila; Vardi, Ayelet; Futerman, Anthony H.; Thiele, Christoph; Wachten, Dagmar
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SaveCharacterization of Drosophila Saposin-related mutants as a model for lysosomal sphingolipid storage diseases
Sellin, Julia; Schulze, Heike; Paradis, Marie; Gosejacob, Dominic; Papan, Cyrus; Shevchenko, Andrej; Psathaki, Olympia Ekaterina; Paululat, Achim; Thielisch, Melanie; Sandhoff, Konrad; Hoch, Michael
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SaveAccumulation of Glucosylceramide in the Absence of the Beta-Glucosidase GBA2 Alters Cytoskeletal Dynamics
Raju, Diana; Schonauer, Sophie; Hamzeh, Hussein; Flynn, Kevin C.; Bradke, Frank; Dorp, Katharina Vom; Doermann, Peter; Yildiz, Yildiz; Troetschel, Christian; Poetsch, Ansgar; Breiden, Bernadette; Sandhoff, Konrad; Koerschen, Heinz G.; Wachten, Dagmar
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