arrow
Back
K

Konrad Sandhoff

university of bonn

103H-index
2.3KPaper Count
3.6WCitation Count
Published Papers 141
Publication Date
Lysosomal Glycosphingolipid Storage Diseases
err2019-06-20
err80
PREAI
errBreiden, Bernadette; Sandhoff, Konrad
errShare
errSave
Inactivation of ceramide synthase 2 catalytic activity in mice affects transcription of genes involved in lipid metabolism and cell division
err2018-07-01
err14
PREAI
errBickert, Andreas; Kern, Paul; van Uelft, Martina; Herresthal, Stefanie; Ulas, Thomas; Gutbrod, Katharina; Breiden, Bernadette; Degen, Joachim; Sandhoff, Konrad; Schultze, Joachim L.; Doermann, Peter; Hartmann, Dieter; Bauer, Reinhard; Willecke, Klaus
errShare
errSave
Emerging concepts of ganglioside metabolism
err2018-06-16
err70
errOAAI
errSandhoff, Roger; Sandhoff, Konrad
errShare
errSave
Unbalanced lipolysis results in lipotoxicity and mitochondrial damage in peroxisome-deficient Pex19 mutants
err2018-02-15
err45
errOAAI
errBuelow, Margret H.; Wingen, Christian; Senyilmaz, Deniz; Gosejacob, Dominic; Sociale, Mariangela; Bauer, Reinhard; Schulze, Heike; Sandhoff, Konrad; Teleman, Aurelio A.; Hoch, Michael; Sellin, Julia
errShare
errSave
Ceramide Synthase Schlank Is a Transcriptional Regulator Adapting Gene Expression to Energy Requirements
err2018-01-01
err46
errOAAI
errSociale, Mariangela; Wulf, Anna-Lena; Breiden, Bernadette; Klee, Kathrin; Thielisch, Melanie; Eckardt, Franka; Sellin, Julia; Buelow, Margret H.; Loebbert, Sinah; Weinstock, Nadine; Voelzmann, Andre; Schultze, Joachim; Sandhoff, Konrad; Bauer, Reinhard
errShare
errSave
Synthetic Glycoforms Reveal Carbohydrate-Dependent Bioactivity of Human Saposin D
err2017-04-05
err24
PREAI
errGraf, Christopher G. F.; Schulz, Christian; Schmaelzlein, Marina; Heinlein, Christian; Moennich, Manuel; Perkams, Lukas; Puettner, Markus; Boos, Irene; Hessefort, Markus; Sanchez, Jose Nelson Lombana; Weyand, Michael; Steegborn, Clemens; Breiden, Bernadette; Ross, Kerstin; Schwarzmann, Guenter; Sandhoff, Konrad; Unverzagt, Carlo
errShare
errSave
Identification of a feedback loop involving β-glucosidase 2 and its product sphingosine sheds light on the molecular mechanisms in Gaucher disease
err2017-04-01
err23
errOAAI
errSchonauer, Sophie; Koerschen, Heinz G.; Penno, Anke; Rennhack, Andreas; Breiden, Bernadette; Sandhoff, Konrad; Gutbrod, Katharina; Dormann, Peter; Raju, Diana N.; Haberkant, Per; Gerl, Mathias J.; Bruegger, Britta; Zigdon, Hila; Vardi, Ayelet; Futerman, Anthony H.; Thiele, Christoph; Wachten, Dagmar
errShare
errSave
Lipids regulate the hydrolysis of membrane bound glucosylceramide by lysosomal β-glucocerebrosidase
err2017-03-01
err32
errOAAI
errAbdul-Hammed, Misbaudeen; Breiden, Bernadette; Schwarzmann, Gunter; Sandhoff, Konrad
errShare
errSave
Characterization of Drosophila Saposin-related mutants as a model for lysosomal sphingolipid storage diseases
err2017-01-01
err12
errOAAI
errSellin, Julia; Schulze, Heike; Paradis, Marie; Gosejacob, Dominic; Papan, Cyrus; Shevchenko, Andrej; Psathaki, Olympia Ekaterina; Paululat, Achim; Thielisch, Melanie; Sandhoff, Konrad; Hoch, Michael
errShare
errSave
errShare
errSave
Membrane lipids regulate ganglioside GM2 catabolism and GM2 activator protein activity
err2015-09-01
err32
errOAAI
errAnheuser, Susi; Breiden, Bernadette; Schwarzmann, Gunter; Sandhoff, Konrad
errShare
errSave
Accumulation of Glucosylceramide in the Absence of the Beta-Glucosidase GBA2 Alters Cytoskeletal Dynamics
err2015-03-24
err33
errOAAI
errRaju, Diana; Schonauer, Sophie; Hamzeh, Hussein; Flynn, Kevin C.; Bradke, Frank; Dorp, Katharina Vom; Doermann, Peter; Yildiz, Yildiz; Troetschel, Christian; Poetsch, Ansgar; Breiden, Bernadette; Sandhoff, Konrad; Koerschen, Heinz G.; Wachten, Dagmar
errShare
errSave
Partial synthesis of ganglioside and lysoganglioside lipoforms as internal standards for MS quantification
err2014-12-01
err8
errOAAI
errGantner, Martin; Schwarzmann, Guenter; Sandhoff, Konrad; Kolter, Thomas
errShare
errSave
Acid sphingomyelinase activity is regulated by membrane lipids and facilitates cholesterol transfer by NPC2
err2014-12-01
err73
errOAAI
errOninla, Vincent O.; Breiden, Bernadette; Babalola, Jonathan O.; Sandhoff, Konrad
errShare
errSave