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Amanda Urban

Frederick National Laboratory for Cancer Research

10H-index
60Paper Count
607Citation Count
Published Papers 18
Publication Date
Clinical features, genetics, treatment, and long-term outcomes of STAT3 hyper-IgE syndrome: a single-center cohort analysis.
err2026-04-28
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errAlexandra F. Freeman; Chen Wang; Amanda Urban; Iris Martin; Lauren Dang; Joie Davis; Jenna R.E. Bergerson; Sania Ali; Zixiao Annie An; Meera Patel; Hastings Williamson; Beatriz E. Marciano; Christine Lafeer; Susan Roy; Jean Ulrick; Theo Heller; Disha Sharma; Leslie Castelo-Soccio; Edward W. Cowen; Heidi H. Kong
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Obesity and hepatic steatosis in STAT3 hyper-IgE syndrome
err2025-11-04
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PREAI
errMeera Patel; Chen Wang; Amanda Urban; Iris Martin; Jean Ulrick; Susan Roy; Kirsten Zambell; Anjali Rai; David E. Kleiner; Jatin Raj Matta; Nader S. Metwalli; Ronald Ouwerkerk; Ami Makadia; Theo Heller; Ahmed M. Gharib; Alexandra F. Freeman
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A unified metric of human immune health
err2024-07-03
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errSparks, Rachel; Rachmaninoff, Nicholas; Lau, William W.; Hirsch, Dylan C.; Bansal, Neha; Martins, Andrew J.; Chen, Jinguo; Liu, Candace C.; Cheung, Foo; Failla, Laura E.; Biancotto, Angelique; Fantoni, Giovanna; Sellers, Brian A.; Chawla, Daniel G.; Howe, Katherine N.; Mostaghimi, Darius; Farmer, Rohit; Kotliarov, Yuri; Calvo, Katherine R.; Palmer, Cindy; Daub, Janine; Foruraghi, Ladan; Kreuzburg, Samantha; Treat, Jennifer D.; Urban, Amanda K.; Jones, Anne; Romeo, Tina; Deuitch, Natalie T.; Moura, Natalia Sampaio; Weinstein, Barbara; Moir, Susan; Ferrucci, Luigi; Barron, Karyl S.; Aksentijevich, Ivona; Kleinstein, Steven H.; Townsley, Danielle M.; Young, Neal S.; Frischmeyer-Guerrerio, Pamela A.; Uzel, Gulbu; Pinto-Patarroyo, Gineth Paola; Cudrici, Cornelia D.; Hoffmann, Patrycja; Stone, Deborah L.; Ombrello, Amanda K.; Freeman, Alexandra F.; Zerbe, Christa S.; Kastner, Daniel L.; Holland, Steven M.; Tsang, John S.
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Early intervention in STAT3 dominant negative disease
err2023-12-01
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errAn, Zixiao Annie; Williams, Kelli W.; Urban, Amanda; Ali, Sania; Roy, Susan; Lafeer, Christine; Heimall, Jennifer; Dimitriades, Victoria R.; Davis, Joie; Kong, Heidi H.; Cowen, Edward W.; Holland, Steven M.; Freeman, Alexandra F.
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Efficacy of Cochleated Amphotericin B in Mouse and Human Mucocutaneous Candidiasis
err2022-07-19
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errDesai, Jigar, V; Urban, Amanda; Swaim, Doris Z.; Colton, Benjamin; Kibathi, Lilian W.; Ferre, Elise M. N.; Stratton, Pamela; Merideth, Melissa A.; Hunsberger, Sally; Matkovits, Theresa; Mannino, Raphael; Holland, Steven M.; Tramont, Edmund; Lionakis, Michail S.; Freeman, Alexandra F.
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Treatment of STAT3-deficient hyper-immunoglobulin E syndrome with monoclonal antibodies targeting allergic inflammation
err2022-05-01
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PREAI
errJames, Alyssa E.; West, Laura; Schloss, Katheryn; Nataraj, Pavan; Urban, Amanda; Hirsch, Aleksandra; Krausz, Mate; Kumar, Shashi; Raasch, Jason; Risma, Kimberly; Church, Joseph A.; Grimbacher, Bodo; Bergerson, Jenna R. E.; Chong, Hey; Freeman, Alexandra F.
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Malignancy in STAT3 Deficient Hyper IgE Syndrome (vol 42, pg 699, 2022)
err2022-04-19
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errOAAI
errUrban, Amanda; Pittaluga, Stefania; Freeman, Alexandra F.
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Malignancy in STAT3 Deficient Hyper IgE Syndrome
err2022-01-21
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PREAI
errUrban, Amanda; Pittaluga, Stefania; Freeman, Alexandra F.
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Antibody responses to the SARS-CoV-2 vaccine in individuals with various inborn errors of immunity
err2021-11-01
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errDelmonte, Ottavia M.; Bergerson, Jenna R. E.; Burbelo, Peter D.; Durkee-Shock, Jessica R.; Dobbs, Kerry; Bosticardo, Marita; Keller, Michael D.; McDermott, David H.; Rao, V. Koneti; Dimitrova, Dimana; Quiros-Roldan, Eugenia; Imberti, Luisa; Ferre, Elise M. N.; Schmitt, Monica; Lafeer, Christine; Pfister, Justina; Shaw, Dawn; Draper, Deborah; Truong, Meng; Ulrick, Jean; DiMaggio, Tom; Urban, Amanda; Holland, Steven M.; Lionakis, Michail S.; Cohen, Jeffrey I.; Ricotta, Emily E.; Notarangelo, Luigi D.; Freeman, Alexandra F.
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Lupus-like autoimmunity and increased interferon response in patients with STAT3-deficient hyper-IgE syndrome
err2021-02-01
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errGoel, Rishi R.; Nakabo, Shuichiro; Dizon, Brian L. P.; Urban, Amanda; Waldman, Meryl; Howard, Lillian; Darnell, Dirk; Buhaya, Munir; Carmona-Rivera, Carmelo; Hasni, Sarfaraz; Kaplan, Mariana J.; Freeman, Alexandra F.; Gupta, Sarthak
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An Unusual Pattern of Premature Cervical Spine Degeneration in STAT3-LOF
err2021-01-06
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PREAI
errMitchell, Amelia L.; Urban, Amanda K.; Freeman, Alexandra F.; Hammoud, Dima A.
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Cryptosporidium infection in dedicator of cytokinesis 8 (DOCK 8) deficiency
err2020-11-01
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errBen Yakov, Gil; Sharma, Disha; Cho, Min H.; Shah, Nirali N.; Hickstein, Dennis; Urban, Amanda; Darnell, Dirk; Kapuria, Devika; Marko, Jamie; Kleiner, David E.; Hadigan, Colleen M.; Danielson, Jeffrey; Ham, Hyoungjun; Vittal, Anusha; Su, Helen C.; Freeman, Alexandra F.; Heller, Theo
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Spontaneous Gastrointestinal Perforations in STAT3-Deficient Hyper-IgE Syndrome
err2020-09-11
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errBhattacharya, Sumona; Williamson, Hastings; Urban, Amanda K.; Heller, Theo; Freeman, Alexandra F.
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Obstetric and Gynecological Care in Patients with STAT3-Deficient Hyper IgE Syndrome
err2020-07-21
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PREAI
errParisi, Xenia; Bergerson, Jenna; Urban, Amanda; Darnell, Dirk; Stratton, Pamela; Freeman, Alexandra F.
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Risk factors for Recurrent Stillbirth (SB): Results from the Stillbirth Collaborative Research Network (SCRN)
err2020-01-01
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errWhitham, Megan; Gammon, Elizabeth; Chronister, Briana C.; Urban, Amanda; Silver, Robert M.; Reddy, Uma M.; Dudley, Donald J.
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Stress alteres mast cell protease profiles in murine skin and allergy
err2019-10-01
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PREAI
errPeters, E. M. J.; Rommel, F. R.; Tumala, S.; Urban, A.; Siebenhaar, F.; Gieler, U.
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Obstetric and Gynecological Outcomes in Patients with STAT3-deficient Hyper IgE Syndrome
err2018-05-01
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PREAI
errChepa-Lotrea, Xenia; Urban, Amanda; Bergerson, Jenna; Weisman, Hannah; Stratton, Pamela; Freeman, Alexandra
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Endemic mycoses in patients with STAT3-mutated hyper-IgE (Job) syndrome
err2015-11-01
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errOdio, Camila D.; Milligan, Ki Lee; McGowan, Katherine; Spergel, Amanda K. Rudman; Bishop, Rachel; Boris, Lisa; Urban, Amanda; Welch, Pamela; Heller, Theo; Kleiner, David; Jackson, Mary Anne; Holland, Steven M.; Freeman, Alexandra F.
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