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Richard J. Smith

university of iowa

118H-index
1.5KPaper Count
5.7WCitation Count
Published Papers 244
Publication Date
Identification of a Novel Founder EYA4 Structural Variant in North America
err2026-08-21
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errJacquelyn K. DeVries; Miles J. Klimara; Amanda M. Odell; Diana L. Kolbe; Nicole Meyer; Paige L. Harlan; Hela Azaiez; Richard J. H. Smith
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Reduction of hematuria and albuminuria with iptacopan in C3G: findings from APPEAR-C3G study
err2025-10-01
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errFontan, Fernando Caravaca; Zhao, Minghui; Smith, Richard; Israni, Rubeen; Wang, Yaqin; Liu, Junhao; Smeets, Serge; Keefe, Deborah
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A multicenter, randomized, double-blind, placebo-controlled Phase 3 study in patients with idiopathic IC-MPGN: APPARENT protocol amendment
err2025-10-01
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PREAI
errVivarelli, Marina; Bomback, Andrew; Kavanagh, David; Liu, Junhao; Veldandi, Udaykiran; Levitch, Rafael; Lawrence, David; Liu, Chang; Keefe, Deborah; Smith, Richard
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Investigation of GSDME results in the identification of the first pathogenic synonymous variants and genotype-phenotype correlations
err2025-09-29
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errJoseph J. Chin; W. Daniel Walls; Kai Wang; Amanda M. Odell; Diana L. Kolbe; Kevin T. A. Booth; Hela Azaiez; Richard J. H. Smith
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Oral iptacopan therapy in patients with C3 glomerulopathy: a randomised, double-blind, parallel group, multicentre, placebo-controlled, phase 3 study
err2025-09-25
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errDavid Kavanagh; Andrew S Bomback; Marina Vivarelli; Carla M Nester; Giuseppe Remuzzi; Ming-Hui Zhao; Edwin K S Wong; Yaqin Wang; Induja Krishnan; Imelda Schuhmann; Angelo J Trapani; Nicholas J A Webb; Matthias Meier; Rubeen K Israni; Richard J H Smith
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Lmx1a is essential for marginal cell differentiation and stria vascularis formation
err2025-03-05
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errRenauld, Justine M.; Iskusnykh, Igor Y.; Yamoah, Ebenezer N.; Smith, Richard J. H.; Affortit, Corentin; He, David Z.; Liu, Huizhan; Nichols, David; Bouma, Judith; Nayak, Mahesh K.; Weng, Xin; Qin, Tianli; Sham, Mai Har; Chizhikov, Victor V.; Fritzsch, Bernd
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Complement is primarily activated in the lung in a mouse model of severe COVID-19
err2025-03-01
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errSzachowicz, Peter J.; Wohlford-Lenane, Christine; Donelson, Cobey J.; Ghimire, Shreya; Thurman, Andrew; Xue, Biyun; Boly, Timothy J.; Verma, Abhishek; Masinovic, Leila; Bermick, Jennifer R.; Rehman, Tayyab; Perlman, Stanley; Meyerholz, David K.; Pezzulo, Alejandro A.; Zhang, Yuzhou; Smith, Richard J. H.; McCray, Paul B.
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Acquired drivers of C3 glomerulopathy
err2025-01-27
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errWelsh, Seth J.; Zhang, Yuzhou; Smith, Richard J. H.
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Novel immunochromatographic test for rapid detection of anti-factor H autoantibodies with an assessment of its clinical relevance
err2025-01-24
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errde Cordoba, Santiago Rodriguez; Reparaz, Andrea; Sanchez, Daniel; Pinto, Sheila; Lopez, Lucia Juana; Merinero, Hector Martin; Calvete, Iria; Perez-Perez, Julian; Jellison, Sydney S.; Zhang, Yuzhou; Smith, Richard J. H.; Moreno, Inmaculada; Dominguez, Mercedes
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Outcomes from the International Society of Nephrology Hemolytic Uremic Syndromes International Forum
err2024-12-01
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errKavanagh, David; Ardissino, Gianluigi; Brocklebank, Vicky; Bouwmeester, Romy N.; Bagga, Arvind; ter Heine, Rob; Johnson, Sally; Licht, Christoph; Ma, Alison L. T.; Noris, Marina; Praga, Manuel; Rondeau, Eric; Sinha, Aditi; Smith, Richard J. H.; Sheerin, Neil S.; Trimarchi, H.; Wetzels, Jack F. M.; Vivarelli, Marina; van de Kar, Nicole C. A. J.; Greenbaum, Larry A.
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Advancing Genetic Testing in Kidney Diseases: Report From a National Kidney Foundation Working Group
err2024-12-01
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PREAI
errFranceschini, Nora; Feldman, David L.; Berg, Jonathan S.; Besse, Whitney; Chang, Alexander R.; Dahl, Neera K.; Gbadegesin, Rasheed; Pollak, Martin R.; Rasouly, Hila Milo; Smith, Richard J. H.; Winkler, Cheryl A.; Gharavi, Ali G.
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An expert discussion on the atypical hemolytic uremic syndrome nomenclature- - identifying a road map to precision: a report of a National Kidney Foundation Working Group OPEN
err2024-09-01
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errNester, Carla M.; Feldman, David L.; Burwick, Richard; Cataland, Spero; Chaturvedi, Shruti; Cook, H. Terence; Cuker, Adam; Dixon, Bradley P.; Fakhouri, Fadi; Hingorani, Sangeeta R.; Java, Anuja; Kar, Nicole C. A. J. van de; Kavanagh, David; Leung, Nelson; Licht, Christoph; Noris, Marina; O'Shaughnessy, Michelle M.; Parikh, Samir, V; Peyandi, Flora; Remuzzi, Giuseppe; Smith, Richard J. H.; Sperati, C. John; Waldman, Meryl; Walker, Patrick; Vivarelli, Marina
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The role of complement in kidney disease: conclusions from a Kidney Disease: Improving Global Outcomes (KDIGO) Controversies Conference
err2024-09-01
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errVivarelli, Marina; Barratt, Jonathan; Beck, Jr Laurence H.; Fakhouri, Fadi; Gale, Daniel P.; de Jorge, Elena Goicoechea; Mosca, Marta; Noris, Marina; Pickering, Matthew C.; Susztak, Katalin; Thurman, Joshua M.; Cheung, Michael; King, Jennifer M.; Jadoul, Michel; Winkelmayer, Wolfgang C.; Smith, Richard J. H.
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Functional evaluation of rare variants in complement factor I using a minigene assay
err2024-08-22
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errDonelson, Cobey J. H.; Borsa, Nicolo Ghiringhelli; Taylor, Amanda O.; Smith, Richard J. H.; Zhang, Yuzhou
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Force Field X: A computational microscope to study genetic variation and organic crystals using theory and experiment
err2024-07-03
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errGogal, Rose A.; Nessler, Aaron J.; Thiel, Andrew C.; Bernabe, Hernan V.; Corrigan Grove, Rae A.; Cousineau, Leah M.; Litman, Jacob M.; Miller, Jacob M.; Qi, Guowei; Speranza, Matthew J.; Tollefson, Mallory R.; Fenn, Timothy D.; Michaelson, Jacob J.; Okada, Okimasa; Piquemal, Jean-Philip; Ponder, Jay W.; Shen, Jana; Smith, Richard J. H.; Yang, Wei; Ren, Pengyu; Schnieders, Michael J.
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DEVELOPING THERAPIES FOR C3G: REPORT OF THE KIDNEY HEALTH INITIATIVE C3G TRIAL ENDPOINTS WORK GROUP
err2024-06-03
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PREAI
errNester, Carla; Decker, Dima A.; Meier, Matthias; Aslam, Shakil; Bomback, Andrew S.; Caravaca-Fontan, Fernando; Cook, Terence H.; Feldman, David L.; Fremeaux-Bacchi, Veronique; Gale, Daniel P.; Gooch, Ann; Johnson, Sally; Licht, Christoph; Mathur, Mohit; Pickering, Matthew C.; Praga, Manuel; Remuzzi, Giuseppe; Selvarajah, Viknesh; Smith, Richard J.; Tabriziani, Hossein; van de Kar, Nicole; Wang, Yaqin; Wong, Edwin; Mistry, Kirtida; Lim, Mark; Portillo, Cesia; Balogun, Seyi; Trachtman, Howard; Thompson, Aliza
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A case-based narrative review of pregnancy-associated atypical hemolytic uremic syndrome/complement-mediated thrombotic microangiopathy
err2024-05-01
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errChe, Michael; Moran, Sarah M.; Smith, Richard J.; Ren, Kevin Y. M.; Smith, Graeme N.; Shamseddin, M. Khaled; Avila-Casado, Carmen; Garland, Jocelyn S.
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Renin and renin blockade have no role in complement activity
err2024-02-01
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errZhang, Yuzhou; Martin, Bertha; Spies, M. Ashley; Roberts, Sarah M.; Nott, Joel; Goodfellow, Renee X.; Nelson, Angela F. M.; Blain, Samantha J.; Redondo, Elena; Nester, Carla M.; Smith, Richard J. H.
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Defining Nephritic Factors as Diverse Drivers of Systemic Complement Dysregulation in C3 Glomerulopathy
err2024-02-01
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errHauer, Jill J.; Zhang, Yuzhou; Goodfellow, Renee; Taylor, Amanda; Meyer, Nicole C.; Roberts, Sarah; Shao, Dingwu; Fergus, Lauren; Borsa, Nicolo Ghiringhelli; Hall, Monica; Nester, Carla M.; Smith, Richard J. H.
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Iptacopan in Idiopathic Immune Complex-Mediated Membranoproliferative Glomerulonephritis: Protocol of the APPARENT Multicenter, Randomized Phase 3 Study
err2024-01-01
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errVivarelli, Marina; Bomback, Andrew S.; Meier, Matthias; Wang, Yaqin; Webb, Nicholas J. A.; Veldandi, Uday Kiran; Smith, Richard J. H.; Kavanagh, David
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