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Leonard H. van den Berg

university medical center utrecht

90H-index
447Paper Count
3.0WCitation Count
Published Papers 187
Publication Date
Feasibility and sensitivity of a multimodal digital endpoint panel for amyotrophic lateral sclerosis: a prospective cohort study
err2026-07-06
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errLianne C.M. Botman; Jordi W.J. van Unnik; Anita Beelen; Jaap N.E. Bakers; Nina D. van der Schoot; Manon A.P. Gremmen; Sybel van Helm; Leonard H. van den Berg; Ruben P.A. van Eijk
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Clinical drug development in amyotrophic lateral sclerosis: industry-reported challenges and opportunities
err2026-05-20
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errFamke S. Cosijn; Jordi W.J. van Unnik; Lieza G. Exalto; Larah N. de Groot; Daphne N. Weemering; Rene C. van Rijssen; Roel G. Vink; Leonard H. van den Berg; Ruben P.A. van Eijk
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Associations of cognitive and behavioural impairment in ALS with brain pathology: pTDP-43 versus microglial activation
err2026-05-15
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errHanneke M. J. Slaghekke; Rosanne Govaarts; Lucia Mesarosova; Angelika Mühlebner; Emma Beeldman; Marianne de Visser; Michael A. van Es; Leonard H. van den Berg; Anneke J. van der Kooi; Yolande A. L. Pijnenburg; Eleonora Aronica; Joost Raaphorst
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Serum small non-coding RNA define molecular subtypes in amyotrophic lateral sclerosis
err2025-11-01
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errSharada Baindoor; Hesham A. Y. Gibriel; Lindy Kool; Junyi Su; Koen C. Demaegd; Morten T. Venø; Leonard H. Van Den Berg; Jørgen Kjems; Michael A. Van Es; Jochen H. M. Prehn
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Prodromal symptoms in amyotrophic lateral sclerosis from the perspective of the patient and of the caregiver
err2025-10-25
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errIris F. van Wijk; Lisa Kraneburg; Ruben P. A. van Eijk; Jan H. Veldink; Michael A. van Es; Henk-Jan Westeneng; Leonard H. van den Berg
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Patterns of altered in vivo brain metabolism in patients with amyotrophic lateral sclerosis (ALS) and asymptomatic C9orf72 mutation carriers: a cross-sectional 1H and 31P magnetic resonance spectroscopic 7T imaging study
err2025-10-15
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errHenk-Jan Westeneng; Abram D. Nitert; Kevin van Veenhuijzen; Carrie Wismans; Graziella Donatelli; Harold H.G. Tan; Wytse van Hoek; Michael A. van Es; Dennis W.J. Klomp; Alex A. Bhogal; Jan H. Veldink; Jannie P. Wijnen; Leonard H. van den Berg
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On the Two-Step Hybrid Design for Augmenting Randomized Trials Using Real-World Data
err2025-10-01
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errXu, Jiapeng; van Eijk, Ruben P. A.; Ellis, Alicia; Pan, Tianyu; Nelson, Lorene M.; Roes, Kit C. B.; van Dijk, Marc; Sarno, Maria; van den Berg, Leonard H.; Tian, Lu; Lu, Ying
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Altered EEG Response of the Parietal Network in Asymptomatic C9orf72 Carriers
err2025-07-25
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errStefan Dukic; Kevin van Veenhuijzen; Henk-Jan Westeneng; Roisin McMackin; Ruben P. A. van Eijk; Boudewijn T. H. M. Sleutjes; Bahman Nasseroleslami; Orla Hardiman; Leonard H. van den Berg
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Neuropsychological assessment practices in PRECISION-ALS: challenges and opportunities for harmonization
err2025-07-21
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errEmmet Costello; Joke De Vocht; Emily Beswick; Éanna Mac Domhnaill; Colm Peelo; Juliette Foucher; Emily J. Mayberry; Theresa Chiwera; Fenna Hiemstra; Alejandro Caravaca Puchades; Barbara Iazzolino; Francesca Palumbo; Inês Alves; Elisabeth Kasper; Miriam Galvin; Mark Heverin; Caroline Ingre; Christopher J. Mcdermott; Pamela Shaw; Ammar Al-Chalabi; Leonard H. Van Den Berg; Mónica Povedano Panadés; Adriano Chiò; Mamede De Carvalho; Sofiane Bencheikh; Philippe Corcia; Mohammed Mouzouri; Andreas Hermann; Sharon Abrahams; Niall Pender; Philip Van Damme; Orla Hardiman
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Natural history of the revised ALS functional rating scale and its association with survival: the PRECISION-ALS Extant Study
err2025-05-06
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PREAI
errvan Eijk, Ruben P. A.; Weemering, Daphne N.; Opie-Martin, Sarah; van Unnik, Jordi W. J.; Caravaca Puchades, Alejandro; Chio, Adriano; Corcia, Philippe; Galvin, Miriam; Hardiman, Orla; Heverin, Mark; Hobin, Frederik; Holmdahl, Oskar; Ingre, Caroline; Lamaire, Nikita; Mac Domhnaill, Eanna; Mcdonough, Harry; Manera, Umberto; Mcdermott, Christopher J.; Mcfarlane, Robert; Mouzouri, Mohammed; Ombelet, Fouke; Povedano Panades, Monica; Sennfalt, Stefan; Shaw, Pamela J.; Terrafeta Pastor, Cristina; Van Damme, Philip; Vasta, Rosario; Veldink, Jan H.; Al-Chalabi, Ammar; van den Berg, Leonard H.
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Mapping the natural history of amyotrophic lateral sclerosis: time-to-event analysis of clinical milestones in the pan-European, population-based PRECISION-ALS cohort
err2025-05-06
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errCaravaca Puchades, Alejandro; McDonough, Harry E.; Al-Chalabi, Ammar; Chio, Adriano; Corcia, Philippe; Galvin, Miriam; Hardiman, Orla; Heverin, Mark; Hobin, Frederik; Holmdahl, Oskar; Ingre, Caroline; Lamaire, Nikita; Mac Domhnaill, Eanna; Manera, Umberto; Mcfarlane, Robert; Mouzouri, Mohammed; Ombelet, Fouke; Opie-Martin, Sarah; Sennfaelt, Stefan; Terrafeta Pastor, Cristina; Veldink, Jan H.; Van Damme, Philip; van den Berg, Leonard; van Eijk, Ruben P. A.; Vasta, Rosario; Weemering, Daphne N.; Shaw, Pamela; McDermott, Christopher J.; Povedano Panades, Monica
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An open-label Phase 2a study to assess the safety and tolerability of trimetazidine in patients with amyotrophic lateral sclerosis
err2025-02-08
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errvan Eijk, Ruben P. A.; Steyn, Frederik J.; van Mantgem, Mark R. Janse; Schmidt, Angela; Meyjes, Myrte; Allen, Sally; Daygon, Dara, V; Loeffler, Jean-Philippe; Al-Chalabi, Ammar; van den Berg, Leonard H.; Henderson, Robert D.; Ngo, Shyuan T.
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Diagnostic Accuracy of Median Nerve Cross-Sectional Area in Suspected Amyotrophic Lateral Sclerosis
err2025-01-20
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errGarcia, Diederik J. L. Stikvoort; van den Berg, Leonard H.; Sleutjes, Boudewijn T. H. M.; Goedee, H. Stephan
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Neuroimaging correlates of domain-specific cognitive deficits in amyotrophic lateral sclerosis
err2025-01-01
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errTan, Harold H. G.; Nitert, Abram D.; van Veenhuijzen, Kevin; Dukic, Stefan; Zandvoort, Martine J. E. van; Hendrikse, Jeroen; Es, Michael A. van; Veldink, Jan H.; Westeneng, Henk-Jan; Berg, Leonard H. van den
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Molecular pathology, developmental changes and synaptic dysfunction in (pre-) symptomatic human C9ORF72-ALS/FTD cerebral organoids
err2024-09-18
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errvan der Geest, Astrid T.; Jakobs, Channa E.; Ljubikj, Tijana; Huffels, Christiaan F. M.; Luna, Marta Canizares; de Sa, Renata Vieira; Adolfs, Youri; de Wit, Marina; Rutten, Daan H.; Kaal, Marthe; Zwartkruis, Maria M.; Carcole, Mireia; Groen, Ewout J. N.; Hol, Elly M.; Basak, Onur; Isaacs, Adrian M.; Westeneng, Henk-Jan; van den Berg, Leonard H.; Veldink, Jan H.; Schlegel, Domino K.; Pasterkamp, R. Jeroen
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Mutations in the tail and rod domains of the neurofilament heavy-chain gene increase the risk of ALS
err2024-05-22
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errMarriott, Heather; Spargo, Thomas P.; Al Khleifat, Ahmad; Andersen, Peter M.; Basak, Nazli A.; Cooper-Knock, Johnathan; Corcia, Philippe; Couratier, Philippe; de Carvalho, Mamede; Drory, Vivian; Gotkine, Marc; Landers, John E.; McLaughlin, Russell; Pardina, Jesus S. Mora; Morrison, Karen E.; Pinto, Susana; Shaw, Christopher E.; Shaw, Pamela J.; Silani, Vincenzo; Ticozzi, Nicola; van Damme, Philip; van den Berg, Leonard H.; Vourc'h, Patrick; Weber, Markus; Veldink, Jan H.; Dobson, Richard J.; Schwab, Patrick; Al-Chalabi, Ammar; Iacoangeli, Alfredo
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Revisiting distinct nerve excitability patterns in patients with amyotrophic lateral sclerosis
errBRAIN
IF11.7
err2024-04-25
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errGarcia, Diederik J. L. Stikvoort; Goedee, H. Stephan; van Eijk, Ruben P. A.; van Schelven, Leonard J.; van den Berg, Leonard H.; Sleutjes, Boudewijn T. H. M.
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IgM anti-GM2 antibodies in patients with multifocal motor neuropathy target Schwann cells and are associated with early onset
err2024-04-17
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errBudding, Kevin; Bos, Jeroen W.; Dijkxhoorn, Kim; de Zeeuw, Elisabeth; Bloemenkamp, Lauri M.; Zekveld, Eva M.; Groen, Ewout J. N.; Jacobs, Bart C.; Huizinga, Ruth; Goedee, H. Stephan; Cats, Elisabeth A.; Leusen, Jeanette H. W.; van den Berg, Leonard H.; Hack, C. Erik; van der Pol, W. Ludo
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A 21-bp deletion in the complement regulator CD55 promotor region is associated with multifocal motor neuropathy and its disease course
err2024-03-25
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errBos, Jeroen W.; Groen, Ewout J. N.; Otten, Henny G.; Budding, Kevin; van Eijk, Ruben P. A.; Curial, Chantall; Kardol-Hoefnagel, Tineke; Goedee, H. Stephan; van den Berg, Leonard H.; van Der Pol, W. Ludo
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Development of a Rasch-Built Amyotrophic Lateral Sclerosis Impairment Multidomain Scale to Measure Disease Progression in ALS
err2023-08-08
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errde Jongh, Adriaan D.; van Eijk, Ruben; Bakker, Leonhard A.; Bunte, Tommy M.; Beelen, Anita; van der Meijden, Conny; van Es, Michael A.; Visser-Meily, Johanna; Kruitwagen, Esther T.; Veldink, Jan H.; van den Berg, Leonard H.
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