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SaveThe Phenotypic Spectrum of Sporadic Creutzfeldt-Jakob Disease Cortical Subtype
Baiardi, Simone; Vargiu, Claudia Marina; Appleby, Brian S.; Barria, Marcelo; Bentivenga, Giuseppe Mario; Cali, Ignazio; Carla, Benedetta; Cohen, Mark; Giese, Armin; Herms, Jochen; Kortelainen, Aino-minerva; Ladogana, Anna; Mammana, Angela; Ritchie, Diane; Windl, Otto; Capellari, Sabina; Parchi, Piero
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SaveCase report: Atypical young case of MV1 Creutzfeldt-Jakob disease with unusually long survival
Ahn, Lucie Yeongran; Cohen, Mark L.; Cali, Ignazio; Russell, Tia; Ludwig, Jessica; Jia, Xun; Bizzi, Alberto; Schonberger, Lawrence B.; Maddox, Ryan A.; Paul, Rohini; Ghazarian, Tania C.; Garcha, Jaspreet; Hammoudi, Mostafa; Appleby, Brian Stephen
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SaveEfficient transmission of human prion diseases to a glycan-free prion protein-expressing host
Cracco, Laura; Cali, Ignazio; Cohen, Mark L.; Aslam, Rabail; Notari, Silvio; Kong, Qingzhong; Newell, Kathy L.; Ghetti, Bernardino; Appleby, Brian S.; Gambetti, Pierluigi
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SaveA novel subtype of sporadic Creutzfeldt-Jakob disease with PRNP codon 129MM genotype and PrP plaques (May, 10.1007/s00401-023-02581-1, 2023)
Bayazid, Rabeah; Orru, Christina; Aslam, Rabail; Cohen, Yvonne; Silva-Rohwer, Amelia; Lee, Seong-Ki; Occhipinti, Rossana; Kong, Qingzhong; Shetty, Shashirekha; Cohen, Mark L.; Caughey, Byron; Schonberger, Lawrence B.; Appleby, Brian S.; Cali, Ignazio
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SaveA novel subtype of sporadic Creutzfeldt-Jakob disease with PRNP codon 129MM genotype and PrP plaques
Bayazid, Rabeah; Orru', Christina; Aslam, Rabail; Cohen, Yvonne; Silva-Rohwer, Amelia; Lee, Seong-Ki; Occhipinti, Rossana; Kong, Qingzhong; Shetty, Shashirekha; Cohen, Mark L.; Caughey, Byron; Schonberger, Lawrence B.; Appleby, Brian S.; Cali, Ignazio
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SaveGeneration of human chronic wasting disease in transgenic mice
Wang, Zerui; Qin, Kefeng; Camacho, Manuel V.; Cali, Ignazio; Yuan, Jue; Shen, Pingping; Greenlee, Justin; Kong, Qingzhong; Mastrianni, James A.; Zou, Wen-Quan
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SaveCharacterization of Prion Disease Associated with a Two-Octapeptide Repeat Insertion
Brennecke, Nicholas; Cali, Ignazio; Mok, Tze How; Speedy, Helen; Hosszu, Laszlo L. P.; Stehmann, Christiane; Cracco, Laura; Puoti, Gianfranco; Prior, Thomas W.; Cohen, Mark L.; Collins, Steven J.; Mead, Simon; Appleby, Brian S.
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SavePhenotypic diversity of genetic Creutzfeldt-Jakob disease: a histo-molecular-based classification
Baiardi, Simone; Rossi, Marcello; Mammana, Angela; Appleby, Brian S.; Barria, Marcelo A.; Cali, Ignazio; Gambetti, Pierluigi; Gelpi, Ellen; Giese, Armin; Ghetti, Bernardino; Herms, Jochen; Ladogana, Anna; Mikol, Jacqueline; Pal, Suvankar; Ritchie, Diane L.; Ruf, Viktoria; Windl, Otto; Capellari, Sabina; Parchi, Piero
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SaveTwo distinct conformers of PrPD type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo
Cali, Ignazio; Espinosa, Juan Carlos; Nemani, Satish K.; Marin-Moreno, Alba; Camacho, Manuel V.; Aslam, Rabail; Kitamoto, Tetsuyuki; Appleby, Brian S.; Torres, Juan Maria; Gambetti, Pierluigi
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SaveA novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease
Nemani, Satish K.; Xiao, Xiangzhu; Cali, Ignazio; Cracco, Laura; Puoti, Gianfranco; Nigro, Massimiliano; Lavrich, Jody; Bharara Singh, Anuradha; Appleby, Brian S.; Sim, Valerie L.; Notari, Silvio; Surewicz, Witold K.; Gambetti, Pierluigi
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SaveCo-existence of PrPD types 1 and 2 in sporadic Creutzfeldt-Jakob disease of the VV subgroup: phenotypic and prion protein characteristics
Cali, Ignazio; Puoti, Gianfranco; Smucny, Jason; Curtiss, Paul Michael; Cracco, Laura; Kitamoto, Tetsuyuki; Occhipinti, Rossana; Cohen, Mark Lloyd; Appleby, Brian Stephen; Gambetti, Pierluigi
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SavePMCA-replicated PrPD in urine of vCJD patients maintains infectivity and strain characteristics of brain PrPD: Transmission study
Cali, Ignazio; Lavrich, Jody; Moda, Fabio; Kofskey, Diane; Nemani, Satish Kumar; Appleby, Brian; Tagliavini, Fabrizio; Soto, Claudio; Gambetti, Pierluigi; Notari, Silvio
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SaveVariable Protease-Sensitive Prionopathy Transmission to Bank Voles
Nonno, Romolo; Notari, Silvio; Di Bari, Michele Angelo; Cali, Ignazio; Pirisinu, Laura; d'Agostino, Claudia; Cracco, Laura; Kofskey, Diane; Vanni, Ilaria; Lavrich, Jody; Parchi, Piero; Agrimi, Umberto; Gambetti, Pierluigi
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