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Ignazio Calì

case western reserve university

28H-index
61Paper Count
2.6KCitation Count
Published Papers 41
Publication Date
Understanding the Phenotypic Heterogeneity Within the Sporadic Creutzfeldt–Jakob Disease MV1 Subtype
err2026-05-05
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errSatish K. Nemani; Leonardo M. Cortez; Jennifer Myskiw; Ignazio Cali; Stephanie A. Booth; Gerard H. Jansen; Valerie L. Sim
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Genetic Creutzfeldt-Jakob disease linked to the E200K mutation: a large cohort study
err2026-01-13
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errBrian S. Appleby; Matteo Manca; Megan S. Piazza; Travis D. Kerr; Antonio Cornacchia; Alberto Bizzi; Allison Kraus; Mark L. Cohen; Ignazio Cali
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The Phenotypic Spectrum of Sporadic Creutzfeldt-Jakob Disease Cortical Subtype
err2025-12-01
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errBaiardi, Simone; Vargiu, Claudia Marina; Appleby, Brian S.; Barria, Marcelo; Bentivenga, Giuseppe Mario; Cali, Ignazio; Carla, Benedetta; Cohen, Mark; Giese, Armin; Herms, Jochen; Kortelainen, Aino-minerva; Ladogana, Anna; Mammana, Angela; Ritchie, Diane; Windl, Otto; Capellari, Sabina; Parchi, Piero
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Case report: Atypical young case of MV1 Creutzfeldt-Jakob disease with unusually long survival
err2025-01-03
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errAhn, Lucie Yeongran; Cohen, Mark L.; Cali, Ignazio; Russell, Tia; Ludwig, Jessica; Jia, Xun; Bizzi, Alberto; Schonberger, Lawrence B.; Maddox, Ryan A.; Paul, Rohini; Ghazarian, Tania C.; Garcha, Jaspreet; Hammoudi, Mostafa; Appleby, Brian Stephen
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Efficient transmission of human prion diseases to a glycan-free prion protein-expressing host
errBRAIN
IF11.7
err2023-11-24
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errCracco, Laura; Cali, Ignazio; Cohen, Mark L.; Aslam, Rabail; Notari, Silvio; Kong, Qingzhong; Newell, Kathy L.; Ghetti, Bernardino; Appleby, Brian S.; Gambetti, Pierluigi
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Novel histotypes of sporadic Creutzfeldt-Jakob disease linked to 129MV genotype
err2023-08-31
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errCracco, Laura; Puoti, Gianfranco; Cornacchia, Antonio; Glisic, Katie; Lee, Seong-Ki; Wang, Zerui; Cohen, Mark L.; Appleby, Brian S.; Cali, Ignazio
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A novel subtype of sporadic Creutzfeldt-Jakob disease with PRNP codon 129MM genotype and PrP plaques (May, 10.1007/s00401-023-02581-1, 2023)
err2023-05-30
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errBayazid, Rabeah; Orru, Christina; Aslam, Rabail; Cohen, Yvonne; Silva-Rohwer, Amelia; Lee, Seong-Ki; Occhipinti, Rossana; Kong, Qingzhong; Shetty, Shashirekha; Cohen, Mark L.; Caughey, Byron; Schonberger, Lawrence B.; Appleby, Brian S.; Cali, Ignazio
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A novel subtype of sporadic Creutzfeldt-Jakob disease with PRNP codon 129MM genotype and PrP plaques
err2023-05-08
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errBayazid, Rabeah; Orru', Christina; Aslam, Rabail; Cohen, Yvonne; Silva-Rohwer, Amelia; Lee, Seong-Ki; Occhipinti, Rossana; Kong, Qingzhong; Shetty, Shashirekha; Cohen, Mark L.; Caughey, Byron; Schonberger, Lawrence B.; Appleby, Brian S.; Cali, Ignazio
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A comprehensive study of E200K genetic Creutzfeldt Jakob disease cases; effects of codon 129 polymorphism
err2022-03-01
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errKeinath, Melissa; Cali, Ignazio; Piazza, Megan; Cohen, Mark; Tatsuoka, Curtis; Prior, Thomas; Appleby, Brian; Shetty, Shashirekha
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Sporadic Creutzfeldt-Jakob Disease in a Very Young Person
err2021-10-26
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errAppleby, Brian Stephen; Maddox, Ryan; Schonberger, Lawrence B.; Cali, Ignazio; Hammett, Teresa; Cohen, Mark; Belay, Ermias
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Generation of human chronic wasting disease in transgenic mice
err2021-09-26
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errWang, Zerui; Qin, Kefeng; Camacho, Manuel V.; Cali, Ignazio; Yuan, Jue; Shen, Pingping; Greenlee, Justin; Kong, Qingzhong; Mastrianni, James A.; Zou, Wen-Quan
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Characterization of Prion Disease Associated with a Two-Octapeptide Repeat Insertion
err2021-09-08
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errBrennecke, Nicholas; Cali, Ignazio; Mok, Tze How; Speedy, Helen; Hosszu, Laszlo L. P.; Stehmann, Christiane; Cracco, Laura; Puoti, Gianfranco; Prior, Thomas W.; Cohen, Mark L.; Collins, Steven J.; Mead, Simon; Appleby, Brian S.
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Phenotypic diversity of genetic Creutzfeldt-Jakob disease: a histo-molecular-based classification
err2021-07-29
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errBaiardi, Simone; Rossi, Marcello; Mammana, Angela; Appleby, Brian S.; Barria, Marcelo A.; Cali, Ignazio; Gambetti, Pierluigi; Gelpi, Ellen; Giese, Armin; Ghetti, Bernardino; Herms, Jochen; Ladogana, Anna; Mikol, Jacqueline; Pal, Suvankar; Ritchie, Diane L.; Ruf, Viktoria; Windl, Otto; Capellari, Sabina; Parchi, Piero
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Two distinct conformers of PrPD type 1 of sporadic Creutzfeldt-Jakob disease with codon 129VV genotype faithfully propagate in vivo
err2021-03-25
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errCali, Ignazio; Espinosa, Juan Carlos; Nemani, Satish K.; Marin-Moreno, Alba; Camacho, Manuel V.; Aslam, Rabail; Kitamoto, Tetsuyuki; Appleby, Brian S.; Torres, Juan Maria; Gambetti, Pierluigi
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Case Report: Histopathology and Prion Protein Molecular Properties in Inherited Prion Disease With aDe NovoSeven-Octapeptide Repeat Insertion
err2020-07-08
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errCali, Ignazio; Cracco, Laura; Saracino, Dario; Occhipinti, Rossana; Coppola, Cinzia; Appleby, Brian Stephen; Puoti, Gianfranco
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A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease
err2020-06-19
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errNemani, Satish K.; Xiao, Xiangzhu; Cali, Ignazio; Cracco, Laura; Puoti, Gianfranco; Nigro, Massimiliano; Lavrich, Jody; Bharara Singh, Anuradha; Appleby, Brian S.; Sim, Valerie L.; Notari, Silvio; Surewicz, Witold K.; Gambetti, Pierluigi
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Co-existence of PrPD types 1 and 2 in sporadic Creutzfeldt-Jakob disease of the VV subgroup: phenotypic and prion protein characteristics
err2020-01-30
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errCali, Ignazio; Puoti, Gianfranco; Smucny, Jason; Curtiss, Paul Michael; Cracco, Laura; Kitamoto, Tetsuyuki; Occhipinti, Rossana; Cohen, Mark Lloyd; Appleby, Brian Stephen; Gambetti, Pierluigi
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Gerstmann-Straussler-Scheinker disease revisited: accumulation of covalently-linked multimers of internal prion protein fragments
err2019-05-29
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errCracco, Laura; Xiao, Xiangzhu; Nemani, Satish K.; Lavrich, Jody; Cali, Ignazio; Ghetti, Bernardino; Notari, Silvio; Surewicz, Witold K.; Gambetti, Pierluigi
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PMCA-replicated PrPD in urine of vCJD patients maintains infectivity and strain characteristics of brain PrPD: Transmission study
err2019-03-26
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errCali, Ignazio; Lavrich, Jody; Moda, Fabio; Kofskey, Diane; Nemani, Satish Kumar; Appleby, Brian; Tagliavini, Fabrizio; Soto, Claudio; Gambetti, Pierluigi; Notari, Silvio
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Variable Protease-Sensitive Prionopathy Transmission to Bank Voles
err2019-01-01
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errNonno, Romolo; Notari, Silvio; Di Bari, Michele Angelo; Cali, Ignazio; Pirisinu, Laura; d'Agostino, Claudia; Cracco, Laura; Kofskey, Diane; Vanni, Ilaria; Lavrich, Jody; Parchi, Piero; Agrimi, Umberto; Gambetti, Pierluigi
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