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Moaçir Wajner

universidade federal do rio grande do sul

60H-index
742Paper Count
1.5WCitation Count
Published Papers 236
Publication Date
L-Carnitine Prevents Lipopolysaccharide-Induced Inflammatory Response, Microglia Activation and Neuronal Damage in Cerebral Cortex, as Well as Neuromotor Development Delay in Neonatal Glutaryl-CoA Dehydrogenase Deficient (Gcdh−/−) Mice
err2026-09-21
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errEdiandra Tissot Castro; Ângela Zanatta; Rafael Teixeira Ribeiro; Diorlon Nunes Machado; Andrey Vinicios Soares Carvalho; Ângela Beatris Zemniaçak; Sâmela de Azevedo Cunha; Tailine Quevedo Tavares; Manuela Bianchin Marcuzzo; Larissa Daniele Bobermin; Carlos Alexandre Netto; Alexandre Umpierrez Amaral; Carmen Regla Vargas; Guilhian Leipnitz; Moacir Wajner
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L-carnitine modulates molecular responses associated with inflammation, endoplasmic reticulum stress, and neurotrophic signaling in cerebral cortex of neonatal Gcdh−/− mice exposed to glutaric and quinolinic acids
err2026-09-05
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errEdiandra Tissot Castro; Ângela Zanatta; Andrey Vinicios Soares Carvalho; Amanda Uggeri de Moraes; Carlos Alexandre Netto; Guilhian Leipnitz; Alexandre Umpierrez Amaral; Carmen Regla Vargas; Rafael Teixeira Ribeiro; Moacir Wajner
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Renal tubular injury and inflammation in patients with methylmalonic and propionic acidemias: the role of β2-microglobulin
err2026-09-01
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PREAI
errdos Reis, Bianca Gomes; Becker, Graziela Schmitt; Marchetti, Desiree Padilha; Wailer, Luiza Rodrigues; Clarindo, Isabelle; Tedesco, Luisa; Lopes, Franciele Fatima; Wajner, Moacir; Vargas, Carmen Regla
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Mitochondria-targeted reactive species scavenger JP4-039 protects against disturbances of redox homeostasis, mitochondrial quality control, and glucose metabolism in brains of glutaryl-CoA dehydrogenase-deficient mice: A potential new therapeutic strategy for glutaric acidemia type 1
err2026-07-24
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PREAI
errRenata de Britto; Leonardo de Moura Alvorcem; Manuela Bianchin Marcuzzo; Rafael T. Ribeiro; Carolina Soares; Adriana Fernanda K. Vizuete; Larissa D. Bobermin; Gianina Teribele Venturin; Samuel Greggio; Eduardo R. Zimmer; André Quincozes-Santos; Diogo Onofre de Souza; Carlos-Alberto Gonçalves; Peter Wipf; Jerry Vockley; Bianca Seminotti; Moacir Wajner; Guilhian Leipnitz
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Ethylmalonic and Methylsuccinic Acids Disrupt Bioenergetics and Induce Mitochondrial Permeability Transition Through Thiol Redox Modulation in Rat Striatum: Potential Mechanisms Involved in Ethylmalonic Encephalopathy
err2026-05-27
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errManuela Bianchin Marcuzzo; Ângela Beatris Zemniaçak; Jaqueline Santana da Rosa; Bianca Silveira Signorini Verdi; Maria Paula Dalla Vechia Benati; Josyane de Andrade Silveira; Juliana Gomes do Nascimento; Helena de Almeida Moreira; Mateus Dias-Oliveira; Diogo Onofre Souza; Alexandre Umpierrez Amaral; Geancarlo Zanatta; Moacir Wajner; Guilhian Leipnitz
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Deleterious in vitro effects of ammonia and accumulated urea cycle amino acids on leukocyte DNA: assessment of the antioxidant effects of N-acetylcysteine and L-carnitine
err2026-05-22
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PREAI
errFranciele Fátima Lopes; Jéssica Lamberty Faverzani; Bianca Gomes dos Reis; Ana Kalise Böttcher; Luisa Maria Bosquetti Tedesco; Stefani Altenhofen; Laura Smolski dos Santos; Gênifer Erminda Schreiner; Vanusa Manfredini; Moacir Wajner; Carmen Regla Vargas
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Nitrosative Stress Mediates Disruption of Redox Homeostasis and Oxidative Phosphorylation Caused by 3-Hydroxyisobutyric Acid in Cerebral Cortex of Developing Rats
err2025-12-20
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PREAI
errRafael Teixeira Ribeiro; Rafael Palavro; Ângela Beatris Zeminiaçak; Ângela Zanatta; Ediandra Tissot Castro; Sâmela de Azevedo Cunha Cunha ; Tailine Quevedo Tavares; Alexandre Umpierrez Amaral; Guilhian Leipnitz; Moacir Wajner
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Neuroprotective, antioxidant and anti-inflammatory effect of carnitine in patients with Maple syrup urine disease: branched-chain amino acids and branched-chain keto acids levels
err2025-11-15
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PREAI
errJúlia Girardi; Jéssica Lamberty Faverzani; Franciele Fátima Lopes; Angela Sitta; Daniella de Moura Coelho; Luísa Maria Bosquetti Tedesco; Natacha Dornelles; Moacir Wajner; Carmen Regla Vargas
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Nitisinone treatment protect hereditary tyrosinemia type I patients against inflammation, DNA and protein oxidative damage by decreasing succinylacetone levels
err2025-09-26
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PREAI
errRoberta Barbizan Mascarello; Jéssica Lamberty Faverzani; Franciele Fátima Lopes; Luísa Maria Bosquetti Tedesco; Ana Kalise Böttcher; Moacir Wajner; Carmen Regla Vargas
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Intracerebral Administration of Hydrogen Sulfide Impairs Bioenergetics, Redox Status and Mitochondrial Quality Control in Rat Striatum
err2025-09-20
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PREAI
errManuela Bianchin Marcuzzo; Josyane de Andrade Silveira; Camila Vieira Pinheiro; Jaqueline Santana da Rosa; Angela B. Zemniaçak; Morgana Brondani; Nathalia Simon Kist; Chrístofer Ian Hernandez Hoffmann; Helgi B. Schioth; Alexandre U. Amaral; Moacir Wajner; Guilhian Leipnitz
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Maternal lactoferrin supplementation prevents mitochondrial and redox homeostasis dysfunction, and improves antioxidant defenses through Nrf2 and UCP2 signaling after neonatal hypoxia-ischemia
err2025-04-01
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PREAI
errCarvalho, Andrey Vinicios S.; Sanches, Eduardo F.; Ribeiro, Rafael T.; Duran-Carabali, Luz Elena; Ramires Junior, Osmar; Muniz, Bruna Dutra; Wajner, Moacir; Wyse, Angela T.; Netto, Carlos Alexandre; Sizonenko, Stephane V.
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Neuroprotective effects of L-carnitine towards oxidative stress and inflammatory processes: a review of its importance as a therapeutic drug in some disorders
err2025-02-15
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PREAI
errGuerreiro, Gilian; Deon, Marion; Becker, Graziela Schmitt; dos Reis, Bianca Gomes; Wajner, Moacir; Vargas, Carmen Regla
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L-carnitine protects against oxidative damage and neuroinflammation in cerebral cortex of rats submitted to chronic chemically-induced model of hyperphenylalaninemia
err2025-01-18
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PREAI
errFaverzani, Jessica Lamberty; Guerreiro, Gilian; Lopes, Franciele Fatima; Sitta, Angela; Coelho, Daniella de Moura; Mescka, Caroline Paula; Sehn, Luisa Degrandi; Rosa, Gabriel de Lima; de Lima, Amanda Muliterno Domingues Lourenco; Gonzalez, Esteban Alberto; Ribeiro, Rafael Teixeira; Palavro, Rafael; Coitinho, Adriana Simon; Baldo, Guilherme; Wajner, Moacir; Vargas, Carmen Regla
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α-Ketoisocaproic Acid Disrupts Mitochondrial Bioenergetics in the Brain of Neonate Rats: Molecular Modeling Studies of α-ketoglutarate Dehydrogenase Subunits Inhibition
err2025-01-09
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PREAI
errZemniacak, angela Beatris; Ribeiro, Rafael Teixeira; das Neves, Gustavo Machado; Cunha, Samela de Azevedo; Tavares, Tailine Quevedo; Carvalho, Andrey Vinicios Soares; Netto, Carlos Alexandre; Castilho, Roger Frigerio; Wajner, Moacir; Amaral, Alexandre Umpierrez
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Protective effects of the PPAR agonist bezafibrate against disruption of redox and energy homeostasis, neuronal death, astroglial reactivity, and neuroinflammation induced in vivo by D-2-hydroxyglutaric acid in rat brain
err2025-01-01
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PREAI
errRibeiro, Rafael Teixeira; Marcuzzo, Manuela Bianchin; Carvalho, Andrey Vinicios Soares; Palavro, Rafael; Castro, Ediandra Tissot; Pinheiro, Camila Vieira; Bobermin, Larissa Daniele; Amaral, Alexandre Umpierrez; Leipnitz, Guilhian; Netto, Carlos Alexandre; Wajner, Moacir
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Increased ROS levels, antioxidant defense disturbances and bioenergetic disruption induced by thiosulfate administration in the brain of neonatal rats
err2024-12-20
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PREAI
errGlanzel, Nicolas Manzke; da Rosa-Junior, Nevton Teixeira; Signori, Marian F.; Silveira, Josyane de Andrade; Pinheiro, Camila Vieira; Marcuzzo, Manuela Bianchin; Campos-Carraro, Cristina; Araujo, Alex Sander da Rosa; Schioth, Helgi B.; Wajner, Moacir; Leipnitz, Guilhian
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Impairment of neuromotor development and cognition associated with histopathological and neurochemical abnormalities in the cerebral cortex and striatum of glutaryl-CoA dehydrogenase deficient mice
err2024-12-01
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PREAI
errCastro, Ediandra Tissot; Ribeiro, Rafael Teixeira; Carvalho, Andrey Vinicios Soares; Machado, Diorlon Nunes; Zemniacak, Angela Beatris; Palavro, Rafael; Cunha, Samela de Azevedo; Tavares, Tailine Quevedo; Souza, Diogo Onofre Gomes de; Netto, Carlos Alexandre; Leipnitz, Guilhian; Amaral, Alexandre Umpierrez; Wajner, Moacir
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Neurodegenerative biomarkers and inflammation in patients with propionic and methylmalonic acidemias: effect of L-carnitine treatment
err2024-11-16
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PREAI
errdos Reis, Bianca Gomes; Becker, Graziela Schmitt; Marchetti, Desiree Padilha; Coelho, Daniella de Moura; Sitta, Angela; Wajner, Moacir; Vargas, Carmen Regla
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3-Hydroxy-3-Methylglutaric Acid Disrupts Brain Bioenergetics, Redox Homeostasis, and Mitochondrial Dynamics and Affects Neurodevelopment in Neonatal Wistar Rats
err2024-07-15
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errSilveira, Josyane de Andrade; Marcuzzo, Manuela Bianchin; da Rosa, Jaqueline Santana; Kist, Nathalia Simon; Hoffmann, Christofer Ian Hernandez; Carvalho, Andrey Soares; Ribeiro, Rafael Teixeira; Quincozes-Santos, Andre; Netto, Carlos Alexandre; Wajner, Moacir; Leipnitz, Guilhian
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