Not logged in Inherited human CARD9 deficiency impairs lymphoid cell, but not fibroblast, IL-17-mediated immunity Della Mina, Erika; El-Haddad, Carlos G.; West, Timothy A.; Chung, Clara W. T.; Li, Jing Jing; Lea, Vivienne; Deenick, Elissa K.; Haerynck, Filomeen; Casanova, Jean-Laurent; Puel, Anne; Ma, Cindy S.; Tangye, Stuart G.; Kane, Alisa Share Save
Defects in intron recycling suppress the antiviral response via a mechanism of intronic endogenous dsRNA Duan, Chaorui; Buerer, Luke; Bowers, Cory; Taggart, Allison J.; O'brien, Mara H.; Gunasekera, Sarah; Lin, Chien-Ling; Wang, Jing; Zeng, Yi; Staley, Jonathan P.; Fredericks, Alger M.; Monaghan, Sean F.; Welch, Anastasia; Clark, Nathaniel E.; Gao, Daxing; Marr, Nico; Zhang, Shen-Ying; Casanova, Jean-Laurent; Fairbrother, William G. Share Save
The STING HAQ haplotype and clinical non-penetrance in COPA syndrome David, Clemence; Wauquier, Tifenn; de Becdelievre, Alix; Louvrier, Camille; Tusseau, Maud; Masson, Cecile; Seabra, Luis; Kannengiesser, Caroline; Al Arab, Hayssam; Ba, Ibrahima; Brennan, Mary; Belot, Alexandre; Nathan, Nadia; Maillard, Helene; Reumaux, Heloise; Sellam, Jeremie; Cadranel, Jacques; Hatchuel, Yves; Weiss, Laurence; de Almeida, Sebastien; Rames, Cinthia; Wislez, Marie; Vigier, Clementine; Labouret, Geraldine; Kastner, Claire; Provot, Francois; Tarabeux, Julien; Schaefer, Elise; Duffy, Darragh; Bondet, Vincent; Bastard, Paul; Puel, Anne; Casanova, Jean-Laurent; Rice, Gillian I.; Bader-Meunier, Brigitte; Crow, Yanick J.; Lepelley, Alice; Fremond, Marie-Louise Share Save
Human iPSC-derived alveolar macrophages reveal macrophage subtype functions of itaconate in M. tuberculosis defense Krebs, Adam S.; Lazarov, Tomi; Reynolds, Anthony T.; Dill-Mcfarland, Kimberly A.; Xie, Abigail; Bean, James M.; Du, Muxue; Levy, Olivier; Buglino, John A.; Zhong, Aaron; Neehus, Anna-Lena; Boisson-Dupuis, Stephanie; Casanova, Jean-Laurent; Kroon, Elouise E.; Moller, Marlo; Hawn, Thomas R.; Zhou, Ting; Finley, Lydia W. S.; Juste, Marc Antoine Jean; Fitzgerald, Dan W.; Geissmann, Frederic; Glickman, Michael S. Share Save
CD28-deficient mice are vulnerable to mouse papillomavirus MmuPV1 infection of the skin and mucosae Brendle, Sarah; Li, Jingwei; Lu, Song; Schell, Todd D.; Kozak, Michael; Walter, Vonn; Shearer, Debra; Place, Joshua; Balogh, Karla; Casanova, Jean-Laurent; Christensen, Neil; Burgener, Adam D.; Murooka, Thomas T.; Zhu, Yusheng; Beziat, Vivien; Hu, Jiafen Share Save
DOCK8 and STAT3 cooperate to restrain IgE-inducing T follicular helper cells Siniscalco, Emily R.; Fisher, Courtney; Lu, Meng-Ping; Grassmann, Jessica D. S.; Mack, Corinne D.; Yaakoubi, Roukaya; Jacobsen, Danielle; Chen, Qian; Lee, Donguk; Rajamanimuthu, Priya; Simoneau, Tregony; Preece, Kahn; Gray, Paul; Okada, Satoshi; Boisson, Bertrand; Kayaoglu, Basak; Danielson, Jeffrey; Freeman, Alexandra F.; Casanova, Jean-Laurent; Chatila, Talal A.; Su, Helen C.; Ma, Cindy S.; Williams, Adam; Eisenbarth, Stephanie C.; Gowthaman, Uthaman Share Save
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Autoantibodies neutralizing type I IFNs in patients with fulminant herpes simplex virus hepatitis Gervais, Adrian; Marchal, Astrid; Boucherit, Soraya; Abi Haidar, Anthony; Bizien, Lucy; Yalcinkaya, Ahmet; Sandstrom, Ella; Kong, Xiao-Fei; Jacquemin, Emmanuel; Bernard, Olivier; Debray, Dominique; Lacaille, Florence; Ichai, Philippe; Arikan, Cigdem; Javouhey, Etienne; Roquelaure, Bertrand; Gottrand, Frederic; Trespidi, Francesca; Codullo, Veronica; Cavagna, Lorenzo; Schleinitz, Nicolas; Bousfiha, Mohamed; Amenzoui, Naima; Bousfiha, Ahmed Aziz; Jorgensen, Sofie E.; Mork, Nanna; Mogensen, Trine H.; Bastard, Paul; Puel, Anne; Borghesi, Alessandro; Rule, Jody A.; Lee, William M.; Landegren, Nils; Cobat, Aurelie; Casanova, Jean-Laurent; Jouanguy, Emmanuelle Share Save
Autoantibodies neutralizing type I IFNs in a fatal case of H5N1 avian influenza Zhang, Qian; Conrad, Taylor S.; Moncada-Velez, Marcela; Jiang, Kaijun; Cupic, Anastasija; Eaton, Jonathan; Hutchinson, Kimberley; Gervais, Adrian; Chen, Ruyue; Puel, Anne; Bastard, Paul; Cobat, Aurelie; Sokol, Theresa; Langlois, Ryan A.; Miorin, Lisa; Garcia-Sastre, Adolfo; Vanchiere, John A.; Casanova, Jean-Laurent Share Save
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Human type I interferons protect Vero E6 and ARPE-19 cells against West Nile virus and are neutralized by pathogenic autoantibodies Ferrari, Alessandro; Cassaniti, Irene; Rovida, Francesca; Lilleri, Daniele; Croce, Stefania; Trespidi, Francesca; Ghirardello, Stefano; Gervais, Adrian; Zhang, Shen-Ying; Casanova, Jean-Laurent; Borghesi, Alessandro; Baldanti, Fausto Share Save
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Application of whole-exome sequencing to predict inborn errors of immunity in pediatric severe infections and sepsis Moundir, Abderrahmane; Aissaoui, Ouissal; Akhrichi, Nassima; Allaoui, Abire; Benhsaien, Ibtihal; Jouanguy, Emmanuelle; Casanova, Jean-Laurent; El Bakkouri, Jalila; Ailal, Fatima; Bousfiha, Ahmed Aziz Share Save
Therapeutic plasma exchange accelerates immune cell recovery in severe COVID-19 Guironnet-Paquet, Aurelie; Hamzeh-Cognasse, Hind; Berard, Frederic; Cognasse, Fabrice; Richard, Jean Christophe; Yonis, Hodane; Mezidi, Mehdi; Desebbe, Olivier; Delannoy, Bertrand; Demeret, Sophie; Marois, Clemence; Saheb, Samir; Le, Quoc Viet; Schoeffler, Mathieu; Pugliesi, Paul Simon; Debord, Sophie; Bastard, Paul; Cobat, Aurelie; Casanova, Jean Laurent; Pescarmona, Remi; Viel, Sebastien; Nicolas, Jean Francois; Nosbaum, Audrey; Vocanson, Marc; Hequet, Olivier Share Save