arrow
Back
R

Ralph J. DeBerardinis

Children's Medical Center Research Institute

111H-index
736Paper Count
7.6WCitation Count
Published Papers 236
Publication Date
GLS2 reshapes glycolytic metabolism and bioenergetic homeostasis in glioblastoma cells
err2026-10-14
err0
errOAAI
errJuan De Los Santos-Jiménez; José A. Campos-Sandoval; Jessica Sudderth; Lauren G. Zacharias; João Santos Patricio; Francisco J. Alonso; Javier Márquez; Thomas P. Mathews; Ralph J. DeBerardinis; José M. Matés
errShare
errSave
Rare science, real impact: shaping the future of research on rare metabolic diseases
err2026-09-23
err0
PREAI
errAnu Suomalainen; Ralph J. DeBerardinis; Julien Baruteau; Hélène Puccio; Takanobu Otomo; Marni J. Falk
errShare
errSave
Author Correction: Characterizing the metabolomes of microglia, astrocytes and neurons in ageing and Alzheimer’s brains
err2026-09-01
err0
errOAAI
errJie Yu; Fengzhi Li; Xing-jun Chen; Chenye Mou; Di Yao; Zhanying Bi; Xiaoli Chen; Lulu Du; Ziyan Feng; Xinshuang Zhang; Xiaoqian Yu; Lauren G. Zacharias; Ralph J. DeBerardinis; Li Zhang; Zhen Li; Benyan Luo; Xiao-Ling Hu; Woo-ping Ge
errShare
errSave
Vorasidenib improves response to subsequent chemoradiation in a genetically engineered mouse model of IDH-mutant glioma
err2026-08-05
err0
PREAI
errDiana D. Shi; Ester Calvo Fernández; Vinesh T. Puliyappadamba; Tyler A. Lanman; Yi Xiao; Zebin Wen; Maria Minor; Diego Prost; Aleksandra B. Lasica; Feng Cai; Ethan Neumann; Sriram Gudipelly; Louise M. Clark; Quang-De Nguyen; Salvador Peña; Janaka Wansapura; Pranita Kaphle; Tracey Shipman; Michael M. Levitt; Mathew D. Lin; Alexander C.-Y. Tsai; Joyce H. Lee; Daniel P. Cahill; Rifaquat Rahman; Daphne A. Haas-Kogan; Timothy E. Richardson; Itay Tirosh; Payal Jain; Adriana E. Tron; Vihang Nakhate; Gilbert Youssef; Caroline Dehais; Julian Jacob; David A. Reardon; Julie J. Miller; Kalil G. Abdullah; Patrick Y. Wen; Ralph J. DeBerardinis; Lin Xu; Mehdi Touat; Katherine B. Peters; L. Nicolas Gonzalez Castro; William G. Kaelin; Mario L. Suvà; Samuel K. McBrayer
errShare
errSave
Mitochondria directly interact with the nuclear pore complex
errNature
IF48.5
err2026-06-10
err0
PREAI
errIvan Menendez-Montes; Consuelo Marin-Vicente; Shibani Mukherjee; Mahmoud Salama Ahmed; Manuel Jose Gomez; Chukwuemeka George Anene-Nzelu; Chang Jie Mick Lee; Svenja Koslowski; Ashley Solmonson; Tara Tassin; Shah R. Ali; Pedro Pessoa; Abdallah Elnwasany; Nicholas T. Lam; Suwannee Thet; Enrique Calvo; Alisson C. Cardoso; Ana Helena M. Pereira; Feng Xiao; Ping Wang; Asim Mohamed; Hamed El-feky; Ahmed Elghamry; Gonzalo Gancedo-Alonso; Ngoc Uyen Nhi Nguyen; Ching-Cheng Hsu; Aundrea K. Westfall; Ralph DeBerardinis; Roger Sik-Yin Foo; Michael Kinter; Steve Pressé; Chao Xing; Luke Szweda; Asaithamby Aroumougame; Fatima Sanchez-Cabo; Jose Antonio Enriquez; Miguel Torres; Jesus Vazquez; Hesham A. Sadek
errShare
errSave
Hyperglycosylation is a metabolic driver of Alzheimer’s disease
err2026-06-09
err0
errOAAI
errTara R. Hawkinson; Zizhen Liu; Roberto A. Ribas; Terrymar Medina; Rikke S. Nielsen; Harrison A. Clarke; Xin Ma; Angela C. Mueller; Adrielle F. Plasencia; Alexander L. Sheer; Samantha T. Simpson; Charles M. Soto; Jessica Sudderth; Feng Cai; Alex R. Cantrell; Matthieu G. Colpaert; Cameron J. Shedlock; Lei Wu; Lyndsay E. A. Young; Damon D. Kooser; Li Chen; Alison M. Ryan; Sadi Quinones; Jihye Son; Parastoo Azadi; Ralph J. Deberardinis; Stefan Prokop; Derek Allison; Shuang Yang; Hongyu Chen; Yu Huang; Xing He; Kimberly M. Alonge; Jingchuan Guo; Yi Guo; Jiang Bian; Craig W. Vander Kooi; Matthew S. Gentry; Ramon C. Sun
errShare
errSave
Characterizing the metabolomes of microglia, astrocytes and neurons in ageing and Alzheimer’s brains
err2026-04-30
err0
errOAAI
errJie Yu; Fengzhi Li; Xing-jun Chen; Chenye Mou; Di Yao; Zhanying Bi; Xiaoli Chen; Lulu Du; Ziyan Feng; Xinshuang Zhang; Xiaoqian Yu; Lauren G. Zacharias; Ralph J. DeBerardinis; Li Zhang; Zhen Li; Benyan Luo; Xiao-Ling Hu; Woo-ping Ge
errShare
errSave
Nitrogen metabolism profiling reveals cell state-specific pyrimidine synthesis pathway choice
err2026-04-29
err0
errOAAI
errMilan R. Savani; Bingbing Li; Bailey C. Smith; Wen Gu; Yi Xiao; Gerard Baquer; Tracey Shipman; Skyler S. Oken; Namya Manoj; Lauren G. Zacharias; Vinesh T. Puliyappadamba; Sylwia A. Stopka; Michael S. Regan; Michael M. Levitt; Charles K. Edgar; William H. Hicks; Soummitra Anand; Misty S. Martin-Sandoval; Rainah Winston; João S. Patrício; Xandria Johnson; Trevor S. Tippetts; Diana D. Shi; Andrew Lemoff; Timothy E. Richardson; Pascal O. Zinn; Ashley Solmonson; Thomas P. Mathews; Nathalie Y. R. Agar; Ralph J. DeBerardinis; Kalil G. Abdullah; Samuel K. McBrayer
errShare
errSave
Repeatability of Metabolic Imaging With Hyperpolarized Pyruvate: Back-to-Back Neuroimaging and Blood Analysis
err2026-04-23
err0
errOAAI
errJun Chen; Sung-Han Lin; Jessica Sudderth; Kelley A. Derner; Crystal E. Harrison; Maheen Zaidi; Jeannie D. Baxter; Jeff Liticker; Zohreh Erfani; Craig R. Malloy; Marco C. Pinho; Ralph J. DeBerardinis; Jae Mo Park
errShare
errSave
A recurrent ACAA2 variant causes a dominant syndrome of lipodystrophy, lipomatosis, infantile steatohepatitis, and hypoglycemia
err2026-01-02
err0
errOAAI
errSimha, Vinaya; LoPiccolo, Mary Kate; Platt, Anna; Brown, Rebecca J.; Johnson, Xandria; Carere, Deanna Alexis; Donnelly, Colleen; Snyder, Matthew T.; Xing, Chao; Mathews, Thomas P.; Gopal, Purva; Ward, Stephen C.; Tomchick, Diana R.; Agarwal, Anil K.; DeBerardinis, Ralph J.; Garg, Abhimanyu
errShare
errSave
NUDT5 regulates purine metabolism and thiopurine sensitivity by interacting with PPAT
errScience
IF45.8
err2025-11-06
err0
errOAAI
errZheng Wu; Phong T. Nguyen; Varun Sondhi; Run-Wen Yao; Zhifang Lu; Tao Dai; Jui-Chung Chiang; Feng Cai; Imani M. Williams; Eliot B. Blatt; Zengfu Shang; Ling Cai; Jing Zhang; Mya D. Moore; Islam Alshamleh; Xiangyi Li; Tamaratare Ogu; Lauren G. Zacharias; Rainah Winston; Joao S. Patricio; Xandria Johnson; Wei-Min Chen; Qian Cong; Thomas P. Mathews; Yuanyuan Zhang; Limei Zhang; Ralph J. DeBerardinis
errShare
errSave
Cell-intrinsic pyrimidine synthesis pathway choice in human brain and glioma
err2025-11-01
err0
errOAAI
errSavani, Milan; Smith, Bailey; Gu, Wen; Xiao, Yi; Baquer, Gerard; Li, Bingbing; Oken, Skyler; Manoj, Namya; Zacharias, Lauren; Puliyappadamba, Vinesh; Stopka, Sylwia; Regan, Michael; Levitt, Michael; Edgar, Charles; Hicks, William; Anand, Soummitra; Shi, Diana; Lemoff, Andrew; Solmonson, Ashley; Mathews, Thomas; Agar, Nathalie; DeBerardinis, Ralph; Abdullah, Kalil; McBrayer, Samuel
errShare
errSave
Mutant IDH silences GSX2 to reprogram neural progenitor cell fate and promote gliomagenesis
err2025-11-01
err0
errOAAI
errXiao, Yi; Shi, Diana; Guo, Lei; Neumann, Ethan; Levitt, Michael; Kaphle, Pranita; Shipman, Tracey; Li, Haocheng; Cai, Feng; Ramirez, Denise; Zacharias, Lauren; Chen, Zhenkang; Lin, Mathew; Thidil, Vinesh; Mathews, Thomas; Mishra, Prashant; Kim, Yoon Jung; Xu, Jian; Mack, Stephen; Deberardinis, Ralph; Tirosh, Itay; Suva, Mario; Xu, Lin; Abdullah, Kalil; Mcbrayer, Samuel
errShare
errSave
Cancer Metabolism: Aspirations for the Coming Decade
err2025-10-01
err2
PREAI
errDeBerardinis, Ralph J.; Vousden, Karen H.; Chandel, Navdeep S.
errShare
errSave
PEX39 facilitates the peroxisomal import of PTS2-containing proteins
err2025-07-30
err0
errOAAI
errWalter W. Chen; Tony A. Rodrigues; Daniel Wendscheck; Ana G. Pedrosa; Chendong Yang; Tânia Francisco; Till Möcklinghoff; Alexandros Zografakis; Bernardo Nunes-Silva; Reut E. Avraham; Ana R. Silva; Maria J. Ferreira; Hirak Das; Janet Koster; Simone Neuwirth; Julian Bender; Silke Oeljeklaus; Varun Sondhi; Christos Gatsogiannis; Maya Schuldiner; Einat Zalckvar; Kay Hofmann; Hans R. Waterham; Ralph J. DeBerardinis; Jorge E. Azevedo; Bettina Warscheid
errShare
errSave
The redox sensor KEAP1 facilitates adaptation of T cells to chronic antigen stimulation by preventing hyperactivation
err2024-11-29
err0
errOAAI
errZhu, Ziang; Luo, Ying; Lou, Guohua; Yihunie, Kiddist; Wizzard, Safuwra; Devilbiss, Andrew W.; Muh, Sarah; Ma, Chaoyu; Shinde, Sejal S.; Hoar, Jonathan; Hu, Taidou; Zhang, Nu; Biswal, Shyam; Deberardinis, Ralph J.; Wu, Tuoqi; Yao, Chen
errShare
errSave
Pathogenic mitochondrial DNA mutations inhibit melanoma metastasis
err2024-11-01
err0
errOAAI
errShelton, Spencer D.; House, Sara; Melo, Luiza Martins Nascentes; Ramesh, Vijayashree; Chen, Zhenkang; Wei, Tao; Wang, Xun; Llamas, Claire B.; Venigalla, Siva Sai Krishna; Menezes, Cameron J.; Allies, Gabriele; Krystkiewicz, Jonathan; Roesler, Jonas; Meckelmann, Sven W.; Zhao, Peihua; Rambow, Florian; Schadendorf, Dirk; Zhao, Zhiyu; Gill, Jennifer G.; DeBerardinis, Ralph J.; Morrison, Sean J.; Tasdogan, Alpaslan; Mishra, Prashant
errShare
errSave
Electron transport chain inhibition increases cellular dependence on purine transport and salvage
err2024-07-01
err1
errOAAI
errWu, Zheng; Bezwada, Divya; Cai, Feng; Harris, Robert C.; Ko, Bookyung; Sondhi, Varun; Pan, Chunxiao; Vu, Hieu S.; Nguyen, Phong T.; Faubert, Brandon; Cai, Ling; Chen, Hongli; Martin-Sandoval, Misty; Do, Duyen; Gu, Wen; Zhang, Yuanyuan; Zhang, Yuannyu; Brooks, Bailey; Kelekar, Sherwin; Zacharias, Lauren G.; Oaxaca, K. Celeste; Patricio, Joao S.; Mathews, Thomas P.; Garcia-Bermudez, Javier; Ni, Min; DeBerardinis, Ralph J.
errShare
errSave
Tryptophan fuels MYC-dependent liver tumorigenesis through indole 3-pyruvate synthesis
err2024-05-20
err5
errOAAI
errVenkateswaran, Niranjan; Garcia, Roy; Lafita-Navarro, M. Carmen; Hao, Yi-Heng; Perez-Castro, Lizbeth; Nogueira, Pedro A. S.; Solmonson, Ashley; Mender, Ilgen; Kilgore, Jessica A.; Fang, Shun; Brown, Isabella N.; Li, Li; Parks, Emily; dos Santos, Igor Lopes; Bhaskar, Mahima; Kim, Jiwoong; Jia, Yuemeng; Lemoff, Andrew; Grishin, Nick V.; Kinch, Lisa; Xu, Lin; Williams, Noelle S.; Shay, Jerry W.; Deberardinis, Ralph J.; Zhu, Hao; Conacci-Sorrell, Maralice
errShare
errSave
A review of multiple diagnostic approaches in the Undiagnosed Diseases Network to identify inherited metabolic diseases
err2024-04-01
err0
PREAI
errFuruta, Yutaka; Tinker, Rory; Hamid, Rizwan; Cogan, Joy; Ezell, Kimberly; Oglesbee, Devin; DeBerardinis, Ralph; Phillips, John
errShare
errSave