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The diagnostic role of pharmacological provocation testing in cardiac electrophysiology: a clinical consensus statement of the European Heart Rhythm Association and the European Association of Percutaneous Cardiovascular Interventions (EAPCI) of the ESC, the ESC Working Group on Cardiovascular Pharmacotherapy, the Association of European Paediatric and Congenital Cardiology (AEPC), the Paediatric & Congenital Electrophysiology Society (PACES), the Heart Rhythm Society (HRS), the Asia Pacific Heart Rhythm Society (APHRS), and the Latin American Heart Rhythm Society (LAHRS) Behr, Elijah R.; Winkel, Bo Gregers; Ensam, Bode; Alfie, Alberto; Arbelo, Elena; Berry, Colin; Cerrone, Marina; Conte, Giulio; Crotti, Lia; Corcia, Cecilia M. Gonzalez; Kaski, Juan Carlos; Nademanee, Koonlawee; Postema, Pieter G.; Priori, Silvia; Probst, Vincent; Sarquella-Brugada, Georgia; Schulze-Bahr, Eric; Tadros, Rafik; Wilde, Arthur; Tfelt-Hansen, Jacob; Wolpert, Christian; Cuesta, Alejandro; Damman, Peter; Dobrev, Dobromir; Drago, Fabrizio; Haugaa, Kristina; Krahn, Andrew; Krause, Ulrich; Lambiase, Pier D.; Napolitano, Carlo; Odening, Katja E.; Shimizu, Wataru; Veltmann, Christian Share Save
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Efficacy and safety of HERG channel agonists for treatment of Long QT Syndrome type 8 Kukavica, D.; Mazzanti, A.; Trancuccio, A.; Porta-Sanchez, A.; Jauregui Abularach, M. E.; Pergola, V.; Tarifa, C.; Hernandez Lopez, K.; Lentini, G.; Priori, S. G. Share Save
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Characterization and natural history of patients with LMNA-related dilated cardiomyopathy in the phase 3 REALM-DCM trial Garcia-Pavia, Pablo; Lakdawala, Neal K.; Sinagra, Gianfranco; Ripoll-Vera, Tomas; Afshar, Kia; Priori, Silvia G.; Ware, James S.; Owens, Anjali; Li, Huihua; Angeli, Franca S.; Elliott, Perry; Macrae, Calum A.; Judge, Daniel P. Share Save
A Clinical Diagnostic Test for Calcium Release Deficiency Syndrome Ni, Mingke; Dadon, Ziv; Ormerod, Julian O. M.; Saenen, Johan; Hoeksema, Wiert F.; Antiperovitch, Pavel; Tadros, Rafik; Christiansen, Morten K.; Steinberg, Christian; Arnaud, Marine; Tian, Shanshan; Sun, Bo; Estillore, John Paul; Wang, Ruiwu; Khan, Habib R.; Roston, Thomas M.; Mazzanti, Andrea; Giudicessi, John R.; Siontis, Konstantinos C.; Alak, Aiman; Acosta, J. Gabriel; Menon, Syamkumar M. Divakara; Tan, Nigel S.; van der Werf, Christian; Nazer, Babak; Vivekanantham, Hari; Pandya, Tanvi; Cunningham, Jennifer; Gula, Lorne J.; Wong, Jorge A.; Amit, Guy; Scheinman, Melvin M.; Krahn, Andrew D.; Ackerman, Michael J.; Priori, Silvia G.; Gollob, Michael H.; Healey, Jeff S.; Sacher, Frederic; Nof, Eyal; Glikson, Michael; Wilde, Arthur A. M.; Watkins, Hugh; Jensen, Henrik K.; Postema, Pieter G.; Belhassen, Bernard; Chen, S. R. Wayne; Roberts, Jason D. Share Save
Real-world candidacy to mavacamten in a contemporary hypertrophic obstructive cardiomyopathy population Bertero, Edoardo; Chiti, Chiara; Schiavo, Maria Alessandra; Tini, Giacomo; Costa, Paolo; Todiere, Giancarlo; Mabritto, Barbara; Dei, Lorenzo-Lupo; Giannattasio, Alessia; Mariani, Davide; Lofiego, Carla; Santolamazza, Caterina; Monda, Emanuele; Quarta, Giovanni; Barbisan, Davide; Mandoli, Giulia Elena; Mapelli, Massimo; Sguazzotti, Maurizio; Negri, Francesco; De Vecchi, Simona; Ciabatti, Michele; Tomasoni, Daniela; Mazzanti, Andrea; Marzo, Francesca; de Gregorio, Cesare; Raineri, Claudia; Vianello, Pier Filippo; Marchi, Alberto; Biagioni, Giulia; Insinna, Eleonora; Parisi, Vanda; Ditaranto, Raffaello; Barison, Andrea; Giammarresi, Andrea; De Ferrari, Gaetano Maria; Priori, Silvia; Metra, Marco; Pieroni, Maurizio; Patti, Giuseppe; Imazio, Massimo; Perugini, Enrica; Agostoni, Piergiuseppe; Cameli, Matteo; Merlo, Marco; Sinagra, Gianfranco; Senni, Michele; Limongelli, Giuseppe; Ammirati, Enrico; Vagnarelli, Fabio; Crotti, Lia; Badano, Luigi; Calore, Chiara; Gabrielli, Domenico; Re, Federica; Musumeci, Giuseppe; Emdin, Michele; Barbato, Emanuele; Musumeci, Beatrice; Autore, Camillo; Biagini, Elena; Porto, Italo; Olivotto, Iacopo; Canepa, Marco Share Save
Unexpected impairment of INa current underpins reentrant arrhythmias in a knock-in swine model of Timothy syndrome Porta-Sanchez, Andreu; Mazzanti, Andrea; Tarifa, Carmen; Kukavica, Deni; Trancuccio, Alessandro; Mohsin, Muhammad; Zanfrini, Elisa; Perota, Andrea; Duchi, Roberto; Hernandez-Lopez, Kevin; Jauregui-Abularach, Miguel Eduardo; Pergola, Valerio; Fernandez, Eugenio; Bongianino, Rossana; Tavazzani, Elisa; Gambelli, Patrick; Memmi, Mirella; Scacchi, Simone; Pavarino, Luca; Franzone, Piero Colli; Lentini, Giovanni; Filgueiras-Rama, David; Galli, Cesare; Santiago, Demetrio Julian; Priori, Silvia G. Share Save
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RyR2 C-terminal truncating variants identified in patients with arrhythmic phenotypes exert a dominant negative effect through formation of wildtype-truncation heteromers Tian, Shanshan; Zhong, Xiaowei; Wang, Hui; Wei, Jinhong; Guo, Wenting; Wang, Ruiwu; Estillore, John Paul; Napolitano, Carlo; Duff, Henry H.; Ilhan, Erkan; Knight, Linda M.; Lloyd, Michael S.; Roberts, Jason D.; Priori, Silvia G.; Chen, S. R. Wayne Share Save
Characterization of Skeletal Muscle Biopsy and Derived Myoblasts in a Patient Carrying Arg14del Mutation in Phospholamban Gene Zanotti, Simona; Ripolone, Michela; Napoli, Laura; Velardo, Daniele; Salani, Sabrina; Ciscato, Patrizia; Priori, Silvia; Kukavica, Deni; Mazzanti, Andrea; Diamanti, Luca; Vegezzi, Elisa; Moggio, Maurizio; Corti, Stefania; Comi, Giacomo; Sciacco, Monica Share Save
Characteristics of Patients with Spontaneous Versus Drug-Induced Brugada Electrocardiogram: Sub-Analysis From the SABRUS Milman, Anat; Sabbag, Avi; Conte, Giulio; Postema, Pieter G.; Andorin, Antoine; Gourraud, Jean-Baptiste; Sacher, Frederic; Mabo, Philippe; Kim, Sung-Hwan; Maeda, Shingo; Takahashi, Yoshihide; Kamakura, Tsukasa; Aiba, Takeshi; Juang, Jimmy J. M.; Michowitz, Yoav; Leshem, Eran; Mizusawa, Yuka; Arbelo, Elena; Huang, Zhengrong; Denjoy, Isabelle; Giustetto, Carla; Wijeyeratne, Yanushi D.; Mazzanti, Andrea; Brugada, Ramon; Casado-Arroyo, Ruben; Champagne, Jean; Calo, Leonardo; Sarquella-Brugada, Georgia; Tfelt-Hansen, Jacob; Priori, Silvia G.; Takagi, Masahiko; Veltmann, Christian; Delise, Pietro; Corrado, Domenico; Behr, Elijah R.; Gaita, Fiorenzo; Yan, Gan-Xin; Brugada, Josep; Leenhardt, Antoine; Wilde, Arthur A. M.; Brugada, Pedro; Kusano, Kengo F.; Hirao, Kenzo; Nam, Gi-Byoung; Probst, Vincent; Belhassen, Bernard Share Save
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Value of 3D echocardiography in the diagnosis of arrhythmogenic right ventricular cardiomyopathy Addetia, Karima; Mazzanti, Andrea; Maragna, Riccardo; Monti, Lorenzo; Yamat, Megan; Kukavica, Deni; Pagan, Eleonora; Kishiki, Kanako; Prado, Aldo; Marino, Maira; Bagnardi, Vincenzo; Priori, Silvia; Lang, Roberto M. Share Save
2022 ESC Guidelines for the management of patients with ventricular arrhythmias and the prevention of sudden cardiac death Developed by the task force for the management of patients with ventricular arrhythmias and the prevention of sudden cardiac death of the European Society of Cardiology (ESC) Endorsed by the Association for European Paediatric and Congenital Cardiology (AEPC) Zeppenfeld, Katja; Tfelt-Hansen, Jacob; de Riva, Marta; Winkel, Bo Gregers; Behr, Elijah R.; Blom, Nico A.; Charron, Philippe; Corrado, Domenico; Dagres, Nikolaos; de Chillou, Christian; Eckardt, Lars; Friede, Tim; Haugaa, Kristina H.; Hocini, Meleze; Lambiase, Pier D.; Marijon, Eloi; Merino, Jose L.; Peichl, Petr; Priori, Silvia G.; Reichlin, Tobias; Schulz-Menger, Jeanette; Sticherling, Christian; Tzeis, Stylianos; Verstrael, Axel; Volterrani, Maurizio; Cikes, Maja; Kirchhof, Paulus; Abdelhamid, Magdy; Aboyans, Victor; Arbelo, Elena; Arribas, Fernando; Asteggiano, Riccardo; Basso, Cristina; Bauer, Axel; Bertaglia, Emanuele; Biering-Sorensen, Tor; Blomstrom-Lundqvist, Carina; Borger, Michael A.; Celutkiene, Jelena; Cosyns, Bernard; Falk, Volkmar; Fauchier, Laurent; Gorenek, Bulent; Halvorsen, Sigrun; Hatala, Robert; Heidbuchel, Hein; Kaab, Stefan; Konradi, Aleksandra; Koskinas, Konstantinos C.; Kotecha, Dipak; Landmesser, Ulf; Lewis, Basil S.; Linhart, Ales; Lochen, Maja Lisa; Lund, Lars H.; Metzner, Andreas; Mindham, Richard; Nielsen, Jens Cosedis; Norekval, Tone M.; Patten, Monica; Prescott, Eva; Rakisheva, Amina; Remme, Carol Ann; Roca-Luque, Ivo; Sarkozy, Andrea; Scherr, Daniel; Sitges, Marta; Touyz, Rhian M.; Van Mieghem, Nicolas; Velagic, Vedran; Viskin, Sami; Volders, Paul G. A. Share Save