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Adam Helms

University of Michigan

33H-index
139Paper Count
4.4KCitation Count
Published Papers 50
Publication Date
Recruitment of transcriptional effectors by Cas9 creates cis-regulatory elements and demonstrates distance-dependent transcriptional regulation
err2025-11-12
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errJubran Boulos; Arkadiy K. Golov; Nadav Keren; Itai Erlich; Nardeen Shehadeh; Nili Avidan; Hagai Kariti; Omer Sadeh; Lilac Haimovich-Caspi; Adam Helms; Noam Kaplan; Izhak Kehat
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Altered cardiac excitability and arrhythmia in models of SCN1B-linked developmental and epileptic encephalopathy
err2025-09-09
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errRamos-Mondragon, Roberto; Wang, Shuyun; Edokobi, Nnamdi; Liu, Qinghua; Qiao, Xiaotan; Shih, Maya; Dang, Louis T.; Tsan, Yao-Chang; Sterbova, Katalin; Helms, Adam S.; Weckhuysen, Sarah; Lopez-Santiago, Luis F.; Parent, Jack M.; Isom, Lori L.
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Sex-Specific Clinical and Genetic Factors Associated With Adverse Outcomes in Hypertrophic Cardiomyopathy
err2025-02-01
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PREAI
errButters, Alexandra; Arnott, Clare; Sweeting, Joanna; Claggett, Brian; Cuomo, Anna S. E.; Abrams, Dominic; Ashley, Euan A.; Day, Sharlene M.; Helms, Adam S.; Lampert, Rachel; Lin, Kim Y.; Michels, Michelle; Miller, Erin M.; Olivotto, Iacopo; Owens, Anjali; Parikh, Victoria N.; Pereira, Alexandre C.; Rossano, Joseph W.; Ryan, Thomas D.; Saberi, Sara; Stendahl, John C.; Ware, James S.; Atherton, John; Semsarian, Christopher; Lakdawala, Neal K.; Ho, Carolyn Y.; Ingles, Jodie
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Desmoplakin Cardiomyopathy: Role of Inflammation and Potential Role of Disease-Modifying Therapies
err2025-01-09
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PREAI
errGasperetti, Alessio; Carrick, Richard T.; Muller, Steven; Murray, Brittney; Adamo, Luigi; Bauce, Barbara; Mcnally, Elizabeth; Helms, Adam
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Matrix Architecture and Mechanics Regulate Myofibril Organization, Costamere Assembly, and Contractility in Engineered Myocardial Microtissues
err2024-11-18
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errDePalma, Samuel J.; Jilberto, Javiera; Stis, Austin E.; Huang, Darcy D.; Lo, Jason; Davidson, Christopher D.; Chowdhury, Aamilah; Kent III, Robert N.; Jewett, Maggie E.; Kobeissi, Hiba; Chen, Christopher S.; Lejeune, Emma; Helms, Adam S.; Nordsletten, David A.; Baker, Brendon M.
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The Impact of Genotype in Dilated and Arrhythmogenic Cardiomyopathy: Insights from the SHaRE Registry
err2024-11-12
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PREAI
errPadalia, Kishan; Slaven, Sarah; Medo, Kristen; Graw, Sharon; Claggett, Brian; Bundgaard, Henning; Helms, Adam; Heymans, Stephane; Ho, Carolyn; Khan, Sadiya; Lakdawala, Neal; Olivotto, Iacopo; Owens, Anjali; Prasad, Sanjay; Axelsson, Anna; Reza, Nosheen; Shore, Supriya; Sinagra, Gianfranco; Tayal, Upasana; Verdonschot, Job; Wheeler, Matthew; Taylor, Matthew; Merlo, Marco; Fornaro, Alessandra; Parikh, Victoria; Wilsbacher, Lisa; Mestroni, Luisa
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Social Determinants of Health and Outcomes in Patients with Hypertrophic Cardiomyopathy in the Sarcomeric Human Cardiomyopathy Registry (SHaRe)
err2024-11-12
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PREAI
errHafeez, Neha; Claggett, Brian; Owens, Anjali; Helms, Adam; Saberi, Sara; Lampert, Rachel; Stendahl, John; Ashley, Euan; Parikh, Victoria; Lakdawala, Neal; Ingles, Jodie; Olivotto, Iacopo; Ho, Carolyn; Taylor, Matthew; Khan, Sadiya; Day, Sharlene
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Long-Term Outcomes After Septal Reduction Therapies in Obstructive Hypertrophic Cardiomyopathy: Insights From the SHARE Registry
err2024-10-22
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PREAI
errMaurizi, Niccolo; Antiochos, Panagiotis; Owens, Anjali; Lakdwala, Neal; Saberi, Sara; Russell, Mark W.; Fumagalli, Carlo; Skalidis, Ioannis; Lin, Kimberly Y.; Nathan, Ashwin S.; De Feria Alsina, Alejandro; Reza, Nosheen; Stendahl, John C.; Abrams, Dominic; Semsarian, Christopher; Clagget, Brian; Lampert, Rachel; Wheeler, Matthew; Parikh, Victoria N.; Ashley, Euan; Michels, Michelle; Rossano, Joseph; Ryan, Thomas D.; Ingles, Jodie; Ware, James; Ho, Carolyn Y.; Helms, Adam S.; Day, Sharlene M.; Olivotto, Iacopo
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Clinical features and outcomes in carriers of pathogenic desmoplakin variants
err2024-09-17
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errGasperetti, Alessio; Carrick, Richard T.; Protonotarios, Alexandros; Murray, Brittney; Laredo, Mikael; van der Schaaf, Iris; Lekanne, Ronald H.; Syrris, Petros; Cannie, Douglas; Tichnell, Crystal; Cappelletto, Chiara; Gigli, Marta; Medo, Kristen; Saguner, Ardan M.; Duru, Firat; Gilotra, Nisha A.; Zimmerman, Stefan; Hylind, Robyn; Abrams, Dominic J.; Lakdawala, Neal K.; Cadrin-Tourigny, Julia; Targetti, Mattia; Olivotto, Iacopo; Graziosi, Maddalena; Cox, Moniek; Biagini, Elena; Charron, Philippe; Casella, Michela; Tondo, Claudio; Yazdani, Momina; Ware, James S.; Prasad, Sanjay K.; Calo, Leonardo; Smith, Eric D.; Helms, Adam S.; Hespe, Sophie; Ingles, Jodie; Tandri, Harikrishna; Ader, Flavie; Peretto, Giovanni; Peters, Stacey; Horton, Ari; Yao, Jess; Dittmann, Sven; Schulze-Bahr, Eric; Qureshi, Maria; Young, Katelyn; Carruth, Eric D.; Haggerty, Chris; Parikh, Victoria N.; Taylor, Matthew; Mestroni, Luisa; Wilde, Arthur; Sinagra, Gianfranco; Merlo, Marco; Gandjbakhch, Estelle; van Tintelen, J. Peter; te Riele, Anneline S. J. M.; Elliott, Perry M.; Calkins, Hugh; James, Cynthia A.
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Development of a Novel Biallelic, Haploinsufficient Mouse Model of MYBPC3 Related Hypertrophic Cardiomyopathy
err2024-08-02
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PREAI
errMeisner, Joshua; Bullard, Abbey; Friedline, Sabrina; Rechsteiner, Olivia; Previs, Michael; Helms, Adam
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A novel tool for arrhythmic risk stratification in desmoplakin gene variant carriers
err2024-07-16
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errCarrick, Richard T.; Gasperetti, Alessio; Protonotarios, Alexandros; Murray, Brittney; Laredo, Mikael; van der Schaaf, Iris; Dooijes, Dennis; Syrris, Petros; Cannie, Douglas; Tichnell, Crystal; Gilotra, Nisha A.; Cappelletto, Chiara; Medo, Kristen; Saguner, Ardan M.; Duru, Firat; Hylind, Robyn J.; Abrams, Dominic J.; Lakdawala, Neal K.; Cadrin-Tourigny, Julia; Targetti, Mattia; Olivotto, Iacopo; Graziosi, Maddalena; Cox, Moniek; Biagini, Elena; Charron, Philippe; Compagnucci, Paolo; Casella, Michela; Conte, Giulio; Tondo, Claudio; Yazdani, Momina; Ware, James S.; Prasad, Sanjay K.; Calo, Leonardo; Smith, Eric D.; Helms, Adam S.; Hespe, Sophie; Ingles, Jodie; Tandri, Harikrishna; Ader, Flavie; Peretto, Giovanni; Peters, Stacey; Horton, Ari; Yao, Jessica; Schulze-Bahr, Eric; Dittman, Sven; Carruth, Eric D.; Young, Katelyn; Qureshi, Maria; Haggerty, Chris; Parikh, Victoria N.; Taylor, Matthew; Mestroni, Luisa; Wilde, Arthur; Sinagra, Gianfranco; Merlo, Marco; Gandjbakhch, Estelle; van Tintelen, J. Peter; te Riele, Anneline S. J. M.; Elliot, Perry; Calkins, Hugh; Wu, Katherine C.; James, Cynthia A.
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Imaging Features of Arrhythmogenic Cardiomyopathies
err2024-04-01
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PREAI
errGalizia, Mauricio S.; Attili, Anil K.; Truesdell, William R.; Smith, Eric D.; Helms, Adam S.; Sulaiman, Abdulbaset M. A.; Madamanchi, Chaitanya; Agarwal, Prachi P.
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Sex and Gene Based Differences in Age Related Penetrance of Dilated and Arrhythmogenic Cardiomyopathy
err2023-11-07
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PREAI
errBart, Nicole K.; Stroeks, Sophie; Khan, Sadiya S.; Reza, Nosheen; Olivotto, Iacopo; Vissing, Christoffer; Sinnette, Corine; Owens, Anjali T.; Fornaro, Alessandra; Mestroni, Luisa; Taylor, Matthew; Helms, Adam S.; Prasad, Sanjay K.; Saberi, Sara; Shore, Supriya; Verdonschot, Job; Sinagra, Gianfranco; Merlo, Marco; Gigli, Marta; Wilsbacher, Lisa D.; Heymans, Stephane; Wheeler, Matthew
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An Unbiased Screen Identified the Hsp70-BAG3 Complex as a Regulator of Myosin-Binding Protein C3
err2023-09-01
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errThompson, Andrea D.; Wagner, Marcus J.; Rodriguez, Juliani; Malhotra, Alok; Vander Roest, Steve; Lilienthal, Ulla; Shao, Hao; Vignesh, Mathav; Weber, Keely; Yob, Jaime M.; Prosser, Benjamin L.; Helms, Adam S.; Gestwicki, Jason E.; Ginsburg, David; Day, Sharlene M.
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Left Ventricular Systolic Dysfunction in Patients Diagnosed With Hypertrophic Cardiomyopathy During Childhood: Insights From the SHaRe Registry
err2023-08-01
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errAlaiwi, Sarah Abou; Roston, Thomas M.; Marstrand, Peter; Claggett, Brian Lee; Parikh, Victoria N.; Helms, Adam S.; Ingles, Jodie; Lampert, Rachel; Lakdawala, Neal K.; Michels, Michelle; Owens, Anjali T.; Rossano, Joseph W.; Saberi, Sara; Abrams, Dominic J.; Ashley, Euan A.; Semsarian, Christopher; Stendahl, John C.; Ware, James S.; Miller, Erin; Ryan, Thomas D.; Russell, Mark W.; Day, Sharlene M.; Olivotto, Iacopo; Vissing, Christoffer R.; Ho, Carolyn Y. Y.
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Left and Right PVC-Induced Ventricular Dysfunction
err2023-02-01
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errHuntrakul, Anurut; Helms, Adam; Attili, Anil; Agarwal, Prachi P.; Ghannam, Michael; Liang, Jackson J.; Latchamsetty, Rakesh; Jongnarangsin, Krit; Morady, Fred; Bogun, Frank
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Probabilistic integration of transcriptome-wide association studies and colocalization analysis identifies key molecular pathways of complex traits
err2023-01-01
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errOkamoto, Jeffrey; Wang, Lijia; Yin, Xianyong; Luca, Francesca; Pique-Regi, Roger; Helms, Adam; Im, Hae Kyung; Morrison, Jean; Wen, Xiaoquan
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Impact of SARS-Cov-2 infection in patients with hypertrophic cardiomyopathy: results of an international multicentre registry
err2022-06-03
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errGimeno, Juan R.; Olivotto, Iacopo; Isabel Rodriguez, Ana; Ho, Carolyn Y.; Fernandez, Adrian; Quiroga, Alejandro; Angeles Espinosa, Mari; Gomez-Gonzalez, Cristina; Robledo, Maria; Tojal-Sierra, Lucas; Day, Sharlene M.; Owens, Anjali; Barriales-Villa, Roberto; Maria Larranaga, Jose; Rodriguez-Palomares, Jose; Gonzalez-del-Hoyo, Maribel; Piqueras-Flores, Jesus; Reza, Nosheen; Chumakova, Olga; Ashley, Euan A.; Parikh, Victoria; Wheeler, Matthew; Jacoby, Daniel; Pereira, Alexandre C.; Saberi, Sara; Helms, Adam S.; Villacorta, Eduardo; Gallego-Delgado, Maria; Castro, Daniel; Dominguez, Fernando; Ripoll-Vera, Tomas; Zorio-Grima, Esther; Sanchez-Martinez, Jose Carlos; Garcia-Alvarez, Ana; Arbelo, Elena; Victoria Mogollon, Maria; Fuentes-Canamero, Maria Eugenia; Grande, Elias; Pena, Carlos; Monserrat, Lorenzo; Lakdawala, Neal K.
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Translation of New and Emerging Therapies for Genetic Cardiomyopathies
err2022-01-01
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errHelms, Adam S.; Thompson, Andrea D.; Day, Sharlene M.
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Predictors of Major Atrial Fibrillation Endpoints in the National Heart, Lung, and Blood Institute HCMR
err2021-11-01
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errKramer, Christopher M.; DiMarco, John P.; Kolm, Paul; Ho, Carolyn Y.; Desai, Milind Y.; Kwong, Raymond Y.; Dolman, Sarahfaye F.; Desvigne-Nickens, Patrice; Geller, Nancy; Kim, Dong-Yun; Maron, Martin S.; Appelbaum, Evan; Jerosch-Herold, Michael; Friedrich, Matthias G.; Schulz-Menger, Jeanette; Piechnik, Stefan K.; Mahmod, Masliza; Jacoby, Daniel; White, James; Chiribiri, Amedeo; Helms, Adam; Choudhury, Lubna; Michels, Michelle; Bradlow, William; Salerno, Michael; Dawson, Dana K.; Weinsaft, Jonathan W.; Berry, Colin; Nagueh, Sherif F.; Buccarelli-Ducci, Chiara; Owens, Anjali; Casadei, Barbara; Watkins, Hugh; Weintraub, William S.; Neubauer, Stefan
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