Not logged in The Dp16 Down syndrome mouse model does not exhibit oral interferon-gammopathy or susceptibility to oral candidiasis Lubkin, Ashira; Lujan, Ramon A.; Pontejo, Sergio M.; Oikonomou, Vasileios; Fellows, Abigail M.; Dos Santos Dias, Lucas; Snarr, Brendan D.; Macalpine, Jessie; Sullivan, Kelly D.; Espinosa, Joaquin M.; Hickman, Heather; Lionakis, Michail S. Share Save
XBB.1.5-Adapted COVID-19 mRNA Vaccines but Not Infections With Previous Omicron Variants Boost Neutralisation Against the SARS-CoV-2 JN.1 Variant in Patients With Inflammatory Bowel Disease Woelfel, Simon; Duetschler, Joel; Junker, Daniel; Koenig, Marius; Graf, Nicole; Krieger, Claudia; Truniger, Samuel; Oikonomou, Vasileios; Leinenkugel, Georg; Koller, Seraina; Metzger-Peter, Katline; Wyss, Jacqueline; Krupka, Niklas; Frei, Nicola; Albrich, Werner C.; Friedrich, Matthias; Niess, Jan Hendrik; Schneiderhan-Marra, Nicole; Dulovic, Alex; Misselwitz, Benjamin; Korte, Wolfgang; Buergi, Justus J.; Brand, Stephan Share Save
A deep intronic splice-altering AIRE variant causes APECED syndrome through antisense oligonucleotide-targetable pseudoexon inclusion Ochoa, Sebastian; Hsu, Amy P.; Oler, Andrew J.; Kumar, Dhaneshwar; Chauss, Daniel; van Hamburg, Jan Piet; van Laar, Gustaaf G.; Oikonomou, Vasileios; Ganesan, Sundar; Ferre, Elise M. N.; Schmitt, Monica M.; Dimaggio, Tom; Barber, Princess; Constantine, Gregory M.; Rosen, Lindsey B.; Auwaerter, Paul G.; Gandhi, Bhumika; Miller, Jennifer L.; Eisenberg, Rachel; Rubinstein, Arye; Schussler, Edith; Balliu, Erjola; Shashi, Vandana; Neth, Olaf; Olbrich, Peter; Le, Kim My; Mamia, Nanni; Laakso, Saila; Nevalainen, Pasi I.; Groenholm, Juha; Seppaenen, Mikko R. J.; Boon, Louis; Uzel, Gulbu; Franco, Luis M.; Heller, Theo; Winer, Karen K.; Ghosh, Rajarshi; Seifert, Bryce A.; Walkiewicz, Magdalena; Notarangelo, Luigi D.; Zhou, Qing; Askentijevich, Ivona; Gahl, William; Dalgard, Cliffton L.; Perera, Lalith; Afzali, Behdad; Tas, Sander W.; Holland, Steven M.; Lionakis, Michail S. Share Save
A human STAT3 gain-of-function variant drives local Th17 dysregulation and skin inflammation in mice Toth, Kelsey A.; Schmitt, Erica G.; Kolicheski, Ana; Greenberg, Zev J.; Levendosky, Elizabeth; Saucier, Nermina; Trammel, Kelsey; Oikonomou, Vasileios; Lionakis, Michail S.; Klechevsky, Eynav; Kim, Brian S.; Schuettpelz, Laura G.; Saligrama, Naresha; Cooper, Megan A. Share Save
The immune and microbial homeostasis determines the Candida-mast cells cross-talk in celiac disease Renga, Giorgia; Pariano, Marilena; D'Onofrio, Fiorella; Pieraccini, Giuseppe; Di Serio, Claudia; Villella, Valeria Rachela; Abbate, Carlo; Puccetti, Matteo; Giovagnoli, Stefano; Stincardini, Claudia; Bellet, Marina Maria; Ricci, Maurizio; Costantini, Claudio; Oikonomou, Vasileios; Romani, Luigina Share Save
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STAR SIGN study: Evaluation of COVID-19 vaccine efficacy against the SARS-CoV-2 variants BQ.1.1 and XBB.1.5 in patients with inflammatory bowel disease Woelfel, Simon; Duetschler, Joel; Koenig, Marius; Dulovic, Alex; Graf, Nicole; Junker, Daniel; Oikonomou, Vasileios; Krieger, Claudia; Truniger, Samuel; Franke, Annett; Eckhold, Annika; Forsch, Kristina; Koller, Seraina; Wyss, Jacqueline; Krupka, Niklas; Oberholzer, Melanie; Frei, Nicola; Geissler, Nora; Schaub, Peter C.; STAR SIGN Study Investigator, Matthias; Albrich, Werner; Friedrich, Matthias; Schneiderhan-Marra, Nicole; Misselwitz, Benjamin J.; Korte, Wolfgang; Buergi, Justus; Brand, Stephan Share Save
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Case report: Discovery of a de novo FAM111B pathogenic variant in a patient with an APECED-like clinical phenotype Ferre, Elise M. N.; Yu, Yunting; Oikonomou, Vasileios; Hilfanova, Anna; Lee, Chyi-Chia R.; Rosen, Lindsey B.; Burbelo, Peter D.; Vazquez, Sara E.; Anderson, Mark S.; Barocha, Amisha; Heller, Theo; Soldatos, Ariane; Holland, Steven M.; Walkiewicz, Magdalena A.; Lionakis, Michail S. Share Save
Human Dectin-1 deficiency impairs macrophage-mediated defense against phaeohyphomycosis Drummond, Rebecca A.; Desai, Jigar V.; Hsu, Amy P.; Oikonomou, Vasileios; Vinh, Donald C.; Acklin, Joshua A.; Abers, Michael S.; Walkiewicz, Magdalena A.; Anzick, Sarah L.; Swamydas, Muthulekha; Vautier, Simon; Natarajan, Mukil; Oler, Andrew J.; Yamanaka, Daisuke; Mayer-Barber, Katrin D.; Iwakura, Yoichiro; Bianchi, David; Driscoll, Brian; Hauck, Ken; Kline, Ahnika; Viall, Nicholas S. P.; Zerbe, Christa S.; Ferre, Elise M. N.; Schmitt, Monica M.; DiMaggio, Tom; Pittaluga, Stefania; Butman, John A.; Zelazny, Adrian M.; Shea, Yvonne R.; Arias, Cesar A.; Ashbaugh, Cameron; Mahmood, Maryam; Temesgen, Zelalem; Theofiles, Alexander G.; Nigo, Masayuki; Moudgal, Varsha; Bloch, Karen C.; Kelly, Sean G.; Whitworth, M. Suzanne; Rao, Ganesh; Whitener, Cindy J.; Mafi, Neema; Gea-Banacloche, Juan; Kenyon, Lawrence C.; Miller, William R.; Boggian, Katia; Gilbert, Andrea; Sincock, Matthew; Freeman, Alexandra F.; Bennett, John E.; Hasbun, Rodrigo; Mikelis, Constantinos M.; Kwon-Chung, Kyung J.; Belkaid, Yasmine; Brown, Gordon D.; Lim, Jean K.; Kuhns, Douglas B.; Holland, Steven M.; Lionakis, Michail S. Share Save
Systemic and T cell-associated responses to SARS-CoV-2 immunisation in gut inflammation (STAR SIGN study): effects of biologics on vaccination efficacy of the third dose of mRNA vaccines against SARS-CoV-2 Woelfel, Simon; Duetschler, Joel; Koenig, Marius; Graf, Nicole; Oikonomou, Vasileios; Krieger, Claudia; Truniger, Samuel; Franke, Annett; Eckhold, Annika; Forsch, Kristina; Wyss, Jacqueline; Krupka, Niklas; Albrich, Werner; Frei, Nicola; Geissler, Nora; Schaub, Peter; Friedrich, Matthias; Misselwitz, Benjamin; Korte, Wolfgang; Burgi, Justus J.; Brand, Stephan Share Save
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Immunopathological signatures in multisystem inflammatory syndrome in children and pediatric COVID-19 Sacco, Keith; Castagnoli, Riccardo; Vakkilainen, Svetlana; Liu, Can; Delmonte, Ottavia M.; Oguz, Cihan; Kaplan, Ian M.; Alehashemi, Sara; Burbelo, Peter D.; Bhuyan, Farzana; de Jesus, Adriana A.; Dobbs, Kerry; Rosen, Lindsey B.; Cheng, Aristine; Shaw, Elana; Vakkilainen, Mikko S.; Pala, Francesca; Lack, Justin; Zhang, Yu; Fink, Danielle L.; Oikonomou, Vasileios; Snow, Andrew L.; Dalgard, Clifton L.; Chen, Jinguo; Sellers, Brian A.; Sanchez, Gina A. Montealegre; Barron, Karyl; Rey-Jurado, Emma; Vial, Cecilia; Poli, Maria Cecilia; Licari, Amelia; Montagna, Daniela; Marseglia, Gian Luigi; Licciardi, Francesco; Ramenghi, Ugo; Discepolo, Valentina; Lo Vecchio, Andrea; Guarino, Alfredo; Eisenstein, Eli M.; Imberti, Luisa; Sottini, Alessandra; Biondi, Andrea; Mato, Sayonara; Gerstbacher, Dana; Truong, Meng; Stack, Michael A.; Magliocco, Mary; Bosticardo, Marita; Kawai, Tomoki; Danielson, Jeffrey J.; Hulett, Tyler; Askenazi, Manor; Hu, Shaohui; Cohen, Jeffrey, I; Su, Helen C.; Kuhns, Douglas B.; Lionakis, Michail S.; Snyder, Thomas M.; Holland, Steven M.; Goldbach-Mansky, Raphaela; Tsang, John S.; Notarangelo, Luigi D. Share Save
Anakinra restores cellular proteostasis by coupling mitochondrial redox balance to autophagy van de Veerdonk, Frank L.; Renga, Giorgia; Pariano, Marilena; Bellet, Marina M.; Servillo, Giuseppe; Fallarino, Francesca; De Luca, Antonella; Iannitti, Rossana G.; Piobbico, Danilo; Gargaro, Marco; Manni, Giorgia; D'Onofrio, Fiorella; Stincardini, Claudia; Sforna, Luigi; Borghi, Monica; Castelli, Marilena; Pieroni, Stefania; Oikonomou, Vasileios; Villella, Valeria R.; Puccetti, Matteo; Giovagnoli, Stefano; Galarini, Roberta; Barola, Carolina; Maiuri, Luigi; Della Fazia, Maria Agnese; Cellini, Barbara; Talesa, Vincenzo Nicola; Dinarello, Charles A.; Costantini, Claudio; Romani, Luigina Share Save
CARD9 Expression Pattern, Gene Dosage, and Immunodeficiency Phenotype Revisited Goel, Shubham; Kuehn, Hye Sun; Chinen, Javier; Niemela, Julie; Stoddard, Jennifer; Yamanaka, Daisuke; Garofalo, Mary; Samir, Sophia; Migaud, Melanie; Oikonomou, Vasileios; Fleisher, Thomas; Puel, Anne; Lionakis, Michail S.; Rosenzweig, Sergio D. Share Save
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Response to Comments on Aberrant type 1 immunity drives susceptibility to mucosal fungal infections Break, Timothy J.; Oikonomou, Vasileios; Dutzan, Nicolas; Desai, Jigar V.; Swidergall, Marc; Freiwald, Tilo; Chauss, Daniel; Harrison, Oliver J.; Alejo, Julie; Williams, Drake W.; Pittaluga, Stefania; Lee, Chyi-Chia R.; Bouladoux, Nicolas; Swamydas, Muthulekha; Hoffman, Kevin W.; Greenwell-Wild, Teresa; Bruno, Vincent M.; Rosen, Lindsey B.; Lwin, Wint; Renteria, Andy; Pontejo, Sergio M.; Shannon, John P.; Myles, Ian A.; Olbrich, Peter; Ferre, Elise M. N.; Schmitt, Monica; Martin, Daniel; Barber, Daniel L.; Solis, Norma V.; Notarangelo, Luigi D.; Serreze, David V.; Matsumoto, Mitsuru; Hickman, Heather D.; Murphy, Philip M.; Anderson, Mark S.; Lim, Jean K.; Holland, Steven M.; Filler, Scott G.; Afzali, Behdad; Belkaid, Yasmine; Moutsopoulos, Niki M.; Lionakis, Michail S. Share Save
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An immune-based biomarker signature is associated with mortality in COVID-19 patients Abers, Michael S.; Delmonte, Ottavia M.; Ricotta, Emily E.; Fintzi, Jonathan; Fink, Danielle L.; de Jesus, Adriana A. Almeida; Zarember, Kol A.; Alehashemi, Sara; Oikonomou, Vasileios; Desai, Jigar, V; Canna, Scott W.; Shakoory, Bita; Dobbs, Kerry; Imberti, Luisa; Sottini, Alessandra; Quiros-Roldan, Eugenia; Castelli, Francesco; Rossi, Camillo; Brugnoni, Duilio; Biondi, Andrea; Bettini, Laura Rachele; D'Angio', Mariella; Bonfanti, Paolo; Castagnoli, Riccardo; Montagna, Daniela; Licari, Amelia; Marseglia, Gian Luigi; Gliniewicz, Emily F.; Shaw, Elana; Kahle, Dana E.; Rastegar, Andre T.; Stack, Michael; Myint-Hpu, Katherine; Levinson, Susan L.; DiNubile, Mark J.; Chertow, Daniel W.; Burbelo, Peter D.; Cohen, Jeffrey, I; Calvo, Katherine R.; Tsang, John S.; Su, Helen C.; Gallin, John, I; Kuhns, Douglas B.; Goldbach-Mansky, Raphaela; Lionakis, Michail S.; Notarangelo, Luigi D. Share Save
Aspergillus fumigatus tryptophan metabolic route differently affects host immunity Zelante, Teresa; Choera, Tsokyi; Beauvais, Anne; Fallarino, Francesca; Paolicelli, Giuseppe; Pieraccini, Giuseppe; Pieroni, Marco; Galosi, Claudia; Beato, Claudia; De Luca, Antonella; Boscaro, Francesca; Romoli, Riccardo; Liu, Xin; Warris, Adilia; Verweij, Paul E.; Ballard, Eloise; Borghi, Monica; Pariano, Marilena; Costantino, Gabriele; Calvitti, Mario; Vacca, Carmine; Oikonomou, Vasilis; Gargaro, Marco; Wong, Alicia Yoke Wei; Boon, Louis; den Hartog, Marcel; Spacil, Zdenek; Puccetti, Paolo; Latge, Jean-Paul; Keller, Nancy P.; Romani, Luigina Share Save