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收藏Using chanarin-dorfman syndrome patient fibroblasts to explore disease mechanisms and new treatment avenues
Angel, Mor; Kleinberg, Yuval; Newaz, Tanmoy; Li, Victoria; Zaid, Rinat; Oved, Keren; Dorot, Orly; Pichinuk, Edward; Avitan-Hersh, Emily; Saada, Ann; Weiss, Karin; Zaremberg, Vanina; Tal, Galit; Zalckvar, Einat
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收藏Transcriptome analysis of atad3-null zebrafish embryos elucidates possible disease mechanisms
Ezer, Shlomit; Ronin, Nathan; Yanovsky-Dagan, Shira; Rotem-Bamberger, Shahar; Halstuk, Orli; Wexler, Yair; Ben-Moshe, Zohar; Plaschkes, Inbar; Benyamini, Hadar; Saada, Ann; Inbal, Adi; Harel, Tamar
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收藏Protein kinase C epsilon activation improves early survival in an acute porcine model of controlled hemorrhage
Simchoni, Maya; Wagnert-Avraham, Linn; Derazne, Estela; Nachman, Dean; Gershon, Yuval; Cohen Levi, Eliraz; Horesh, Adi; Cohen, Yaron; Nitecki, Maya; Glick, Yuval; Eisenkraft, Arik; Suissa, Nir; Twig, Gilad; Gertz, S. David; Saada, Ann; Furer, Ariel
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收藏Sengers syndrome caused by biallelic TIMM29 variants and RNAi silencing in Drosophila orthologue recapitulates the human phenotype
Shalata, Adel; Saada, Ann; Mahroum, Mohammed; Hadid, Yarin; Furman, Chaya; Shalata, Zaher Eldin; Desnick, Robert J.; Lorber, Avraham; Khoury, Asaad; Higazi, Adnan; Shaag, Avraham; Barash, Varda; Spiegel, Ronen; Vlodavsky, Euvgeni; Rustin, Pierre; Pietrokovski, Shmuel; Manov, Irena; Gieger, Dan; Tal, Galit; Salzberg, Adi; Mandel, Hanna
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收藏Ovariectomy and High Fat-Sugar-Salt Diet Induced Alzheimer's Disease/Vascular Dementia Features in Mice
Sweetat, Sahar; Ben Shabat, Moti; Theotokis, Paschalis; Suissa, Nir; Karafoulidou, Eleni; Touloumi, Olga; Abu-Fanne, Rami; Abramsky, Oded; Wolf, Gilly; Saada, Ann; Lotan, Amit; Grigoriadis, Nikolaos; Rosenmann, Hanna
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收藏High Sucrose Diet-Induced Subunit I Tyrosine 304 Phosphorylation of Cytochrome c Oxidase Leads to Liver Mitochondrial Respiratory Dysfunction in the Cohen Diabetic Rat Model
Arroum, Tasnim; Pham, Lucynda; Raisanen, Taryn E.; Morse, Paul T.; Wan, Junmei; Bell, Jamie; Lax, Rachel; Saada, Ann; Huttemann, Maik; Weksler-Zangen, Sarah
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收藏Early Infiltration of Innate Immune Cells to the Liver Depletes HNF4α and Promotes Extrahepatic Carcinogenesis
Goldman, Omer; Adler, Lital N.; Hajaj, Emma; Croese, Tommaso; Darzi, Naama; Galai, Sivan; Tishler, Hila; Ariav, Yarden; Lavie, Dor; Fellus-Alyagor, Liat; Oren, Roni; Kuznetsov, Yuri; David, Eyal; Jaschek, Rami; Stossel, Chani; Singer, Oded; Malitsky, Sergey; Barak, Renana; Seger, Rony; Erez, Neta; Amit, Ido; Tanay, Amos; Saada, Ann; Golan, Talia; Rubinek, Tamar; Sang Lee, Joo; Ben-Shachar, Shay; Wolf, Ido; Erez, Ayelet
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收藏The Beneficial Effect of Mitochondrial Transfer Therapy in 5XFAD Mice via Liver-Serum-Brain Response
Sweetat, Sahar; Nitzan, Keren; Suissa, Nir; Haimovich, Yael; Lichtenstein, Michal; Zabit, Samar; Benhamron, Sandrine; Akarieh, Karameh; Mishra, Kumudesh; Barasch, Dinorah; Saada, Ann; Ziv, Tamar; Kakhlon, Or; Lorberboum-Galski, Haya; Rosenmann, Hanna
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收藏Mitochondrial-derived vesicles retain membrane potential and contain a functional ATP synthase
Hazan (Ben-Menachem), Reut; Lintzer, Dvora; Ziv, Tamar; Das, Koyeli; Rosenhek-Goldian, Irit; Porat, Ziv; Ben Ami Pilo, Hila; Karniely, Sharon; Saada, Ann; Regev-Rudzki, Neta; Pines, Ophry
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收藏Multifaceted Analyses of Isolated Mitochondria Establish the Anticancer Drug 2-Hydroxyoleic Acid as an Inhibitor of Substrate Oxidation and an Activator of Complex IV-Dependent State 3 Respiration
Mishra, Kumudesh; Peter, Maria; Nardiello, Anna Maria; Keller, Guy; Llado, Victoria; Fernandez-Garcia, Paula; Kahlert, Ulf D.; Barasch, Dinorah; Saada, Ann; Torok, Zsolt; Balogh, Gabor; Escriba, Pablo V.; Piotto, Stefano; Kakhlon, Or
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收藏Infantile SOD1 deficiency syndrome caused by a homozygous SOD1 variant with absence of enzyme activity
Ezer, Shlomit; Daana, Muhannad; Park, Julien H.; Yanovsky-Dagan, Shira; Nordstrom, Ulrika; Basal, Adily; Edvardson, Simon; Saada, Ann; Otto, Markus; Meiner, Vardiella; Marklund, Stefan L.; Andersen, Peter Munch; Harel, Tamar
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收藏Levodopa-responsive dystonia caused by biallelic PRKN exon inversion invisible to exome sequencing
Mor-Shaked, Hagar; Paz-Ebstein, Emuna; Basal, Adily; Ben-Haim, Simona; Grobe, Hanna; Heymann, Sami; Israel, Zvi; Namnah, Montaser; Nitzan, Anat; Rosenbluh, Chaggai; Saada, Ann; Tzur, Tomer; Yanovsky-Dagan, Shira; Zaidel-Bar, Ronen; Harel, Tamar; Arkadir, David
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