未登录DUCT reveals architectural mechanisms contributing to bile duct recovery in a mouse model for Alagille syndrome
Hankeova, Simona; Salplachta, Jakub; Zikmund, Tomas; Kavkova, Michaela; Van Hul, Noemi; Brinek, Adam; Smekalova, Veronika; Laznovsky, Jakub; Dawit, Feven; Jaros, Josef; Bryja, Vitezslav; Lendahl, Urban; Ellis, Ewa; Nemeth, Antal; Fischler, Bjorn; Hannezo, Edouard; Kaiser, Jozef; Andersson, Emma Rachel
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收藏Mouse Model of Alagille Syndrome and Mechanisms of Jagged1 Missense Mutations
Andersson, Emma R.; Chivukula, Indira V.; Hankeova, Simona; Sjoqvist, Marika; Tsoi, Yat Long; Ramskold, Daniel; Masek, Jan; Elmansuri, Aiman; Hoogendoorn, Anita; Vazquez, Elenae; Storvall, Helena; Netusilova, Julie; Huch, Meritxell; Fischler, Bjorn; Ellis, Ewa; Contreras, Adriana; Nemeth, Antal; Chien, Kenneth C.; Clevers, Hans; Sandberg, Rickard; Bryja, Vitezslav; Lendahl, Urban
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收藏De Novo Donor-Specific HLA Antibody Formation in Two Patients With Crigler-Najjar Syndrome Type I Following Human Hepatocyte Transplantation With Partial Hepatectomy Preconditioning
Jorns, C.; Nowak, G.; Nemeth, A.; Zemack, H.; Mork, L. -M.; Johansson, H.; Gramignoli, R.; Watanabe, M.; Karadagi, A.; Alheim, M.; Hauzenberger, D.; van Dijk, R.; Bosma, P. J.; Ebbesen, F.; Szakos, A.; Fischler, B.; Strom, S.; Ellis, E.; Ericzon, B. -G.
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收藏Budesonide versus Prednisone with Azathioprine for the Treatment of Autoimmune Hepatitis in Children and Adolescents
Woynarowski, Marek; Nemeth, Antal; Baruch, Yaacov; Koletzko, Sibylle; Melter, Michael; Rodeck, Burkhard; Strassburg, Christian P.; Proels, Markus; Wozniak, Magorzata; Manns, Michael P.
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收藏BUDESONIDE 3 MG TID IN THE TREATMENT OF AUTOIMMUNE HEPATITIS (AIH) IN ADOLESCENTS, A SUBGROUP ANALYSIS OF THE EUROPEAN AIH-BUC-STUDY
Woynarowski, M.; Nemeth, A.; Baruch, Y.; Koletzko, S.; Melter, M.; Rodeck, B.; Strassburg, C.; Proels, M.; Manns, M. P.
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收藏Differences in presentation and progression between severe FIC1 and BSEP deficiencies
Pawlikowska, Ludmila; Strautnieks, Sandra; Jankowska, Irena; Czubkowski, Piotr; Emerick, Karan; Antoniou, Anthony; Wanty, Catherine; Fischler, Bjorn; Jacquemin, Emmanuel; Wali, Sami; Blanchard, Samra; Nielsen, Inge-Merete; Bourke, Billy; McQuaid, Shirley; Lacaille, Florence; Byrne, Jane A.; van Eerde, Albertien M.; Kolho, Kaija-Leena; Klomp, Leo; Houwen, Roderick; Bacchetti, Peter; Lobritto, Steven; Hupertz, Vera; McClean, Patricia; Mieli-Vergani, Giorgina; Shneider, Benjamin; Nemeth, Antal; Sokal, Etienne; Freimer, Nelson B.; Knisely, A. S.; Rosenthal, Philip; Whitington, Peter F.; Pawlowska, Joanna; Thompson, Richard J.; Bull, Laura N.
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收藏Severe bile salt export pump deficiency:: 82 different ABCB11 mutations in 109 families
Strautnieks, Sandra S.; Byrne, Jane A.; Pawlikowska, Ludmila; Cebecauerova, Dita; Rayner, Anne; Dutton, Laura; Meier, Yvonne; Antoniou, Anthony; Stieger, Bruno; Arnell, Henrik; Ozcay, Figen; Al-Hussaini, Hussa F.; Bassas, Atif F.; Verkade, Henkjan J.; Fischler, Bjorn; Nemeth, Antal; Kotalova, Radana; Shneider, Benjamin L.; Cielecka-Kuszyk, Joanna; McClean, Patricia; Whitington, Peter F.; Sokal, Etienne; Jirsa, Milan; Wali, Sami H.; Jankowska, Irena; Pawlowska, Joanna; Mieli-Vergani, Giorgina; Knisely, A. S.; Bull, Laura N.; Thompson, Richard J.
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收藏Hepatocellular carcinoma in ten children under five years of age with bile salt export pump deficiency
Knisely, A. S.; Strautnieks, Sandra S.; Meier, Yvonne; Stieger, Bruno; Byrne, Jane A.; Portmann, Bernard C.; Bull, Laura N.; Pawlikowska, Ludmila; Bilezikci, Banu; Ozcay, Figen; Laszlo, Aranka; Tiszlavicz, Laszlo; Moore, Lynette; Raftos, Jeremy; Arnell, Henrik; Fischler, Bjoern; Nemeth, Antal; Papadogiannakis, Nikos; Cielecka-Kuszyk, Joanna; Jankowska, Irena; Pawlowska, Joanna; Melin-Aldana, Hector; Emerick, Karan M.; Whitington, Peter F.; Mieli-Vergani, Giorgina; Thompson, Richard J.
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收藏Successful treatment of severe unconjugated hyperbilirubinemia via induction of UGT1A1 by rifampicin
Ellis, E; Wagner, M; Lammert, F; Nemeth, A; Gumhold, J; Strassburg, CP; Kylander, C; Katsika, D; Trauner, M; Einarsson, C; Marschall, HU
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