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Regulatory T-cell dysfunction and cutaneous exposure to Staphylococcus aureus underlie eczema in DOCKS deficiency Wilkie, Hazel; Das, Mrinmoy; Pelovitz, Tyler; Bainter, Wayne; Woods, Brian; Alasharee, Mohammed; Sobh, Ali; Baris, Safa; Eltan, Sevgi Bilgic; Al-Herz, Waleed; Barbouche, Mohamed-Ridha; Ben-Mustapha, Imen; Ben-Ali, Meriem; Sallam, Mohamed T. H.; Awad, Amany; Lotfy, Sohilla; El Marsafy, Aisha; Ezzelarab, Moushira; Farrar, Michael; Schmidt, Brigitta A. R.; NandyMazumdar, Monali; Guttman-Yassky, Emma; Sheets, Anthony; Vidic, Katie Maria; Murphy, George; Schlievert, Patrick M.; Chou, Janet; Leyva-Castillo, Juan Manuel; Janssen, Erin; Timilshina, Maheshwor; Geha, Raif S. 分享 收藏
Symptoms and management of cow's milk allergy: perception and evidence 牛奶过敏的症状和管理: 感知和证据 Robert, E.; Al-Hashmi, H. A.; Al-Mehaidib, A.; Alsarraf, K.; Al-Turaiki, M.; Aldekhail, W.; Al-Herz, W.; Alkhabaz, A.; Bawakid, Khalid O.; Elghoudi, A.; El Hodhod, M.; Hussain, Ali A.; Kamal, Naglaa M.; Goronfolah, L. T.; Nasrallah, B.; Sengupta, K.; Broekaert, I.; Domellof, M.; Indrio, F.; Lapillonne, A.; Pienar, C.; Ribes-Koninckx, C.; Shamir, R.; Szajewska, H.; Thapar, N.; Thomassen, R. A.; Verduci, E.; West, C. E.; Vandenplas, Y. 分享 收藏
The Middle East and North Africa Diagnosis and Management Guidelines for Inborn Errors of Immunity 中东和北非先天性免疫错误的诊断和管理指南 Baris, Safa; Abolhassani, Hassan; Massaad, Michel J.; Al-Nesf, Maryam; Chavoshzadeh, Zahra; Keles, Sevgi; Reisli, Ismail; Tahiat, Azzeddine; Shendi, Hiba Mohammad; Abd Elaziz, Dalia; Belaid, Brahim; Al Dhaheri, Fatima; Haskologlu, Sule; Dogu, Figen; Ben-Mustapha, Imen; Sobh, Ali; Galal, Nermeen; Meshaal, Safa; Elhawary, Rabab; El-marsafy, Aisha; Alroqi, Fayhan J.; Al-Saud, Bandar; Al-Ahmad, Mona; Al Farsi, Tariq; AL Sukaiti, Nashat; Al-Tamemi, Salem; Mehawej, Cybel; Dbaibo, Ghassan; ElGhazali, Gehad; Kilic, Sara Sebnem; Genel, Ferah; Kiykim, Ayca; Musabak, Ugur; Artac, Hasibe; Guner, Sukru Nail; Boukari, Rachida; Djidjik, Reda; Kechout, Nadia; Cagdas, Deniz; El-Sayed, Zeinab Awad; Karakoc-Aydiner, Elif; Alzyoud, Raed; Barbouche, Mohamed Ridha; Adeli, Mehdi; Wakim, Rima Hanna; Reda, Shereen M.; Ikinciogullari, Aydan; Ozen, Ahmet; Bousfiha, Aziz; Al-Mousa, Hamoud; Rezaei, Nima; Al-Herz, Waleed; Geha, Raif S. 分享 收藏
Consensus on diagnosis and management of Hereditary Angioedema in the Middle East: A Delphi initiative Maurer, Marcus; Abuzakouk, Mohamed; Al-Ahmad, Mona; Al-Herz, Waleed; Alrayes, Hassan; Al-Tamemi, Salem; Arnaout, Rand; Binghadeer, Hend; Gutta, Ravi; Irani, Carla; Mobayed, Hassan; Nasr, Iman; Shendi, Hiba; Zaitoun, Fares 分享 收藏
Predictors of early death risk among untransplanted patients with combined immunodeficiencies affecting cellular and humoral immunity: A multicenter report Al-Herz, Waleed; Ziyab, Ali H.; Adeli, Mehdi; Al Farsi, Tariq; Al-Hammadi, Suleiman; Al Kuwaiti, Amna Ali; Al-Nesf, Maryam; Al Sukaiti, Nashat; Al-Tamemi, Salem; Shendi, Hiba 分享 收藏
The 2022 Update of IUIS Phenotypical Classification for Human Inborn Errors of Immunity Bousfiha, Aziz; Moundir, Abderrahmane; Tangye, Stuart G.; Picard, Capucine; Jeddane, Leila; Al-Herz, Waleed; Rundles, Charlotte C.; Franco, Jose Luis; Holland, Steven M.; Klein, Christoph; Morio, Tomohiro; Oksenhendler, Eric; Puel, Anne; Puck, Jennifer; Seppanen, Mikko R. J.; Somech, Raz; Su, Helen C.; Sullivan, Kathleen E.; Torgerson, Troy R.; Meyts, Isabelle 分享 收藏
STAT5B restrains human B-cell differentiation to maintain humoral immune homeostasis Pelham, Simon J.; Caldirola, Maria Soledad; Avery, Danielle T.; Mackie, Joseph; Rao, Geetha; Gothe, Florian; Peters, Timothy J.; Guerin, Antoine; Neumann, David; Vokurkova, Doris; Hwa, Vivian; Zhang, Wenming; Lyu, Shu-Chen; Chang, Iris; Manohar, Monali; Nadeau, Kari C.; Gaillard, Maria Isabel; Bezrodnik, Liliana; Iotova, Violeta; Zwirner, Norberto Walter; Gutierrez, Mavel; Al-Herz, Waleed; Goodnow, Christopher C.; Vargas-Hernandez, Alexander; Satter, Lisa R. Forbes; Hambleton, Sophie; Deenick, Elissa K.; Ma, Cindy S.; Tangye, Stuart G. 分享 收藏
Partial RAG deficiency in humans induces dysregulated peripheral lymphocyte development and humoral tolerance defect with accumulation of T-bet+ B cells Csomos, Krisztian; Ujhazi, Boglarka; Blazso, Peter; Herrera, Jose L.; Tipton, Christopher M.; Kawai, Tomoki; Gordon, Sumai; Ellison, Maryssa; Wu, Kevin; Stowell, Matthew; Haynes, Lauren; Cruz, Rachel; Zakota, Bence; Nguyen, Johnny; Altrich, Michelle; Geier, Christoph B.; Sharapova, Svetlana; Dasso, Joseph F.; Leiding, Jennifer W.; Smith, Grace; Al-Herz, Waleed; Dorna, Mayra de Barros; Fadugba, Olajumoke; Fronkova, Eva; Kanderova, Veronika; Svaton, Michael; Henrickson, Sarah E.; Hernandez, Joseph D.; Kuijpers, Taco; Kandilarova, Snezhina Mihailova; Naumova, Elizaveta; Milota, Tomas; Sediva, Anna; Moshous, Despina; Neven, Benedicte; Saco, Tara; Sargur, Ravishankar; Savic, Sinisa; Sleasman, John; Sunkersett, Gauri; Ward, Brant R.; Komatsu, Masanobu; Pittaluga, Stefania; Kumanovics, Attila; Butte, Manish J.; Cancro, Michael P.; Pillai, Shiv; Meffre, Eric; Notarangelo, Luigi D.; Walter, Jolan E. 分享 收藏
Human Inborn Errors of Immunity: 2022 Update on the Classification from the International Union of Immunological Societies Expert Committee 人类先天性免疫错误: 国际免疫学会联盟专家委员会对分类的2022更新 Tangye, Stuart G.; Al-Herz, Waleed; Bousfiha, Aziz; Cunningham-Rundles, Charlotte; Franco, Jose Luis; Holland, Steven M.; Klein, Christoph; Morio, Tomohiro; Oksenhendler, Eric; Picard, Capucine; Puel, Anne; Puck, Jennifer; Seppanen, Mikko R. J.; Somech, Raz; Su, Helen C.; Sullivan, Kathleen E.; Torgerson, Troy R.; Meyts, Isabelle 分享 收藏
Allergic manifestations of inborn errors of immunity and their impact on the diagnosis: A worldwide study 先天性免疫缺陷的过敏表现及其对诊断的影响: 一项全球研究 El-Sayed, Zeinab A.; El-Ghoneimy, Dalia H.; Ortega-Martell, Jose A.; Radwan, Nesrine; Aldave, Juan C.; Al-Herz, Waleed; Al-Nesf, Maryam A.; Condino-Neto, Antonio; Cole, Theresa; Eley, Brian; Erwa, Nahla H. H.; Espinosa-Padilla, Sara; Faria, Emilia; Rosario Filho, Nelson A.; Fuleihan, Ramsay; Galal, Nermeen; Garabedian, Elizabeth; Hintermeyer, Mary; Imai, Kohsuke; Irani, Carla; Kamal, Ebtihal; Kechout, Nadia; Klocperk, Adam; Levin, Michael; Milota, Tomas; Ouederni, Monia; Paganelli, Roberto; Pignata, Claudio; Qamar, Farah N.; Quinti, Isabella; Qureshi, Sonia; Radhakrishnan, Nita; Rezaei, Nima; Routes, John; Singh, Surjit; Siniah, Sangeetha; Taha, Intisar Abdel-Hakam; Tanno, Luciana K.; Van Dort, Ben; Volokha, Alla; Sullivan, Kathleen 分享 收藏
DOCK8 functions as an adaptor that links TLR-MyD88 signaling to B cell activation (vol 13, 612, 2012) Jabara, Haifa H.; McDonald, Douglas R.; Janssen, Erin; Massaad, Michel J.; Ramesh, Narayanaswamy; Borzutzky, Arturo; Rauter, Ingrid; Benson, Halli; Schneider, Lynda; Baxi, Sachin; Recher, Mike; Notarangelo, Luigi D.; Wakim, Rima; Dbaibo, Ghassan; Dasouki, Majed; Al-Herz, Waleed; Barlan, Isil; Baris, Safa; Kutukculer, Necil; Ochs, Hans D.; Plebani, Alessandro; Kanariou, Maria; Lefranc, Gerard; Reisli, Ismail; Fitzgerald, Katherine A.; Golenbock, Douglas; Manis, John; Keles, Sevgi; Ceja, Reuben; Chatila, Talal A.; Geha, Raif S. 分享 收藏
Rubella Virus Infected Macrophages and Neutrophils Define Patterns of Granulomatous Inflammation in Inborn and Acquired Errors of Immunity Perelygina, Ludmila; Faisthalab, Raeesa; Abernathy, Emily; Chen, Min-hsin; Hao, LiJuan; Bercovitch, Lionel; Bayer, Diana K.; Noroski, Lenora M.; Lam, Michael T.; Cicalese, Maria Pia; Al-Herz, Waleed; Nanda, Arti; Hajjar, Joud; Vanden Driessche, Koen; Schroven, Shari; Leysen, Julie; Rosenbach, Misha; Peters, Philipp; Raedler, Johannes; Albert, Michael H.; Abraham, Roshini S.; Rangarjan, Hemalatha G.; Buchbinder, David; Kobrynski, Lisa; Pham-Huy, Anne; Dhossche, Julie; Cunningham Rundles, Charlotte; Meyer, Anna K.; Theos, Amy; Atkinson, T. Prescott; Musiek, Amy; Adeli, Mehdi; Derichs, Ute; Walz, Christoph; Krueger, Renate; von Bernuth, Horst; Klein, Christoph; Icenogle, Joseph; Hauck, Fabian; Sullivan, Kathleen E. 分享 收藏
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The Ever-Increasing Array of Novel Inborn Errors of Immunity: an Interim Update by the IUIS Committee 不断增加的新的先天性免疫错误: IUIS委员会的临时更新 Tangye, Stuart G.; Al-Herz, Waleed; Bousfiha, Aziz; Cunningham-Rundles, Charlotte; Franco, Jose Luis; Holland, Steven M.; Klein, Christoph; Morio, Tomohiro; Oksenhendler, Eric; Picard, Capucine; Puel, Anne; Puck, Jennifer; Seppaenen, Mikko R. J.; Somech, Raz; Su, Helen C.; Sullivan, Kathleen E.; Torgerson, Troy R.; Meyts, Isabelle 分享 收藏
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