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Fabrizio De Benedetti

irccs ospedale pediatrico bambino gesù

76H指数
707论文数
2.3W被引数
收录论文 164
发表时间
Treatment approaches to macrophage activation syndrome in real life and priorities for future research: results from the international METAPHOR project巨噬细胞活化综合征的治疗方法与现实应用及未来研究重点:国际METAPHOR项目的研究结果
err2026-09-22
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PREAI
errFrancesco Baldo; Greta Rogani; Remco G.A. Erkens; Mao Mizuta; Claudia Bracaglia; Dirk Foell; Marco Gattorno; Marija Jelusic; Jordi Anton; Paul Brogan; Scott Canna; Shanmuganathan Chandrakasan; Randy Q. Cron; Fabrizio De Benedetti; Alexei Grom; Merav Heshin-Bekenstein; AnnaCarin Horne; Raju Khubchandani; Seza Ozen; Pierre Quartier; Angelo Ravelli; Masaki Shimizu; Grant Schulert; Christiaan Scott; Rashmi Sinha; Nicolino Ruperto; Joost F Swart; Sebastiaan Vastert; Francesca Minoia; The PReS MAS/sJIA Working Party and the Paediatric Rheumatology International Trial Organisation (PRINTO)
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AMETHYST: a Retrospective Cohort Study of Treatment Patterns and Outcomes in Patients With Glucocorticoid-refractory Macrophage Activation Syndrome Complicating Still's DiseaseAMETHYST:一项回顾性队列研究,探讨糖皮质激素难治性巨噬细胞活化综合征合并Still病的治疗模式与结局
err2026-09-07
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PREAI
errAlexei Grom MD; Jordi Antón MD; Edward M. Behrens MD; Corey Best MS, MBA; Norbert Blank MD, PhD; Josefin Blomkvist MS; Scott W. Canna MD; Sonia Carriquí MD; Shanmuganathan Chandrakasan MD; Andrew Danquah MS; Ngoc-Bao Duong MD; Brian D. Jamieson MD; Paivi Miettunen MD; Abiola Oladapo PhD; Sampath Prahalad MD; Pierre Quartier MD; Grant Schulert MD, PhD; Anna Stoltenberg PhL; Uwe Ullmann MD; Erika Van Nieuwenhove MD, PhD; Sebastiaan J. Vastert MD, PhD; Fabrizio De Benedetti MD, PhD
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Anti-CD19 CAR T cells for pediatric patients with treatment-refractory autoimmune diseasesAnti-CD19 CAR T细胞治疗难治性自身免疫性疾病的儿科患者
err2026-02-05
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PREAI
errMarco Becilli; Markus Metzler; Claudia Bracaglia; Rebecca Nicolai; Tobias Krickau; Francesca Del Bufalo; Chiara Rosignoli; Emiliano Marasco; Nora Naumann-Bartsch; Virginia Messia; Pietro Merli; Daria Pagliara; Mattia Algeri; Aurelio Secinaro; Maria Giuseppina Cefalo; Francesca Diomedi Camassei; Valentina Bertaina; Matilde Sinibaldi; Antonella Insalaco; Michael Aigner; Giovanna Leone; Giuseppina Li Pira; Monica Gunetti; Stefan Berg; Biagio De Angelis; Simon Völkl; Linda Hanssens; Fabian Müller; Andreas Mackensen; Concetta Quintarelli; Georg Schett; Fabrizio De Benedetti; Franco Locatelli
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Impaired Generation of High-Affinity Memory B Cells and Neutralizing Antibodies Against SARS-CoV-2 in Adolescents and Young Adults With Juvenile Idiopathic Arthritis Treated With Tumor Necrosis Factor Inhibitors青少年和年轻成年类风湿性关节炎患者在接受肿瘤坏死因子抑制剂治疗后,对SARS-CoV-2的高亲和力记忆B细胞和中和抗体的产生受损
err2026-01-11
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errAquilani, Angela; Marinaro, Francesca; Tarantino, Giusyda; Caiello, Ivan; Nobili, Lorenzo; Mortari, Eva Piano; Nicolai, Rebecca; Petrone, Maria Isabella; Castilletti, Concetta; Magni-manzoni, Silvia; De Benedetti, Fabrizio; Carsetti, Rita; Marasco, Emiliano
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Interleukin-18 levels are associated with disease course in patients with Still's disease treated with IL-1 inhibitors白细胞介素-18水平与接受IL-1抑制剂治疗的Still病患者的疾病病程相关。
err2025-12-15
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errMatteo Trevisan MD; Manuela Pardeo MD; Ivan Caiello BSc; Claudia Bracaglia MD; Arianna de Matteis MD; Valentina Matteo PhD; Elena Loricchio PhD; Fabrizio De Benedetti MD, PhD; Giusi Prencipe PhD
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Sarilumab in Polyarticular-Course Juvenile Idiopathic Arthritis: Dose-Finding and One-Year Analysis of a Phase 2b, Open-Label, Multicenter Study萨利鲁单抗在多关节型幼年特发性关节炎中的应用:一项IIb期、开放标签、多中心研究的剂量探索和一年分析
err2025-11-14
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errFabrizio De Benedetti; Inmaculada C. Penadés; Irina Nikishina; Ivan Foeldvari; Alberto J. Spindler; Anna Kozlova; Nadina Rubio-Pérez; Pierre Quartier; Zbigniew Żuber; Raul Barria; Daniel Clemente; Gabriel V. Cornejo; Katherine Marzan; Nancy Liu; Christine Xu; Stephen DiMartino; Angeliki Giannelou MD; Fei Cao-Ghoul; Bolanle Akinlade; Lydie Baret-Cormel
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Gene therapy supports long-term reconstitution of patient hematopoietic stem cells in deficiency of adenosine deaminase 2基因疗法支持腺苷脱氨酶2缺乏症患者造血干细胞的长期重建
err2025-10-30
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errChiara Rigamonti; Dimitri Bulté; Federica Barzaghi; Cristina Mesa-Nuñez; Luca Basso-Ricci; Emanuela Pettinato; Camilla Visconti; Sara Degl’Innocenti; Francesco Gazzo; Fabrizio Benedicenti; Sergio Arévalo; Pamela Quaranta; Francesca Sanvito; Roberta Caorsi; Francesca Schena; Michela Lupia; Silvia Federici; Antonella Insalaco; Fabrizio De Benedetti; Serena Scala; Maurizio Miano; Francesca Conti; Maria Pia Cicalese; Eugenio Montini; Marco Gattorno; Carlo Dufour; Alessandro Aiuti; Alessandra Mortellaro
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Musculoskeletal manifestations in children with inflammatory bowel disease: a multicenter cohort study (GASTROREUM study)炎症性肠病患儿的肌肉骨骼表现:一项多中心队列研究(GASTROREUM研究)
err2025-10-11
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errAdele Civino; Federico Diomeda; Romina Gallizzi; Marco Gattorno; Silvia Magni-Manzoni; Davide Montin; Gabriele Simonini; Giovanni Conti; Emanuela Del Giudice; Giovanni Filocamo; Fortunata Civitelli; Angela Miniaci; Serena Pastore; Francesco La Torre; Bianca Lattanzi; Angela Mauro; Lorenzo Mambelli; Patrizia Barone; Alma Nunzia Olivieri; Gianluca Vergine; Maria Cristina Maggio; Ilenia Floretta; Simona Campus; Luca Cantarini; Emanuela Sacco; Michela Cappella; Serena Arrigo; Giusyda Tarantino; Manuela Taurisano; Silvia Greco; Rossella Greco; Fabrizio De Benedetti; Francesca Bovis; Angelo Ravelli
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Genome-wide DNA methylation analysis identifies kidney epigenetic dysregulation in a cystinosis mouse model全基因组DNA甲基化分析鉴定出胱氨酸尿症小鼠模型中的肾脏表观遗传失调
err2025-08-21
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errM. N. Rossi; A. Ciolfi; V. Matteo; L. Pedace; C. Nardini; E. Loricchio; I. Caiello; F. Bellomo; A. Taranta; E. De Leo; M. Tartaglia; F. Emma; F. De Benedetti; E. Miele; G. Prencipe
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STING induces ZBP1-mediated necroptosis independently of TNFR1 and FADDSTING独立于TNFR1和FADD诱导ZBP1介导的坏死性凋亡
errNature
IF48.5
err2025-08-20
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PREAI
errKonstantinos Kelepouras; Julia Saggau; Debora Bonasera; Christine Kiefer; Federica Locci; Hassan Rakhsh-Khorshid; Louisa Grauvogel; Ana Beatriz Varanda; Martin Peifer; Elena Loricchio; Antonella Montinaro; Marijana Croon; Aleksandra Trifunovic; Giusi Prencipe; Antonella Insalaco; Fabrizio De Benedetti; Henning Walczak; Gianmaria Liccardi
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Understanding, predicting, and treating depression in pregnancy to improve mothers' and offspring's mental health outcomes: The HappyMums study了解,预测和治疗妊娠期抑郁症以改善母亲和后代的精神卫生结局: HappyMums研究
err2025-03-01
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errBiaggi, A.; Zonca, V; Anacker, C.; Begni, V.; Benedetti, F.; Bramante, A.; Braniecka, A.; Brenna, V; Bulgheroni, M.; Buss, C.; Cavaliere, L.; Cecil, C. A. M.; Couch, A. C.; de Barra, D.; El Marroun, H.; Entringer, S.; Grassi-Oliveira, R.; Jackowska, M.; Korosi, A.; Kwant, P. J. C.; Lahti, J.; Lekadir, K.; Mansuy, I.; Manuella, F.; Marizzoni, M.; Meyer, U.; Monk, C.; Rados, S. Nakic; Pariante, C. M.; Pollux, B. J. A.; Priestley, K.; Raikkonen, K.; Richetto, J.; Riva, M. A.; Rothmann, L. M.; Simonetti, V; Vai, B.; Vernon, A. C.; Zutic, M.; Cattaneo, A.
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Anifrolumab in Monogenic Lupus caused by TREX1 Mutation (vol 45, 60, 2025)Anifrolumab在由TREX1突变引起的单基因狼疮中的应用(卷45,期60,2025)
err2025-02-03
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errMoran-Alvarez, Patricia; Messia, Virginia; Matteo, Valentina; Soscia, Francesca; Prencipe, Giusi; De Benedetti, Fabrizio; Insalaco, Antonella
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Sirolimus as a possible treatment in cleavage-resistant RIPK1-induced autoinflammatory syndrome
err2025-02-01
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PREAI
errCattalini, Marco; Cortesi, Manuela; Baronio, Manuela; Insalaco, Antonella; de Benedetti, Fabrizio; Lougaris, Vassilios; Badolato, Raffaele
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Anifrolumab in Monogenic Lupus caused by TREX1 Mutation
err2024-12-30
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PREAI
errMoran-Alvarez, Patricia; Messia, Virginia; Matteo, Valentina; Soscia, Francesca; Prencipe, Giusi; De Benedetti, Fabrizio; Insalaco, Antonella
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Autologous CD19-Targeting CAR T Cells in a Patient With Refractory Juvenile Dermatomyositis难治性青少年皮肌炎患者的自体CD19-Targeting CAR T细胞
err2024-07-31
err5
PREAI
errNicolai, Rebecca; Merli, Pietro; Alvarez, Patricia Moran; Bracaglia, Claudia; Del Bufalo, Francesca; Marasco, Emiliano; Caiello, Ivan; Prencipe, Giusi; Algeri, Mattia; Cefalo, Maria G.; Becilli, Marco; Quintarelli, Concetta; Sinibaldi, Matilde; Hanssens, Linda; De Benedetti, Fabrizio; Locatelli, Franco
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The HyperPed-COVID international registry: Impact of age of onset, disease presentation and geographical distribution on the final outcome of MIS-C
err2024-07-01
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PREAI
errCaorsi, Roberta; Consolaro, Alessandro; Speziani, Camilla; Sozeri, Betul; Ulu, Kadir; Faugier-Fuentes, Enrique; Menchaca-Aguayo, Hector; Ozen, Seza; Sener, Seher; Rahman, Shahana Akhter; Islam, Mohammad Imnul; Haerynck, Filomeen; Simonini, Gabriele; Viviana Mastri, Mariel; Avcin, Tadej; Srsen, Sasa; Pedrosa Fernandes, Taciana de Albuquerque; Stanevicha, Valda; Vojinovic, Jelena; Sobh, Ali; Fingerhutova, Sarka; Minxova, Lenka; Gagro, Alenka; Fonseca, Adriana Rodrigues; Pandya, Devang; Varbanova, Boriana; Sanchez-Manubens, Judith; Ganeva, Margarita; Montin, Davide; Boyarchuk, Oksana; Minghini, Andrea; Bracaglia, Claudia; Brogan, Paul; Candotti, Fabio; Cattalini, Marco; Meyts, Isabelle; Minoia, Francesca; Taddio, Andrea; Wouters, Carine; De Benedetti, Fabrizio; Bovis, Francesca; Ravelli, Angelo; Ruperto, Nicolino; Gattorno, Marco; Bilginer, Yelda; Laila, Kamrul; Islam, Mohammed Mahbubul; Meertens, Bram; Hoste, Levi; Dehoorne, Joke; Schelstraete, Petra; Vandekerckhove, Kristof; Willems, Jef; Matthijs, Inge; Beretta, Giovanni Filocamo e Gisella Beatrice; Magalhaes, Claudia Saad; Chubata, Oksana; Ricci, Francesca; Vukovic, Antonija; Temelkova, Katya; Avramovic, Mojca Zajc; Emersic, Nina; Bizjak, Masa; Vesel, Tina; Rodrigues, Marta Felix; de Almeida, Rozana Gasparello; Lukjanovica, Kristine; Elnagdy, Marwa H.; Soliman, Ahmed; Terifajova, Eva; Brejchova, Ivana; Magner, Martin; Myrup, Charlotte; Vougiouka, Olga; Jelusic, Marija; La Torre, Francesco; Rigante, Donato; Maggio, Maria Cristina; Verdoni, Lucio; Rubio-Perez, Nadina; Vega Cornejo, Gabriel; Villarreal Trevino, Ana Victoria; Brito, Iva; Oliveira-Ramos, Filipa; Alexeeva, Ekaterina; Chasnyk, Vyacheslav; Arkachaisri, Thaschawee; Boyko, Yaryna; Vyzhga, Yulia; Samsonenko, Svitlana
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Defining Criteria for Disease Activity States in Systemic Juvenile Idiopathic Arthritis Based on the Systemic Juvenile Arthritis Disease Activity Score
err2024-06-11
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errRosina, Silvia; Rebollo-Gimenez, Ana I.; Tarantola, Letizia; Pistorio, Angela; Vyzhga, Yulia; El Miedany, Yasser; Lotfy, Hala M.; Abu-Shady, Hend; Eissa, Mervat; Osman, Naglaa S.; Hassan, Waleed; Mahgoub, Marwa Y.; Fouad, Nermeen A.; Mosa, Doaa M.; Adel, Yasmin; Mohamed, Sheren E. M.; Radwan, Ahmed R.; Abu-Zaid, Mohamed H.; Tabra, Samar A. A.; Shalaby, Radwa H.; Nasef, Samah I.; Khubchandani, Raju; Khan, Archana; Maldar, Naziya P.; Ozen, Seza; Bayindir, Yagmur; Alsuweiti, Motasem; Alzyoud, Raed; Almaaitah, Hiba; Vilaiyuk, Soamarat; Lerkvaleekul, Butsabong; Alexeeva, Ekaterina; Dvoryakovskaya, Tatyana; Kriulin, Ivan; Bracaglia, Claudia; Pardeo, Manuela; De Benedetti, Fabrizio; Licciardi, Francesco; Montin, Davide; Robasto, Francesca; Minoia, Francesca; Filocamo, Giovanni; Rossano, Martina; Simonini, Gabriele; Marrani, Edoardo; Abu-Rumeleih, Sarah; Kostik, Mikhail M.; Belozerov, Konstantin E.; Pal, Priyankar; Bathia, Jigna N.; Katsicas, Maria M.; Villarreal, Giselle; Marino, Achille; Costi, Stefania; Sztajnbok, Flavio; Silva, Rodrigo M.; Maggio, Maria C.; El-Ghoneimy, Dalia H.; El Owaidy, Rasha; Civino, Adele; Diomeda, Federico; Al-Mayouf, Sulaiman M.; Al-Sofyani, Fuad; Davidsone, Zane; Patrone, Elisa; Saad-Magalhaes, Claudia; Consolaro, Alessandro; Ravelli, Angelo
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