未登录 Systemic clinical-grade recombinant decorin reduces disease burden and fibrosis in advanced recessive dystrophic epidermolysis bullosa 系统性临床级重组 decorin 可减轻显性营养不良型大疱性表皮松解症的疾病负担和纤维化 Gretzmeier, Christine; Hang, Bing; Sengle, Gerhard; Phillips, Christopher; Buer, Ben; Fletcher, Sarah; Belov, Arseniy; Bleck, Gregory; Collins, Ian J.; Brinckmann, Jurgen; de Souza, Mark P.; Landy, Hal; Nystrom, Alexander 分享 收藏
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Extracellular matrix alterations in inflammatory skin diseases: emerging biomarkers and clinical implications 炎症性皮肤疾病中的细胞外基质改变:新兴生物标志物及其临床意义 Port, Helena; Andelic, Matej; Nystrom, Alexander; Haack, Aleksander Moldt; Kalogeropoulos, Konstantinos; Nielsen, Valdemar Wendelboe; van den Heuvel, Antonius Pieter; Bihlet, Asger Reinstrup; Thomsen, Simon Francis; Holm Nielsen, Signe 分享 收藏
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Advances in Extracellular Matrix-Associated Diagnostics and Therapeutics 细胞外基质相关诊断和治疗的研究进展 Karsdal, Morten; Cox, Thomas R.; Parker, Amelia L.; Willumsen, Nicholas; Sand, Jannie Marie Buelow; Jenkins, Gisli; Hansen, Henrik H.; Oldenburger, Anouk; Geillinger-Kaestle, Kerstin E.; Larsen, Anna Thorso; Black, Darcey; Genovese, Federica; Eckersley, Alexander; Heinz, Andrea; Nystroem, Alexander; Holm Nielsen, Signe; Bennink, Lucas; Johannsson, Lars; Bay-Jensen, Anne-Christine; Orange, Dana E.; Friedman, Scott; Ropke, Mads; Fiore, Vincent; Schuppan, Detlef; Rieder, Florian; Simona, Benjamin; Borthwick, Lee; Skarsfeldt, Mark; Wennbo, Haakan; Thakker, Paresh; Stoffel, Ruedi; Clarke, Graham W.; Kalluri, Raghu; Ruane, Darren; Zannad, Faiez; Mortensen, Joachim Hog; Sinkeviciute, Dovile; Sundberg, Fred; Coseno, Molly; Thudium, Christian; Croft, Adam P.; Khanna, Dinesh; Cooreman, Michael; Broermann, Andre; Leeming, Diana Julie; Mobasheri, Ali; Ricard-Blum, Sylvie 分享 收藏
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Safety and tolerability of losartan to treat recessive dystrophic epidermolysis bullosa in children (REFLECT): an open-label, single-arm, phase 1/2 trial Kiritsi, Dimitra; Schauer, Franziska; Gewert, Stella; Reineker, Katja; Reimer-Taschenbrecker, Antonia; Schwieger-Briel, Agnes; Ott, Hagen; Schmoor, Claudia; Grishina, Olga; Murrell, Dedee; Stiller, Brigitte; Zahn, Tobias; Nystroem, Alexander; Bruckner-Tuderman, Leena 分享 收藏
Dipeptidyl Peptidase-4-Mediated Fibronectin Processing Evokes a Profibrotic Extracellular Matrix Zeyer, Karina A.; Bornert, Olivier; Nelea, Valentin; Bao, Xinyi; Leytens, Alexandre; Sharoyan, Svetlana; Sengle, Gerhard; Antonyan, Alvard; Bruckner-Tuderman, Leena; Dengjel, Jorn; Reinhardt, Dieter P.; Nystrom, Alexander 分享 收藏
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Histone deacetylase inhibition mitigates fibrosis-driven disease progression in recessive dystrophic epidermolysis bullosa Primerano, Alessia; De Domenico, Emanuela; Cianfarani, Francesca; De Luca, Naomi; Floriddia, Giovanna; Teson, Massimo; Cristofoletti, Cristina; Cardarelli, Silvia; Scaglione, Giovanni Luca; Baldini, Enke; Cangelosi, Davide; Uva, Paolo; Sanchez, Jonathan Fernando Reinoso; Roubaty, Carole; Dengjel, Joern; Nystroem, Alexander; Mastroeni, Simona; Ulisse, Salvatore; Castiglia, Daniele; Odorisio, Teresa 分享 收藏
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Identification of PCPE-2 as the endogenous specific inhibitor of human BMP-1/tolloid-like proteinases Vadon-Le Goff, Sandrine; Tessier, Agnes; Napoli, Manon; Dieryckx, Cindy; Bauer, Julien; Dussoyer, Melissa; Lagoutte, Priscillia; Peyronnel, Celian; Essayan, Lucie; Kleiser, Svenja; Tueni, Nicole; Bettler, Emmanuel; Mariano, Natacha; Errazuriz-Cerda, Elisabeth; Fruchart Gaillard, Carole; Ruggiero, Florence; Becker-Pauly, Christoph; Allain, Jean-Marc; Bruckner-Tuderman, Leena; Nystroem, Alexander; Moali, Catherine 分享 收藏
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