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收藏Differential pathology of P102L-associated Gerstmann-Stäussler-Scheinker disease: exclusive presence of 8-kDa protease-resistant prion protein vs. co-existence of 8-kDa and type-1 protease-resistant prion protein, with a focus on codon 129 polymorphismP102L相关的Gerstmann-Stäussler-Scheinker疾病的差异病理学:仅存在8-kDa蛋白酶抗性朊病毒蛋白与8-kDa和类型1蛋白酶抗性朊病毒蛋白的共存,重点在于密码子129多态性
Noguchi, Hideko; Yoshimura, Motoi; Watanabe, Akihiro; Koyama, Sachiko; Sakurada, Naonori; Shijo, Masahiro; Kanemaru, Takaaki; Kai, Keita; Aishima, Shinichi; Koike, Haruki; Tsuboi, Yoshio; Sasagasako, Naokazu; Honda, Hiroyuki
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收藏Involvement of the nigrostriatal system in Gerstman-Straussler-Scheinker disease with the PRNP-P102L mutation
Ono, Natsuki; Suzuyama, Kohei; Minagawa, Hiromu; Uwatoko, Kiku; Yoshikawa, Masaaki; Ide, Toshihiro; Mitsuoka, Miyuki; Honda, Kazuo; Hirai, Tetsuyoshi; Otsuka, Takateru; Kai, Keita; Honda, Hiroyuki; Kitamoto, Tetsuyuki; Irie, Hiroyuki; Yukitake, Motohiro; Koike, Haruki
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收藏Altered expression of human myxovirus resistance protein a in amyotrophic lateral sclerosis
Honda, Hiroyuki; Sadashima, Shoko; Yoshimura, Motoi; Sakurada, Naonori; Koyama, Sachiko; Yagita, Kaoru; Hamasaki, Hideomi; Noguchi, Hideko; Arahata, Hajime; Sasagasako, Naokazu
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收藏Altered properties of amyloidogenic prion protein in genetic Creutzfeldt-Jakob disease with PRNP V180I mutation in response to pentosan polysulfate
Shijo, Masahiro; Yoshimura, Motoi; Omae, Tsuyoshi; Hashimoto, Go; Mizoguchi, Tadataka; Kuwashiro, Takahiro; Komori, Takashi; Tsuboi, Yoshio; Saito, Tomoko; Nakagawa, Masanori; Itoh, Kyoko; Honda, Hiroyuki
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收藏Mutated FUS in familial amyotrophic lateral sclerosis involves multiple hnRNPs in the formation of neuronal cytoplasmic inclusions家族性肌萎缩性侧索硬化症中突变的FUS涉及神经元细胞质包涵体形成中的多个hnRNPs
Honda, Hiroyuki; Yoshimura, Motoi; Arahata, Hajime; Yagita, Kaoru; Sadashima, Shoko; Hamasaki, Hideomi; Shijo, Masahiro; Koyama, Sachiko; Noguchi, Hideko; Sasagasako, Naokazu
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收藏Silence of resident microglia in GPI anchorless prion disease and activation of microglia in Gerstmann-Straussler-Scheinker disease and sporadic Creutzfeldt-Jakob disease
Noguchi, Hideko; Koyama, Sachiko; Yagita, Kaoru; Shijo, Masahiro; Matsuzono, Kosuke; Hamasaki, Hideomi; Kanemaru, Takaaki; Okamoto, Tsuyoshi; Kai, Keita; Aishima, Shinichi; Abe, Koji; Sasagasako, Naokazu; Honda, Hiroyuki
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收藏Chronological Changes in the Expression Pattern of Hippocampal Prion Proteins During Disease Progression in Sporadic Creutzfeldt-Jakob Disease MM1 Subtype
Yagita, Kaoru; Noguchi, Hideko; Koyama, Sachiko; Hamasaki, Hideomi; Komori, Takashi; Aishima, Shinichi; Kosaka, Takayuki; Ueda, Mitsuharu; Komohara, Yoshihiro; Watanabe, Akihiro; Sasagasako, Naokazu; Ninomiya, Toshiharu; Oda, Yoshinao; Honda, Hiroyuki
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收藏A Comparative Study of Site-Specific Distribution of Aging-Related Tau Astrogliopathy and Its Risk Factors Between Alzheimer Disease and Cognitive Healthy Brains: The Hisayama Study
Yagita, Kaoru; Honda, Hiroyuki; Ohara, Tomoyuki; Hamasaki, Hideomi; Koyama, Sachiko; Noguchi, Hideko; Mihara, Akane; Nakazawa, Taro; Hata, Jun; Ninomiya, Toshiharu; Iwaki, Toru
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收藏PCBP2 Is Downregulated in Degenerating Neurons and Rarely Observed in TDP-43-Positive Inclusions in Sporadic Amyotrophic Lateral Sclerosis
Yoshimura, Motoi; Honda, Hiroyuki; Sasagasako, Naokazu; Mori, Shinichiro; Hamasaki, Hideomi; Suzuki, Satoshi O.; Ishii, Takashi; Ninomiya, Toshiharu; Kira, Jun-Ichi; Iwaki, Toru
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收藏Prion Gene PRNP Y162X Truncation Mutation Can Induce a Refractory Esophageal Achalasia
Matsuzono, Kosuke; Kim, Younhee; Honda, Hiroyuki; Anan, Yuhei; Tsunoda, Masato; Amano, Yusuke; Fukusima, Noriyoshi; Iwaki, Toru; Kitamoto, Tetsuyuki; Fujimoto, Shigeru
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