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RAPID EARLY PROGRESSION IN GLIOBLASTOMA: A COMPREHENSIVE REVIEW OF CLINICAL, IMAGING AND HISTOPATHOLOGICAL FEATURES Waqar, Mueez; Roncaroli, Federico; O'leary, Claire; Forte, Gabriella; Wright, Jenny; Parikh, Shefali; Sudell, Lindsay; Coope, David; Djoukhadar, Ibrahim; Borst, Gerben 分享 收藏
Systemic immune challenge exacerbates neurodegeneration in a model of neurological lysosomal disease Mandolfo, Oriana; Parker, Helen; Aguado, Elia; Learmonth, Yuko Ishikawa; Liao, Ai Yin; O'Leary, Claire; Ellison, Stuart; Forte, Gabriella; Taylor, Jessica; Wood, Shaun; Searle, Rachel; Holley, Rebecca J.; Boutin, Herve; Bigger, Brian W. 分享 收藏
Intraparenchymal convection enhanced delivery of AAV in sheep to treat Mucopolysaccharidosis IIIC O'Leary, Claire; Forte, Gabriella; Mitchell, Nadia L.; Youshani, Amir Saam; Dyer, Adam; Wellby, Martin P.; Russell, Katharina N.; Murray, Samantha J.; Jolinon, Nelly; Jones, Simon A.; Stacey, Kevin; Davis, Daniel M.; Henckaerts, Els; Palmer, David N.; Kamaly-Asl, Ian; Bigger, Brian W. 分享 收藏
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Identification of novel peptide sequences to fuse to iduronate-2-sulfatase for the treatment of Hunter syndrome Wood, Shaun R.; Chaudrhy, Ahsan; Ellison, Stuart M.; Searle, Rachel; Forte, Gabriella; O'Leary, Claire; Gleitz, Helene; Liao, Aiyin; Holley, Rebecca; Bigger, Brian 分享 收藏
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Intrinsic Electrical Remodeling Underlies Atrioventricular Block in Athletes Mesirca, Pietro; Nakao, Shu; Nissen, Sarah Dalgas; Forte, Gabriella; Anderson, Cali; Trussell, Tariq; Li, Jue; Cox, Charlotte; Zi, Min; Logantha, Sunil; Yaar, Sana; Cartensen, Helena; Bidaud, Isabelle; Stuart, Luke; Soattin, Luca; Morris, Gwilym M.; Martins, Paula A. da Costa; Cartwright, Elizabeth J.; Oceandy, Delvac; Mangoni, Matteo E.; Jespersen, Thomas; Buhl, Rikke; Dobrzynski, Halina; Boyett, Mark R.; D'Souza, Alicia 分享 收藏
Genetic Ablation of G Protein-Gated Inwardly Rectifying K+ Channels Prevents Training-Induced Sinus Bradycardia Bidaud, Isabelle; D'Souza, Alicia; Forte, Gabriella; Torre, Eleonora; Greuet, Denis; Thirard, Steeve; Anderson, Cali; Chong, Antony Chung You; Torrente, Angelo G.; Roussel, Julien; Wickman, Kevin; Boyett, Mark R.; Mangoni, Matteo E.; Mesirca, Pietro 分享 收藏
Actinomycin D downregulates Sox2 and improves survival in preclinical models of recurrent glioblastoma 放线菌素d在复发性胶质母细胞瘤的临床前模型中下调Sox2并改善生存率 Taylor, Jessica T.; Ellison, Stuart; Pandele, Alina; Wood, Shaun; Nathan, Erica; Forte, Gabriella; Parker, Helen; Zindy, Egor; Elvin, Mark; Dickson, Alan; Williams, Kaye J.; Karabatsou, Konstantina; McCabe, Martin; McBain, Catherine; Bigger, Brian W. 分享 收藏
mTORC1 directly inhibits AMPK to promote cell proliferation under nutrient stress 营养胁迫下mTORC1直接抑制AMPK促进细胞增殖 Ling, Naomi X. Y.; Kaczmarek, Adrian; Hoque, Ashfaqul; Davie, Elizabeth; Ngoei, Kevin R. W.; Morrison, Kaitlin R.; Smiles, William J.; Forte, Gabriella M.; Wang, Tingting; Lie, Shervi; Dite, Toby A.; Langendorf, Christopher G.; Scott, John W.; Oakhill, Jonathan S.; Petersen, Janni 分享 收藏
Import of extracellular ATP in yeast and man modulates AMPK and TORC1 signalling Forte, Gabriella M.; Davie, Elizabeth; Lie, Shervi; Franz-Wachtel, Mirita; Ovens, Ashley J.; Wang, Tingting; Oakhill, Jonathan S.; Macek, Boris; Hagan, Iain M.; Petersen, Janni 分享 收藏
Translation factor mRNA granules direct protein synthetic capacity to regions of polarized growth Pizzinga, Mariavittoria; Bates, Christian; Lui, Jennifer; Forte, Gabriella; Mores-Polanco, Fabian; Linney, Emma; Knotkova, Barbora; Wilson, Beverley; Solari, Clara A.; Berchowitz, Luke E.; Portela, Paula; Ashe, Mark P. 分享 收藏
Non-myeloablative busulfan chimeric mouse models are less pro-inflammatory than head-shielded irradiation for studying immune cell interactions in brain tumours Youshani, A. Saam; Rowlston, Samuel; O'Leary, Claire; Forte, Gabriella; Parker, Helen; Liao, Aiyin; Telfer, Brian; Williams, Kaye; Kamaly-Asl, Ian D.; Bigger, Brian W. 分享 收藏
Improving brain delivery of adeno-associated viral gene therapy vectors for the treatment of MPS IIIC O'Leary, Claire; Forte, Gabriella; Mitchell, Nadia; Youshani, Amir Saam; Wellby, Martin; Russell, Katharina; Palmer, David; Henckaerts, Els; Asl, Ian Kamaly; Bigger, Brian 分享 收藏
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A type I interferon signature identifies bilateral striatal necrosis due to mutations in ADAR1 Livingston, John H.; Lin, Jean-Pierre; Dale, Russell C.; Gill, Deepak; Brogan, Paul; Munnich, Arnold; Kurian, Manju A.; Gonzalez-Martinez, Victoria; De Goede, Christian G. E. L.; Falconer, Alastair; Forte, Gabriella; Jenkinson, Emma M.; Kasher, Paul R.; Szynkiewicz, Marcin; Rice, Gillian I.; Crow, Yanick J. 分享 收藏
Synonymous Mutations in RNASEH2A Create Cryptic Splice Sites Impairing RNase H2 Enzyme Function in Aicardi-Goutieres Syndrome RNASEH2A中的同义突变会产生隐蔽的剪接位点,从而损害aicardi-goutieres综合征中的RNase H2酶功能 Rice, Gillian I.; Reijns, Martin A. M.; Coffin, Stephanie R.; Forte, Gabriella M. A.; Anderson, Beverley H.; Szynkiewicz, Marcin; Gornall, Hannah; Gent, David; Leitch, Andrea; Botella, Maria P.; Fazzi, Elisa; Gener, Blanca; Lagae, Lieven; Olivieri, Ivana; Orcesi, Simona; Swoboda, Kathryn J.; Perrino, Fred W.; Jackson, Andrew P.; Crow, Yanick J. 分享 收藏
Mutations in ADAR1 cause Aicardi-Goutieres syndrome associated with a type I interferon signature Rice, Gillian I.; Kasher, Paul R.; Forte, Gabriella M. A.; Mannion, Niamh M.; Greenwood, Sam M.; Szynkiewicz, Marcin; Dickerson, Jonathan E.; Bhaskar, Sanjeev S.; Zampini, Massimiliano; Briggs, Tracy A.; Jenkinson, Emma M.; Bacino, Carlos A.; Battini, Roberta; Bertini, Enrico; Brogan, Paul A.; Brueton, Louise A.; Carpanelli, Marialuisa; De Laet, Corinne; de Lonlay, Pascale; del Toro, Mireia; Desguerre, Isabelle; Fazzi, Elisa; Garcia-Cazorla, Angels; Heiberg, Arvid; Kawaguchi, Masakazu; Kumar, Ram; Lin, Jean-Pierre S-M; Lourenco, Charles M.; Male, Alison M.; Marques, Wilson, Jr.; Mignot, Cyril; Olivieri, Ivana; Orcesi, Simona; Prabhakar, Prab; Rasmussen, Magnhild; Robinson, Robert A.; Rozenberg, Flore; Schmidt, Johanna L.; Steindl, Katharina; Tan, Tiong Y.; van der Merwe, William G.; Vanderver, Adeline; Vassallo, Grace; Wakeling, Emma L.; Wassmer, Evangeline; Whittaker, Elizabeth; Livingston, John H.; Lebon, Pierre; Suzuki, Tamio; McLaughlin, Paul J.; Keegan, Liam P.; O'Connell, Mary A.; Lovell, Simon C.; Crow, Yanick J. 分享 收藏