未登录Weaning from mechanical ventilation during myasthenic crisis, a monocentric retrospective study肌无力危机期间从机械通气中断奶,单中心回顾性研究
Mazeraud, Aurelien; Sivanandamoorthy, Sivanthiny; Mancusi, Rossella; Clair, Bernard; Friedman, Diane; Fadel, Fouad; Maxime, Virginie; Legouy, Camille; Orlikowski, David; Sharshar, Tarek; Heming, Nicholas; Annane, Djillali
分享
收藏Identifying digital biomarkers for the self-monitoring of patients living with generalized myasthenia gravis: A proof of concept
Laforet, Pascal; Orlikowski, David; Nicolas, Guillaume; Prigent, Helene; Berling, Edouard; Gorin, Clarissa; Moreira, Ana Julia; Narcy, Juliette; Plaud, Angeline; Toure, Emma; Keller, Martin; Werneburg, Brian; Aras, Emrah; Benatar, Michael
分享
收藏Prognosis of Right Ventricular Systolic Dysfunction in Patients With Duchenne Muscular DystrophyDuchenne型肌营养不良患者右心室收缩功能障碍的预后
Fayssoil, Abdallah; Mansencal, Nicolas; Nguyen, Lee S.; Nardi, Olivier; Yaou, Rabah Ben; Leturcq, France; Amthor, Helge; Wahbi, Karim; Becane, Henri Marc; Lofaso, Frederic; Prigent, Helene; Bassez, Guillaume; Behin, Anthony; Stojkovic, Tanya; Fontaine, Bertrand; Duboc, Denis; Dubourg, Olivier; Clair, Bernard; Laforet, Pascal; Annane, Djillali; Orlikowski, David
分享
收藏Hypersensitivity infusion-associated reactions induced by enzyme replacement therapy in a cohort of patients with late-onset Pompe disease: An experience from the French Pompe Registry
Lessard, Lola E. R.; Tard, Celine; Salort-Campana, Emmanuelle; Sacconi, Sabrina; Behin, Anthony; Bassez, Guillaume; Orlikowski, David; Merle, Philippe; Nollet, Sylvain; Gallay, Laure; Berard, Frederic; Robinson, Philip; Bouhour, Francoise; Laforet, Pascal
分享
收藏Identifying Digital Biomarkers for the Self-Monitoring of Patients Living with Generalized Myasthenia gravis: a Proof of Concept
Laforet, Pascal; Orlikowski, David; Nicolas, Guillaume; Prigent, Helene; Berling, Edouard; N'Dah-Sekou, Ghislain; Gorin, Clarissa; Moreira, Ana Julia; Narcy, Juliette; Plaud, Angeline; Cuq, Emma Toure; Keller, Martin; Werneburg, Brian; Aras, Emrah; Benatar, Michael
分享
收藏A Restructured Hospital Into a One-Building Organization for COVID-19 Patients: A Resilient and Effective Response to the Pandemic将医院改组为新型冠状病毒肺炎患者的一站式组织: 对大流行的弹性和有效反应
Bessis, Simon; Dinh, Aurelien; Gautier, Sylvain; Davido, Benjamin; Levy, Jonathan; Lawrence, Christine; Lot, Anne-Sophie; Bensmail, Djamel; Rech, Celia; Farcy-Afif, Muriel; Bouchand, Frederique; de Truchis, Pierre; Herrmann, Jean-Louis; Barbot, Frederic; Orlikowski, David; Moine, Pierre; Perronne, Christian; Josseran, Loic; Prigent, Helene; Annane, Djillali
分享
收藏
分享
收藏Association between prophylactic angiotensin-converting enzyme inhibitors and overall survival in Duchenne muscular dystrophy-analysis of registry data预防性血管紧张素转换酶抑制剂与杜氏肌营养不良症总生存率之间的关联-注册数据分析
Porcher, Raphael; Desguerre, Isabelle; Amthor, Helge; Chabrol, Brigitte; Audic, Frederique; Rivier, Francois; Isapof, Arnaud; Tiffreau, Vincent; Campana-Salort, Emmanuelle; Leturcq, France; Tuffery-Giraud, Sylvie; Ben Yaou, Rabah; Annane, Djillali; Amedro, Pascal; Barnerias, Christine; Becane, Henri Marc; Behin, Anthony; Bonnet, Damien; Bassez, Guillaume; Cossee, Mireille; de La Villeon, Gregoire; Delcourte, Claire; Fayssoil, Abdallah; Fontaine, Bertand; Godart, Francois; Guillaumont, Sophie; Jaillette, Emmanuelle; Laforet, Pascal; Leonard-Louis, Sarah; Lofaso, Frederic; Mayer, Michele; Morales, Raul Juntas; Meune, Christophe; Orlikowski, David; Ovaert, Caroline; Prigent, Helene; Saadi, Malika; Sochala, Maximilien; Tard, Celine; Vaksmann, Guy; Walther-Louvier, Ulrike; Eymard, Bruno; Stojkovic, Tanya; Ravaud, Philippe; Duboc, Denis; Wahbi, Karim
分享
收藏
分享
收藏Early mechanical ventilation in patients with Guillain-Barre syndrome at high risk of respiratory failure: a randomized trial
Melone, Marie-Anne; Heming, Nicholas; Meng, Paris; Mompoint, Dominique; Aboab, Jerome; Clair, Bernard; Salomon, Jerome; Sharshar, Tarek; Orlikowski, David; Chevret, Sylvie; Annane, Djillali
分享
收藏The clinical, histologic, and genotypic spectrum ofSEPN1-related myopathy A case series
Villar-Quiles, Rocio N.; von Der Hagen, Maja; Metay, Corinne; Gonzalez, Victoria; Donkervoort, Sandra; Bertini, Enrico; Castiglioni, Claudia; Chaigne, Denys; Colomer, Jaume; Cuadrado, Maria Luz; de Visser, Marianne; Desguerre, Isabelle; Eymard, Bruno; Goemans, Nathalie; Kaindl, Angela; Lagrue, Emmanuelle; Lutschg, Jurg; Malfatti, Edoardo; Mayer, Michele; Merlini, Luciano; Orlikowski, David; Reuner, Ulrike; Salih, Mustafa A.; Schlotter-Weigel, Beate; Stoetter, Mechthild; Straub, Volker; Topaloglu, Haluk; Urtizberea, J. Andoni; van der Kooi, Anneke; Wilichowski, Ekkehard; Romero, Norma B.; Fardeau, Michel; Bonnemann, Carsten G.; Estournet, Brigitte; Richard, Pascale; Quijano-Roy, Susana; Schara, Ulrike; Ferreiro, Ana
分享
收藏Consensus-Based Care Recommendations for Pulmonologists Treating Adults with Myotonic Dystrophy Type 1
Boentert, Matthias; Cao, Michelle; Mass, Daphne; De Mattia, Elisa; Falcier, Elisa; Goncalves, Miguel; Holland, Venessa; Katz, Sherri Lynne; Orlikowski, David; Sannicolo, Giulia; Wijkstra, Peter; Hellerstein, Leah; Sansone, Valeria A.
分享
收藏
分享
收藏Risk factors for respiratory tract bacterial colonization in adults with neuromuscular or neurological disorders and chronic tracheostomy患有神经肌肉或神经系统疾病和慢性气管切开术的成年人呼吸道细菌定植的危险因素
Lepainteur, Margaux; Ogna, Adam; Clair, Bernard; Dinh, Aurelien; Tarragon, Catherine; Prigent, Helene; Davido, Benjamin; Barbot, Frederic; Vaugier, Isabelle; Afif, Muriel; Roux, Anne-Laure; Rottman, Martin; Orlikowski, David; Herrmann, Jean-Louis; Annane, Djillali; Lawrence, Christine
分享
收藏ACTN2 mutations cause Multiple structured Core Disease (MsCD)
Lornage, Xaviere; Romero, Norma B.; Grosgogeat, Claire A.; Malfatti, Edoardo; Donkervoort, Sandra; Marchetti, Michael M.; Neuhaus, Sarah B.; Foley, A. Reghan; Labasse, Clemence; Schneider, Raphael; Carlier, Robert Y.; Chao, Katherine R.; Medne, Livija; Deleuze, Jean-Francois; Orlikowski, David; Bonnemann, Carsten G.; Gupta, Vandana A.; Fardeau, Michel; Bohm, Johann; Laporte, Jocelyn
分享
收藏Echographic Assessment of Diaphragmatic Function in Duchenne Muscular Dystrophy from Childhood to Adulthood从儿童到成年的Duchenne肌营养不良症的diaphragm肌功能的超声评估
Fayssoil, Abdallah; Chaffaut, Cendrine; Ogna, Adam; Stojkovic, Tanya; Lamothe, Laure; Mompoint, Dominique; Meng, Paris; Prigent, Helene; Clair, Bernard; Behin, Anthony; Laforet, Pascal; Bassez, Guillaume; Carlier, Robert; Orlikowski, David; Amthor, Helge; Roy, Susana Quijano; Crenn, Pascal; Chevret, Sylvie; Eymard, Bruno; Lofaso, Frederic; Annane, Djillali
分享
收藏
分享
收藏
分享
收藏Physiological predictors of respiratory and cough assistance needs after extubation
Terzi, Nicolas; Lofaso, Frederic; Masson, Romain; Beuret, Pascal; Normand, Herve; Dumanowski, Edith; Falaize, Line; Sauneuf, Bertrand; Daubin, Cedric; Brunet, Jennifer; Annane, Djillali; Parienti, Jean-Jacques; Orlikowski, David
分享
收藏
分享
收藏