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收藏Single-cell multiomics reveals the interplay of clonal evolution and cellular plasticity in hepatoblastoma
Roehrig, Amelie; Hirsch, Theo Z.; Pire, Aurore; Morcrette, Guillaume; Gupta, Barkha; Marcaillou, Charles; Imbeaud, Sandrine; Chardot, Christophe; Gonzales, Emmanuel; Jacquemin, Emmanuel; Sekiguchi, Masahiro; Takita, Junko; Nagae, Genta; Hiyama, Eiso; Guerin, Florent; Fabre, Monique; Aerts, Isabelle; Taque, Sophie; Laithier, Veronique; Branchereau, Sophie; Guettier, Catherine; Brugieres, Laurence; Fresneau, Brice; Zucman-Rossi, Jessica; Letouze, Eric
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收藏Mutational signature, cancer driver genes mutations and transcriptomic subgroups predict hepatoblastoma survival
Pire, Aurore; Hirsch, Theo Z.; Morcrette, Guillaume; Imbeaud, Sandrine; Gupta, Barkha; Pilet, Jill; Cornet, Marianna; Fabre, Monique; Guettier, Catherine; Branchereau, Sophie; Brugieres, Laurence; Guerin, Florent; Laithier, Veronique; Coze, Carole; Nagae, Genta; Hiyama, Eiso; Laurent-Puig, Pierre; Rebouissou, Sandra; Sarnacki, Sabine; Chardot, Christophe; Capitom, Carmen; Faure-Conter, Cecile; Aerts, Isabelle; Taque, Sophie; Fresneau, Brice; Zucman-Rossi, Jessica
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收藏Modelling the impact of liver regeneration on hepatoblastoma patient-derived-xenograft tumor growth
Cornet, Marianna; Brulle-Soumare, Laura; Bisio, Valeria; Deas, Olivier; Mussini, Charlotte; Guettier, Catherine; Fabre, Monique; Pigazzi, Martina; Judde, Jean-Gabriel; Tordjmann, Thierry; Branchereau, Sophie; Cairo, Stefano
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收藏Preneoplastic liver colonization by 11p15.5 altered mosaic cells in young children with hepatoblastoma11 p15.5改变的镶嵌细胞在肝母细胞瘤幼儿中的肿瘤前肝脏定植
Pilet, Jill; Hirsch, Theo Z.; Gupta, Barkha; Roehrig, Amelie; Morcrette, Guillaume; Pire, Aurore; Letouze, Eric; Fresneau, Brice; Taque, Sophie; Brugieres, Laurence; Branchereau, Sophie; Chardot, Christophe; Aerts, Isabelle; Sarnacki, Sabine; Fabre, Monique; Guettier, Catherine; Rebouissou, Sandra; Zucman-Rossi, Jessica
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收藏Cystic fibrosis-related liver disease: Clinical presentations, diagnostic and monitoring approaches in the era of CFTR modulator therapies囊性纤维化相关肝病: CFTR调节剂治疗时代的临床表现,诊断和监测方法
Dana, Jeremy; Debray, Dominique; Beaufrere, Aurelie; Hillaire, Sophie; Fabre, Monique; Reinhold, Caroline; Baumert, Thomas F.; Berteloot, Laureline; Vilgrain, Valerie
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收藏Integrated Genomic Analysis Identifies Driver Genes and Cisplatin-Resistant Progenitor Phenotype in Pediatric Liver Cancer整合基因组分析确定小儿肝癌的驱动基因和顺铂耐药祖细胞表型
Hirsch, Theo Z.; Pilet, Jill; Morcrette, Guillaume; Roehrig, Amelie; Monteiro, Benedict J. E.; Molina, Laura; Bayard, Quentin; Trepo, Eric; Meunier, Lea; Caruso, Stefano; Renault, Victor; Deleuze, Jean-Francois; Fresneau, Brice; Chardot, Christophe; Gonzales, Emmanuel; Jacquemin, Emmanuel; Guerin, Florent; Fabre, Monique; Aerts, Isabelle; Taque, Sophie; Laithier, Veronique; Branchereau, Sophie; Guettier, Catherine; Brugieres, Laurence; Rebouissou, Sandra; Letouze, Eric; Zucman-Rossi, Jessica
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收藏Epigenetic footprint enables molecular risk stratification of hepatoblastoma with clinical implications
Carrillo-Reixach, Juan; Torrens, Laura; Simon-Coma, Marina; Royo, Laura; Domingo-Sabat, Montserrat; Abril-Fornaguera, Jordi; Akers, Nicholas; Sala, Margarita; Ragull, Sonia; Arnal, Magdalena; Villalmanzo, Nuria; Cairo, Stefano; Villanueva, Alberto; Kappler, Roland; Garrido, Marta; Guerra, Laura; Sabado, Constantino; Guillen, Gabriela; Mallo, Mar; Pineyro, David; Vazquez-Vitali, Maria; Kuchuk, Olga; Elena Mateos, Maria; Ramirez, Gema; Lopez Santamaria, Manuel; Mozo, Yasmina; Soriano, Aroa; Grotzer, Michael; Branchereau, Sophie; Garcia de Andoin, Nagore; Lopez-Ibor, Blanca; Lopez-Almaraz, Ricardo; Antonio Salinas, Jose; Torres, Barbara; Hernandez, Francisco; Javier Uriz, Jose; Fabre, Monique; Blanco, Julia; Paris, Claudia; Bajciova, Viera; Laureys, Genevieve; Masnou, Helena; Clos, Ariadna; Belendez, Cristina; Guettier, Catherine; Sumoy, Lauro; Planas, Ramon; Jorda, Mireia; Nonell, Lara; Czauderna, Piotr; Morland, Bruce; Sia, Daniela; Losic, Bojan; Buendia, Marie Annick; Rosa Sarrias, Maria; Llovet, Josep M.; Armengol, Carolina
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收藏APC germline hepatoblastomas demonstrate cisplatin-induced intratumor tertiary lymphoid structures
Morcrette, Guillaume; Hirsch, Theo Z.; Badour, Elise; Pilet, Jill; Caruso, Stefano; Calderaro, Julien; Martin, Yoann; Imbeaud, Sandrine; Letouze, Eric; Rebouissou, Sandra; Branchereau, Sophie; Taque, Sophie; Chardot, Christophe; Guettier, Catherine; Scoazec, Jean-Yves; Fabre, Monique; Brugieres, Laurence; Zucman-Rossi, Jessica
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收藏New insights into diagnosis and therapeutic options for proliferative hepatoblastoma
Hooks, Katarzyna B.; Audoux, Jerome; Fazli, Helena; Lesjean, Sarah; Ernault, Tony; Dugot-Senant, Nathalie; Leste-Lasserre, Thierry; Hagedorn, Martin; Rousseau, Benoit; Danet, Coralie; Branchereau, Sophie; Brugieres, Laurence; Taque, Sophie; Guettier, Catherine; Fabre, Monique; Rullier, Anne; Buendia, Marie-Annick; Commes, Therese; Grosset, Christophe F.; Raymond, Anne-Aurelie
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收藏CCDC115-CDG: A new rare and misleading inherited cause of liver disease
Girard, Muriel; Poujois, Aurelia; Fabre, Monique; Lacaille, Florence; Debray, Dominique; Rio, Marlene; Fenaille, Francois; Cholet, Sophie; Ruel, Coralie; Causse, Elizabeth; Selves, Janick; Bridoux-Henno, Laure; Woimant, France; Dupre, Thierry; Vuillaumier-Barrot, Sandrine; Seta, Nathalie; Alric, Laurent; de Lonlay, Pascale; Bruneel, Arnaud
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收藏Contrast harmonic EUS for the prediction of pancreatic neuroendocrine tumor aggressiveness (with videos)
Palazzo, Maxime; Napoleon, Bertrand; Gincul, Rodica; Pioche, Mathieu; Pujol, Bertrand; Lefort, Christine; Fumex, Fabien; Hautefeuille, Vincent; Fabre, Monique; Cros, Jerome; Felce, Michele; Couvelard, Anne; Sauvanet, Alain; Levy, Philippe; Ruszniewski, Philippe; Palazzo, Laurent
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收藏Type I interferon-mediated autoinflammation due to DNase II deficiency
Rodero, Mathieu P.; Tesser, Alessandra; Bartok, Eva; Rice, Gillian I.; Della Mina, Erika; Depp, Marine; Beitz, Benoit; Bondet, Vincent; Cagnard, Nicolas; Duffy, Darragh; Dussiot, Michael; Fremond, Marie-Louise; Gattorno, Marco; Guillem, Flavia; Kitabayashi, Naoki; Porcheray, Fabrice; Rieux-Laucat, Frederic; Seabra, Luis; Uggenti, Carolina; Volpi, Stefano; Zeef, Leo A. H.; Alyanakian, Marie-Alexandra; Beltrand, Jacques; Bianco, Anna Monica; Boddaert, Nathalie; Brouzes, Chantal; Candon, Sophie; Caorsi, Roberta; Charbit, Marina; Fabre, Monique; Faletra, Flavio; Girard, Muriel; Harroche, Annie; Hartmann, Evelyn; Lasne, Dominique; Marcuzzi, Annalisa; Neven, Benedicte; Nitschke, Patrick; Pascreau, Tiffany; Pastore, Serena; Picard, Capucine; Picco, Paolo; Piscianz, Elisa; Polak, Michel; Quartier, Pierre; Rabant, Marion; Stocco, Gabriele; Taddio, Andrea; Uettwiller, Florence; Valencic, Erica; Vozzi, Diego; Hartmann, Gunther; Barchet, Winfried; Hermine, Olivier; Bader-Meunier, Brigitte; Tommasini, Alberto; Crow, Yanick J.
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收藏MicroRNA Therapy Inhibits Hepatoblastoma Growth In Vivo by Targeting β-Catenin and Wnt Signaling
Indersie, Emilie; Lesjean, Sarah; Hooks, Katarzyna B.; Sagliocco, Francis; Ernault, Tony; Cairo, Stefano; Merched-Sauvage, Maria; Rullier, Anne; Le Bail, Brigitte; Taque, Sophie; Grotzer, Michael; Branchereau, Sophie; Guettier, Catherine; Fabre, Monique; Brugieres, Laurence; Hagedorn, Martin; Buendia, Marie-Annick; Grosset, Christophe F.
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收藏Molecular Classification of Hepatocellular Adenoma Associates With Risk Factors, Bleeding, and Malignant Transformation
Nault, Jean-Charles; Couchy, Gabrielle; Balabaud, Charles; Morcrette, Guillaume; Caruso, Stefano; Blanc, Jean-Frederic; Bacq, Yannick; Calderaro, Julien; Paradis, Valerie; Ramos, Jeanne; Scoazec, Jean-Yves; Gnemmi, Viviane; Sturm, Nathalie; Guettier, Catherine; Fabre, Monique; Savier, Eric; Chiche, Laurence; Labrune, Philippe; Selves, Janick; Wendum, Dominique; Pilati, Camilla; Laurent, Alexis; De Muret, Anne; Le Bail, Brigitte; Rebouissou, Sandra; Imbeaud, Sandrine; Bioulac-Sage, Paulette; Letouze, Eric; Zucman-Rossi, Jessica
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收藏Efficacy of the Janus kinase 1/2 inhibitor ruxolitinib in the treatment of vasculopathy associated with TMEM173-activating mutations in 3 children
Fremond, Marie-Louise; Rodero, Mathieu Paul; Jeremiah, Nadia; Belot, Alexandre; Jeziorski, Eric; Duffy, Darragh; Bessis, Didier; Cros, Guilhem; Rice, Gillian I.; Charbit, Bruno; Hulin, Anne; Khoudour, Nihel; Caballero, Consuelo Modesto; Bodemer, Christine; Fabre, Monique; Berteloot, Laureline; Le Bourgeois, Muriel; Reix, Philippe; Walzer, Thierry; Moshous, Despina; Blanche, St Ephane; Fischer, Alain; Bader-Meunier, Brigitte; Rieux-Laucat, Frederic; Crow, Yanick Joseph; Neven, Benedicte
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收藏DCDC2 Mutations Cause Neonatal Sclerosing Cholangitis
Girard, Muriel; Bizet, Albane A.; Lachaux, Alain; Gonzales, Emmanuel; Filhol, Emilie; Collardeau-Frachon, Sophie; Jeanpierre, Cecile; Henry, Charline; Fabre, Monique; Viremouneix, Loic; Galmiche, Louise; Debray, Dominique; Bole-Feysot, Christine; Nitschke, Patrick; Pariente, Daniele; Guettier, Catherine; Lyonnet, Stanislas; Heidet, Laurence; Bertholet, Aurelia; Jacquemin, Emmanuel; Henrion-Caude, Alexandra; Saunier, Sophie
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收藏Patient- Derived Mouse Xenografts From Pediatric Liver Cancer Predict Tumor Recurrence and Advise Clinical Management
Nicolle, Delphine; Fabre, Monique; Simon-Coma, Marina; Gorse, Aurore; Kappler, Roland; Nonell, Lara; Mallo, Mar; Haidar, Hazar; Deas, Olivier; Mussini, Charlotte; Guettier, Catherine; Redon, Marie-Jose; Brugieres, Laurence; Ghigna, Maria Rosa; Fadel, Elie; Galmiche-Rolland, Louise; Chardot, Christophe; Judde, Jean-Gabriel; Armengol, Carolina; Branchereau, Sophie; Cairo, Stefano
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收藏Feasibility and Diagnostic Accuracy of Supersonic Shear-Wave Elastography for the Assessment of Liver Stiffness and Liver Fibrosis in Children: A Pilot Study of 96 Patients
Franchi-Abella, Stephanie; Corno, Lucie; Gonzales, Emmanuel; Antoni, Guillemette; Fabre, Monique; Ducot, Beatrice; Pariente, Daniele; Gennisson, Jean-Luc; Tanter, Mickael; Correas, Jean-Michel
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收藏NOSOLOGY AND MOLECULAR CLASSIFICATION OF HEPATOCELLULAR ADENOMAS
Nault, J. C.; Couchy, G.; Bioulac-Sage, P.; Bacq, Y.; Calderaro, J.; Paradis, V.; Ramos, J.; Scoazec, J. -Y.; Leteurtre, E.; Sturm, N.; Guettier, C.; Fabre, M.; Savier, E.; Chiche, L.; Labrune, P.; Selves, J.; Wendum, D.; Morcrette, G.; Gelabale, E.; Pilati, C.; Laurent, A.; De Muret, A.; Blanc, J. -F.; Le Bail, B.; Imbeaud, S.; Balabaud, C.; Rebouissou, S.; Zucman-Rossi, J.
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