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Andrew R. Gennery

universites de strasbourg etablissements associes

88H指数
629论文数
2.7W被引数
收录论文 250
发表时间
Current Usage of Extracorporeal Photopheresis in Solid Organ Transplantations in Europe: A Narrative Review
err2025-11-03
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errOAAI
errCashmore, Sarah-Jane; Barten, Markus Johannes; Diekmann, Fritz; Epailly, Eric; Fisher, Andrew J.; Gennery, Andrew R.; Gibbons, Ben; Gokler, Johannes; Guest, Julie; Heng, Anne-Elisabeth; Hutchinson, James A.; Rampino, Teresa; Vos, Robin; Potena, Luciano
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Correction to: Self-reported Clinical Outcomes and Quality of Life in Agammaglobulinemia: the Importance of an Early Diagnosis更正:Agammaglobulinemia患者自报的临床结局和生活质量:早期诊断的重要性
err2025-10-09
err0
errOAAI
errMaartje Blom; Annelotte J. Duintjer; Mahnaz Jamee; Melanie de Gier; Markéta Bloomfield; Adam Klocperk; Pavlina Kralickova; Neslihan E. Karaca; Oksana Boyarchuk; Peter Čižnár; Miloš Jeseňák; Svetlana Sharapova; Ekaterina Skopovets; Luis I. Gonzalez-Granado; Serena Palmeri; Stefano Volpi; Andrea Martin Nalda; Sonia Rodriguez Tello; Pere Soler-Palacín; Hassan Abolhassani; Federica Pulvirenti; Bianca Cinicola; Uwe Wintergerst; Godelieve J. de Bree; J. Merlijn van den Berg; Helen L. Leavis; Clementien Vermont; Virgil A.S.H. Dalm; Koen van Aerde; Stefanie Henriet; Hetty Jolink; Judith Potjewijd; Arjan Lankester; Chandoshi Rhea Mukherjee; Dagmar Berghuis; Małgorzata Pac; Benjamin M.J. Shillitoe; Andrew R. Gennery; Mirjam van der Burg
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Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis免疫性先天错误中的死亡率及死亡原因:一项系统综述和荟萃分析
err2025-09-27
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PREAI
errSaba Fekrvand; Zahra Hamidi Esfahani; Mohammadmehdi Yarahmadi; Ali Saeedi-Boroujeni; Helia Salehi; Ali Hakimelahi; Amir Almasi-Hashiani; Mahshid Rahmati; Sanaz Afshar-Ghasemlou; Najmeh Nameh Goshay Fard; Fateme Tarighat Monfared; Ehsan Khoshnezhad Afkham; Nazanin Fathi; Tannaz Moeini Shad; Fateme Babaha; Farzad Nazari; Matineh Nirouei; Amir Salehi Farid; Negin Sanadgol; Hosein Rafiemanesh; Mahsa Yousefpour Marzbali; Gholamreza Hassanpour; Peter Olbrich; Antonio Condino-Neto; Tomohiro Morio; Andrew R. Gennery; Isabelle Meyts; Hans D. Ochs; Hassan Abolhassani; Nima Rezaei; Reza Yazdani
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OMNImet®•GUT collection kit supports sample collection and ambient temperature preservation of faecal short chain fatty acidsOMNImet®•GUT采集试剂盒支持粪便短链脂肪酸的样本采集和常温保存
err2025-09-26
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PREAI
errJemma Cleminson; Caroline Kerbiriou; Shona McKirdy; Lauren Beck; David I. Campbell; Andrew R. Gennery; Janet E. Berrington; Konstantinos Gerasimidis; Christopher J. Stewart
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Hematopoietic stem-cell transplantation for Purine nucleoside phosphorylase deficiency: an EBMT-IEWP retrospective study嘌呤核苷磷酸化酶缺乏症的血细胞干细胞移植:一项EBMT-IEWP回顾性研究
errBlood
IF23.1
err2025-09-24
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errOAAI
errUli S. Herrmann; Matthias Felber; Austen Worth; Sule Haskologlu; Figen Dogu; Victor A. Lewis; Brigitte Strahm; Andreas Groll; Andrew R. Gennery; Fabian Hauck; Robert Wynn; Mary Coussons; Isabelle Meyts; Caroline Lindemans; Victoria Bordon; Robbert G. M. Bredius; Jörn-Sven Kühl; Mirjam Völler; Felix Zirngibl; Irina Zaidman; Alexandra Laberko; Ulrike Zeilhofer; Mathias Hauri-Hohl; Arjan Lankester; Aydan Ikinciogullari; Gregory M.T. Guilcher; Annette Hackenberg; Akif Yeşilipek; Graham Davies; Michael Hershfield; Suhag H. Parikh; Patrick Gilbert; Michael H. Albert; Ansgar S. Schütz; Manfred Hönig; Bénédicte Neven; Tayfun Güngör
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Self-reported Clinical Outcomes and Quality of Life in Agammaglobulinemia: the Importance of an Early Diagnosis自报的临床结局和生活质量在无丙种球蛋白血症中的研究:早期诊断的重要性
err2025-08-25
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errOAAI
errMaartje Blom; Annelotte J. Duintjer; Mahnaz Jamee; Melanie de Gier; Markéta Bloomfield; Adam Klocperk; Pavlina Kralickova; Neslihan E. Karaca; Oksana Boyarchuk; Peter Čižnár; Miloš Jeseňák; Svetlana Sharapova; Ekaterina Skopovets; Luis I. Gonzalez-Granado; Serena Palmeri; Stefano Volpi; Andrea Martin Nalda; Sonia Rodriguez Tello; Pere Soler Palacín; Hassan Abolhassani; Federica Pulvirenti; Bianca Cinicola; Uwe Wintergerst; Godelieve J. de Bree; J. Merlijn van den Berg; Helen L. Leavis; Clementien Vermont; Virgil A.S.H. Dalm; Koen van Aerde; Stefanie Henriet; Hetty Jolink; Judith Potjewijd; Arjan Lankester; Chandoshi Rhea Mukherjee; Dagmar Berghuis; Małgorzata Pac; Benjamin M.J. Shillitoe; Andrew R. Gennery; Mirjam van der Burg
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Allogeneic hematopoietic stem cell transplantation for STAT3 hyper-IgE syndrome: a worldwide study异基因造血干细胞移植治疗STAT3高IgE综合征:一项全球性研究
err2025-06-23
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errOAAI
errChristo Tsilifis; Johannes Raedler; Joanna Renke; Michael Medinger; Alexandra Laberko; Ásgeir Haraldsson; Niraj Patel; Peter Ciznar; Melanie Wong; Steven J. Keogh; Paul Gray; Richard Mitchell; Venetia Bigley; Suzanne Elcombe; Fabian Hauck; Michael H. Albert; Eleni Tholouli; Archana Herwadkar; Shuayb Elkhalifa; Chris Kosmidis; Giorgio Callisti; Lauri M. Burroughs; Karin Chen; Ben Carpenter; Thomas A. Fox; Emma C. Morris; Ramya Uppuluri; Revathi Raj; Masakatsu Yanagimachi; Emilie P. Buddingh; Christina Oikonomopoulou; Corina Gonzalez; Dimana Dimitrova; Jennifer A. Kanakry; Danielle Arnold; Sung-Yun Pai; Mary A. Slatter; Mark S. Pearce; Austen Worth; Alexandra F. Freeman; Andrew R. Gennery
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Gut microbiome in paediatric short bowel syndrome: a systematic review and sequencing re-analysis儿童短肠综合征中的肠道微生物组:一项系统综述和测序再分析
err2025-05-07
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errOAAI
errCleminson, Jemma S.; Young, Gregory R.; Campbell, David I.; Campbell, Fiona; Gennery, Andrew R.; Berrington, Janet E.
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Outcomes of Hematopoietic Stem Cell Transplantation in 5 Patients with Autosomal Recessive RIPK1-Deficiency造血干细胞移植治疗5例常染色体隐性RIPK1-Deficiency的疗效分析
err2025-01-06
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errOAAI
errWalsh, Rebecca B.; Mcnaughton, Peter; Nademi, Zohreh; Laberko, Alexandra; Balashov, Dmitry; Al-Mousa, Hamoud; Arkwright, Peter D.; Wynn, Robert F.; Flood, Terry; Williams, Eleri; Cant, Andrew; Abinun, Mario; Hambleton, Sophie; Slatter, Mary; Gennery, Andrew R.; Lum, Su Han; Owens, Stephen
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Recommendations for Transitioning Young People with Primary Immunodeficiency Disorders and Autoinflammatory Diseases to Adult Care将患有原发性免疫缺陷病和自身炎症性疾病的年轻人转变为成人护理的建议
err2024-12-17
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errOAAI
errIsrani, Muskan; Alderson, Eliska; Mahlaoui, Nizar; Obici, Laura; Rossi-Semerano, Linda; Lachmann, Helen; Avramovic, Mojca Zajc; Guffroy, Aurelien; Dalm, Virgil; Rimmer, Rachel; Solis, Leire; Villar, Carlota; Gennery, Andrew R.; Skeffington, Stephanie; Nordin, Julia; Warnatz, Klaus; Korganow, Anne-Sophie; Anton, Jordi; Cattalini, Marco; Berg, Stefan; Soler-Palacin, Pere; Campbell, Mari; Burns, Siobhan O.; ESID Clinical Working Party, Ann; ERN RITA Transition Working Grp Consortium, Anna
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European Society for Immunodeficiencies guidelines for the management of patients with congenital athymia
err2024-12-01
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errOAAI
errKreins, Alexandra Y.; Dhalla, Fatima; Flinn, Aisling M.; Howley, Evey; Ekwall, Olov; Villa, Anna; Staal, Frank J. T.; Anderson, Graham; Gennery, Andrew R.; Hollander, Georg A.; Davies, E. Graham
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Hematopoietic stem cell transplantation for CTLA-4 insufficiency across Europe: A European Society for Blood and Marrow Transplantation Inborn Errors Working Party study
err2024-12-01
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errOAAI
errTsilifis, Christo; Speckmann, Carsten; Lum, Su Han; Fox, Thomas A.; Soler, Adriana Margarit; Mozo, Yasmina; Corral, Dolores; Ewins, Anna-Maria; Hague, Rosie; Oikonomopoulou, Christina; Kalwak, Krzysztof; Drabko, Katarzyna; Wynn, Robert; Morris, Emma C.; Elcombe, Suzanne; Bigley, Venetia; Lougaris, Vassilios; Malagola, Michele; Hauck, Fabian; Sedlacek, Petr; Laberko, Alexandra; Tjon, Jennifer M. L.; Buddingh, Emilie P.; Wehr, Claudia; Grimbacher, Bodo; Gennery, Andrew R.; Lankester, Arjan C.; Albert, Michael H.; Neven, Benedicte; Slatter, Mary A.
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Outcomes of X-Linked Agammaglobulinaemia PatientsX连锁无丙种球蛋白血症患者的预后情况
err2024-11-14
err0
PREAI
errShillitoe, Ben; Duque, Jaime S. Rosa; Lai, Sophie H. Y.; Lau, Tsun Ming; Chan, Jeffery C. H.; Bourne, Helen; Stroud, Catherine; Flood, Terry; Buckland, Matthew; Ip, Winnie; Worth, Austen; Hackett, Scott; Herwadkar, Archana; Coulter, Tanya; Blaney, Catherine; Jolles, Stephen; Garcez, Tomaz; Moya, Eduardo; Faust, Saul; Pearce, Mark S.; Lau, Yu Lung; Gennery, Andrew R.
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Hematopoietic Stem Cell Transplantation for C1q Deficiency: A Study on Behalf of the EBMT Inborn Errors Working Party
err2024-10-29
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errOAAI
errBuso, Helena; Adam, Etai; Arkwright, Peter D.; Bhattad, Sagar; Hamidieh, Amir Ali; Behfar, Maryam; Belot, Alexandre; Benezech, Sarah; Chan, Alice Y.; Crow, Yanick J.; Dvorak, Christopher C.; Flinn, Aisling M.; Kapoor, Urvi; Lankester, Arjan; Kobayashi, Masao; Matsumura, Risa; Mottaghipisheh, Hadi; Okada, Satoshi; Ouachee, Marie; Parvaneh, Nima; Ramprakash, Stalin; Satwani, Prakash; Sharafian, Samin; Triaille, Clement; Wynn, Robert F.; Movahedi, Nasim; Ziaee, Vahid; Williams, Eleri; Slatter, Mary; Gennery, Andrew R.
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Hereditary C1q Deficiency is Associated with Type 1 Interferon-Pathway Activation and a High Risk of Central Nervous System Inflammation
err2024-08-28
err2
errOAAI
errTriaille, Clement; Rao, Neha Mohan; Rice, Gillian I.; Seabra, Luis; Sutherland, Fraser J. H.; Bondet, Vincent; Duffy, Darragh; Gennery, Andrew R.; Fournier, Benjamin; Bader-Meunier, Brigitte; Troedson, Christopher; Cleary, Gavin; Buso, Helena; Dalby-Payne, Jacqueline; Ranade, Prajakta; Jansen, Katrien; De Somer, Lien; Fremond, Marie-Louise; Chavan, Pallavi Pimpale; Wong, Melanie; Dale, Russell C.; Wouters, Carine; Quartier, Pierre; Khubchandani, Raju; Crow, Yanick J.
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Allogeneic Hematopoietic Stem Cell Transplantation in Immunodeficiency-Centromeric Instability-Facial Dysmorphism (ICF) Syndrome: an EBMT/ESID Inborn Errors Working Party Study
err2024-08-21
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errOAAI
errBerghuis, Dagmar; Mehyar, Lubna S.; Abu-Arja, Rolla; Albert, Michael H.; Barnum, Jessie L.; von Bernuth, Horst; Elfeky, Reem; Lewalle, Philippe; Laberko, Alexandra; Ghosh, Sujal; Slatter, Mary A.; Weemaes, Corry M. R.; Yesilipek, Akif; Sirait, Tiarlan; Neven, Benedicte; Gennery, Andrew R.; Lankester, Arjan C.
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Gut microbiota and intestinal rehabilitation: a prospective childhood cohort longitudinal study of short bowel syndrome (the MIRACLS study): study protocol
err2024-08-17
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errOAAI
errCleminson, Jemma S.; Thomas, Julian; Stewart, Christopher J.; Campbell, David; Gennery, Andrew; Embleton, Nicholas D.; Koglmeier, Jutta; Wong, Theodoric; Spruce, Marie; Berrington, Janet E.
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NUDCD3 deficiency disrupts V(D)J recombination to cause SCID and Omenn syndrome
err2024-05-24
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errOAAI
errChen, Rui; Lukianova, Elena; van der Loeff, Ina Schim; Spegarova, Jarmila Stremenova; Willet, Joseph D. P.; James, Kieran D.; Ryder, Edward J.; Griffin, Helen; Ijspeert, Hanna; Gajbhiye, Akshada; Lamoliatte, Frederic; Marin-Rubio, Jose L.; Woodbine, Lisa; Lemos, Henrique; Swan, David J.; Pintar, Valeria; Sayes, Kamal; Ruiz-Morales, Elias R.; Eastham, Simon; Dixon, David; Prete, Martin; Prigmore, Elena; Jeggo, Penny; Boyes, Joan; Mellor, Andrew; Huang, Lei; van der Burg, Mirjam; Engelhardt, Karin R.; Stray-Pedersen, Asbjorg; Erichsen, Hans Christian; Gennery, Andrew R.; Trost, Matthias; Adams, David J.; Anderson, Graham; Lorenc, Anna; Trynka, Gosia; Hambleton, Sophie
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Extracorporeal photopheresis (ECP) in the treatment of chronic lung allograft dysfunction (CLAD): a prospective, multicentre, open-label, randomised controlled trial studying the addition of ECP to standard care in the treatment of bilateral lung transplant patients with CLAD (E-CLAD UK)
err2024-05-09
err1
errOAAI
errFisher, Andrew J.; White, Michael; Goudie, Nicola; Kershaw, Anneka; Phillipson, Julia; Bardgett, Michelle; Lally, Joanne; Bevin-Nicholls, Alex; Chadwick, Thomas; Bryant, Andrew; Russell, Sian; Smith, Hesther; Frisby, Laura; Errington, Rebecca; Carby, Martin; Thompson, Richard; Santhanakrishnan, Karthik; Parmar, Jasvir; Lordan, James L.; Vale, Luke; Hancock, Helen; Exley, Catherine; Gennery, Andrew R.; Wason, James M. S.
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