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Véronique Frémeaux‐Bacchi

centre national de la recherche scientifique (cnrs)

0H指数
1论文数
0被引数
收录论文 133
发表时间
Death following high-dose AAV9 gene therapy in a patient with advanced SMA-PME高级脊髓性肌萎缩症-肌阵挛性癫痫(SMA-PME)患者接受高剂量AAV9基因疗法后死亡
err2026-05-26
err0
errOAAI
errOdile Boespflug-Tanguy; Arnaud Valent; Jérôme Rambaud; Pierre-Louis Léger; Isabelle Plu; Danielle Seilhean; Véronique Frémeaux-Bacchi; Thierry Levade; Martina Marinello; Jérôme Denard; Marion Derome; Pierre-Romain le Brun; Nicolas Guerchet; Philippe Veron; Michael Blatzer; Romain Fragnoud; Laura Prieto; Tanguy Corbel; Nathalie Knuchel-Legendre; Béatrice Beaurain
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Digital Ischemia as a Rare Manifestation of C3 Glomerulopathy Associated With Monoclonal Gammopathy
err2024-03-01
err1
errOAAI
errBaber, Alistair; Legendre, Paul; Chauvet, Sophie; Karras, Alexandre; Deshayes, Samuel; Huart, Antoine; Vignon, Marguerite; Dessaix, Kathleen; Hervier, Baptiste; Legallicier, Bruno; Silva, Nicolas Martin; Fremeaux-Bacchi, Veronique; Terrier, Benjamin
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Complement in human disease: approved and up-andcoming therapeutics
errLANCET
IF88.5
err2024-01-01
err32
errOAAI
errWest, Erin E.; Woodruff, Trent; Fremeaux-Bacchi, Veronique; Kemper, Claudia
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Diffuse Endocapillary Glomerulonephritis in a Child With IL-17RA Deficiency Emphasizes the Pivotal Role of the Complement Cascade and AnaphylatoxinsIL-17RA缺乏症患儿的弥漫性毛细血管内肾小球肾炎强调了补体级联反应和过敏毒素的关键作用
err2023-11-01
err0
errOAAI
errd'Izarny-Gargas, Thibaut; Grapin, Mathilde; Grunenwald, Anne; Duong-Van-Huyen, Jean -Paul; Rabant, Marion; Levy, Romain; Puel, Anne; Toubiana, Julie; Boyer, Olivia; Fremeaux-Bacchi, Veronique; Charbit, Marina; Isnard, Pierre
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The Rational Use of Complement Inhibitors in Kidney Diseases
err2022-06-01
err27
errOAAI
errFakhouri, Fadi; Schwotzer, Nora; Golshayan, Dela; Fremeaux-Bacchi, Veronique
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Ex Vivo Test for Measuring Complement Attack on Endothelial Cells: From Research to Bedside
err2022-04-12
err9
errOAAI
errMeuleman, Marie-Sophie; Duval, Anna; Fremeaux-Bacchi, Veronique; Roumenina, Lubka T.; Chauvet, Sophie
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Improving Clinical Trials for Anticomplement Therapies in Complement-Mediated Glomerulopathies: Report of a Scientific orkshop Sponsored by the National Kidney Foundation改善补体介导的肾小球疾病中抗补体疗法的临床试验: 国家肾脏基金会赞助的科学orkshop的报告
err2022-04-01
err12
PREAI
errBomback, Andrew S.; Appel, Gerald B.; Gipson, Debbie S.; Hladunewich, Michelle A.; Lafayette, Richard; Nester, Carla M.; Parikh, Samir, V; Smith, Richard J. H.; Trachtman, Howard; Heeger, Peter S.; Ram, Sanjay; Rovin, Brad H.; Ali, Shadab; Arceneaux, Nicole; Ashoor, Isa; Bailey-Wickins, Laura; Barratt, Jonathan; Beck, Laurence; Cattran, Daniel C.; Cravedi, Paolo; Erkan, Elif; Fervenza, Fernando; Frazer-Abel, Ashley A.; Fremeaux-Bacchi, Veronique; Fuller, Lindsey; Gbadegesin, Rasheed; Hogan, Jonathan J.; Kiryluk, Krzysztof; Le Quintrec-Donnette, Moglie; Licht, Christoph; Mahan, John D.; Pickering, Matthew C.; Quigg, Richard; Rheault, Michelle; Ronco, Pierre; Sarwal, Minnie M.; Sethna, Christine; Spino, Cathie; Stegall, Mark; Vivarelli, Marina; Feldman, David L.; Thurman, Joshua M.
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Case Report: Adult Post-COVID-19 Multisystem Inflammatory Syndrome and Thrombotic Microangiopathy
err2021-06-23
err24
errOAAI
errBoudhabhay, Idris; Rabant, Marion; Roumenina, Lubka T.; Coupry, Louis-Marie; Poillerat, Victoria; Marchal, Armance; Fremeaux-Bacchi, Veronique; El Karoui, Khalil; Monchi, Mehran; Pourcine, Franck
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Identification of Distinct Immunophenotypes in Critically Ill Coronavirus Disease 2019 Patients
errCHEST
IF8.6
err2021-05-01
err12
errOAAI
errDupont, Thibault; Caillat-Zucman, Sophie; Fremeaux-Bacchi, Veronique; Morin, Florence; Lengline, Etienne; Darmon, Michael; de Latour, Regis Peffault; Zafrani, Lara; Azoulay, Elie; Dumas, Guillaume
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Role of C5 inhibition in Idiopathic Inflammatory Myopathies and Scleroderma Renal Crisis-Induced Thrombotic Microangiopathies
err2021-04-01
err17
errOAAI
errGouin, Anna; Ribes, David; Colombat, Magali; Chauveau, Dominique; Prevot, Gregoire; Lairez, Olivier; Pugnet, Gregory; Fremeaux-Bacchi, Veronique; Huart, Antoine; Belliere, Julie; Faguer, Stanislas
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Complement activation is a crucial driver of acute kidney injury in rhabdomyolysis
err2021-03-01
err55
errOAAI
errBoudhabhay, Idris; Poillerat, Victoria; Grunenwald, Anne; Torset, Carine; Leon, Juliette; Daugan, Marie, V; Lucibello, Francesca; El Karoui, Khalil; Ydee, Amandine; Chauvet, Sophie; Girardie, Patrick; Sacks, Steven; Farrar, Conrad A.; Garred, Peter; Berthaud, Romain; Le Quintrec, Moglie; Rabant, Marion; de Lonlay, Pascale; Rambaud, Caroline; Gnemmi, Viviane; Fremeaux-Bacchi, Veronique; Frimat, Marie; Roumenina, Lubka T.
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Circulating FH Protects Kidneys From Tubular Injury During Systemic Hemolysis
err2020-08-07
err11
errOAAI
errMerle, Nicolas S.; Leon, Juliette; Poillerat, Victoria; Grunenwald, Anne; Boudhabhay, Idris; Knockaert, Samantha; Robe-Rybkine, Tania; Torset, Carine; Pickering, Matthew C.; Chauvet, Sophie; Fremeaux-Bacchi, Veronique; Roumenina, Lubka T.
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Complement C5 inhibition in patients with COVID-19-a promising target?
err2020-07-23
err47
errOAAI
errde Latour, Regis Peffault; Bergeron, Anne; Lengline, Etienne; Dupont, Thibault; Marchal, Armance; Galicier, Lionel; de Castro, Nathalie; Bondeelle, Louise; Darmon, Michael; Dupin, Clairelyne; Dumas, Guillaume; Leguen, Pierre; Madelaine, Isabelle; Chevret, Sylvie; Molina, Jean-Michel; Azoulay, Elie; Fremeaux-Bacchi, Veronique
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Shiga toxin-producing Escherichia coli-associated hemolytic uremic syndrome in solid organ transplant recipients
err2019-12-01
err6
errOAAI
errVille, Simon; Ydee, Amandine; Garandeau, Claire; Canet, Emmanuel; Tissot, Adrien; Cantarovich, Diego; Fremeaux-Bacchi, Veronique; Mariani-Kurkdjian, Patricia; Provot, Francois; Fakhouri, Fadi
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Atypical hemolytic uremic syndrome and hypertensive crisis
err2019-11-01
err3
errOAAI
errEl Karoui, Khalil; Boudhabhay, Idris; Fremeaux-Bacchi, Veronique
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Glomerulonephritis With Isolated C3 Deposits as a Manifestation of Subtotal Factor I Deficiency
err2019-09-01
err5
errOAAI
errBoudhabhay, Idris; Fremeaux-Bacchi, Veronique; Roumenina, Lubka T.; Moktefi, Anissa; Goujon, Jean-Michel; Matignon, Marie; Caudwell, Valerie; Audard, Vincent; El Karoui, Khalil
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THROMBOTIC MICROANGIOPATHY AFTER RENAL TRANSPLANTATION: A CLINICOPATHOLOGICAL STUDY AND IDENTIFICATION OF PROGNOSTIC FACTORS
err2019-09-01
err1
PREAI
errRabant, Marion; Dessaix, Kathleen; Aubert, Olivier; Bontoux, Christophe; Zuber, Julien; Soussan, Rebecca Sberro; Bacchi, Veronique Fremeaux; Legendre, Christophe
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Structural Basis for Properdin Oligomerization and Convertase Stimulation in the Human Complement System人体补体系统中备解素寡聚化和转化酶刺激的结构基础
err2019-08-22
err52
errOAAI
errPedersen, Dennis V.; Gadeberg, Trine A. F.; Thomas, Caroline; Wang, Yong; Joram, Nicolas; Jensen, Rasmus K.; Mazarakis, Sofia M. M.; Revel, Margot; El Sissy, Carine; Petersen, Steen V.; Lindorff-Larsen, Kresten; Thiel, Steffen; Laursen, Nick S.; Fremeaux-Bacchi, Veronique; Andersen, Gregers R.
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