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Frank J. Accurso

rho

67H指数
322论文数
2.0W被引数
收录论文 81
发表时间
Entering the era of highly effective CFTR modulator therapy
errLANCET
IF88.5
err2019-11-01
err7
PREAI
errZemanick, Edith T.; Accurso, Frank J.
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Azithromycin for Early Pseudomonas Infection in Cystic Fibrosis The OPTIMIZE Randomized Trial
err2018-11-01
err0
errOAAI
errMayer-Hamblett, Nicole; Retsch-Bogart, George; Kloster, Margaret; Accurso, Frank; Rosenfeld, Margaret; Albers, Gary; Black, Philip; Brown, Perry; Cairns, AnneMarie; Davis, Stephanie D.; Graff, Gavin R.; Kerby, Gwendolyn S.; Orenstein, David; Buckingham, Rachael; Ramsey, Bonnie W.
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Characteristics and outcomes of oral antibiotic treated pulmonary exacerbations in children with cystic fibrosis
err2018-11-01
err16
errOAAI
errHoppe, Jordana E.; Wagner, Brandie D.; Accurso, Frank J.; Zemanick, Edith T.; Sagel, Scott D.
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KB001-A, a novel anti-inflammatory, found to be safe and well-tolerated in cystic fibrosis patients infected with Pseudomonas aeruginosa
err2018-07-01
err74
errOAAI
errJain, R.; Beckett, V. V.; Konstan, M. W.; Accurso, F. J.; Burns, J. L.; Mayer-Hamblett, N.; Milla, Carlos; VanDevanter, D. R.; Chmiel, J. F.
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Airway microbiota across age and disease spectrum in cystic fibrosis
err2017-11-16
err172
errOAAI
errZemanick, Edith T.; Wagner, Brandie D.; Robertson, Charles E.; Ahrens, Richard C.; Chmiel, James F.; Clancy, John P.; Gibson, Ronald L.; Harris, William T.; Kurland, Geoffrey; Laguna, Theresa A.; McColley, Susanna A.; McCoy, Karen; Retsch-Bogart, George; Sobush, Kurtis T.; Zeitlin, Pamela L.; Stevens, Mark J.; Accurso, Frank J.; Sagel, Scott D.; Harris, J. Kirk
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Restoring Cystic Fibrosis Transmembrane Conductance Regulator Function Reduces Airway Bacteria and Inflammation in People with Cystic Fibrosis and Chronic Lung Infections
err2017-06-15
err326
errOAAI
errHisert, Katherine B.; Heltshe, Sonya L.; Pope, Christopher; Jorth, Peter; Wu, Xia; Edwards, Rachael M.; Radey, Matthew; Accurso, Frank J.; Wolter, Daniel J.; Cooke, Gordon; Adam, Ryan J.; Carter, Suzanne; Grogan, Brenda; Launspach, Janice L.; Donnelly, Seamas C.; Gallagher, Charles G.; Bruce, James E.; Stoltz, David A.; Welsh, Michael J.; Hoffman, Lucas R.; McKone, Edward F.; Singh, Pradeep K.
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Diagnosis of Cystic Fibrosis in Screened Populations筛查人群中囊性纤维化的诊断
err2017-02-01
err83
errOAAI
errFarrell, Philip M.; White, Terry B.; Howenstine, Michelle S.; Munck, Anne; Parad, Richard B.; Rosenfeld, Margaret; Sommerburg, Olaf; Accurso, Frank J.; Davies, Jane C.; Rock, Michael J.; Sanders, Don B.; Wilschanski, Michael; Sermet-Gaudelus, Isabelle; Blau, Hannah; Gartner, Silvia; McColley, Susanna A.
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Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation
err2017-02-01
err643
errOAAI
errFarrell, Philip M.; White, Terry B.; Ren, Clement L.; Hempstead, Sarah E.; Accurso, Frank; Derichs, Nico; Howenstine, Michelle; McColley, Susanna A.; Rock, Michael; Rosenfeld, Margaret; Sermet-Gaudelus, Isabelle; Southern, Kevin W.; Marshall, Bruce C.; Sosnay, Patrick R.
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Biomarkers for cystic fibrosis drug development
err2016-11-01
err58
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errMuhlebach, Marianne S.; Clancy, J. P.; Heltshe, Sonya L.; Ziady, Assem; Kelley, Tom; Accurso, Frank; Pilewski, Joseph; Mayer-Hamblett, Nicole; Joseloff, Elizabeth; Sagel, Scott D.
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Glucose >200 mg/dL during Continuous Glucose Monitoring Identifies Adult Patients at Risk for Development of Cystic Fibrosis Related Diabetes
err2016-01-01
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errOAAI
errTaylor-Cousar, J. L.; Janssen, J. S.; Wilson, A.; Clair, C. G. St.; Pickard, K. M.; Jones, M. C.; Brayshaw, S. J.; Chacon, C. S.; Barboa, C. M.; Sontag, M. K.; Accurso, F. J.; Nichols, D. P.; Saavedra, M. T.; Nick, J. A.
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Use of ibuprofen to assess inflammatory biomarkers in induced sputum: Implications for clinical trials in cystic fibrosis
err2015-11-01
err49
errOAAI
errChmiel, James F.; Konstan, Michael W.; Accurso, Frank J.; Lymp, James; Mayer-Hamblett, Nicole; VanDevanter, Donald R.; Rose, Lynn M.; Ramsey, Bonnie W.
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Genome-wide association meta-analysis identifies five modifier loci of lung disease severity in cystic fibrosis全基因组关联荟萃分析确定了囊性纤维化中肺部疾病严重程度的五个修饰位点
err2015-09-29
err237
errOAAI
errCorvol, Harriet; Blackman, Scott M.; Boelle, Pierre-Yves; Gallins, Paul J.; Pace, Rhonda G.; Stonebraker, Jaclyn R.; Accurso, Frank J.; Clement, Annick; Collaco, Joseph M.; Dang, Hong; Dang, Anthony T.; Franca, Arianna; Gong, Jiafen; Guillot, Loic; Keenan, Katherine; Li, Weili; Lin, Fan; Patrone, Michael V.; Raraigh, Karen S.; Sun, Lei; Zhou, Yi-Hui; O'Neal, Wanda K.; Sontag, Marci K.; Levy, Hara; Durie, Peter R.; Rommens, Johanna M.; Drumm, Mitchell L.; Wright, Fred A.; Strug, Lisa J.; Cutting, Garry R.; Knowles, Michael R.
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Considerations for the Conduct of Clinical Trials with Antiinflammatory Agents in Cystic Fibrosis A Cystic Fibrosis Foundation Workshop Report
err2015-09-01
err32
PREAI
errTorphy, Theodore J.; Allen, Janet; Cantin, Andre M.; Konstan, Michael W.; Accurso, Frank J.; Joseloff, Elizabeth; Ratjen, Felix A.; Chmiel, James F.
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Variants in Solute Carrier SLC26A9 Modify Prenatal Exocrine Pancreatic Damage in Cystic Fibrosis
err2015-05-01
err41
errOAAI
errMiller, Melissa R.; Soave, David; Li, Weili; Gong, Jiafen; Pace, Rhonda G.; Boelle, Pierre-Yves; Cutting, Garry R.; Drumm, Mitchell L.; Knowles, Michael R.; Sun, Lei; Rommens, Johanna M.; Accurso, Frank; Durie, Peter R.; Corvol, Harriet; Levy, Hara; Sontag, Marci K.; Strug, Lisa J.
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Pharmacokinetics and tolerability of oral sildenafil in adults with cystic fibrosis lung disease
err2015-03-01
err35
errOAAI
errTaylor-Cousar, J. L.; Wiley, C.; Felton, L. A.; St Clair, C.; Jones, M.; Curran-Everett, D.; Poch, K.; Nichols, D. P.; Solomon, G. M.; Saavedra, M. T.; Accurso, F. J.; Nick, J. A.
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Assessment of Airway Microbiota and Inflammation in Cystic Fibrosis Using Multiple Sampling Methods
err2015-02-01
err117
errOAAI
errZemanick, Edith T.; Wagner, Brandie D.; Robertson, Charles E.; Stevens, Mark J.; Szefler, Stanley J.; Accurso, Frank J.; Sagel, Scott D.; Harris, J. Kirk
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Ataluren for the treatment of nonsense-mutation cystic fibrosis: a randomised, double-blind, placebo-controlled phase 3 trial
err2014-07-01
err300
errOAAI
errKerem, Elton; Konstan, Michael W.; De Boeck, Kris; Accurso, Frank J.; Sermet-Gaudelus, Isabelle; Wilschanski, Michael; Elborn, J. Stuart; Melotti, Paola; Bronsveld, Inez; Fajac, Isabelle; Malfroot, Anne; Rosenbluth, Daniel B.; Walker, Patricia A.; McColley, Susanna A.; Knoop, Christiane; Quattrucci, Serena; Rietschel, Ernst; Zeitlin, Pamela L.; Barth, Jay; Elfring, Guy L.; Welch, Ellen M.; Branstrom, Arthur; Spiegel, Robert J.; Peltz, Stuart W.; Ajayi, Temitayo; Rowe, Steven M.
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Evidence for a Causal Relationship Between Early Exocrine Pancreatic Disease and Cystic Fibrosis-Related Diabetes: A Mendelian Randomization Study
err2014-05-15
err69
errOAAI
errSoave, David; Miller, Melissa R.; Keenan, Katherine; Li, Weili; Gong, Jiafen; Ip, Wan; Accurso, Frank; Sun, Lei; Rommens, Johanna M.; Sontag, Marci; Durie, Peter R.; Strug, Lisa J.
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