未登录 分享 收藏
分享 收藏
分享 收藏
分享 收藏
分享 收藏
分享 收藏
分享 收藏
分享 收藏
Efficacy and safety of inhaled α1-antitrypsin in patients with severe α1-antitrypsin deficiency and frequent exacerbations of COPD Stolk, Jan; Tov, Naveh; Chapman, Kenneth R.; Fernandez, Pablo; MacNee, William; Hopkinson, Nicholas S.; Piitulainen, Eeva; Seersholm, Niels; Vogelmeier, Claus F.; Bals, Robert; McElvaney, Gerry; Stockley, Robert A. 分享 收藏
分享 收藏
European Respiratory Society statement: diagnosis and treatment of pulmonary disease in α1-antitrypsin deficiency Miravitlles, Marc; Dirksen, Asger; Ferrarotti, Ilaria; Koblizek, Vladimir; Lange, Peter; Mahadeva, Ravi; McElvaney, Noel G.; Parr, David; Piitulainen, Eeva; Roche, Nicolas; Stolk, Jan; Thabut, Gabriel; Turner, Alice; Vogelmeier, Claus; Stockley, Robert A. 分享 收藏
分享 收藏
Long-term efficacy and safety of α1 proteinase inhibitor treatment for emphysema caused by severe α1 antitrypsin deficiency: an open-label extension trial (RAPID-OLE) McElvaney, Noel G.; Burdon, Jonathan; Holmes, Mark; Glanville, Allan; Wark, Peter A. B.; Thompson, Philip J.; Hernandez, Paul; Chlumsky, Jan; Teschler, Helmut; Ficker, Joachim H.; Seersholm, Niels; Altraja, Alan; Makitaro, Riitta; Chorostowska-Wynimko, Joanna; Sanak, Marek; Stoicescu, Paul I.; Piitulainen, Eeva; Vit, Oliver; Wencker, Marion; Tortorici, Michael A.; Fries, Michael; Edelman, Jonathan M.; Chapman, Kenneth R. 分享 收藏
LATE-BREAKING ABSTRACT: Long-term efficacy of A1-PI therapy in RAPID and RAPID extension trials McElvaney, N. Gerard; Chapman, Kenneth R.; Burdon, Jonathan; Piitulainen, Eeva; Seersholm, Niels; Stocks, James; Sandhaus, Robert; Vit, Oliver; Fries, Michael; Edelman, Jonathan M. 分享 收藏
分享 收藏
Assessment of A1-PI dose-exposure and exposure-response relationships in patients with Alpha-1 antitrypsin inhibitor deficiency Tortorici, Michael A.; Yao, Zhenling; Rogers, James A.; Vit, Oliver; Bexon, Martin; Sandhaus, Robert; Burdon, Jonathan; Piitulainen, Eeva; Seersholm, Niels; Stocks, James; McElvaney, N. Gerard; Chapman, Kenneth R.; Edelman, Jonathan 分享 收藏
Safety of bi-weekly infusion of A1-PI augmentation therapy in RAPID Seersholm, Niels; Sandhaus, Robert; Chapman, Kenneth R.; Burdon, Jonathan; Piitulainen, Eeva; Stocks, James; Tortorici, Michael; Rosenberg, Tanja; Vit, Oliver; Bexon, Martin; Edelman, Jonathan; McElvaney, N. Gerard 分享 收藏
Population pharmacokinetics of A1-PI in patients with Alpha-1 antitrypsin deficiency Tortorici, Michael A.; Vit, Oliver; Bexon, Martin; Sandhaus, Robert; Burdon, Jonathan; Piitulainen, Eeva; Seersholm, Niels; Stocks, James; McElvaney, N. Gerard; Chapman, Kenneth R.; Edelman, Jonathan 分享 收藏
Intravenous augmentation treatment and lung density in severe α1 antitrypsin deficiency (RAPID): a randomised, double-blind, placebo-controlled trial 严重 α1抗胰蛋白酶缺乏症 (RAPID) 的静脉增强治疗和肺密度: 一项随机,双盲,安慰剂对照试验 Chapman, Kenneth R.; Burdon, Jonathan G. W.; Piitulainen, Eeva; Sandhaus, Robert A.; Seersholm, Niels; Stocks, James M.; Stoel, Berend C.; Huang, Liping; Yao, Zhenling; Edelman, Jonathan M.; McElvaney, Noel G. 分享 收藏
分享 收藏