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Diffuse alveolar haemorrhage in children: an international multicentre study Ring, Astrid; Schwerk, Nicolaus; Kiper, Nural; Aslan, Ayse Tana; Aurora, Paul; Ayats, Roser; Azevedo, Ines; Bandeira, Teresa; Carlens, Julia; Castillo-Corullon, Silvia; Cobanoglu, Nazan; Elnazir, Basil; Emiralioglu, Nagehan; Eyuboglu, Tugba Sismanlar; Gursoy, Tugba Ramasli; Hogg, Claire; Karadag, Bulent; Latalova, Vendula; Krenke, Katarzyna; Lange, Joanna; Osona, Borja; Proesmann, Marijke; Reix, Philippe; Renoux, Marie-Catherine; Roditis, Lea; Rubak, Sune; Rumman, Nisreen; Thumerelle, Caroline; Weiss, Laurence; Yalcin, Ebru; Zirek, Fazilcan; Bush, Andy; Clement, Annick; Buchvald, Frederik Fouirnaies; Griese, Matthias; Nathan, Nadia; Nielsen, Kim Gjerum 分享 收藏
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An observational study of the lung clearance index throughout childhood in cystic fibrosis: early years matter Davies, Gwyneth; Stanojevic, Sanja; Raywood, Emma; Duncan, Julie A.; Stocks, Janet; Lum, Sooky; Bush, Andrew; Viviani, Laura; Wade, Angie; Calder, Alistair; Owens, Catherine M.; Goubau, Christophe; Carr, Siobhan B.; Bossley, Cara J.; Pao, Caroline; Aurora, Paul 分享 收藏
Clinical utility of NGS diagnosis and disease stratification in a multiethnic primary ciliary dyskinesia cohort Fassad, Mahmoud R.; Patel, Mitali P.; Shoemark, Amelia; Cullup, Thomas; Hayward, Jane; Dixon, Mellisa; Rogers, Andrew, V; Ollosson, Sarah; Jackson, Claire; Goggin, Patricia; Hirst, Robert A.; Rutman, Andrew; Thompson, James; Jenkins, Lucy; Aurora, Paul; Moya, Eduardo; Chetcuti, Philip; O'Callaghan, Chris; Morris-Rosendahl, Deborah J.; Watson, Christopher M.; Wilson, Robert; Carr, Siobhan; Walker, Woolf; Pitno, Andreia; Lopes, Susana; Morsy, Heba; Shoman, Walaa; Pereira, Luisa; Constant, Carolina; Loebinger, Michael R.; Chung, Eddie M. K.; Kenia, Priti; Rumman, Nisreen; Fasseeh, Nader; Lucas, Jane S.; Hogg, Claire; Mitchison, Hannah M. 分享 收藏
One-year outcomes in a multicentre cohort study of incident rare diffuse parenchymal lung disease in children (ChILD) Cunningham, Steve; Graham, Catriona; MacLean, Morag; Aurora, Paul; Ashworth, Michael; Barbato, Angelo; Calder, Alistair; Carlens, Julia; Clement, Annick; Hengst, Meike; Kammer, Birgit; Kiper, Nural; Krenke, Katarzyna; Kronfeld, Kai; Lange, Joanna; Ley-Zaporozhan, Julia; Nicholson, Andrew G.; Reu, Simone; Wesselak, Traudl; Wetzke, Martin; Bush, Andrew; Schwerk, Nicolaus; Griese, Matthias 分享 收藏
Mutations in Outer Dynein Arm Heavy Chain DNAH9 Cause Motile Cilia Defects and Situs Inversus Fassad, Mahmoud R.; Shoemark, Amelia; Legendre, Marie; Hirst, Robert A.; Koll, France; le Borgne, Pierrick; Louis, Bruno; Daudvohra, Farheen; Patel, Mitali P.; Thomas, Lucie; Dixon, Mellisa; Burgoyne, Thomas; Hayes, Joseph; Nicholson, Andrew G.; Cullup, Thomas; Jenkins, Lucy; Carr, Siobhan B.; Aurora, Paul; Lemullois, Michel; Aubusson-Fleury, Anne; Papon, Jean-Francois; O'Callaghan, Christopher; Amselem, Serge; Hogg, Claire; Escudier, Estelle; Tassin, Anne-Marie; Mitchison, Hannah M. 分享 收藏
An observational study of incident diagnoses of children's diffuse parenchymal lung disease (ChILDEU) Cunningham, Steve; Graham, Cat; Maclean, Morag; Aurora, Paul; Ashworth, Michael; Calder, Alistair; Clement, Annick; Hengste, Meike; Kiper, Nural; Krenke, Katarzyna; Lange, Joanna; Nicholson, Andrew; Reu, Simone; Snijders, Deborah; Bush, Andrew; Schwerk, Nico; Griese, Matthias 分享 收藏
Comparison of facemask and mouthpiece interfaces for multiple breath washout measurements Robinson, Paul D.; Lum, Sooky; Moore, Courtney; Hardaker, Kate M.; Benseler, Nick; Aurora, Paul; Cooper, Peter; Fitzgerald, Dominic; Jensen, Renee; McDonald, Reginald; Selvadurai, Hiran; Ratjen, Felix; Stanojevic, Sanja 分享 收藏
Preschool Multiple-Breath Washout Testing An Official American Thoracic Society Technical Statement: Executive Summary Robinson, Paul D.; Latzin, Philipp; Ramsey, Kathryn A.; Stanojevic, Sanja; Aurora, Paul; Davis, Stephanie D.; Gappa, Monika; Hall, Graham L.; Horsley, Alex; Jensen, Renee; Lum, Sooky; Milla, Carlos; Nielsen, Kim G.; Pittman, Jessica E.; Rosenfeld, Margaret; Singer, Florian; Subbarao, Padmaja; Gustafsson, Per M.; Ratjen, Felix 分享 收藏
Pulmonary function deficits in newborn screened infants with cystic fibrosis managed with standard UK care are mild and transient Davies, Gwyneth; Stocks, Janet; Thia, Lena P.; Hoo, Ah-Fong; Bush, Andrew; Aurora, Paul; Brennan, Lucy; Lee, Simon; Lum, Sooky; Cottam, Philippa; Miles, Joanne; Chudleigh, Jane; Kirkby, Jane; Balfour-Lynn, Ian M.; Carr, Siobhan B.; Wallis, Colin; Wyatt, Hilary; Wade, Angie 分享 收藏
International management platform for children's interstitial lung disease (chILD-EU) Griese, Matthias; Seidl, Elias; Hengst, Meike; Reu, Simone; Rock, Hans; Anthony, Gisela; Kiper, Nural; Emiralioglu, Nagehan; Snijders, Deborah; Goldbeck, Lutz; Leidl, Reiner; Ley-Zaporozhan, Julia; Krueger-Stollfuss, Ingrid; Kammer, Birgit; Wesselak, Traudl; Eismann, Claudia; Schams, Andrea; Neuner, Doerthe; MacLean, Morag; Nicholson, Andrew G.; Lauren, McCann; Clement, Annick; Epaud, Ralph; de Blic, Jacques; Ashworth, Michael; Aurora, Paul; Calder, Alistair; Wetzke, Martin; Kappler, Matthias; Cunningham, Steve; Schwerk, Nicolaus; Bush, Andy 分享 收藏
X-linked primary ciliary dyskinesia due to mutations in the cytoplasmic axonemal dynein assembly factor PIH1D3 Olcese, Chiara; Patel, Mitali P.; Shoemark, Amelia; Kiviluoto, Santeri; Legendre, Marie; Williams, Hywel J.; Vaughan, Cara K.; Hayward, Jane; Goldenberg, Alice; Emes, Richard D.; Munye, Mustafa M.; Dyer, Laura; Cahill, Thomas; Bevillard, Jeremy; Gehrig, Corinne; Guipponi, Michel; Chantot, Sandra; Duquesnoy, Philippe; Thomas, Lucie; Jeanson, Ludovic; Copin, Bruno; Tamalet, Aline; Thauvin-Robinet, Christel; Papon, Jean-Francois; Garin, Antoine; Pin, Isabelle; Vera, Gabriella; Aurora, Paul; Fassad, Mahmoud R.; Jenkins, Lucy; Boustred, Christopher; Cullup, Thomas; Dixon, Mellisa; Onoufriadis, Alexandros; Bush, Andrew; Chung, Eddie M. K.; Antonarakis, Stylianos E.; Loebinger, Michael R.; Wilson, Robert; Armengot, Miguel; Escudier, Estelle; Hogg, Claire; Amselem, Serge; Sun, Zhaoxia; Bartoloni, Lucia; Blouin, Jean-Louis; Mitchison, Hannah M. 分享 收藏
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Interim results for INSPIRE-CF: A 24-month RCT evaluating effects of weekly supervised exercise in children with CF Ledger, Sean; Wade, Angie; Douglas, Helen; Sarria, Laura; Rayner, Paul; Goldman, Allan; Giardini, Alessandro; Prasad, S. Ammani; Aurora, Paul; Main, Eleanor 分享 收藏
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Validity and Reliability Concerns Associated with Cardiopulmonary Exercise Testing Young People with Cystic Fibrosis Reply Hebestreit, Helge; Arets, Hubertus G. M.; Aurora, Paul; Boas, Steve; Cerny, Frank; Hulzebos, Erik H. J.; Karila, Chantal; Lands, Larry C.; Lowman, John D.; Swisher, Anne; Urquhart, Don S. 分享 收藏