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Kimberly M. Huber

university of texas southwestern medical center

54H指数
123论文数
1.4W被引数
收录论文 47
发表时间
The E3 Ubiquitin Ligase UBE3B Regulates Synaptic Development and Cortical Network ActivityE3泛素连接酶UBE3B调控突触发育和皮层网络活动
err2026-03-17
err0
errOAAI
errShayal Vashisth; Aleya Shedd; Ariel Aiken; Solmi Cheon; Josh Bandopadhay; Kiran Kaur; Kimberly M. Huber; Maria H. Chahrour
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A Targetable Metabolic Signal Drives Neuronal Hyperexcitability and Glioma Aggressiveness一种可靶向的代谢信号驱动神经元过度兴奋性和胶质瘤侵袭性
err2025-11-01
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errAbdullah, Kalil; Miki, Kenji; Edgar, Charles; Wu, Shuangcheng; Xiao, Yi; Savani, Milan; Ghoche, Maged; Kotermanski, Shawn; Huang, Yuan-Tai; Traylor, Jeffrey; Hicks, William; Shi, Diana; Tang, Min; Oken, Skyler; Manoj, Namya; Smith, Bailey; Puliyappadamba, Vinesh; Kaphle, Pranita; Shipman, Tracey; West III, Raymond; Ma, Shang; Ksendzovsky, Alexander; Nolin, Thomas; Zinn, Pascal; Zacharias, Lauren; Mathews, Thomas; Gibson, Jay; Huber, Kimberly; Chamberland, Simon; DeBerardinis, Ralph; McBrayer, Samuel
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Developmental trajectory and sex differences in auditory processing in a PTEN-deletion model of autism spectrum disorders
err2024-10-01
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errOAAI
errCroom, Katilynne; Rumschlag, Jeffrey A.; Molinaro, Gemma; Erickson, Michael A.; Binder, Devin K.; Huber, Kimberly M.; Razak, Khaleel A.
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Female-specific dysfunction of sensory neocortical circuits in a mouse model of autism mediated by mGluR5 and estrogen receptor a
err2024-04-01
err3
errOAAI
errMolinaro, Gemma; Bowles, Jacob E.; Croom, Katilynne; Gonzalez, Darya; Mirjafary, Saba; Birnbaum, Shari G.; Razak, Khaleel A.; Gibson, Jay R.; Huber, Kimberly M.
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Excitatory neuron-specific suppression of the integrated stress response contributes to autism-related phenotypes in fragile X syndrome
errNEURON
IF15
err2023-10-01
err6
PREAI
errHooshmandi, Mehdi; Sharma, Vijendra; Perez, Carolina Thorn; Sood, Rapita; Krimbacher, Konstanze; Wong, Calvin; Lister, Kevin C.; Guzman, Alba Urena; Bartley, Trevor D.; Rocha, Cecilia; Maussion, Gilles; Nadler, Emma; Roque, Patricia Margarita; Gantois, Ilse; Popic, Jelena; Levesque, Maxime; Kaufman, Randal J.; Avoli, Massimo; Sanz, Elisenda; Nader, Karim; Hagerman, Randi Jenssen; Durcan, Thomas M.; Costa-Mattioli, Mauro; Prager-Khoutorsky, Masha; Lacaille, Jean-Claude; Martinez-Cerdeno, Veronica; Gibson, Jay R.; Huber, Kimberly M.; Sonenberg, Nahum; Gkogkas, Christos G.; Khoutorsky, Arkady
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FMRP phosphorylation and interactions with Cdh1 regulate association with dendritic RNA granules and MEF2-triggered synapse elimination
err2023-06-01
err4
errOAAI
errWilkerson, Julia R.; Ifrim, Marius F.; Valdez-Sinon, Arielle N.; Hahn, Patricia; Bowles, Jacob E.; Molinaro, Gemma; Janusz-Kaminska, Aleksandra; Bassell, Gary J.; Huber, Kimberly M.
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Editorial: Recent advances in mechanisms and therapeutics for Fragile X Syndrome and autism
err2023-05-12
err0
errOAAI
errMolinaro, Gemma; Huber, Kimberly M. M.; McCullagh, Elizabeth A. A.; Thomson, Sophie R. R.
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Autism-Associated Chromatin Regulator Brg1/SmarcA4 Is Required for Synapse Development and Myocyte Enhancer Factor 2-Mediated Synapse Remodeling
err2023-03-18
err34
errOAAI
errZhang, Zilai; Cao, Mou; Chang, Chia-Wei; Wang, Cindy; Shi, Xuanming; Zhan, Xiaoming; Birnbaum, Shari G.; Bezprozvanny, Ilya; Huber, Kimberly M.; Wu, Jiang I.
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A sound-driven cortical phase-locking change in the Fmr1 KO mouse requires Fmr1 deletion in a subpopulation of brainstem neurons
err2022-08-01
err6
errOAAI
errHolley, Andrew J.; Shedd, Aleya; Boggs, Anna; Lovelace, Jonathan; Erickson, Craig; Gross, Christina; Jankovic, Miranda; Razak, Khaleel; Huber, Kimberly; Gibson, Jay R.
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Functional coordination of BET family proteins underlies altered transcription associated with memory impairment in fragile X syndrome
err2021-05-21
err11
errOAAI
errKim, Seung-Kyoon; Liu, Xihui; Park, Jongmin; Um, Dahun; Kilaru, Gokhul; Chiang, Cheng-Ming; Kang, Mingon; Huber, Kimberly M.; Kang, Keunsoo; Kim, Tae-Kyung
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GABAA Alpha 2,3 Modulation Improves Select Phenotypes in a Mouse Model of Fragile X Syndrome
err2021-05-21
err11
errOAAI
errSchaefer, Tori L.; Ashworth, Amy A.; Tiwari, Durgesh; Tomasek, Madison P.; Parkins, Emma V.; White, Angela R.; Snider, Andrew; Davenport, Matthew H.; Grainger, Lindsay M.; Becker, Robert A.; Robinson, Chandler K.; Mukherjee, Rishav; Williams, Michael T.; Gibson, Jay R.; Huber, Kimberly M.; Gross, Christina; Erickson, Craig A.
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Ribosome profiling in mouse hippocampus: plasticity-induced regulation and bidirectional control by TSC2 and FMRP
err2020-10-14
err13
errOAAI
errHien, Annie; Molinaro, Gemma; Liu, Botao; Huber, Kimberly M.; Richter, Joel D.
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Selective inhibition of glycogen synthase kinase 3α corrects pathophysiology in a mouse model of fragile X syndrome
err2020-05-20
err43
errOAAI
errMcCamphill, Patrick K.; Stoppel, Laura J.; Senter, Rebecca K.; Lewis, Michael C.; Heynen, Arnold J.; Stoppel, David C.; Sridhar, Vinay; Collins, Katie A.; Shi, Xi; Pan, Jen Q.; Madison, Jon; Cottrell, Jeffrey R.; Huber, Kimberly M.; Scolnick, Edward M.; Holson, Edward B.; Wagner, Florence F.; Bear, Mark F.
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FMRP Control of Ribosome Translocation Promotes Chromatin Modifications and Alternative Splicing of Neuronal Genes Linked to Autism
err2020-03-01
err70
errOAAI
errShah, Sneha; Molinaro, Gemma; Liu, Botao; Wang, Ruijia; Huber, Kimberly M.; Richter, Joel D.
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Local cortical circuit correlates of altered EEG in the mouse model of Fragile X syndrome
err2019-04-01
err31
errOAAI
errGoswami, Sonal; Cavalier, Sheridan; Sridhar, Vinay; Huber, Kimberly M.; Gibson, Jay R.
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Optimization of ribosome profiling using low-input brain tissue from fragile X syndrome model mice
err2018-12-24
err15
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errLiu, Botao; Molinaro, Gemma; Shu, Huan; Stackpole, Emily E.; Huber, Kimberly M.; Richter, Joel D.
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Distinct stages of synapse elimination are induced by burst firing of CA1 neurons and differentially require MEF2A/D
err2017-09-13
err18
errOAAI
errChang, Chia-Wei; Wilkerson, Julia R.; Hale, Carly F.; Gibson, Jay R.; Huber, Kimberly M.
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