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Bing‐Wen Soong

Taipei Veterans General Hospital

42H指数
192论文数
5.9K被引数
收录论文 78
发表时间
A dominant negative Kcnd3 F227del mutation in mice causes spinocerebellar ataxia type 22 (SCA22) by impairing ER and Golgi functioning
err2024-11-19
err0
PREAI
errHung, Hao-Chih; Lin, Jia-Han; Teng, Yuan-Chi; Kao, Cheng-Heng; Wang, Pei-Yu; Soong, Bing-Wen; Tsai, Ting-Fen
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MRl and MRS hints for the differentiation of cerebellar multiple system atrophy from spinocerebellar ataxia type II
errHELIYON
IF3.6
err2024-04-01
err1
errOAAI
errChen, Hung-Chieh; Lee, Li-Hua; Lirng, Jiing-Feng; Soong, Bing-wen
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Scale for Ocular motor Disorders in Ataxia (SODA)
err2022-12-01
err4
PREAI
errShaikh, Aasef G.; Kim, Ji-Soo; Froment, Caroline; Koo, Yu Jin; Dupre, Nicolas; Hadjivassiliou, Marios; Honnorat, Jerome; Kothari, Sudhir; Mitoma, Hiroshi; Rodrigue, Xavier; Soong, Bing-Wen; Subramony, S. H.; Strupp, Michael; Schmahmann, Jeremy; Manto, Mario
err分享
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Reply to: Low Frequency of p.S510G in PIAS1 Challenges Its Relevance for Modifying Repeat Expansion Disorders
err2022-10-17
err0
PREAI
errLee, Yan Hua; Lee, Yi-Chung; Tsai, Yu-Shuen; Yang, Ueng-Cheng; Cheng, Tzu-Hao; Chern, Yijuang; Soong, Bing-Wen
err分享
err收藏
Radiological hints for differentiation of cerebellar multiple system atrophy from spinocerebellar ataxia
err2022-06-22
err4
errOAAI
errChen, Hung-Chieh; Lee, Li-Hua; Lirng, Jiing-Feng; Soong, Bing-wen
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A PIAS1 Protective Variant S510G Delays polyQ Disease Onset by Modifying Protein Homeostasis
err2021-12-23
err10
PREAI
errLee, Yan Hua; Tsai, Yu-Shuen; Chang, Che-Chang; Ho, Chun-Chen; Shih, Hsiu-Ming; Chen, Hui-Mei; Lai, Hsing-Lin; Lee, Chia-Wei; Lee, Yi-Chung; Liao, Yi-Chu; Yang, Ueng-Cheng; Cheng, Tzu-Hao; Chern, Yijuang; Soong, Bing-Wen
err分享
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Clinical and genetic characterization of hereditary spastic paraplegia type 3A in Taiwan台湾遗传性痉挛性截瘫3A型的临床和遗传特征
err2021-06-01
err7
PREAI
errHsu, Shao-Lun; Hsueh, Hsueh-Wen; Chen, Shih-Ying; Chang, Yung-Yee; Tan, Shennie; Hong, Chien-Tai; Tsai, Yu-Shuen; Yu, Kai-Wei; Wu, Hsiu-Mei; Liao, Yi-Chu; Soong, Bing-Wen; Hu, Chaur-Jong; Lan, Min-Yu; Lee, Yi-Chung
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Xenografting of human umbilical mesenchymal stem cells from Wharton's jelly ameliorates mouse spinocerebellar ataxia type 1
err2019-09-05
err17
errOAAI
errTsai, Pei-Jiun; Yeh, Chang-Ching; Huang, Wan-Jhen; Min, Ming-Yuan; Huang, Tzu-Hao; Ko, Tsui-Ling; Huang, Pei-Yu; Chen, Tien-Hua; Hsu, Sanford P. C.; Soong, Bing-Wen; Fu, Yu-Show
err分享
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Investigating PUM1 mutations in a Taiwanese cohort with cerebellar ataxia台湾小脑共济失调患者PUM1基因突变研究
err2019-09-01
err9
PREAI
errLai, Kuan-Lin; Liao, Yi-Chu; Tsai, Pei-Chien; Hsiao, Cheng-Tsung; Soong, Bing-Wen; Lee, Yi-Chung
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Novel SCA19/22-associated KCND3 mutations disrupt human KV4.3 protein biosynthesis and channel gating
err2019-08-17
err17
errOAAI
errHsiao, Cheng-Tsung; Fu, Ssu-Ju; Liu, Yo-Tsen; Lu, Yi-Hsiang; Zhong, Ciao-Yu; Tang, Chih-Yung; Soong, Bing-Wen; Jeng, Chung-Jiuan
err分享
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Galectin-3 is required for the microglia-mediated brain inflammation in a model of Huntington's disease
err2019-08-02
err166
errOAAI
errSiew, Jian Jing; Chen, Hui-Mei; Chen, Huan-Yuan; Chen, Hung-Lin; Chen, Chiung-Mei; Soong, Bing-Wen; Wu, Yih-Ru; Chang, Ching-Pang; Chan, Yi-Chen; Lin, Chun-Hung; Liu, Fu-Tong; Chern, Yijuang
err分享
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Comparable progression of spinocerebellar ataxias between Caucasians and Chinese
err2019-05-01
err12
PREAI
errLin, Yi-Cheng; Lee, Yi-Chung; Hsu, Ting-Yi; Liao, Yi-Chu; Soong, Bing-Wen
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Modeling spinocerebellar ataxias 2 and 3 with iPSCs reveals a role for glutamate in disease pathology
err2019-02-04
err30
errOAAI
errChuang, Ching-Yu; Yang, Chih-Chao; Soong, Bing-Wen; Yu, Chun-Ying; Chen, Shu-Hwa; Huang, Hsiang-Po; Kuo, Hung-Chih
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Genetic analysis of ANXA11 variants in a Han Chinese cohort with amyotrophic lateral sclerosis in Taiwan
err2018-12-01
err11
PREAI
errTsai, Pei-Chien; Liao, Yi-Chu; Jih, Kang-Yang; Soong, Bing-Wen; Lin, Kon-Ping; Lee, Yi-Chung
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A randomized controlled pilot trial of game-based training in individuals with spinocerebellar ataxia type 3
err2018-05-18
err29
errOAAI
errWang, Ray-Yau; Huang, Fang-Yi; Soong, Bing-Wen; Huang, Shih-Fong; Yang, Yea-Ru
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Investigating CCNF mutations in a Taiwanese cohort with amyotrophic lateral sclerosis
err2018-02-01
err13
PREAI
errTsai, Pei-Chien; Liao, Yi-Chu; Chen, Po-Lin; Guo, Yuh-Cherng; Chen, Ying-Hao; Jih, Kang-Yang; Lin, Kon-Ping; Soong, Bing-Wen; Tsai, Ching-Paio; Lee, Yi-Chung
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Heterozygous HTRA1 mutations in Taiwanese patients with cerebral small vessel disease
err2017-10-01
err0
PREAI
errLiao, Y. C.; Chao, N. C.; Tsai, P. C.; Soong, B. W.; Lee, Y. C.
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Genetic and clinical paroxysmal kinesigenic dyskinesia in Taiwan: A genetic and clinical study of 69 patients
err2017-10-01
err0
PREAI
errJih, K. Y.; Kwan, S. Y.; Lee, Y. C.; Kon-Ping, L.; Yu, H. Y.; Chen, C.; Yen, D. J.; Chou, C. C.; Soong, B. W.; Liu, Y. T.
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Unmasking adrenoleukodystrophy in a cohort of cerebellar ataxia
err2017-10-01
err0
PREAI
errChen, Y. H.; Lee, Y. C.; Liao, Y. C.; Soong, B. W.
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