未登录 Beyond complement: comprehensive assessment of factor XIII plasma dynamics and genetics in atypical hemolytic uremic 超越补体:对非典型溶血尿毒症中因子XIII血浆动力学和遗传学的全面评估 Janszky, Noemi; Katona, Eva; Sinkovits, Gyorgy; Csuka, Dorottya; Haris, Agnes; Tasic, Velibor; Abazi-Emini, Nora; Aigner, Christof; Schmidt, Alice; Sunder-Plassmann, Gere; Bloudickova, Silvie Rajnochova; Prohaszka, Zoltan; Muszbek, Laszoo; Szilagyi, Agnes 分享 收藏
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Pregnancy in Complement-Mediated Thrombotic Microangiopathy: Maternal and Neonatal Outcomes Haninger-Vacariu, Natalja; Gleiss, Andreas; Gaggl, Martina; Aigner, Christof; Kain, Renate; Prohaszka, Zoltan; Szilagyi, Agnes; Csuka, Dorottya; Boehmig, Georg A.; Sunder-Plassmann, Raute; Sunder-Plassmann, Gere; Schmidt, Alice 分享 收藏
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Hemizygous nonsense variant in the moesin gene (MSN) leads to a new autoimmune phenotype of Immunodeficiency 50 Kovacs, Andras L.; Karteszi, Judit; Prohaszka, Zoltan; Kalmar, Tibor; Kesmarky, Gabor; Koltai, Katalin; Nagy, Zsuzsanna; Sebok, Judit; Vas, Tibor; Molnar, Krisztian; Berki, Timea; Borocz, Katalin; Gyomorei, Csaba; Szalma, Jozsef; Egyed, Miklos; Horvath, Szabina; Olah, Peter; Csuka, Dorottya; Nemeth, Viktoria; Gyulai, Rolland 分享 收藏
Searching for Genetic Biomarkers for Hereditary Angioedema Due to C1-Inhibitor Deficiency (C1-INH-HAE) Parsopoulou, Faidra; Loules, Gedeon; Zamanakou, Maria; Csuka, Dorottya; Szilagyi, Agnes; Kompoti, Maria; Porebski, Grzegorz; Psarros, Fotis; Magerl, Markus; Valerieva, Anna; Staevska, Maria; Obtulowicz, Krystyna; Maurer, Marcus; Speletas, Matthaios; Farkas, Henriette; Germenis, Anastasios E. 分享 收藏
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Complement Levels at Admission Reflecting Progression to Severe Acute Kidney Injury (AKI) in Coronavirus Disease 2019 (COVID-19): A Multicenter Prospective Cohort Study 冠状病毒疾病2019 (新型冠状病毒肺炎) 入院时补体水平反映严重急性肾损伤 (AKI) 进展: 一项多中心前瞻性队列研究 Henry, Brandon M.; Sinkovits, Gyorgy; Szergyuk, Ivan; de Oliveira, Maria Helena Santos; Lippi, Giuseppe; Benoit, Justin L.; Favaloro, Emmanuel J.; Pode-Shakked, Naomi; Benoit, Stefanie W.; Cooper, David S.; Muller, Veronika; Ivanyi, Zsolt; Gal, Janos; Reti, Marienn; Gopcsa, Laszlo; Remenyi, Peter; Szathmary, Beata; Lakatos, Botond; Szlavik, Janos; Bobek, Ilona; Prohaszka, Zita Z.; Forhecz, Zsolt; Csuka, Dorottya; Hurler, Lisa; Kajdacsi, Erika; Cervenak, Laszlo; Mezo, Blanka; Kiszel, Petra; Masszi, Tamas; Valyi-Nagy, Istvan; Prohaszka, Zoltan 分享 收藏
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The international WAO/EAACI guideline for the management of hereditary angioedema - The 2021 revision and update Maurer, Marcus; Magerl, Markus; Betschel, Stephen; Aberer, Werner; Ansotegui, Ignacio J.; Aygoeren-Puersuen, Emel; Banerji, Aleena; Bara, Noemi-Anna; Boccon-Gibod, Isabelle; Bork, Konrad; Bouillet, Laurence; Boysenl, Henrik Balle; Brodszki, Nicholas; Busse, Paula J.; Bygum, Anette; Caballero, Teresa; Cancian, Mauro; Castaldol, Anthony J.; Cohn, Danny M.; Csuka, Dorottya; Farkas, Henriette; Gompels, Mark; Gower, Richard; Grumach, Anete S.; Guidos-Fogelbach, Guillermo; Hide, Michihiro; Kang, Hye-Ryun; Kaplan, Allen P.; Katelaris, Constance H.; Kiani-Alikhan, Sorena; Lei, Wei-Te; Lockey, Richard F.; Longhurst, Hilary; Lumry, William; MacGinnitie, Andrew; Malbran, Alejandro; Martinez Saguer, Inmaculada; Matta Campos, Juan Jose; Nast, Alexander; Dinh Nguyen; Nieto-Martinez, Sandra A.; Pawankar, Ruby; Peter, Jonathan; Porebski, Grzegorz; Prior, Nieves; Reshef, Avner; Riedl, Marc; Ritchie, Bruce; Sheikh, Farrukh Rafique; Smith, William B.; Spaeth, Peter J.; Stobiecki, Marcin; Toubi, Elias; Varga, Lilian Agnes; Weller, Karsten; Zanichelli, Andrea; Zhi, Yuxiang; Zuraw, Bruce; Craig, Timothy 分享 收藏
The international WAO/EAACI guideline for the management of hereditary angioedema-The 2021 revision and update Maurer, Marcus; Magerl, Markus; Betschel, Stephen; Aberer, Werner; Ansotegui, Ignacio J.; Aygoeren-Puersuen, Emel; Banerji, Aleena; Bara, Noemi-Anna; Boccon-Gibod, Isabelle; Bork, Konrad; Bouillet, Laurence; Boysen, Henrik Balle; Brodszki, Nicholas; Busse, Paula J.; Bygum, Anette; Caballero, Teresa; Cancian, Mauro; Castaldo, Anthony; Cohn, Danny M.; Csuka, Dorrottya; Farkas, Henriette; Gompels, Mark; Gower, Richard; Grumach, Anete S.; Guidos-Fogelbach, Guillermo; Hide, Michihiro; Kang, Hye-Ryun; Kaplan, Allen Phillip; Katelaris, Constance; Kiani-Alikhan, Sorena; Lei, Wei-Te; Lockey, Richard; Longhurst, Hilary; Lumry, William R.; MacGinnitie, Andrew; Malbran, Alejandro; Saguer, Inmaculada Martinez; Matta, Juan Jose; Nast, Alexander; Nguyen, Dinh; Nieto-Martinez, Sandra A.; Pawankar, Ruby; Peter, Jonathan; Porebski, Grzegorz; Prior, Nieves; Reshef, Avner; Riedl, Marc; Ritchie, Bruce; Sheikh, Farrukh Rafique; Smith, William R.; Spaeth, Peter J.; Stobiecki, Marcin; Toubi, Elias; Varga, Lilian Agnes; Weller, Karsten; Zanichelli, Andrea; Zhi, Yuxiang; Zuraw, Bruce; Craig, Timothy 分享 收藏
Associations between the von Willebrand Factor-ADAMTS13 Axis, Complement Activation, and COVID-19 Severity and Mortality Sinkovits, Gyoergy; Reti, Marienn; Mueller, Veronika; Ivanyi, Zsolt; Gal, Janos; Gopcsa, Laszlo; Remenyi, Peter; Szathmary, Beata; Lakatos, Botond; Szlavik, Janos; Bobek, Ilona; Prohaszka, Zita Z.; Foerhecz, Zsolt; Mezo, Blanka; Csuka, Dorottya; Hurler, Lisa; Kajdacsi, Erika; Cervenak, Laszlo; Kiszel, Petra; Masszi, Tamas; Valyi-Nagy, Istvan; Prohaszka, Zoltan 分享 收藏
Molecular basis and outcomes of a typical haemolytic uraemic syndrome in Czech children (vol 179, pg 1739, 2020 Stolbova, Sarka; Bezdicka, Martin; Seeman, Tomas; Prohaszka, Zoltan; Csuka, Dorottya; Hrachovinova, Ingrid; Burkert, Jan; Simankova, Nadezda; Pruhova, Stepanka; Zieg, Jakub 分享 收藏
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FHR-5 Serum Levels and CFHR5 Genetic Variations in Patients With Immune Complex-Mediated Membranoproliferative Glomerulonephritis and C3-Glomerulopathy 免疫复合物介导的膜增生性肾小球肾炎和C3-Glomerulopathy患者的FHR-5血清水平和CFHR5遗传变异 Garam, Nora; Cserhalmi, Marcell; Prohaszka, Zoltan; Szilagyi, Agnes; Veszeli, Nora; Szabo, Edina; Uzonyi, Barbara; Ilias, Attila; Aigner, Christof; Schmidt, Alice; Gaggl, Martina; Sunder-Plassmann, Gere; Bajcsi, Dora; Brunner, Jurgen; Dumfarth, Alexandra; Cejka, Daniel; Flaschberger, Stefan; Floegelova, Hana; Haris, Agnes; Hartmann, Agnes; Heilos, Andreas; Mueller, Thomas; Rusai, Krisztina; Arbeiter, Klaus; Hofer, Johannes; Jakab, Daniel; Sinko, Maria; Szigeti, Erika; Bereczki, Csaba; Janko, Viktor; Kelen, Kata; Reusz, Gyoergy S.; Szabo, Attila J.; Klenk, Nora; Kobor, Krisztina; Kojc, Nika; Knechtelsdorfer, Maarten; Laganovic, Mario; Lungu, Adrian Catalin; Meglic, Anamarija; Rus, Rina; Levart, Tanja Kersnik; Macioniene, Ernesta; Miglinas, Marius; Pawlowska, Anna; Stompor, Tomasz; Podracka, Ludmila; Rudnicki, Michael; Mayer, Gert; Rysava, Romana; Reiterova, Jana; Saraga, Marijan; Seeman, Tomas; Zieg, Jakub; Sladkova, Eva; Stajic, Natasa; Szabo, Tamas; Capitanescu, Andrei; Stancu, Simona; Tisljar, Miroslav; Galesic, Kresimir; Tisler, Andras; Vainumae, Inga; Windpessl, Martin; Zaoral, Tomas; Zlatanova, Galia; Jozsi, Mihaly; Csuka, Dorottya 分享 收藏
A Novel Homozygous In-Frame Deletion in Complement Factor 3 Underlies Early-Onset Autosomal Recessive Atypical Hemolytic Uremic Syndrome-Case Report 补体因子3中的新型纯合框内缺失是早发性常染色体隐性遗传非典型溶血性尿毒症综合征的基础-病例报告 Pollack, Shirley; Eisenstein, Israel; Mory, Adi; Paperna, Tamar; Ofir, Ayala; Baris-Feldman, Hagit; Weiss, Karin; Veszeli, Nora; Csuka, Dorottya; Shemer, Revital; Glaser, Fabian; Prohaszka, Zoltan; Magen, Daniella 分享 收藏
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