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Development of Cellular Energy Metabolism During Differentiation of Human iPSCs into Cortical Neurons 人诱导多能干细胞(iPSCs)分化为皮层神经元过程中细胞能量代谢的发展 Danacikova, Sarka; Pecina, Petr; Pecinova, Alena; Svoboda, Jan; Vondrasek, David; Basello, Davide Alessandro; Cajka, Tomas; Hadraba, Daniel; Mracek, Tomas; Korinek, Vladimir; Otahal, Jakub 分享 收藏
Haplotype variability in mitochondrial rRNA predisposes to metabolic syndrome Pecina, Petr; Cunatova, Kristyna; Kaplanova, Vilma; Puertas-Frias, Guillermo; Silhavy, Jan; Tauchmannova, Katerina; Vrbacky, Marek; Cajka, Tomas; Gahura, Ondrej; Hlavackova, Marketa; Stranecky, Viktor; Kmoch, Stanislav; Pravenec, Michal; Houstek, Josef; Mracek, Tomas; Pecinova, Alena 分享 收藏
Ketogenic diet mitigates the pathogenic phenotype in TMEM70 deficient animal models Mracek, Tomas; Markovic, Aleksandra; Pecina, Petr; Pecinova, Alena; Vrbacky, Marek; Mikesova, Jana; Tauchmannova, Katerina; Kucera, Otto; Cervinkova, Zuzana; Pravenec, Michal; Houstek, Josef 分享 收藏
Mitochondrial translation is the primary determinant of secondary mitochondrial complex I deficiencies Cunatova, Kristyna; Vrbacky, Marek; Puertas-Frias, Guillermo; Alan, Lukas; Vanisova, Marie; Saucedo-Rodriguez, Maria Jose; Houstek, Josef; Fernandez-Vizarra, Erika; Neuzil, Jiri; Pecinova, Alena; Pecina, Petr; Mracek, Tomas 分享 收藏
Mitochondrial cytochrome c oxidase subunit 4 isoform 2 (Cox4i2) promotes hypoxia-induced reduction of the electron transport system in pulmonary arterial smooth muscle cells Giordano, Luca; Wittig, Ilka; Nolte-Gruetzner, Anika; Cabrera-Orefice, Alfredo; Jash, Sandipan; Pak, Oleg; Knoepp, Fenja; Ramser, Kerstin; Wahl, Joel; Pecina, Petr; Seeger, Werner; Weissmann, Norbert; Grossman, Lawrence I.; Huttemann, Maik; Sommer, Natascha 分享 收藏
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Haplotype variability in mitochondrial rRNA predisposes to metabolic syndrome Pecina, Petr; Cunatova, Kristyna; Kaplanova, Vilma; Puertas, Guillermo; Silhavy, Jan; Vrbacky, Marek; Tauchmannova, Katerina; Cajka, Tomas; Gahura, Ondrej; Hlavackova, Marketa; Kmoch, Stanislav; Pravenec, Michal; Houstek, Josef; Mracek, Tomas; Pecinova, Alena 分享 收藏
Restored biosynthetic pathways induced by MSCs serve as rescue mechanism in leukemia cells after L-asparaginase therapy Alquezar-Artieda, Natividad; Kuzilkova, Daniela; Roberts, Jennie; Hlozkova, Katerina; Pecinova, Alena; Pecina, Petr; Zwyrtkova, Martina; Potuckova, Eliska; Kavan, Daniel; Hermanova, Ivana; Zaliova, Marketa; Novak, Petr; Mracek, Tomas; Sramkova, Lucie; Tennant, Daniel A.; Trka, Jan; Starkova, Julia 分享 收藏
Mitochondrial oxygen sensing of acute hypoxia in specialized cells- Is there a unifying mechanism? Pak, Oleg; Nolte, Anika; Knoepp, Fenja; Giordano, Luca; Pecina, Petr; Huttemann, Maik; Grossman, Lawrence, I; Weissmann, Norbert; Sommer, Natascha 分享 收藏
Ketogenic diet can reduce pathologic presentation of TMEM70 deficiency in animal models Mracek, Tomas; Markovic, Aleksandra; Mikesova, Jana; Pecina, Petr; Pecinova, Alena; Vrbacky, Marek; Tauchmannova, Katerina; Shekhar, Nivasini; Simakova, Miroslava; Kucera, Otto; Cervinkova, Zuzana; Pravenec, Michal; Houstek, Josef 分享 收藏
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The role of SURF1 protein in cytochrome c oxidase biogenesis Rodriguez, Maria Jose Saucedo; Pecina, Petr; Cunatova, Kristyna; Vrbacky, Marek; Pecinova, Alena; Sobotka, Roman; Viscomi, Carlo; Zeviani, Massimo; Mracek, Tomas; Houstek, Josef 分享 收藏
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Essential Role of Mitochondrial Cytochrome c Oxidase Subunit 4 Isoform 2 (Cox4i2) for Acute Pulmonary Oxygen Sensing Giordano, Luca; Nolte, Anika; Wittig, Ilka; Pak, Oleg; Knoepp, Fenja; Ramser, Kerstin; Wahl, Joel; Huettemann, Maik; Grossman, Lawrence I.; Pecina, Petr; Ghofrani, Hossein A.; Seeger, Werner; Weissmann, Norbert; Giehl, Klaudia; Sommer, Natascha 分享 收藏
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Transgenic rescue approach ameliorates ATP synthase deficiency caused by the dysfunction of TMEM70 assembly factor in rat Alan, Lukas; Markovic, Aleksandra; Tauchmannova, Katerina; Simakova, Miroslava; Mlejnek, Petr; Kaplanova, Vilma; Pecina, Petr; Pecinova, Alena; Silhavy, Jan; Houstek, Josef; Pravenec, Michal; Mracek, Tomas 分享 收藏
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Genetic Complementation of ATP Synthase Deficiency Due to Dysfunction of TMEM70 Assembly Factor in Rat 大鼠TMEM70组装因子功能障碍引起的ATP合酶缺陷的遗传互补 Markovic, Aleksandra; Tauchmannova, Katerina; Simakova, Miroslava; Mlejnek, Petr; Kaplanova, Vilma; Pecina, Petr; Pecinova, Alena; Papousek, Frantisek; Liska, Frantisek; Silhavy, Jan; Mikesova, Jana; Neckar, Jan; Houstek, Josef; Pravenec, Michal; Mracek, Tomas 分享 收藏