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Johannes M. F. G. Aerts

University of Leiden

94H指数
609论文数
2.9W被引数
收录论文 226
发表时间
A Contemporary Pathomechanistic Nosology of Inherited Lysosomal Disorders当代遗传性溶酶体疾病的病理解剖分类学
err2026-09-06
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PREAI
errEamon P. McCarron; Nenad Blau; Emily R. Eden; Frances M. Platt; Johannes M. Aerts; Simon A. Jones; Carlos R. Ferreira; Karolina M. Stepien
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Unraveling A4GALT Mechanism and Its Modulation With Adamantyl-Galactosylceramide Analogues: Advancing Fabry Disease Therapeutic Strategies解析A4GALT机制及其通过金刚烷基-半乳糖基神经酰胺类似物的调控:推进法布里病治疗策略
err2026-08-28
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errOAAI
errNicky de Koster; Òscar Vidal-Gironès; Rowan de Graaf; Ken Kok; Lindsey T. Lelieveld; Jackelien Hoogervorst; Maria J. Ferraz; José Pablo Rivas-Fernández; Rob F. Lammers; Herman S. Overkleeft; Johannes M. F. G. Aerts; Rolf G. Boot; Carme Rovira; Marta Artola
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Links between COVID-19, long COVID and neurodegeneration: the role of glycosphingolipids新型冠状病毒肺炎,长COVID和神经变性之间的联系: 鞘糖脂的作用
err2026-01-29
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errOAAI
errMichael Spedding; Johannes Aerts; Steve Alexander; Aurélie-Gaëlle Bellozzi Woestelandt; Elena Chiricozzi; Alexandre Henriques; Pierre-Marie Lledo; Jean-Philippe Loeffler; Rushika Perera; Frances Platt; Pierre-François Pradat; Frédérique Rene; Anthony Schapira; Laura St Clair; Kevin Talbot; Maxime Taquet; Michal Toborek; Bradley Turner; Michael Zandi; Pierre Gressens
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LIMP-2 deficiency-associated glycolipid abnormalities in miceLIMP-2缺乏相关的糖脂异常在小鼠中
err2025-07-08
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errOAAI
errPaulo Gaspar; André R.A. Marques; Maria J. Ferraz; Markus Damme; Gertjan Kramer; Mina Mirzaian; Marion Gijbels; Roelof Ottenhoff; Cindy van Roomen; Herman S. Overkleeft; Michael Schwake; Saskia Heybrock; Maria Carmo Macário; Paul Saftig; Johannes M. Aerts
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A Multiomic Network Approach to Uncover Disease Modifying Mechanisms of Inborn Errors of Metabolism一种多组学网络方法,用于揭示先天性代谢紊乱的疾病修饰机制
err2025-05-30
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PREAI
errAaron Bender; Pablo Ranea-Robles; Evan G. Williams; Mina Mirzaian; J. Alexander Heimel; Christiaan N. Levelt; Ronald J. Wanders; Johannes M. Aerts; Jun Zhu
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Cultured Macrophage Models for the Investigation of Lysosomal Glucocerebrosidase and Gaucher Disease培养巨噬细胞模型用于溶酶体葡萄糖脑苷酶和戈谢病的研究
err2025-03-18
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errOAAI
errLouwerse, Max; Bila, Kateryna O.; van der Lienden, Martijn J. C.; de Beaufort, Arnout Jan M.; Boot, Rolf G.; Artola, Marta; van Eijk, Marco; Aerts, Johannes M. F. G.
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Lipid profiling in dried blood spots: A tool for diagnosing lysosomal diseases
err2025-02-01
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PREAI
errArevalo-Vargas, Isidro; Gonzalo, Irene Serrano; Roca-Esteve, Sonia; Lahoz, Carlos; Mozas, Pilar; Giraldo, Pilar; Ferraz, Maria Guimaraes Da Lomba; Aerts, Johannes
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Synthesis and Biological Evaluation of Deoxycyclophellitols as Human Retaining β-Glucosidase Inhibitors
err2024-11-03
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errOAAI
errRadchenko, Yevhenii; Su, Qin; Schroder, Sybrin S.; van Gijlswijk, Luke; Artola, Marta; Aerts, Johannes M. F. G.; Codee, Jeroen D. C.; Overkleeft, Herman S.
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substrates for GBA1 in the discovery of glycosylated sterols
err2024-11-01
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PREAI
errBannink, Stef; Bila, Kateryna O.; van Weperen, Joosje; Ligthart, Nina A. M.; Ferraz, Maria J.; Boot, Rolf G.; van der Vliet, Daan; Boer, Daphne. E. C.; Overkleeft, Herman S.; Artola, Marta; Aerts, Johannes M. F. G.
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From Mechanism-Based Retaining Glycosidase Inhibitors to Activity-Based Glycosidase Profiling
err2024-08-30
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errOAAI
errArtola, Marta; Aerts, Johannes M. F. G.; van der Marel, Gijsbert A.; Rovira, Carme; Codee, Jeroen D. C.; Davies, Gideon J.; Overkleeft, Herman S.
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Conformational and Electronic Variations in 1,2-and 1,5a-Cyclophellitols and their Impact on Retaining α-Glucosidase Inhibition
err2024-04-24
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errOAAI
errOfman, Tim P.; Heming, Jurriaan J. A.; Nin-Hill, Alba; Kuellmer, Florian; Moran, Elisha; Bennett, Megan; Steneker, Roy; Klein, Anne-Mei; Ruijgrok, Gijs; Kok, Ken; Armstrong, Zach W. B.; Aerts, Johannes M. F. G.; van Der Marel, Gijsbert A.; Rovira, Carme; Davies, Gideon J.; Artola, Marta; Codee, Jeroen D. C.; Overkleeft, Herman S.
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Exploring lipid biomarkers in Gaucher disease: LC-MS/MS analysis of dried blood spot samples
err2024-02-01
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PREAI
errArevalo-Vargas, Isidro; Gonzalo, Irene Serrano; Lahoz, Carlos; Mozas, Pilar; Giraldo, Pilar; Aerts, Johannes
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Mitochondrial dysfunction in NPC1-deficiency is not rescued by drugs targeting the glucosylceramidase GBA2 and the cholesterol-binding proteins TSPO and StARD1
err2024-02-01
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errOAAI
errWheeler, Simon; Bhardwaj, Meenakshi; Kenyon, Victor; Ferraz, Maria J.; Aerts, Johannes M. F. G.; Sillence, Dan J.
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Selective labelling of GBA2 in cells with fluorescent β-d-arabinofuranosyl cyclitol aziridines
err2024-01-01
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errOAAI
errSu, Qin; Louwerse, Max; Lammers, Rob F.; Maurits, Elmer; Janssen, Max; Boot, Rolf G.; Borlandelli, Valentina; Offen, Wendy A.; Linzel, Daniel; Schroder, Sybrin P.; Davies, Gideon J.; Overkleeft, Herman S.; Artola, Marta; Aerts, Johannes M. F. G.
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Structure-guided design of C3-branched swainsonine as potent and selective human Golgi α-mannosidase (GMII) inhibitor
err2024-01-01
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PREAI
errKoemans, Tony; Bennett, Megan; Ferraz, Maria J.; Armstrong, Zachary; Artola, Marta; Aerts, Johannes M. F. G.; Codee, Jeroen D. C.; Overkleeft, Herman S.; Davies, Gideon J.
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Phase-Separated Lipid-Based Nanoparticles: Selective Behavior at the Nano-Bio Interface相分离的基于脂质的纳米颗粒: 在纳米生物界面的选择行为
err2023-12-06
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errOAAI
errPapadopoulou, Panagiota; van der Pol, Rianne; van Hilten, Niek; van Os, Winant L.; Pattipeiluhu, Roy; Arias-Alpizar, Gabriela; Knol, Renzo Aron; Noteborn, Willem; Moradi, Mohammad-Amin; Ferraz, Maria Joao; Aerts, Johannes Maria Franciscus Gerardus; Sommerdijk, Nicolaas Antonius Johannes Maria; Campbell, Frederick; Risselada, Herre Jelger; Sevink, Geert Jan Agur; Kros, Alexander
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Glycoprotein non-metastatic protein B (GPNMB) plasma values in patients with chronic visceral acid sphingomyelinase deficiency慢性内脏酸鞘磷脂酶缺乏症患者的糖蛋白非转移蛋白B (GPNMB) 血浆值
err2023-08-01
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errOAAI
errEskes, Eline C. B.; van der Lienden, Martijn J. C.; Sjouke, Barbara; van Vliet, Laura; Brands, Marion M. M. G.; Hollak, Carla E. M.; Aerts, Johannes M. F. G.
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Gaucher disease protects against tuberculosis
err2023-02-06
err9
errOAAI
errFan, Jingwen; Hale, Victoria L.; Lelieveld, Lindsey T.; Whitworth, Laura J.; Busch-Nentwich, Elisabeth M.; Troll, Mark; Edelstein, Paul H.; Cox, Timothy M.; Roca, Francisco J.; Aerts, Johannes M. F. G.; Ramakrishnan, Lalita
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Glycosphingolipids assessments of Gaucher disease patients from dried blood spots samples by LC/MS-MS
err2023-02-01
err0
PREAI
errArevalo-Vargas, Isidro; Lopez de Frutos, Laura; Serrano Gonzalo, Irene; Lahoz, Carlos; Mozas, Pilar; Giraldo, Pilar; Ferraz, Maria J.; Aerts, Johannes
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