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French protocol for the diagnosis and management of hereditary angioedema 法国关于遗传性血管性水肿的诊断和管理方案 Boccon-Gibod, Isabelle; Fain, Olivier; Gobert, Delphine; Debord, Sophie; Aubineau, Magali; Ozanne, Nicolas; Defendi, Federica; Gompel, Anne; Hardy, Gaelle; Javaud, Nicolas; Lehmann, Audrey; Pagnier, Anne; Pelletier, Fabien; Bocquet, Alexis; Du Thanh, Aurelie; Launay, David; Bouillet, Laurence 分享 收藏
Janus kinase and calcineurin-inhibitor combination in anti-MDA5 dermatomyositis: No significant survival benefit but reassuring safety profile Janus kinase与钙调神经磷酸酶抑制剂联合治疗抗-MDA5皮肌炎:无显著生存获益但安全性特征令人放心 Pagis, Valentine; Astouati, Quentin; Pacoureau, Lucas; Nguyen, Yann; Bay, Pierre; Roux, Antoine; Gallay, Laure; Cottin, Vincent; Terrier, Benjamin; Meyer, Alain; Cerf, Charles; Neuville, Mathilde; Hervier, Baptiste; Renaud, Arthur; Suzon, Benoit; Schleinitz, Nicolas; Papo, Thomas; Priou, Pascaline; Mekinian, Arsene; Ullmer, Audrey; Oehler, Erwan; Gensous, Noemie; Berezne, Alice; Martin, Luc De Saint; Marhadour, Thierry; Martin, Mickael; Servettaz, Amelie; Samson, Maxime; Gilardin, Laurent; Charles, Pierre; Woessner, Juliette; Carmoi, Thierry; Dilly, Baptiste; Mauhin, Wladimir; Baillet, Nicolas; Humbert, Sebastien; Thoreau, Benjamin; Lemaitre, Marine; Pendu, Claire Le; Loiseau, Pierre; Quemeneur, Thomas; Blanchard, Elodie; Voermans, Nicol; Launay, David; Nunes, Hilario; Benveniste, Olivier; Uzunhan, Yurdagul; Allenbach, Yves 分享 收藏
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An untargeted metabolomic study using MALDI-mass spectrometry imaging reveals region-specific biomarkers associated with bowel inflammation 使用MALDI质谱成像的非靶向代谢组学研究揭示了与肠道炎症相关的区域特异性生物标志物 Ponzoni, Adele; Speca, Silvia; Hartle, Matthew; Gerstenberg, Amandine; Tomezyk, Aurore; Senechal, Victor; Karnik, Shane; Dubuquoy, Laurent; Launay, David; Deprez-Poulain, Rebecca; Gaudin, Mathieu; Ramos, Corinne; Deprez, Benoit 分享 收藏
Angioedema due to Acquired C1-Inhibitor Deficiency Associated With Monoclonal Gammopathies of Undetermined Significance Characteristics of a French National Cohort 法国国家队列的特征与未确定的意义的单克隆丙种球蛋白病相关的获得性C1-Inhibitor缺乏症引起的血管性水肿 Lahuna, Constance; Defendi, Federica; Bouillet, Laurence; Boccon-Gibod, Isabelle; Mekinian, Arsene; Coppo, Paul; Adamski, Henri; Amarger, Stephanie; Armengol, Guillaume; Aubineau, Magali; Bibes, Beatrice; Blanchard-Delaunay, Claire; Blaison, Gilles; Brihaye, Benoit; Cathebras, Pascal; Caubet, Olivier; Demoreuil, Claire; Desblache, Julien; Durupt, Francois; Gayet, Stephane; Gondran, Guillaume; Hadjadj, Jerome; Kalmi, Galith; Kanny, Gisele; Lacoste, Marion; Launay, David; Ly, Kim Heang; Mcavoy, Chloe; Martin, Ludovic; Ollivier, Yann; Pelletier, Fabien; Robbins, Aylsa; Roos-Weil, Damien; Fain, Olivier; Gobert, Delphine 分享 收藏
Diffusing Capacity of the Lungs for Carbon Monoxide and Echocardiographic Parameters in Identifying Mild Pulmonary Hypertension in the EUSTAR Cohort of Patients With Systemic Sclerosis 在系统性硬化症患者的EUSTAR队列中,一氧化碳和超声心动图参数的肺扩散能力可识别轻度肺动脉高压 Colalillo, Amalia; Hachulla, Eric; Pellicano, Chiara; Smith, Vanessa; Bergmann, Christina; Riemekasten, Gabriela; Zanatta, Elisabetta; Henes, Jorg; Launay, David; Marcoccia, Antonella; Gheorghiu, Ana Maria; Truchetet, Marie-Elise; Iannone, Florenzo; Aznar, Carmen Pilar Simeon; Oliveira, Susana; Vonk, Madelon; Del Galdo, Francesco; Rosato, Edoardo 分享 收藏
Comparison of prognostic scores according to WHO classification in 170 patients with advanced mastocytosis and C-finding treated with midostaurin 根据WHO分类的170例晚期肥大细胞增多症和midostaurin治疗的C发现患者的预后评分比较 Heiblig, Mael; Gourguechon, Clement; Guilpain, Philippe; Bulai-Livideanu, Cristina; Barete, Stephane; Chantran, Yannick; Agopian, Julie; Brenet, Fabienne; Dubreuil, Patrice; Lespinasse, Jeremie; Lemal, Richard; Tournilhac, Olivier; Terriou, Louis; Launay, David; Bouillet, Laurence; Chatain, Catharina; Damaj, Ghandi; Ballul, Thomas; Greco, Celine; Polivka, Laura; Frenzel, Laurent; Meni, Cecile; Bouktit, Hassiba; Benabou, Dina; Gaudy-Marqueste, Caroline; Gousseff, Marie; Le Mouel, Edwige; Neel, Antoine; Ranta, Dana; Jaussaud, Roland; Molina, Thierry Jo; Bruneau, Julie; Villarese, Patrick; Lhermitte, Ludovic; Maouche-Chretien, Leila; Temple, Marie; Kosmider, Olivier; Javier, Rose-Marie; Pelletier, Fabien; Castelain, Florence; Retornaz, Frederique; Cabrera, Quentin; Zunic, Patricia; Gourin, Marie Pierre; Wierzbicka-Hainaut, Ewa; Viallard, Jean Francois; Lavigne, Christian; Hoarau, Cyrille; Durieu, Isabelle; Dimicoli-Salazar, Sophie; Torregrosa-Diaz, Jose Miguel; Wemeau, Mathieu; Soria, Angele; Arock, Michel; Bodemer, Christine; Lortholary, Olivier; Hermine, Olivier; Rossignol, Julien 分享 收藏
Comparative Analysis of Laboratory-Scale Immunoglobulin G Purification Methods from Human Serum 实验室规模人血清免疫球蛋白G纯化方法的比较分析 Bourel, Louisa; Bray, Fabrice; Vivier, Solange; Flament, Stephanie; Guilbert, Lucile; Chepy, Aurelien; Rolando, Christian; Launay, David; Dubucquoi, Sylvain; Sobanski, Vincent 分享 收藏
Characteristics and impact of infiltration of B-cells from systemic sclerosis patients in a 3D healthy skin model 3D健康皮肤模型中系统性硬化症患者b细胞浸润的特征和影响 Le Maitre, Mathilde; Guerrier, Thomas; Collet, Aurore; Derhourhi, Mehdi; Meneboo, Jean-Pascal; Toussaint, Benedicte; Bonnefond, Amelie; Villenet, Celine; Sebda, Sheherazade; Bongiovanni, Antonino; Tardivel, Meryem; Simon, Myriam; Jendoubi, Manel; Daunou, Blanche; Largy, Alexis; Figeac, Martin; Dubucquoi, Sylvain; Launay, David 分享 收藏
Chronic Exposure to Both Electronic and Conventional Cigarettes Alters Ileum and Colon Turnover, Immune Function, and Barrier Integrity in Mice 长期接触电子烟和传统香烟会改变小鼠的回肠和结肠周转,免疫功能和屏障完整性 Djouina, Madjid; Ollivier, Anais; Waxin, Christophe; Kervoaze, Gwenola; Pichavant, Muriel; Caboche, Segolene; Achour, Djamal; Grare, Celine; Beury, Delphine; Hot, David; Antherieu, Sebastien; Lo-Guidice, Jean-Marc; Dubuquoy, Laurent; Launay, David; Vignal, Cecile; Gosset, Philippe; Body-Malapel, Mathilde 分享 收藏
Prevalence of anti-Ro52-kDa/SSA (TRIM21) antibodies and associated clinical phenotype in systemic sclerosis: Data from a French cohort, a systematic review and meta-analysis 系统性硬化症中anti-Ro52-kDa/SSA (TRIM21) 抗体的患病率和相关的临床表型: 来自法国队列的数据,系统评价和荟萃分析 Martel, Marie-Elise; Leurs, Amelie; Launay, David; Behal, Helene; Chepy, Aurelien; Collet, Aurore; Sanges, Sebastien; Hachulla, Eric; Dubucquoi, Sylvain; Dauchet, Luc; Sobanski, Vincent 分享 收藏
Efficacy and safety of mammalian target of rapamycin inhibitors in systemic mastocytosis: A nationwide French pilot study 哺乳动物雷帕霉素靶蛋白抑制剂在系统性肥大细胞增多症中的疗效和安全性: 一项全国性的法国试点研究 Moraly, Josquin; Rossignol, Julien; Rouzaud, Claire; Gabas, Thomas; Bouktit, Hassiba; Lhermitte, Ludovic; Canioni, Danielle; Fraitag, Sylvie; Bruneau, Julie; Barete, Stephane; Suarez, Felipe; Ballul, Thomas; Meni, Cecile; Polivka, Laura; Terriou, Louis; Launay, David; Bouillet, Laurence; Gaudy-Marqueste, Caroline; Gousseff, Marie; Le Mouel, Edwige; Neel, Antoine; Ranta, Dana; Jaussaud, Roland; Guilpain, Philippe; Frenzel, Laurent; Agopian, Julie; Dubreuil, Patrice; Greco, Celine; Dimicoli-Salazar, Sophie; Heiblig, Mael; Gourguechon, Clement; Tournilhac, Olivier; Javier, Rose-Marie; Castelain, Florence; Cabrera, Quentin; Gourin, Marie Pierre; Wierzbicka-Hainaut, Ewa; Torregrosa-Diaz, Jose Miguel; Bulai, Cristina; Lavigne, Christian; Hoarau, Cyrille; Arock, Michel; Damaj, Gandhi; Lortholary, Olivier; Hermine, Olivier 分享 收藏