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William T. Pu

Boston Children's Hospital

91H指数
333论文数
2.8W被引数
收录论文 180
发表时间
SORBS2 regulates diastolic function through cytoskeletal networks and calcium handlingSORBS2通过细胞骨架网络和钙处理调节舒张功能
err2026-06-17
err0
errOAAI
errZexuan Wu; Camille Blandin; Jiehui Chen; Jiajin Li; Li He; Qing Ma; Michael M. Peters; Anna Ponek; Dogacan Yucel; Kevin Kit Parker; Fujian Lu; William T. Pu
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An RYR2-interacting fragment of MYBPC3 mitigates arrhythmia in human iPSC-CM and mouse models of CPVTMYBPC3与RYR2相互作用的一个片段可减轻人类iPSC-CM和CPVT小鼠模型中的心律失常
err2026-05-05
err0
PREAI
errFujian Lu; Zexuan Wu; Shaopeng Chi; Jiajin Li; Anna Ponek; Carter Liou; Qing Ma; Durgesh Bonde; Nikoleta Pavlaki; Mason E. Sweat; Sanam Shafaattalab; Yashasvi Tharani; Maksymilian Prondzynski; Vassilios J. Bezzerides; William T. Pu
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PCBP1 regulates alternative splicing of AARS2 in congenital cardiomyopathyPCBP1调节先天性心肌病中AARS2的可变剪接
err2026-04-20
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errOAAI
errYao Wei Lu; Zhuomin Liang; Kerry Dorr; Samantha Ruiz; Xiaoran Huang; Denise Fangnibo Hanvi; Sheri M. Juntilla; Gisela Beutner; Shuhan Lyu; Haipeng Guo; Tiago Fernandes; Ramon A. Espinoza-Lewis; Tingting Wang; Kathryn Li; Xue Li; Gurinder Bir Singh; Yi Wang; Rui Deng; Douglas Cowan; John D. Mably; William T. Pu; Jessie Huang; George A. Porter; Frank Conlon; Hong Chen; Da-Zhi Wang
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Nrf1 coordinates proteasome activity and autophagy to maintain cardiac proteostasisNrf1协调蛋白酶体活性和自噬以维持心脏蛋白质稳态
err2026-04-17
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errOAAI
errLakindu P. Kankanamge; Hyunji An; Qin Guo; Maksymillian Prondzynski; Soon Ho Kwon; Durgesh Anil Bonde; William T. Pu; Eric N. Olson; Miao Cui
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Mechanotyping of Organoids for Assessing Drug-Induced Injuries类器官的力学分型用于评估药物诱导损伤
err2025-11-05
err0
PREAI
errMurat Kaynak; Mehmet D. Aşık; Elif E. Inan; Maksymilian Prondzynski; Hamzeh Ghasemzadeh; Amir Poorghani; Yashasvi Tharani; Matilda Holtz; Daryush D. Mehta; William T. Pu; Orhun K. Muratoglu; Martin L. Yarmush; Alexander Alexeev; O. Berk Usta
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The drug-elicitable alternative splicing module for tunable vector expression in the heart该药物可诱导的替代性剪接模块用于心脏中可调向量的表达
err2025-06-13
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PREAI
errZhan Chen; Luzi Yang; Yueyang Zhang; Jiting Li; Yuhan Yang; Yue Li; Linwei Fan; Wei Chen; Lei Miao; Jin Liu; Gonglie Chen; Ze Wang; Yifei Li; Fei Gao; Jing Zhou; Lemin Zheng; Yan Zhang; Dongyu Zhao; William T. Pu; Ke Yang; Erdan Dong; Yuxuan Guo
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Rapid generation of functional vascular organoids via simultaneous transcription factor activation of endothelial and mural lineages通过同时激活内皮和壁细胞系转录因子,快速生成功能性血管类器官
err2025-06-13
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PREAI
errLiyan Gong; Yadong Zhang; Yonglin Zhu; Umji Lee; Allen Chilun Luo; Xiang Li; Xi Wang; Danyang Chen; William T. Pu; Ruei-Zeng Lin; Minglin Ma; Miao Cui; Kaifu Chen; Kai Wang; Juan M. Melero-Martin
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Dysregulation of N-terminal acetylation causes cardiac arrhythmia and cardiomyopathyN-末端乙酰化失调导致心律失常和心肌病
err2025-04-16
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errYoshinaga, Daisuke; Craven, Isabel; Feng, Rui; Prondzynski, Maksymilian; Shani, Kevin; Tharani, Yashasvi; Mayourian, Joshua; Joseph, Milosh; Walker, David; Bortolin, Raul H.; Carreon, Chrystalle Katte; Boss, Bridget; Upton, Sheila; Parker, Kevin Kit; Pu, William T.; Bezzerides, Vassilios J.
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Non-Cell-Autonomous Cardiomyocyte Regulation Complicates Gene Supplementation Therapy for Lmna-Associated Cardiac Defects in Mice
err2024-11-01
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errOAAI
errSun, Yueshen; Guo, Congting; Chen, Zhan; Lin, Junsen; Yang, Luzi; Zhang, Yueyang; Wu, Chenyang; Zhao, Dongyu; Jardin, Blake; Pu, William T.; Zhao, Mingming; Dong, Erdan; Hu, Xiaomin; Zhang, Shuyang; Guo, Yuxuan
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Antisense Oligonucleotide Therapy for Calmodulinopathy
err2024-10-08
err0
PREAI
errBortolin, Raul H.; Nawar, Farina; Park, Chaehyoung; Trembley, Michael A.; Prondzynski, Maksymilian; Sweat, Mason E.; Wang, Peizhe; Chen, Jiehui; Lu, Fujian; Liou, Carter; Berkson, Paul; Keating, Erin M.; Yoshinaga, Daisuke; Pavlaki, Nikoleta; Samenuk, Thomas; Cavazzoni, Cecilia B.; Sage, Peter T.; Ma, Qing; Whitehill, Robert D.; Abrams, Dominic J.; Carreon, Chrystalle Katte; Putra, Juan; Alexandrescu, Sanda; Guo, Shuai; Tsai, Wen-Chin; Rubart, Michael; Kubli, Dieter A.; Mullick, Adam E.; Bezzerides, Vassilios J.; Pu, William T.
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Virally delivered CMYA5 enhances the assembly of cardiac dyads
err2024-09-05
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PREAI
errLu, Fujian; Liou, Carter; Ma, Qing; Wu, Zexuan; Xue, Bingqing; Xia, Yu; Xia, Shutao; Trembley, Michael A.; Ponek, Anna; Xie, Wenjun; Shani, Kevin; Bortolin, Raul H.; Prondzynski, Maksymilian; Berkson, Paul; Zhang, Xiaoran; Naya, Francisco J.; Bedi, Kenneth C.; Margulies, Kenneth B.; Zhang, Donghui; Parker, Kevin K.; Pu, William T.
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Activation of VGLL4 Suppresses Cardiomyocyte Maturational Hypertrophic Growth
errCELLS
IF5.2
err2024-08-13
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errOAAI
errFarley, Aaron; Gao, Yunan; Sun, Yan; Zohrabian, Sylvia; Pu, William T.; Lin, Zhiqiang
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RBFOX2 haploinsufficiency impairs cardiomyocyte adhesion and contractility through faulty RNA metabolism
err2024-08-02
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PREAI
errHuang, Mengmeng; Gao, Xinlei; Trembley, Michael; Prondzynski, Maksymilian; Tharani, Yashasvi; Nawar, Farina; Zheng, Rongbin; Aigner, Stefan; Yeo, Gene; Pu, William; Chen, Kaifu; Burns, C. Geoffrey; Burns, Caroline
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Antisense Oligonucleotide Treatment of Calmodulinopathy
err2024-08-02
err0
PREAI
errBortolin, Raul; Nawar, Farina; Trembley, Michael; Prondzynski, Maksymilian; Sweat, Mason; Wang, Peizhe; Chaehyoung, Park; Lu, Fujian; Keating, Erin; Yoshinaga, Daisuke; Pavlaki, Nikoleta; Cavazzoni, Cecilia B.; Sage, Peter T.; Whitehill, Robert D.; Abrams, Dominic; Carreon, Chrystalle; Putra, Juan; Alexandrescu, Sanda; Guo, Shuai; Tsai, Owen; Rubart, Michael; Kubli, Dieter; Mullick, Adam; Bezzerides, Vassilios; Pu, William
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CHD4 Interacts With TBX5 to Maintain the Gene Regulatory Network of Postnatal Atrial Cardiomyocytes
err2024-08-02
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PREAI
errSweat, Mason; Shi, Wei; Keating, Erin; Ponek, Anna; Conlon, Frank; Pu, William
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In vivo proximity proteomics uncovers palmdelphin (PALMD) as a Z-disc-associated mitigator of isoproterenol-induced cardiac injury
err2024-07-23
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PREAI
errGuo, Cong-ting; Jardin, Blake D.; Lin, Jun-sen; Ambroise, Rachelle L.; Wang, Ze; Yang, Lu-zi; Mazumdar, Neil; Lu, Fu-jian; Ma, Qing; Cao, Yang-po; Liu, Can-zhao; Li, Kai-long; Liu, Xu-jie; Lan, Feng; Zhao, Ming-ming; Xiao, Han; Dong, Er-dan; Pu, William T.; Guo, Yu-xuan
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Allele-Specific Suppression of Variant MHC With High-Precision RNA Nuclease CRISPR-Cas13d Prevents Hypertrophic Cardiomyopathy
err2024-07-23
err2
errOAAI
errYang, Ping; Lou, Yingmei; Geng, Zilong; Guo, Zhizhao; Wu, Shuo; Li, Yige; Song, Kaiyuan; Shi, Ting; Zhang, Shasha; Xiong, Junhao; Chen, Alex F.; Li, Dali; Pu, William T.; Da, Lintai; Zhang, Yan; Sun, Kun; Zhang, Bing
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Therapeutic Inhibition of LincRNA-p21 Protects Against Cardiac Hypertrophy
err2024-07-19
err1
PREAI
errWang, Yi; Zhang, Mingming; Wang, Rong; Lin, Jing; Ma, Qing; Guo, Haipeng; Huang, Huihui; Liang, Zhuomin; Cao, Yangpo; Zhang, Xiaoran; Lu, Yao Wei; Liu, Jianming; Xiao, Feng; Yan, Hualin; Dimitrova, Nadya; Huang, Zhan-Peng; Mably, John D.; Pu, William T.; Wang, Da-Zhi
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