Raymond A. Frizzell - Publications, H-index & Citations

Raymond A. Frizzell

Erasmus MC

75H指数

207论文数

2.0W被引数

收录论文 65

发表时间

Separating the contributions of SLC26A9 and CFTR to anion secretion in primary human bronchial epithelia

AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

IF3.5

2021-12-01

OAAI

Larsen, Mads B.; Choi, Jeannie J.; Wang, Xiaohui; Myerburg, Michael M.; Frizzell, Raymond A.; Bertrand, Carol A.

Cystic Fibrosis Transmembrane Conductance Regulator Folding Mutations Reveal Differences in Corrector Efficacy Linked to Increases in Immature Cystic Fibrosis Transmembrane Conductance Regulator Expression

FRONTIERS IN PHYSIOLOGY

IF3.4

2021-10-26

OAAI

Peters, Kathryn W.; Gong, Xiaoyan; Frizzell, Raymond A.

SFPQ rescues F508del-CFTR expression and function in cystic fibrosis bronchial epithelial cells

SCIENTIFIC REPORTS

IF3.9

2021-08-17

OAAI

Kumar, Parameet; Soni, Dharmendra Kumar; Sen, Chaitali; Larsen, Mads B.; Mazan-Mamczarz, Krystyna; Piao, Yulan; De, Supriyo; Gorospe, Myriam; Frizzell, Raymond A.; Biswas, Roopa

Phenotypes of CF rabbits generated by CRISPR/Cas9-mediated disruption of the CFTR gene

JCI INSIGHT

IF6.1

2021-01-11

OAAI

Xu, Jie; Livraghi-Butrico, Alessandra; Hou, Xia; Rajagopalan, Carthic; Zhang, Jifeng; Song, Jun; Jiang, Hong; Wei, Hong-Guang; Wang, Hui; Bouhamdan, Mohamad; Ruan, Jinxue; Yang, Dongshan; Qiu, Yining; Xie, Youming; Barrett, Ronald; McClellan, Sharon; Mou, Hongmei; Wu, Qingtian; Chen, Xuequn; Rogers, Troy D.; Wilkinson, Kristen J.; Gilmore, Rodney C.; Esther, Charles R., Jr.; Zaman, Khalequz; Liang, Xiubin; Sobolic, Michael; Hazlett, Linda; Zhang, Kezhong; Frizzell, Raymond A.; Gentzsch, Martina; O'Neal, Wanda K.; Grubb, Barbara R.; Chen, Y. Eugene; Boucher, Richard C.; Sun, Fei

Global assessment of the integrated stress response in CF patient-derived airway and intestinal tissues CF患者来源的气道和肠组织的综合应激反应的全球评估

JOURNAL OF CYSTIC FIBROSIS

IF6

2020-11-01

OAAI

Bampi, Giovana B.; Rauscher, Robert; Kirchner, Sebastian; Oliver, Kathryn E.; Bijvelds, Marcel J. C.; Santos, Leonardo A.; Wagner, Johannes; Frizzell, Raymond A.; de Jonge, Hugo R.; Sorscher, Eric J.; Ignatova, Zoya

CK19 stabilizes CFTR at the cell surface by limiting its endocytic pathway degradation

FASEB JOURNAL

IF4.2

2019-08-26

OAAI

Hou, Xia; Wu, Qingtian; Rajagopalan, Carthic; Zhang, Chunbing; Bouhamdan, Mohamad; Wei, Hongguang; Chen, Xuequn; Zaman, Khalequz; Li, Chunying; Sun, Xiaonan; Chen, Song; Frizzell, Raymond A.; Sun, Fei

Different SUMO paralogues determine the fate of wild-type and mutant CFTRs: biogenesis versus degradation

MOLECULAR BIOLOGY OF THE CELL

IF2.7

2019-01-01

OAAI

Gong, Xiaoyan; Liao, Yong; Ahner, Annette; Larsen, Mads Breum; Wang, Xiaohui; Bertrand, Carol A.; Frizzell, Raymond A.

Silencing of the Hsp70-specific nucleotide-exchange factor BAG3 corrects the F508del-CFTR variant by restoring autophagy Hsp70-specific核苷酸交换因子BAG3的沉默通过恢复自噬来纠正F508del-CFTR变异

JOURNAL OF BIOLOGICAL CHEMISTRY

IF3.9

2018-08-01

OAAI

Hutt, Darren M.; Mishra, Sanjay Kumar; Roth, Daniela Martino; Larsen, Mads Breum; Angles, Frederic; Frizzell, Raymond A.; Balch, William E.

The CFTR trafficking mutation F508del inhibits the constitutive activity of SLC26A9

AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY

IF3.5

2017-06-01

OAAI

Bertrand, Carol A.; Mitra, Shalini; Mishra, Sanjay K.; Wang, Xiaohui; Zhao, Yu; Pilewski, Joseph M.; Madden, Dean R.; Frizzell, Raymond A.

Functional and molecular identification of a TASK-1 potassium channel regulating chloride secretion through CFTR channels in the shark rectal gland: implications for cystic fibrosis

AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY

IF4.7

2016-12-01

OAAI

Telles, Connor J.; Decker, Sarah E.; Motley, William W.; Peters, Alexander W.; Mehr, Ali Poyan; Frizzell, Raymond A.; Forrest, John N., Jr.

VAMP-associated Proteins (VAP) as Receptors That Couple Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Proteostasis with Lipid Homeostasis

JOURNAL OF BIOLOGICAL CHEMISTRY

IF3.9

2016-03-01

OAAI

Ernst, Wayne L.; Shome, Kuntala; Wu, Christine C.; Gong, Xiaoyan; Frizzell, Raymond A.; Aridor, Meir

Simple image-based no-wash method for quantitative detection of surface expressed CFTR

METHODS

IF4.3

2016-03-01

OAAI

Larsen, Mads Breum; Hu, Jennifer; Frizzell, Raymond A.; Watkins, Simon C.

From CFTR biology toward combinatorial pharmacotherapy: expanded classification of cystic fibrosis mutations

MOLECULAR BIOLOGY OF THE CELL

IF2.7

2016-02-01

473

OAAI

Veit, Gudio; Avramescu, Radu G.; Chiang, Annette N.; Houck, Scott A.; Cai, Zhiwei; Peters, Kathryn W.; Hong, Jeong S.; Pollard, Harvey B.; Guggino, William B.; Balch, William E.; Skach, William R.; Cutting, Garry R.; Frizzell, Raymond A.; Sheppard, David N.; Cyr, Douglas M.; Sorscher, Eric J.; Brodsky, Jeffrey L.; Lukacs, Gergely L.

Divergent signaling via SUMO modification: potential for CFTR modulation

AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY

IF4.7

2016-02-01

OAAI

Ahner, Annette; Gong, Xiaoyan; Frizzell, Raymond A.

Non-native Conformers of Cystic Fibrosis Transmembrane Conductance Regulator NBD1 Are Recognized by Hsp27 and Conjugated to SUMO-2 for Degradation

JOURNAL OF BIOLOGICAL CHEMISTRY

IF3.9

2016-01-01

OAAI

Gong, Xiaoyan; Ahner, Annette; Roldan, Ariel; Lukacs, Gergely L.; Thibodeau, Patrick H.; Frizzell, Raymond A.

Activation of 3-Phosphoinositide-dependent Kinase 1 (PDK1) and Serum-and Glucocorticoid-induced Protein Kinase 1 (SGK1) by Short-chain Sphingolipid C4-ceramide Rescues the Trafficking Defect of ΔF508-Cystic Fibrosis Transmembrane Conductance Regulator (ΔF508-CFTR)

JOURNAL OF BIOLOGICAL CHEMISTRY

IF3.9

2014-12-01

OAAI

Caohuy, Hung; Yang, Qingfeng; Eudy, Yvonne; Ha, Thien-An; Xu, Andrew E.; Glover, Matthew; Frizzell, Raymond A.; Jozwik, Catherine; Pollard, Harvey B.

Regulatory R region of the CFTR chloride channel is a dynamic integrator of phospho-dependent intra- and intermolecular interactions

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA

IF9.1

2013-11-04

138

OAAI

Bozoky, Zoltan; Krzeminski, Mickael; Muhandiram, Ranjith; Birtley, James R.; Al-Zahrani, Ateeq; Thomas, Philip J.; Frizzell, Raymond A.; Ford, Robert C.; Forman-Kay, Julie D.

Cystic fibrosis transmembrane conductance regulator degradation: cross-talk between the ubiquitylation and SUMOylation pathways

FEBS JOURNAL

IF4.2

2013-07-22

OAAI

Ahner, Annette; Gong, Xiaoyan; Frizzell, Raymond A.

Small heat shock proteins target mutant cystic fibrosis transmembrane conductance regulator for degradation via a small ubiquitin-like modifier-dependent pathway

MOLECULAR BIOLOGY OF THE CELL

IF2.7

2013-01-15

OAAI

Ahner, Annette; Gong, Xiaoyan; Schmidt, Bela Z.; Peters, Kathryn W.; Rabeh, Wael M.; Thibodeau, Patrick H.; Lukacs, Gergely L.; Frizzell, Raymond A.