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Journal of Cystic Fibrosis cover

Journal of Cystic Fibrosis

IF6
Papers2880
Citations7272
Journal Papers 2879
Publication Date
Antiviral defenses are diminished at birth in cystic fibrosis pig airways
delete2026-08-02
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deleteJennifer A. Bartlett; Miguel E. Ortiz; Linda S. Powers; Christine L. Wohlford-Lenane; Camilla E. Hippee; Laura Marquez Loza; Justin W. Kaufman; Brajesh K. Singh; Daniel I. Sands; Eric D. Huntemann; Ashley L. Cooney; Mark P. Rogan; Clifford C. Taggart; David K. Meyerholz; Paul B. McCray
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Real-world population pharmacokinetic modeling of elexacaftor, tezacaftor, and ivacaftor
delete2026-07-30
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deleteAK Kunzelmann; S Naehrig; C Shad; M Breuling; M Goetschke; K Habler; O Sommerburg; J Behr; LM Schatz; J Starp; M Vogeser; M Paal; U Liebchen
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Forced vital capacity in pulmonary exacerbations of cystic fibrosis
delete2026-07-29
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deleteOliver J. McElvaney; Sonya L. Heltshe; Don B. Sanders; Natalie E. West; Kathleen J. Ramos; Barbra Fogarty; Patrick A. Flume; Christopher H. Goss
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Abnormalities of the distal terminal ileum in people with cystic fibrosis assessed using magnetic resonance imaging
delete2026-07-25
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deleteFaiz Alqarni; Soma Kumasaka; Madeleine Taylor; Arantxa Recto; Darren Sills; Hisham Saumtally; Charlotte Hamann; Grace Lim; Jan Paul; Alexander Yule; Caroline L. Hoad; Daniel Peckham; Iain D. Stewart; Tanya M. Monaghan; Christopher van der Gast; Katie Gathercole; Penny A. Gowland; Robin C. Spiller; Alan R. Smyth; Luca Marciani
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Current diabetes therapy and use of diabetes technology in people living with cystic fibrosis-related diabetes (CFRD): Insights from the DPV network
delete2026-07-24
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deleteThomas Hörtenhuber; Stefanie Schmid; Claudia Boettcher; Silke Herrlinger; Mareike Niemeyer; Martin Tauschmann; Reinhard W Holl; Nicole Prinz
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Timing and rate of reimbursement for cystic fibrosis modulator therapies in EU countries
delete2026-07-21
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deleteEnrico Costa; Silvia Girotti; Saif Elayan; Carlo Castellani; Maria Cavaller Bellaubi; Wim Goettsch; Momir Radulović; João Rocha; Pierluigi Russo; Steven Simoens; Christine Leopold
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Improvement in functional exercise performance and quadriceps muscle strength after two years treatment with elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis: A prospective observational study
delete2026-07-20
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deleteAnne-Sophie Aubriot; Catherine Song; Clémence Gonçalvès; Laura Santelé; Silvia Berardis; Christophe Goubau; Grégory Reychler; Morgane Penelle; Sophie Gohy
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Real-world experience with a generic formulation of elexacaftor/tezacaftor/ivacaftor in children with cystic fibrosis
delete2026-07-19
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deleteMaría Macarena Oneglia; Hilda Giugno; Ariela Agustinho; Paula Plubatsch; Claudio Castaños
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Sleep patterns and glycemia in adults with cystic fibrosis-related diabetes: a remote pilot study
delete2026-07-16
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deleteAnushka Sharma; Evangelos Vassilakis; Hao Deng; Jessica K. Salwen-Deremer; Bethany L. Bartley; Melissa S. Putman; Hassan S. Dashti
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Association of dental diseases with pulmonary outcomes in a multicenter cohort of adolescents and young adults with CF
delete2026-07-07
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deleteMargaret Rosenfeld; Lloyd Mancl; Noel K Childers; Sundass Khan; Isabel Virella-Lowell; Patricia McCurdy; Sharon McNamara; Marianne S Muhlebach; Marissa Nelsen; Josh Orack; Marilyn Rothen; Apoena Ribeiro; Matthew Wolfgang; Lindsey Yap; Alaa A Alkhateeb; Donald L Chi
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Cystic fibrosis nutrition: Addressing emerging trends following the 2024 ESPEN-ESPGHAN-ECFS guidelines. Expert opinion recommendations
delete2026-07-01
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deleteChris Smith; Sarah Collins; Carla Colombo; Dimitri Declercq; Tamarah Katz; Daina Kalnins; Isabelle Scheers; Daniel Peckham; Joanna Snowball; Michael Wilschanski
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Real-time breath metabolomics to assess early response to CFTR modulators in adults with cystic fibrosis: An open-label proof-of-concept study
delete2026-07-01
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deleteEmmanuelle Bardin; Hélène Salvator; Camille Roquencourt; Elodie Lamy; Nicolas Hunzinger; Isabelle Sermet-Gaudelus; Sandra De Miranda; Dominique Grenet; Philippe Devillier; Stanislas Grassin-Delyle
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Hepatic steatosis in adults on CFTR modulators is commonly associated with cardiometabolic criteria consistent with metabolic dysfunction-associated steatotic liver disease
delete2026-07-01
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deleteSofia Manioudaki; Larisa Vasilieva; Eleni Geladari; Iliana Mani; Vasilios Sevastianos; Filia Diamantea; Alexandra Alexopoulou
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Healthcare priorities and needs for LGBTQIA+ people with cystic fibrosis: A concept mapping study
delete2026-06-29
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deleteKacie M Kidd; Rachel E. Salyer; Sydney J Rashid; Abigail S Mitchell; Adrianne Alpern; Jonathan Greenberg; Olivia M Stransky; Asher Prangley; Vin Tangpricha; Gina M. Sequeira; Mitchell R Lunn; John Palla; Leo Cevallos; Raksha Jain; Stephen E. Deci; Nicole F. Kahn; Alexandra “Xan” C.H. Nowakowski; Abraham I. Sender; Gregory S Sawicki; Traci M Kazmerski
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Persistence of large P. aeruginosa aggregates despite reduced airway burden in people with cystic fibrosis on CFTR modulator therapy
delete2026-06-28
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deleteAmanda J. Morris; Shafinaz Eisha; Yvonne C.W. Yau; Sara Goel; Michelle Shaw; William H. DePas; Isaac Martin; Arunan Selvarajah; Mellissa Gaudet; Elizabeth Tullis; Dao Nguyen; Valerie J. Waters
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SPL84 and Trikafta® exhibit comparable and additive effects in patient-derived HBE cells carrying the 3849+10kb C→T/F508del CFTR variants
delete2026-06-26
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deleteYi Cheng; Yifat S. Oren; Jan Harrington; Aurélie Hatton; Efrat Ozeri-Galai; Chava D. Stampfer; Tamar Mordechai; Ofra Barchad-Avitzur; Gili Hart; Kevin Coote; Hermann Bihler; Isabelle Sermet-Gaudelus; Martin Mense; Batsheva Kerem
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Partnership between cystic fibrosis centres in Europe: The Twinning Project
delete2026-06-26
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deletePavel Drevinek; Helen K. Chadwick; Katarina Stepankova; Claire Francis; Hilde de Keyser; Chris Smith; Lutz Naehrlich
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Transcriptomic and functional profiling of human intestinal organoids identifies enhanced calcium signalling and thrombospondin-2 activity in cystic fibrosis
delete2026-06-24
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deleteEllie Slater; Woo Jin Yang; Nefeli Skoufou-Papoutsaki; Stephen A. Renshaw; Róisín M. Owens; Matthias Zilbauer
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