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Journal of Cystic Fibrosis cover

Journal of Cystic Fibrosis

IF6
Papers2898
Citations7272
Journal Papers 2897
Publication Date
Heterozygous CFTR variants associated with low-phospholipid-associated cholelithiasis phenotypes expand hepatobiliary disorders spectrum
delete2026-09-25
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deleteCamille Giannetti; Louis Carmarans; Patrice Bourgeois; René Gerolami; Patrick Borentain; Diane Lorenzo; Solene Hoibian; Alexandre Fabre; Catherine Badens; Christophe Buffat
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Epigenetic regulation and chromatin organization in cystic fibrosis airways
delete2026-09-15
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deleteAgustín De Ganzó; Brian Chan; Michael Rubinstein; Kenichi Okuda; Carla M.P. Ribeiro
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Reducing multiple-breath washout test burden in cystic fibrosis: agreement between the first acceptable trial and mean lung clearance index
delete2026-09-12
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deleteNatalia S. Escobar; Elad Ben-Meir; Renee Jensen; Scott Sagel; Nicole Hamblett; Michelle Shaw; Felix Ratjen
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CFTR modulation alter pancreatic cancer cell growth and signaling: implications for cancer risk in cystic fibrosis
delete2026-09-12
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deleteYunxia O’Malley; Henry Keen; Ian M. Thornell; Zachary Campbell; Anna J. Prouty; Carlos H.F. Chan; Andrew W. Norris; Prabhat Goswami; Aliye Uc
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A functional comparison of readthrough agent ELX-02 across a wide range of nonsense CFTR variants
delete2026-09-11
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deleteMarlies Destoop; Anabela S. Ramalho; Iris A.L. Silva; Annelotte M. Vonk; Sylvia Suen; Marlou C. Bierlaagh; Sylvia F. Boj; Robert G.J. Vries; Jeffrey M. Beekman; Kris De Boeck; Cornelis K. van der Ent; Margarida D. Amaral; Francois Vermeulen; Sacha Spelier
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In Vitro Responsiveness of 417 CFTR Variants to Vanzacaftor/Tezacaftor/Ivacaftor
delete2026-09-11
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deleteHermann Bihler; Andrey Sivachenko; Priyanka Bhatt; Ashley Baldwin; Jan Harrington; Violaine Bailey; Alexi Panagiotou; Divesh Patel; Michael J. Mulligan; Rachel Valdez Misiolek; Kylie Arnold; Yi Cheng; Kevin Coote; Normand E. Allaire; Joshua Conte; Karen S. Raraigh; Garry R. Cutting; Martin Mense
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Microbial content versus microbial interaction: the impact of medications on CF airway microbial ecosystems
delete2026-09-04
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deletePok-Man Ho; Rahan Rudland Nazeer; Isabel Askenasy; Robert A Quinn; Martin Welch
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Association between the childhood opportunity index and healthcare utilization in cystic fibrosis
delete2026-09-04
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deleteAshley Han; Matt Hall; Elizabeth Cromwell; Ronald L. Gibson; Thida Ong; A. Jay Freeman; Clement L. Ren; Don B. Sanders; Jonathan D. Cogen
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The cystic fibrosis gut microbial dysbiosis index (CF-GMDI): a quantitative measure of gut microbial imbalance in children with cystic fibrosis
delete2026-09-03
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deleteB.L.D. Uthpala Pushpakumara; Michael J Coffey; Jennifer Hudson; Jessica Halim; Sandra Chuang; Bernadette Prentice; Adam Jaffe; Robert Edwards; Andrew S Day; Mark Oliver; Sarath Ranganathan; Claire Wainwright; Hiran Selvadurai; Josie van Dorst; Chee Y Ooi
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Peripheral muscle dysfunction persists in the era of highly effective CFTR modulators in cystic fibrosis
delete2026-08-31
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deleteAntoine Bronstein; Elise Zitta; Oussama Saidi; Nadège Goriot-Raynaud; Laurent Mely; Mathieu Gruet
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Incidence, prevalence, and survival of persons living with advanced cystic fibrosis lung disease in the United States
delete2026-08-22
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deleteJonathan V Todd; Kathleen J. Ramos; Erin Tallarico; Abigail Thaxton; Chris Beres; Whitney Brown; Albert Faro; Elizabeth A. Cromwell
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Prenatal CFTR modulator therapy and fetal meconium ileus in cystic fibrosis: a systematic review and individual patient data meta-analysis
delete2026-08-22
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deleteVincenzo G Menditto; Giovanni Pomponio; Nicole Caporelli; Marica Bordicchia; Alessandra Boni; Marco Bruno Luigi Rocchi; Giacomo Menditto; Benedetta Fabrizzi
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Antiviral defenses are diminished at birth in cystic fibrosis pig airways
delete2026-08-02
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deleteJennifer A. Bartlett; Miguel E. Ortiz; Linda S. Powers; Christine L. Wohlford-Lenane; Camilla E. Hippee; Laura Marquez Loza; Justin W. Kaufman; Brajesh K. Singh; Daniel I. Sands; Eric D. Huntemann; Ashley L. Cooney; Mark P. Rogan; Clifford C. Taggart; David K. Meyerholz; Paul B. McCray
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Real-world population pharmacokinetic modeling of elexacaftor, tezacaftor, and ivacaftor
delete2026-07-30
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deleteAK Kunzelmann; S Naehrig; C Shad; M Breuling; M Goetschke; K Habler; O Sommerburg; J Behr; LM Schatz; J Starp; M Vogeser; M Paal; U Liebchen
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