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Papers67
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Journal Papers 67
Publication Date
Exploring light chain cardiotoxicity in AL amyloidosis: impact on hiPSC-derived cardiomyocyte activity
delete2026-06-19
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deleteSerena Calamaio; Anthony Frosio; Dario Melgari; Luca Broggini; Federica Sonzini; Rachele Prevostini; Davide Pignatelli; Luigi Anastasia; Carlo Pappone; Alice Nevone; Giovanni Palladini; Mario Nuvolone; Stefano Ricagno; Ilaria Rivolta
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Long-term efficacy and safety of vutrisiran in hereditary transthyretin amyloidosis with polyneuropathy: final analysis of the HELIOS-A randomized treatment extension
delete2026-06-15
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deleteCécile Cauquil; David Adams; Julian Gillmore; Alejandra Gonzalez-Duarte; Michelle Mezei; Laura Obici; Yoshiki Sekijima; Weizhi Zhao; Katherine Boyle; Prajakta Badri; Marianne Sweetser; Colleen Moffitt; Márcia Waddington-Cruz
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RNA-based full length immunoglobulin light chain sequencing reveals lambda constant domain mutations with potential implications for thermodynamic stability in light chain amyloidosis
delete2026-06-04
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deleteEyad Naser; Sara Oubari; Josefine Jakob; Björn Häupl; Bettina Budeus; Bernd Walkenfort; Melanie Nowakowski; Gabriele Hessler; Claudine Kühn; Mike Hasenberg; Thomas Oellerich; Hans Christian Reinhardt; Alexander Carpinteiro
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Transient focal neurological episodes in hereditary transthyretin-related amyloidosis treated with liver transplantation: electroencephalographic insights and clinical features
delete2026-06-04
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deleteGonçalo Videira; João Moura; Joel Freitas; Cristina Alves; Márcio Neves Cardoso; Ana Paula Sousa; Miguel Mendonça Pinto; Diogo Pereira; Luísa Sousa; Sara Cavaco; Teresa Coelho
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Efficacy of diflunisal for hereditary transthyretin amyloidosis: the Swedish real-world experience
delete2026-06-03
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deleteJohn L. Berk; Kevin J. Carroll; Jorge Mejia Baranda; Björn Pilebro; Kristin Samuelsson; Per Eldhagen; Jonas Wixner
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Proline-rich, polybasic peptides are a structurally distinct class of amyloid-reactive peptides
delete2026-05-25
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PREAI
deleteTrevor J. Hancock; Manasi Balachandran; Angela Williams; James Foster; Anna Sparks; Joseph Jackson; Nic Angell; Ashlyn Wilson; Sallie Macy; Craig Wooliver; Jonathan Wall
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Artificial intelligence-enhanced electrocardiogram findings before and after heart transplantation in cardiac amyloidosis
delete2026-05-18
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PREAI
deleteKamal Awad; Juan M. Farina; Jose N. Nativi Nicolau; Melissa A. Lyle; Andrew N. Rosenbaum; Barry A. Boilson; Omar F. Abou Ezzeddine; Francisco Lopez-Jimenez; Angela Dispenzieri; Martha Grogan; D. Eric Steidley; Reza Arsanjani; Julie L. Rosenthal
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The prognostic value of red blood cell distribution width in AL amyloidosis
delete2026-05-16
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PREAI
deleteDespina Fotiou; Erasmia Boutakoglou; Konstantinos Giannakas; Foteini Theodorakakou; Eirini Solia; Magdalini Migkou; Panagiotis Malandrakis; Ioannis Ntanasis-Stathopoulos; Vasiliki Spiliopoulou; Nikolaos Kanellias; Evangelos Eleutherakis-Papaiakovou; Maria Gavriatopoulou; Evangelos Terpos; Efstathios Kastritis; Meletios A. Dimopoulos
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Evaluation of the yield index of genetic counselling for first-degree relatives of patients with hereditary transthyretin cardiac amyloidosis
delete2026-05-15
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PREAI
deleteBérénice Hébrard; Francois Sauer; Julie Pompougnac; Ariane Lunati-Rozie; Silvia Oghina; Arnault Galat; Amira Zaroui; Mounira Kharoubi; Marina Konyukh; Pascale Fanen; Sophie Mallet; Benoit Funalot; Thibaud Damy
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Left atrial strain identifies early cardiac involvement in variant transthyretin amyloidosis
delete2026-05-07
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PREAI
deleteMatteo Serenelli; Elisa Gardini; Stefania Marazia; Alessandro Barbarossa; Alberto Cipriani; Anna Cantone; Beatrice Dal Passo; Federico Sanguettoli; Rita Pavasini; Matteo Arzenton; Gianluca Campo; Andrea Zaccaro; Emiliano Rossi; Gioele Fabbri; Enrico Monti; Carmine Pizzi; Erika Pedio; Federico Guerra; Giulio Sinigiani; Alberto Aimo; Michele Emdin; Francesco Cappelli; Federica Colio; Simone Longhi
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Accelerated apolipoprotein A-II senile amyloidosis in a plasminogen activator inhibitor-1 knock-out model
delete2026-04-27
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PREAI
deleteGilles R. Codo; Pauline Duchatelet; Gemma Martinez-Rivas; Alessio Lampis; Karolina Weronika Świderska; Emilie Pinault; Camille Cohen; Magali Colombat; Sebastien Bender; Christophe Sirac
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Transthyretin stabilizer therapy increases naturally-occurring antibodies in ATTR cardiomyopathy
delete2026-04-06
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PREAI
deleteStephan Settelmeier; Daniel Agranovski; Maximilian Steinhardt; Sarah Waydhas; Ian Gering; Vladimir Cejka; Caroline Morbach; Stefan Störk; Dieter Willbold; Ralf Küppers; Julia Vogel; Lars Michel; Alexander Carpinteiro; H. Christian Reinhardt; Richard Dodel; Tienush Rassaf; Alexander J. Ross; Ulrike B. Hendgen-Cotta
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Incidence of second primary malignancies in patients with AL amyloidosis and the impact of disease stage and therapies
delete2026-04-01
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PREAI
deleteEfstathios Kastritis; Vassiliki Spiliopoulou; Foteini Theodorakakou; Magdalini Migkou; Panagiotis Malandrakis; Evangelos Terpos; Maria Gavriatopoulou; Meletios Athanasios Dimopoulos
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Development and validation of the modified-comprehensive Kumamoto Score: a multi-organ assessment tool for hereditary transthyretin amyloidosis
delete2026-03-31
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PREAI
deleteShiori Yamakawa; Toshiya Nomura; Yohei Misumi; Tomoaki Taguchi; Keiichi Nakahara; Masayoshi Tasaki; Naoto Kuyama; Hiroki Usuku; Yasuhiro Izumiya; Yuji Takihara; Emre Aldinc; Konen Obayashi; Toshihiro Inoue; Kenichi Tsujita; Yukio Ando; Mitsuharu Ueda
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Serum peripherin as a disease biomarker in hereditary transthyretin amyloidosis: a multicenter cohort study
delete2026-03-16
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PREAI
deleteDomenico Plantone; Delia Righi; Angela Romano; Luca Leonardi; Valeria Guglielmino; Francesca Forcina; Marco Ceccanti; Maurizio Inghilleri; Fiore Manganelli; Stefano Tozza; Maria Ausilia Sciarrone; Francesca Vitali; Andrea Sabino; Carlo Manco; Angela Stufano; Maria Laura Stromillo; Nicola De Stefano; Paolo Calabresi; Guido Primiano; Marco Luigetti
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Clinical impact of lilac-colored aggregates on may-Grünwald-Giemsa-stained bone marrow smears in patients with amyloid light-chain amyloidosis
delete2026-03-09
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PREAI
deleteAyaka Kodama; Ritsuko Nakagoshi; Ryuto Oshita; Suzuho Onagi; Satoshi Fujimura; Yuka Takezawa; Nagaaki Katoh; Yoshiki Sekijima; Masahide Yazaki; Yumiko Higuchi
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Systemic fibrinogen Aα-chain amyloidosis in Manchester Terrier dogs
delete2026-03-04
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PREAI
deleteNatsumi Kobayashi; Keiichi Kuroki; Yoshiyuki Itoh; Tomoaki Murakami
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