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Osamu Onodera

niigata university

69H-index
621Paper Count
1.6WCitation Count
Published Papers 217
Publication Date
TDP-43-related cryptic splicing reflects pathological heterogeneity in amyotrophic lateral sclerosis
err2026-08-08
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errOAAI
errIchiko Ikegami; Shoko Hongo; Akihide Koyama; Yoshika Hayakawa-Yano; Masato Yano; Akihiro Sugai; Tomohiko Ishihara; Mari Tada; Akiyoshi Kakita; Osamu Onodera; Yuka Mitsuhashi Koike
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Persistent export bias of TDP-43 under native autoregulation links insoluble accumulation to nuclear dysfunction
err2026-08-04
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errOAAI
errGenri Toyama; Shingo Koide; Takuma Yamagishi; Aya Washida; Ryutaro Hanyu; Osamu Onodera; Akihiro Sugai
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Clinical and Radiological Features of Aphasia Caused by Brainstem Infarction: Two Case Reports
err2026-02-28
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errOAAI
errMasahiro Hatakeyama; Midori Watanabe; Shin Koide; Hiromi Hashida; Tomone Taneda; Natsuki Akiyama; Takayoshi Tokutake; Masato Kanazawa; Osamu Onodera
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Expansive spatial pattern of Aβ deposition in patients with cerebral amyloid angiopathy: A three-dimensional surface-to-depth analysis
err2026-02-06
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errOAAI
errHideki Hayashi; Rie Saito; Akinori Miyashita; Takeshi Ikeuchi; Mari Tada; Kohei Akazawa; Osamu Onodera; Kazuki Tainaka; Akiyoshi Kakita
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A genome-wide association study identifies the GPM6A locus associated with age at onset in ALS
err2025-12-05
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errOAAI
errRyoichi Nakamura; Genki Tohnai; Naoki Atsuta; Yumi Matsuda; Satoru Morimoto; Daisuke Ito; Masahisa Katsuno; Yuishin Izumi; Mitsuya Morita; Ikuko Iwata; Ichiro Yabe; Tomoko Nakazato; Nobutaka Hattori; Takehisa Hirayama; Osamu Kano; Asako Tamura; Naoki Suzuki; Masashi Aoki; Kazumoto Shibuya; Satoshi Kuwabara; Masaya Oda; Rina Hashimoto; Ikuko Aiba; Tomohiko Ishihara; Osamu Onodera; Toru Yamashita; Hiroyuki Ishiura; Kota Bokuda; Toshio Shimizu; Yoshio Ikeda; Kazuko Hasegawa; Fumiaki Tanaka; Takanori Yokota; Kazuaki Kanai; Yu-ichi Noto; Ryuji Kaji; Hirohisa Watanabe; Tomoko Konishi; Mikiko Hasegawa; Hozuki Fukaya; Jun-ichi Niwa; Manabu Doyu; Yohei Okada; Shiho Nakamura; Fumiko Ozawa; Hideyuki Okano; Masahiro Nakatochi; Gen Sobue
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Quantifying subpercent nuclear TDP-43 loss in cells and ALS cortex using junction-specific cryptic exon RT-qPCR
err2025-10-22
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PREAI
errShingo Koide; Ichiko Ikegami; Ryutaro Hanyu; Yuka Mitsuhashi Koike; Takuma Yamagishi; Genri Toyama; Aya Washida; Mari Tada; Akiyoshi Kakita; Osamu Onodera; Akihiro Sugai
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Association of Plasma Placental Growth Factor with White Matter Hyperintensities in Alzheimer’s Disease
err2025-09-28
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errOAAI
errKazuya Igarashi; Tamao Tsukie; Kazuo Washiyama; Kiyoshi Onda; Yuki Miyagi; Shoya Inagawa; Soichiro Shimizu; Akinori Miyashita; Osamu Onodera; Takeshi Ikeuchi; Kensaku Kasuga
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Tongue shear wave elastography for bulbar dysfunction in amyotrophic lateral sclerosis
err2025-09-20
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errOAAI
errKaori Yanagawa; Makiko Ike; Azusa Aoyama; Takeshi Yokoo; Shuji Terai; Takafumi Hayashi; Osamu Onodera
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Specific Contribution of the Cerebellar Inferior Posterior Lobe to Motor Learning in Degenerative Cerebellar Ataxia
err2025-07-16
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PREAI
errKyota Bando; Takeru Honda; Kinya Ishikawa; Shinichi Shirai; Ichiro Yabe; Tomohiko Ishihara; Osamu Onodera; Yuichi Higashiyama; Fumiaki Tanaka; Yoshiyuki Kishimoto; Masahisa Katsuno; Takahiro Shimizu; Ritsuko Hanajima; Takumi Kanata; Yuji Takahashi; Hidehiro MizusawaMD
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Concurrent Alzheimer's disease pathologies in Lewy body diseases affect cognition and glucose metabolism in the posterior cingulate gyrus: A multimodal PET study
err2025-06-20
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PREAI
errKosei Nakamura; Kenji Tagai; Hitoshi Shinotoh; Shigeki Hirano; Soichiro Kitamura; Hironobu Endo; Keisuke Takahata; Yuhei Takado; Ming-Rong Zhang; Kazunori Kawamura; Osamu Onodera; Makoto Higuchi; Hitoshi Shimada
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TDP-43 mutants with different aggregation properties exhibit distinct toxicity, axonal transport, and secretion for disease progression in a mouse ALS/FTLD model
err2025-06-05
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errOAAI
errHideki Mori; Tokiharu Sato; Shintaro Tsuboguchi; Masahiko Takahashi; Yuka Nakamura; Kana Hoshina; Taisuke Kato; Masahiro Fujii; Osamu Onodera; Masaki Ueno
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Early-onset alopecia and variable age of cerebrovascular disease onset in a Japanese family with a heterozygous HTRA1 mutation
err2025-06-04
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PREAI
errManato Yasuda; Masahiro Mori; Atsuhiko Sugiyama; Tomoki Suichi; Toshio Fukutake; Masahiro Uemura; Osamu Onodera; Satoshi Kuwabara
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Late-onset multiple system atrophy: Neuropathological features associated with slow disease progression
err2025-05-19
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errOAAI
errMisato Ozawa; Rie Saito; Takuya Konno; Yasuko Kuroha; Tetsuhiko Ikeda; Akio Yokoseki; Takashi Tani; Tomoe Sato; Jiro Idezuka; Reiji Koide; Shigeru Fujimoto; Osamu Onodera; Mari Tada; Akiyoshi Kakita
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The analysis of schizophrenia-like psychosis in dentatorubral-pallidoluysian atrophy
err2025-04-09
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errOAAI
errIkegami, Ichiko; Koike, Yuka Mitsuhashi; Hayashi, Hideki; Hirokawa, Sachiko; Ando, Shoichiro; Ishihara, Tomohiko; Onodera, Osamu
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Redefining the Pathogenic CAG Repeat Units Threshold in CACNA1A for Spinocerebellar Ataxia Type 6
err2025-04-01
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PREAI
errHatano, Yuya; Ishihara, Tomohiko; Hirokawa, Sachiko; Date, Hidetoshi; Takahashi, Yuji; Mizusawa, Hidehiro; Onodera, Osamu
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Chocolate Chip Sign on Susceptibility-Weighted Imaging
err2025-04-01
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PREAI
errAndo, Shoichiro; Saito, Rie; Kitahara, Sho; Uemura, Masahiro; Hatano, Yuya; Watanabe, Masaki; Kato, Taisuke; Ito, Yosuke; Nalini, Atchayaram; Ishihara, Tomohiko; Murayama, Shigeo; Igarashi, Hironaka; Kakita, Akiyoshi; Onodera, Osamu
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Novel Aspects of Hereditary Spastic Paraplegia: A Clinicopathologic and Biochemical Study of a Patient With a Heterozygous GCH1 Variant
err2025-02-01
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PREAI
errHongo, Shoko; Ikeda, Tetsuhiko; Tada, Mari; Aida, Rina; Ozawa, Tetsuo; Hara, Norikazu; Miyashita, Akinori; Nakajima, Takashi; Onodera, Osamu; Ikeuchi, Takeshi; Ichinose, Hiroshi; Kakita, Akiyoshi
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A case of cerebral amyloid angiopathy with ipsilateral tau and contralateral amyloid PET uptake related to cadaveric dura mater implanted in childhood
err2024-12-19
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errOAAI
errHatakeyama, Yuki; Kimura, Atsushi Michael; Tsuboguchi, Shintaro; Ratanov, Mikhail; Nakamura, Kosei; Hatakeyama, Masahiro; Nakamura, Yukimi; Watanabe, Masaki; Murakami, Yoshihiro; Saito, Yuko; Murayama, Shigeo; Kasuga, Kensaku; Ikeuchi, Takeshi; Igarashi, Hironaka; Onodera, Osamu; Shimada, Hitoshi
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Frequency of FGF14 intronic GAA repeat expansion in patients with multiple system atrophy and undiagnosed ataxia in the Japanese population
err2024-11-27
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errOAAI
errKakumoto, Toshiyuki; Orimo, Kenta; Matsukawa, Takashi; Mitsui, Jun; Ishihara, Tomohiko; Onodera, Osamu; Suzuki, Yuta; Morishita, Shinichi; Chikada, Ayaka; Toda, Tatsushi; Tsuji, Shoji
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