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Fumihiko Urano

Department of Medicine

56H-index
208Paper Count
2.0WCitation Count
Published Papers 92
Publication Date
Evaluating the use of GLP-1 receptor agonists in Wolfram syndrome patients
err2026-07-30
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errLA Laura A. Lee †; AF Abby F. Tang †; AE Anna E. Asako †; SF Sarah F. Ning; HA Hayden A. Reed; ED Eleanor Duncan; HM Heather M. Lugar; JH James Hoekel; BA Bess A. Marshall; TH Tamara Hershey; FU Fumihiko Urano
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Natural history of 15 patients with autosomal dominant WFS1 pathogenic variants associated with sensorineural hearing loss and optic atrophy
err2026-04-18
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errJessica P. Roberts; Abby F. Tang; Daniela Hernandez; Brianna Carman; Liam Oiknine; Cris Brown; Stacy Hurst; Yunshuo Tang; Fumihiko Urano
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Extracellular vesicle R-Ras is a potential biomarker for human peripheral artery disease
err2025-10-25
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errXiaochao Wei; Mohamed Zaghloul; Shahab Hafezi; Fumihiko Urano; Mohamed A. Zayed; Clay F. Semenkovich
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European and African ancestry-specific plasma protein-QTL and metabolite-QTL analyses identify ancestry-specific T2D effector proteins and metabolites
err2025-08-11
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errChengran Yang; Priyanka Gorijala; Jigyasha Timsina; Lihua Wang; Menghan Liu; Ciyang Wang; William Brock; Yueyao Wang; Fumihiko Urano; Yun Ju Sung; Carlos Cruchaga
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Identification of unique cell type responses in pancreatic islets to stress
err2024-07-02
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errMaestas, Marlie M.; Ishahak, Matthew; Augsornworawat, Punn; Veronese-Paniagua, Daniel A.; Maxwell, Kristina G.; Velazco-Cruz, Leonardo; Marquez, Erica; Sun, Jiameng; Shunkarova, Mira; Gale, Sarah E.; Urano, Fumihiko; Millman, Jeffrey R.
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GLP-1R agonists demonstrate potential to treat Wolfram syndrome in human preclinical models
err2023-03-30
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errGorgogietas, Vyron; Rajaei, Bahareh; Heeyoung, Chae; Santacreu, Bruno J.; Marin-Canas, Sandra; Salpea, Paraskevi; Sawatani, Toshiaki; Musuaya, Anyishai; Arroyo, Maria N.; Moreno-Castro, Cristina; Benabdallah, Khadija; Demarez, Celine; Toivonen, Sanna; Cosentino, Cristina; Pachera, Nathalie; Lytrivi, Maria; Cai, Ying; Carnel, Lode; Brown, Cris; Urano, Fumihiko; Marchetti, Piero; Gilon, Patrick; Eizirik, Decio L.; Cnop, Miriam; Igoillo-Esteve, Mariana
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Autophagy is activated for cell survival after endoplasmic reticulum stress
err2023-03-27
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errOgata, Maiko; Hino, Shin-ichiro; Saito, Atsushi; Morikawa, Keisuke; Kondo, Shinichi; Kanemoto, Soshi; Murakami, Tomohiko; Taniguchi, Manabu; Tanii, Ichiro; Yoshinaga, Kazuya; Shiosaka, Sadao; Hammarback, James A.; Urano, Fumihiko; Imaizumi, Kazunori
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IRE1-Dependent Activation of AMPK in Response to Nitric Oxide
err2023-03-20
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errMeares, Gordon P.; Hughes, Katherine J.; Naatz, Aaron; Papa, Feroz R.; Urano, Fumihiko; Hansen, Polly A.; Benveniste, Etty N.; Corbett, John A.
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Mammalian ECD Protein Is a Novel Negative Regulator of the PERK Arm of the Unfolded Protein Response
err2023-03-17
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errOlou, Appolinaire A.; Sarkar, Aniruddha; Bele, Aditya; Gurumurthy, C. B.; Mir, Riyaz A.; Ammons, Shalis A.; Mirza, Sameer; Saleem, Irfana; Urano, Fumihiko; Band, Hamid; Band, Vimla
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Multidimensional analysis and therapeutic development using patient iPSC-derived disease models of Wolfram syndrome
err2022-09-22
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errKitamura, Rie Asada; Maxwell, Kristina G.; Ye, Wenjuan; Kries, Kelly; Brown, Cris M.; Augsornworawat, Punn; Hirsch, Yoel; Johansson, Martin M.; Weiden, Tzvi; Ekstein, Joseph; Cohen, Joshua; Klee, Justin; Leslie, Kent; Simeonov, Anton; Henderson, Mark J.; Millman, Jeffrey R.; Urano, Fumihiko
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Blocking CHOP-dependent TXNIP shuttling to mitochondria attenuates albuminuria and mitigates kidney injury in nephrotic syndrome
err2022-08-22
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errPark, Sun-Ji; Kim, Yeawon; Li, Chuang; Suh, Junwoo; Sivapackiam, Jothilingam; Goncalves, Tassia M.; Jarad, George; Zhao, Guoyan; Urano, Fumihiko; Sharma, Vijay; Chen, Ying Maggie
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Plasma Neurofilament Light Chain Levels Are Elevated in Children and Young Adults With Wolfram Syndrome
err2022-04-12
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errEisenstein, Sarah A.; Boodram, Raveena S.; Sutphen, Courtney L.; Lugar, Heather M.; Gordon, Brian A.; Marshall, Bess A.; Urano, Fumihiko; Fagan, Anne M.; Hershey, Tamara
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Wolframin is a novel regulator of tau pathology and neurodegeneration
err2022-04-07
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PREAI
errChen, Shuo; Acosta, Diana; Li, Liangping; Liang, Jiawen; Chang, Yuzhou; Wang, Cankun; Fitzgerald, Julie; Morrison, Cody; Goulbourne, Chris N.; Nakano, Yoshi; Villegas, Nancy C. Hernandez; Venkataraman, Lalitha; Brown, Cris; Serrano, Geidy E.; Bell, Erica; Wemlinger, Trina; Wu, Min; Kokiko-Cochran, Olga N.; Popovich, Phillip; Flowers, Xena E.; Honig, Lawrence S.; Vonsattel, Jean Paul; Scharre, Douglas W.; Beach, Thomas G.; Ma, Qin; Kuret, Jeff; Koks, Sulev; Urano, Fumihiko; Duff, Karen E.; Fu, Hongjun
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Loss of Function of WFS1 Causes ER Stress-Mediated Inflammation in Pancreatic Beta-Cells
err2022-03-25
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errMorikawa, Shuntaro; Blacher, Lindsey; Onwumere, Chinyere; Urano, Fumihiko
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Genotype-phenotype correlation analysis and therapeutic development using a patient stem cell-derived disease model of Wolfram syndrome
err2022-03-01
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errUrano, Fumihiko; Kitamura, Rie Asada; Maxwell, Kristina; Ye, Wenjuan; Kries, Kelly; Brown, Cris; Augsornworawat, Punn; Johansson, Martin; Cohen, Joshua; Klee, Justin; Leslie, Kent; Simeonov, Anton; Hirsch, Joel; Weiden, Tzvi; Henderson, Mark; Millman, Jeffrey; Ekstein, Josef
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Fast and Efficient Generation of Isogenic Induced Pluripotent Stem Cell Lines Using Adenine Base Editing
err2021-08-01
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errNami, Fatemeharefeh; Ramezankhani, Roya; Vandenabeele, Marjan; Vervliet, Tim; Vogels, Kristy; Urano, Fumihiko; Verfaillie, Catherine
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A phase Ib/IIa clinical trial of dantrolene sodium in patients with Wolfram syndrome
err2021-06-29
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errAbreu, Damien; Stone, Stephen, I; Pearson, Toni S.; Bucelli, Robert C.; Simpson, Ashley N.; Hurst, Stacy; Brown, Cris M.; Kries, Kelly; Onwumere, Chinyere; Gu, Hongjie; Hoekel, James; Tychsen, Lawrence; Van Stavern, Gregory P.; White, Neil H.; Marshall, Bess A.; Hershey, Tamara; Urano, Fumihiko
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A target-agnostic screen identifies approved drugs to stabilize the endoplasmic reticulum-resident proteome
err2021-04-01
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errHenderson, Mark J.; Trychta, Kathleen A.; Yang, Shyh-Ming; Back, Susanne; Yasgar, Adam; Wires, Emily S.; Danchik, Carina; Yan, Xiaokang; Yano, Hideaki; Shi, Lei; Wu, Kuo-Jen; Wang, Amy Q.; Tao, Dingyin; Zahoranszky-Kohalmi, Gergely; Hu, Xin; Xu, Xin; Maloney, David; Zakharov, Alexey, V; Rai, Ganesha; Urano, Fumihiko; Airavaara, Mikko; Gavrilova, Oksana; Jadhav, Ajit; Wang, Yun; Simeonov, Anton; Harvey, Brandon K.
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Digenic Variants in the FGF21 Signaling Pathway Associated with Severe Insulin Resistance and Pseudoacromegaly
err2020-09-22
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errStone, Stephen, I; Wegner, Daniel J.; Wambach, Jennifer A.; Cole, F. Sessions; Urano, Fumihiko; Ornitz, David M.
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