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Ketone bodies resume mitochondrial respiration in neuronal progenitors from iPSCs of patients with AGC1 deficiency Lasorsa, Francesco M.; Barile, Simona N.; Magnifico, Maria C.; Distelmaier, Felix; Poeta, Eleonora; Viggiano, Luigi; Pignataro, Antonella; Antonicelli, Marica; Palmieri, Luigi; Petralla, Sabrina; Hentschel, Julia; Porcelli, Vito; Tioli, Gaia; Pisano, Isabella; Porcelli, Anna Maria; Fiermonte, Giuseppe; Palmieri, Ferdinando; Anderson, Stewart A.; Iommarini, Luisa; Wallace, Douglas C.; Monti, Barbara Share Save
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Engineering Yarrowia lipolytica for the selective and high-level production of isocitric acid through manipulation of mitochondrial dicarboxylate?tricarboxylate carriers Yuzbasheva, Evgeniya Y.; Scarcia, Pasquale; Yuzbashev, Tigran, V; Messina, Eugenia; Kosikhina, Iuliia M.; Palmieri, Luigi; Shutov, Artem, V; Taratynova, Maria O.; Amaro, Rodrigo Ledesma; Palmieri, Ferdinando; Sineoky, Sergey P.; Agrimi, Gennaro Share Save
Biochemical and functional characterization of a mitochondrial citrate carrier in Arabidopsis thaliana Brito, Danielle S.; Agrimi, Gennaro; Charton, Lennart; Brilhaus, Dominik; Bitetto, Maria Gabriella; Lana-Costa, Jaciara; Messina, Eugenia; Nascimento, Carolina P.; Feitosa-Araujo, Elias; Pires, Marcel Viana; Perez-Diaz, Jorge Luis; Obata, Toshihiro; Porcelli, Vito; Palmieri, Luigi; Araujo, Wagner L.; Weber, Andreas P. M.; Linka, Nicole; Fernie, Alisdair R.; Palmieri, Ferdinando; Nunes-Nesi, Adriano Share Save
Downregulation of a Mitochondrial NAD+ Transporter (NDT2) Alters Seed Production and Germination in Arabidopsis Feitosa-Araujo, Elias; Chaves, Izabel de Souza; Florian, Alexandra; da Fonseca-Pereira, Paula; Condori Apfata, Jorge Alberto; Heyneke, Elmien; Medeiros, David Barbosa; Pires, Marcel Viana; Mettler-Altmann, Tabea; Neuhaus, H. Ekkehard; Palmieri, Ferdinando; Araujo, Wagner L.; Obata, Toshihiro; Weber, Andreas P. M.; Linka, Nicole; Fernie, Alisdair R.; Nunes-Nesi, Adriano Share Save
The human uncoupling proteins 5 and 6 (UCP5/SLC25A14 and UCP6/SLC25A30) transport sulfur oxyanions, phosphate and dicarboxylates Gorgoglione, Ruggiero; Porcelli, Vito; Santoro, Antonella; Daddabbo, Lucia; Vozza, Angelo; Monne, Magnus; Di Noia, Maria Antonietta; Palmieri, Luigi; Fiermonte, Giuseppe; Palmieri, Ferdinando Share Save
The mitochondrial NAD+ transporter (NDT1) plays important roles in cellular NAD+ homeostasis in Arabidopsis thaliana Chaves, Izabel de Souza; Feitosa-Araujo, Elias; Florian, Alexandra; Medeiros, David B.; da Fonseca-Pereira, Paula; Charton, Lennart; Heyneke, Elmien; Apfata, Jorge A. C.; Pires, Marcel, V; Mettler-Altmann, Tabea; Araujo, Wagner L.; Neuhaus, H. Ekkehard; Palmieri, Ferdinando; Obata, Toshihiro; Weber, Andreas P. M.; Linka, Nicole; Fernie, Alisdair R.; Nunes-Nesi, Adriano Share Save
The mitochondrial citrate carrier in Yarrowia lipolytica: Its identification, characterization and functional significance for the production of citric acid Yuzbasheva, Evgeniya Y.; Agrimi, Gennaro; Yuzbashev, Tigran, V; Scarcia, Pasquale; Vinogradova, Elizaveta B.; Palmieri, Luigi; Shutov, Artem, V; Kosikhina, Iuliia M.; Palmieri, Ferdinando; Sineoky, Sergey P. Share Save
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Molecular identification and functional characterization of a novel glutamate transporter in yeast and plant mitochondria Porcelli, Vito; Vozza, Angelo; Calcagnile, Valeria; Gorgoglione, Ruggiero; Arrigoni, Roberto; Fontanesi, Flavia; Marobbio, Carlo M. T.; Castegna, Alessandra; Palmieri, Ferdinando; Palmieri, Luigi Share Save
Uncoupling proteins 1 and 2 (UCP1 and UCP2) from Arabidopsis thaliana are mitochondrial transporters of aspartate, glutamate, and dicarboxylates Monne, Magnus; Daddabbo, Lucia; Gagneul, David; Obata, Toshihiro; Hielscher, Bjoern; Palmieri, Luigi; Miniero, Daniela Valeria; Fernie, Alisdair R.; Weber, Andreas P. M.; Palmieri, Ferdinando Share Save
SLC25A10 biallelic mutations in intractable epileptic encephalopathy with complex I deficiency Punzi, Giuseppe; Porcelli, Vito; Ruggiu, Matteo; Hossain, Md F.; Menga, Alessio; Scarcia, Pasquale; Castegna, Alessandra; Gorgoglione, Ruggiero; Pierri, Ciro L.; Laera, Luna; Lasorsa, Francesco M.; Paradies, Eleonora; Pisano, Isabella; Marobbio, Carlo M. T.; Lamantea, Eleonora; Ghezzi, Daniele; Tiranti, Valeria; Giannattasio, Sergio; Donati, Maria A.; Guerrini, Renzo; Palmieri, Luigi; Palmieri, Ferdinando; De Grassi, Anna Share Save
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Inhibition of the Mitochondrial Glutamate Carrier SLC25A22 in Astrocytes Leads to Intracellular Glutamate Accumulation Goubert, Emmanuelle; Mircheva, Yanina; Lasorsa, Francesco M.; Melon, Christophe; Profilo, Emanuela; Sutera, Julie; Becq, Helene; Palmieri, Ferdinando; Palmieri, Luigi; Aniksztejn, Laurent; Molinari, Florence Share Save