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VWF-ADAMTS13 axis dysfunction in children with sickle cell disease treated with hydroxycarbamide vs blood transfusion Fogarty, Helen; Ahmad, Azaz; Atiq, Ferdows; Doherty, Dearbhla; Ward, Soracha; Karampini, Ellie; Rehill, Aisling; Leon, Gemma; Byrne, Ciara; Geoghegan, Rosena; Conroy, Helena; Byrne, Mary; Budde, Ulrich; Schneppenheim, Sonja; Sheehan, Ciara; Ngwenya, Noel; Baker, Ross I.; Preston, Roger J. S.; Tuohy, Emma; Mcmahon, Corrina; O'Donnell, James S. Share Save
Generation of potentially inhibitory autoantibodies to ADAMTS13 in coronavirus disease 2019 Doevelaar, Adrian A. N.; Bachmann, Martin; Hoelzer, Bodo; Seibert, Felix S.; Rohn, Benjamin J.; Zgoura, Panagiota; Witzke, Oliver; Dittmer, Ulf; Brenner, Thorsten; Paniskaki, Krystallenia; Yilmaz, Serap; Dittmer, Rita; Schneppenheim, Sonja; Wilhelm, Jochen; Stervbo, Ulrik; Babel, Nina; Budde, Ulrich; Westhoff, Timm H. Share Save
Elevated von Willebrand factor levels in multiple myeloma: dysregulated mechanisms of both secretion and clearance Comerford, Claire; Dhami, Sukhraj Pal Singh; Murphy, Philip; Patmore, Sean; Ward, Soracha; Pushkar, Nadiya; Budde, Ulrich; Karampini, Ellie; O'Donnell, James S.; Glavey, Siobhan; Quinn, John; O'Sullivan, Jamie M. Share Save
von Willebrand factor neutralizing and non-neutralizing alloantibodies in 213 subjects with type 3 von Willebrand disease enrolled in 3WINTERS-IPS Pagliari, Maria Teresa; Budde, Ulrich; Baronciani, Luciano; Eshghi, Peyman; Ahmadinejad, Minoo; Badiee, Zahra; Baghaipour, Mohammad-Reza; Hidalgo, Olga Benitez; Biguzzi, Eugenia; Bodo, Imre; Castaman, Giancarlo; Goudemand, Jenny; Karimi, Mehran; Keikhaei, Bijan; Lassila, Riitta; Leebeek, Frank W. G.; Fernandez, Maria Fernanda Lopez; Marino, Renato; Oldenburg, Johannes; Peake, Ian; Santoro, Cristina; Schneppenheim, Reinhard; Tiede, Andreas; Toogeh, Gholamreza; Tosetto, Alberto; Trossaert, Marc; Yadegari, Hamideh; Zetterberg, Eva M. K.; Mannucci, Pier Mannuccio; Federici, Augusto B.; Eikenboom, Jeroen; Peyvandi, Flora Share Save
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Clinical and biochemical endpoints and predictors of response to plasma exchange in septic shock: results from a randomized controlled trial Stahl, Klaus; Wand, Philipp; Seeliger, Benjamin; Wendel-Garcia, Pedro David; Schmidt, Julius J.; Schmidt, Bernhard M. W.; Sauer, Andrea; Lehmann, Felix; Budde, Ulrich; Busch, Markus; Wiesner, Olaf; Welte, Tobias; Haller, Hermann; Wedemeyer, Heiner; Putensen, Christian; Hoeper, Marius M.; Bode, Christian; David, Sascha Share Save
Von Willebrand factor propeptide and pathophysiological mechanisms in European and Iranian patients with type 3 von Willebrand disease enrolled in the 3WINTERS-IPS study Pagliari, Maria Teresa; Rosendaal, Frits R.; Ahmadinejad, Minoo; Badiee, Zahra; Baghaipour, Mohammad-Reza; Baronciani, Luciano; Hidalgo, Olga Benitez; Bodo, Imre; Budde, Ulrich; Castaman, Giancarlo; Eshghi, Peyman; Goudemand, Jenny; Karimi, Mehran; Keikhaei, Bijan; Lassila, Riitta; Leebeek, Frank W. G.; Fernandez, Maria Fernanda Lopez; Mannucci, Pier Mannuccio; Marino, Renato; Oldenburg, Johannes; Peake, Ian; Santoro, Cristina; Schneppenheim, Reinhard; Tiede, Andreas; Toogeh, Gholamreza; Tosetto, Alberto; Trossaert, Marc; Yadegari, Hamideh; Zetterberg, Eva M. K.; Peyvandi, Flora; Federici, Augusto B.; Eikenboom, Jeroen Share Save
Effect of plasma exchange on COVID-19 associated excess of von Willebrand factor and inflammation in critically ill patients Seibert, Felix S.; Blazquez-Navarro, Arturo; Hoelzer, Bodo; Doevelaar, Adrian A. N.; Nusshag, Christian; Merle, Uta; Morath, Christian; Zgoura, Panagiota; Dittmer, Rita; Schneppenheim, Sonja; Wilhelm, Jochen; Babel, Nina; Budde, Ulrich; Westhoff, Timm H. Share Save
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Genotypes of European and Iranian patients with type 3 von Willebrand disease enrolled in 3WINTERS-IPS Baronciani, Luciano; Peake, Ian; Schneppenheim, Reinhard; Goodeve, Anne; Ahmadinejad, Minoo; Badiee, Zahra; Baghaipour, Mohammad-Reza; Benitez, Olga; Bodo, Imre; Budde, Ulrich; Cairo, Andrea; Castaman, Giancarlo; Eshghi, Peyman; Goudemand, Jenny; Hassenpflug, Wolf; Hoorfar, Hamid; Karimi, Mehran; Keikhaei, Bijan; Lassila, Riitta; Leebeek, Frank W. G.; Lopez Fernandez, Maria Fernanda; Mannucci, Pier Mannuccio; Marino, Renato; Niksic, Nikolas; Oyen, Florian; Santoro, Cristina; Tiede, Andreas; Toogeh, Gholamreza; Tosetto, Alberto; Trossaert, Marc; Zetterberg, Eva M. K.; Eikenboom, Jeroen; Federici, Augusto B.; Peyvandi, Flora Share Save
ADAMTS13 regulation of VWF multimer distribution in severe COVID-19 Ward, Soracha E.; Fogarty, Helen; Karampini, Ellie; Lavin, Michelle; Schneppenheim, Sonja; Dittmer, Rita; Morrin, Hannah; Glavey, Siobhan; Cheallaigh, Cliona Ni; Bergin, Colm; Martin-Loeches, Ignacio; Mallon, Patrick W.; Curley, Gerard F.; Baker, Ross, I; Budde, Ulrich; O'Sullivan, Jamie M.; O'Donnell, James S. Share Save
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von Willebrand Factor Multimer Formation Contributes to Immunothrombosis in Coronavirus Disease 2019 Doevelaar, Adrian A. N.; Bachmann, Martin; Hoelzer, Bodo; Seibert, Felix S.; Rohn, Benjamin J.; Bauer, Frederic; Witzke, Oliver; Dittmer, Ulf; Bachmann, Michael; Yilmaz, Serap; Dittmer, Rita; Schneppenheim, Sonja; Babel, Nina; Budde, Ulrich; Westhoff, Timm H. Share Save
Comparison of von Willebrand factor platelet-binding activity assays: ELISA overreads type 2B with loss of HMW multimers Szederjesi, Attila; Baronciani, Luciano; Budde, Ulrich; Castaman, Giancarlo; Colpani, Paola; Lawrie, Andrew S.; Liu, Yuan; Montgomery, Robert; Peyvandi, Flora; Schneppenheim, Reinhard; Patzke, Juergen; Bodo, Imre Share Save
Bleeding symptoms in patients diagnosed as type 3 von Willebrand disease: Results from 3WINTERS-IPS, an international and collaborative cross-sectional study Tosetto, Alberto; Badiee, Zahra; Baghaipour, Mohammad-Reza; Baronciani, Luciano; Battle, Javier; Berntorp, Erik; Bodo, Imre; Budde, Ulrich; Castaman, Giancarlo; Eikenboom, Jeroen C. J.; Eshghi, Peyman; Ettorre, Cosimo; Goodeve, Anne; Goudemand, Jenny; Richard, Charles; Hay, Morris; Hoorfar, Hamid; Karimi, Mehran; Keikhaei, Bijan; Lassila, Riitta; Leebeek, Frank W. G.; Fernandez, Maria Fernanda Lopez; Mannucci, Pier Mannuccio; Mazzucconi, Maria Gabriella; Morfini, Massimo; Oldenburg, Johannes; Peake, Ian; Lopez, Rafael Parra; Peyvandi, Flora; Schneppenheim, Reinhard; Tiede, Andreas; Toogeh, Gholamreza; Trossaert, Marc; Zekavat, Omidreza; Zetterberg, Eva M. K.; Federici, Augusto B. Share Save
Characterization of large in-frame von Willebrand factor deletions highlights differing pathogenic mechanisms Cartwright, Ashley; Webster, Simon J.; de Jong, Annika; Dirven, Richard J.; Bloomer, Lisa D. S.; AL-Buhairan, Ahlam M.; Budde, Ulrich; Hallden, Christer; Habart, David; Goudemand, Jenny; Peake, Ian R.; Eikenboom, Jeroen C. J.; Goodeve, Anne C.; Hampshire, Daniel J. Share Save
A multi-center evaluation of TECHNOSCREEN(R) ADAMTS-13 activity assay as a screening tool for detecting deficiency of ADAMTS-13 Moore, Gary W.; Meijer, Danielle; Griffiths, Margaret; Rushen, Lucy; Brown, Alice; Budde, Ulrich; Dittmer, Rita; Schocke, Barbara; Leyte, Anja; Geiter, Sabine; Moes, Anneke; Cutler, Jacqueline A.; Binder, Nikolaus B. Share Save
Effect of therapeutic plasma exchange on endothelial activation and coagulation-related parameters in septic shock Stahl, Klaus; Schmidt, Julius J.; Seeliger, Benjamin; Schmidt, Bernhard M. W.; Welte, Tobias; Haller, Hermann; Hoeper, Marius M.; Budde, Ulrich; Bode, Christian; David, Sascha Share Save
Characterization of the mutation spectrum in a Pakistani cohort of type 3 von Willebrand disease Ahmed, Shariq; Yadegari, Hamideh; Naz, Arshi; Biswas, Arijit; Budde, Ulrich; Saqlain, Nazish; Amanat, Samina; Tariq, Shehla; Raziq, Fazle; Masood, Shahtaj; Pavlova, Anna; Shamsi, Tahir Sultan; Oldenburg, Johannes Share Save