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Ellen J. Hess

neurology

49H-index
157Paper Count
7.5KCitation Count
Published Papers 56
Publication Date
Changes in Purine Metabolism During Differentiation of Dopamine Neurons from Human Induced Pluripotent Stem Cells
err2026-05-19
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errLauren Grychowski; Fatemeh Seifar; Erkin Ozel; Anika Thite; Diane J. Sutcliffe; Ashok R. Dinasarapu; Ellen J. Hess; H. A. Jinnah
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Modeling rare genetic disease with gene-edited induced pluripotent stem cells: relevance of the starting stock line
err2025-12-01
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PREAI
errDinasarapu, Ashok R.; Sutcliffe, Diane J.; Ozel, Erkin; Thite, Anike; Grychowski, Lauren; Visser, Jasper E.; Hess, Ellen J.; Kolk, Sharon M.; Jinnah, H. A.
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Modeling rare genetic disease with patient-derived induced pluripotent stem cells: reassessment of the minimum numbers of lines needed
err2025-08-01
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PREAI
errDinasarapu, Ashok R.; Sutcliffe, Diane J.; Grychowski, Lauren; Ozel, Erkin; Thite, Anika; Visser, Jasper E.; Hess, Ellen J.; Kolk, Sharon M.; Jinnah, H. A.
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Striatal cell-type–specific molecular signatures reveal potential therapeutic targets in a model of dystonia
err2025-05-28
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errKaitlyn M. Roman; Ashok R. Dinasarapu; Suraj Cherian; Xueliang Fan; Yuping Donsante; Nivetha Aravind; C. Savio Chan; H.A. Jinnah; Ellen J. Hess
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Report Spiny projection neurons exhibit transcriptional signatures within subregions of the dorsal striatum
err2023-11-01
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errRoman, Kaitlyn M.; Dinasarapu, Ashok R.; Vanschoiack, Alison; Ross, P. Martin; Kroeppler, David; Jinnah, H. A.; Hess, Ellen J.
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Development of Novel M4 Muscarinic Acetylcholine Receptor Antagonists for the Treatment of Movement Disorders
err2022-05-13
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PREAI
errRook, Jerri; Bender, Aaron; Dickerson, Jonathan; Foster, Daniel; Rodriguez, Alice; Niswender, Colleen; Hess, Ellen; Conn, Jeff; Lindsley, Craig
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Striatal Synaptic Dysfunction in Dystonia and Levodopa-Induced Dyskinesia
err2022-05-01
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errOAAI
errScarduzio, Mariangela; Hess, Ellen J.; Standaert, David G.; Jaunarajs, Karen L. Eskow
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Differential expression of striatal proteins in a mouse model of DOPA-responsive dystonia reveals shared mechanisms among dystonic disorders
err2021-08-01
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errOAAI
errBriscione, Maria A.; Dinasarapu, Ashok R.; Bagchi, Pritha; Donsante, Yuping; Roman, Kaitlyn M.; Downs, Anthony M.; Fan, Xueliang; Hoehner, Jessica; Jinnah, H. A.; Hess, Ellen J.
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Synaptic effects of ethanol on striatal circuitry: therapeutic implications for dystonia
err2021-07-16
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errImbriani, Paola; Sciamanna, Giuseppe; El Atiallah, Ilham; Cerri, Silvia; Hess, Ellen J.; Pisani, Antonio
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Cell-intrinsic effects of TorsinA(δE) disrupt dopamine release in a mouse model of TOR1A dystonia
err2021-07-01
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errDowns, Anthony M.; Fan, Xueliang; Kadakia, Radhika F.; Donsante, Yuping; Jinnah, H. A.; Hess, Ellen J.
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Induced pluripotent stem cells from subjects with Lesch-Nyhan disease
err2021-04-19
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errSutcliffe, Diane J.; Dinasarapu, Ashok R.; Visser, Jasper E.; den Hoed, Joery; Seifar, Fatemeh; Joshi, Piyush; Ceballos-Picot, Irene; Sardar, Tejas; Hess, Ellen J.; Sun, Yan V.; Wen, Zhexing; Zwick, Michael E.; Jinnah, H. A.
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The neurobiological basis for novel experimental therapeutics in dystonia
err2019-10-01
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errDowns, Anthony M.; Roman, Kaitlyn M.; Campbell, Simone A.; Pisani, Antonio; Hess, Ellen J.; Bionsi, Paola
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Trihexyphenidyl rescues the deficit in dopamine neurotransmission in a mouse model of DYT1 dystonia
err2019-05-01
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errOAAI
errDowns, Anthony M.; Fan, Xueliang; Donsante, Christine; Jinnah, H. A.; Hess, Ellen J.
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Striatal Cholinergic Interneurons in a Knock-in Mouse Model of L-DOPA-Responsive Dystonia
err2018-06-27
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errYalcin-Cakmakli, Gul; Rose, Samuel J.; Villalba, Rosa M.; Williams, Lagena; Jinnah, Hyder A.; Hess, Ellen J.; Smith, Yoland
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Effects of disulfiram on choice behavior in a rodent gambling task: association with catecholamine levels
err2017-10-30
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errOAAI
errDi Ciano, Patricia; Manvich, Daniel F.; Pushparaj, Abhiram; Gappasov, Andrew; Hess, Ellen J.; Weinshenker, David; Le Foll, Bernard
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Parkinsonism Without Dopamine Neuron Degeneration in Aged L-Dopa-Responsive Dystonia Knockin Mice
err2017-09-26
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errRose, Samuel J.; Harrast, Porter; Donsante, Christine; Fan, Xueliang; Joers, Valerie; Tansey, Malu G.; Jinnah, H. A.; Hess, Ellen J.
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A new knock-in mouse model of L-DOPA-responsive dystonia
errBRAIN
IF11.7
err2015-07-27
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errRose, Samuel J.; Yu, Xin Y.; Heinzer, Ann K.; Harrast, Porter; Fan, Xueliang; Raike, Robert S.; Thompson, Valerie B.; Pare, Jean-Francois; Weinshenker, David; Smith, Yoland; Jinnah, Hyder A.; Hess, Ellen J.
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Increased vesicular monoamine transporter enhances dopamine release and opposes Parkinson disease-related neurodegeneration in vivo
err2014-06-16
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errLohr, Kelly M.; Bernstein, Alison I.; Stout, Kristen A.; Dunn, Amy R.; Lazo, Carlos R.; Alter, Shawn P.; Wang, Minzheng; Li, Yingjie; Fan, Xueliang; Hess, Ellen J.; Yi, Hong; Vecchio, Laura M.; Goldstein, David S.; Guillot, Thomas S.; Salahpour, Ali; Miller, Gary W.
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