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Adult male patients with DKC1 mutations present early-onset pulmonary fibrosis and severe prognosis Evrard, Ophelie; Philippot, Quentin; Kannengiesser, Caroline; Debray, Marie Pierre; Guyard, Alice; Fattori, Antonin; Schuller, Armelle; Nunes, Hilario; Montani, David; Bours, Vincent; Cottin, Vincent; Traclet, Julie; Benattia, Amira; Berthoux, Emilie; Daniel, Adrien; Yan-Min, Xu; Lainey, Elodie; Saussereau, Julien; Viallon, Malika Chelbi; Oudin, Claire; Morel, Helene; Crestani, Bruno; Borie, Raphael; Ba, Ibrahima Share Save
Clinical characteristics of diffuse idiopathic pulmonary neuroendocrine cell hyperplasia O'Callaghan, Marissa; Forde, Sarah H.; Franciosi, Alessandro N.; Penugonda, Maitreyi; Diesler, Remi; O'Brien, Helen; Buikhuisen, Wieneke; Almeamar, Hussein; Samhouri, Bilal F.; Ryu, Jay H.; Veltkamp, Marcel; Manali, Effrosyni D.; Lazaratou, Aggeliki; Papiris, Spyros A.; Bonella, Francesco; Carr, Laurie; Cottin, Vincent; Taille, Camille; McCormack, Francis X.; Gupta, Nishant; Strosberg, Jonathan; Lococo, Fillipo M.; Harari, Sergio; Pelosi, Giuseppe; Papa, Riccardo; Bouros, Demosthenes; Kolilekas, Lykourgos; Daniil, Zoe; Dimeas, Ilias; Hernandez-Gonzalez, Fernanda; Sellares, Jacobo; Spagnolo, Paolo; Crowley, Rachel K.; O'Toole, Dermot; O'Shea, Donal; Quinn, Sean; Murphy, David J.; Fabre, Aurelie; Byrne, Adam J.; Keane, Michael P.; Fournel, Ludovic; McCarthy, Cormac Share Save
ERS/EULAR clinical practice guidelines for connective tissue disease-associated interstitial lung disease Antoniou, Katerina M.; Distler, Oliver; Gheorghiu, Ana-Maria; Moor, Catharina C.; Vikse, Jens; Bizymi, Nikoleta; Galetti, Ilaria; Brown, Graham; Bargagli, Elena; Allanore, Yannick; Corte, Tamera J.; Dieude, Philippe; Cottin, Vincent; Fisher, Benjamin A.; Fabre, Aurelie; Giles, Jon T.; Kreuter, Michael; Lundberg, Ingrid E.; Poletti, Venerino; Maurer, Britta; Renzoni, Elisabetta A.; Muller-Ladner, Ulf; Strek, Mary E.; Sverzellati, Nicola; Studenic, Paul; Mohammed, Jibril; Nagavci, Blin; Stamm, Tanja; Tonia, Thomy; Crestani, Bruno; Hoffmann-Vold, Anna-Maria Share Save
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Short telomere length is associated with accelerated lung disease progression in rheumatoid arthritis-associated interstitial lung disease El Husseini, Kinan; Lee, Joyce S.; Juge, Pierre-Antoine; Ebstein, Esther; Ottaviani, Sebastien; Borie, Raphael; Bancal, Catherine; Debray, Marie-Pierre; Kannengiesser, Caroline; Ba, Ibrahima; Marchand-Adam, Sylvain; Richez, Christophe; Nunes, Hilario; Avouac, Jerome; Flipo, Rene-Marc; Wemeau, Lidwine; Boissier, Marie-Christophe; Schaeverbeke, Thierry; Kermanac'h, Nathalie Saidenberg; Kawano-Dourado, Leticia; Cottin, Vincent; Wolters, Paul J.; Granger, Benjamin; Dieude, Philippe; Crestani, Bruno Share Save
Survey of physicians' approaches to the clinical evaluation of interstitial lung disease in Singapore (SoPhoCLES) Teo, Felicia S. W.; Chai, Gin Tsen; Low, Su Ying; Tay, Tunn Ren; Walsh, Simon L. F.; Kokosi, Maria; Takahashi, Masashi; Cottin, Vincent; Wuyts, Wim A.; Chua, Felix; Lee, Pyng; Teo, Lynette L. S.; Kaw, Gregory; Li Ng, Yuen; Shen, Liang; Teoh, Chia Meng; Song, Jin Woo Share Save
The phenotypic state of biallelic SERPINA1 Q0 variants in α1-antitrypsin deficiency Papiris, Spyros A.; Veith, Martina; Ferrarotti, Ilaria; Balduyck, Malika-Leila; Filosa, Asia; Papaioannou, Andriana I.; Lombard, Christine; Ottaviani, Stefania; Rovina, Nikoletta; Kolilekas, Lykourgos; Zerimech, Farid; Odou, Marie-Francoise; Dechomet, Magali; Prountzos, Spyridon; Kontopoulou, Christina; Kallieri, Maria; Cuvelier, Antoine; le Rouzic, Olivier; Apollonatou, Vasiliki; Antonogiannaki, Elvira-Markela; Osaba, Lourdes; Entrena, Edurne; Traclet, Julie; Weisenburger, Gaelle; Cottin, Vincent; Vogelmeier, Claus; Greulich, Timm; Monti, Maria Cristina; Mornex, Jean-Francois; Manali, Effrosyni D. Share Save
Modulation of infiltrating CD206+macrophages restricts progression of pulmonary lymphangioleiomyomatosis Liu, Heng-Jia; Diesler, Remi; Chami, Joelle; Wu, Boxiang; Du, Heng; Jin, Yue; Daou, Melissa; Alesi, Nicola; Khabibullin, Damir; Leroux, Caroline; Cottin, Vincent; Cantley, Lloyd G.; Rudloff, Udo; Henske, Elizabeth P. Share Save
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Treatable traits in interstitial lung disease: opportunities and challenges Khor, Yet H.; Podolanczuk, Anna J.; Renzoni, Elisabetta A.; McDonald, Vanessa M.; Cottin, Vincent; Holland, Anne E.; Inoue, Yoshikazu; Russell, Anne Marie; Song, Jin Woo; Wijsenbeek, Marlies; Strek, Mary E.; Ryerson, Christopher J. Share Save
Characteristics and outcomes of patients with LAM receiving sirolimus in France based on real-life data Cottin, Vincent; Cases, Antoine; Bourdin, Virginie; Reynaud-Gaubert, Martine; Hirschi, Sandrine; Kerjouan, Mallorie; Diesler, Remi; Chardes, Brieux; Fievez, Stephane; Assi, Nada; Schmidt, Aurelie; Denis, Helene; Wemeau-Stervinou, Lidwine; Uzunhan, Yurdagul Share Save