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Autoantibodies neutralizing type I IFNs in patients with fulminant herpes simplex virus hepatitis Gervais, Adrian; Marchal, Astrid; Boucherit, Soraya; Abi Haidar, Anthony; Bizien, Lucy; Yalcinkaya, Ahmet; Sandstrom, Ella; Kong, Xiao-Fei; Jacquemin, Emmanuel; Bernard, Olivier; Debray, Dominique; Lacaille, Florence; Ichai, Philippe; Arikan, Cigdem; Javouhey, Etienne; Roquelaure, Bertrand; Gottrand, Frederic; Trespidi, Francesca; Codullo, Veronica; Cavagna, Lorenzo; Schleinitz, Nicolas; Bousfiha, Mohamed; Amenzoui, Naima; Bousfiha, Ahmed Aziz; Jorgensen, Sofie E.; Mork, Nanna; Mogensen, Trine H.; Bastard, Paul; Puel, Anne; Borghesi, Alessandro; Rule, Jody A.; Lee, William M.; Landegren, Nils; Cobat, Aurelie; Casanova, Jean-Laurent; Jouanguy, Emmanuelle Share Save
Autoantibodies neutralizing type I IFNs in a fatal case of H5N1 avian influenza Zhang, Qian; Conrad, Taylor S.; Moncada-Velez, Marcela; Jiang, Kaijun; Cupic, Anastasija; Eaton, Jonathan; Hutchinson, Kimberley; Gervais, Adrian; Chen, Ruyue; Puel, Anne; Bastard, Paul; Cobat, Aurelie; Sokol, Theresa; Langlois, Ryan A.; Miorin, Lisa; Garcia-Sastre, Adolfo; Vanchiere, John A.; Casanova, Jean-Laurent Share Save
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Therapeutic plasma exchange accelerates immune cell recovery in severe COVID-19 Guironnet-Paquet, Aurelie; Hamzeh-Cognasse, Hind; Berard, Frederic; Cognasse, Fabrice; Richard, Jean Christophe; Yonis, Hodane; Mezidi, Mehdi; Desebbe, Olivier; Delannoy, Bertrand; Demeret, Sophie; Marois, Clemence; Saheb, Samir; Le, Quoc Viet; Schoeffler, Mathieu; Pugliesi, Paul Simon; Debord, Sophie; Bastard, Paul; Cobat, Aurelie; Casanova, Jean Laurent; Pescarmona, Remi; Viel, Sebastien; Nicolas, Jean Francois; Nosbaum, Audrey; Vocanson, Marc; Hequet, Olivier Share Save
Similar Kinetics of Pulmonary SARS-CoV-2 Load in Intensive Care Unit Patients with COVID-19 Pneumonia with or Without Autoantibodies Neutralizing Type I Interferons Le Stang, Valentine; Bastard, Paul; Langouet, Elise; de Chambrun, Marc Pineton; Chommeloux, Juliette; Gervais, Adrian; Bizien, Lucy; Puel, Anne; Cobat, Aurelie; Mayaux, Julien; Demoule, Alexandre; Casanova, Jean-Laurent; Boutolleau, David; Combes, Alain; Burrel, Sonia; Luyt, Charles-Edouard Share Save
Auto-Abs neutralizing type I IFNs in patients with severe Powassan, Usutu, or Ross River virus disease Gervais, Adrian; Bastard, Paul; Bizien, Lucy; Delifer, Celine; Tiberghien, Pierre; Rodrigo, Chaturaka; Trespidi, Francesca; Angelini, Micol; Rossini, Giada; Lazzarotto, Tiziana; Conti, Francesca; Cassaniti, Irene; Baldanti, Fausto; Rovida, Francesca; Ferrari, Alessandro; Mileto, Davide; Mancon, Alessandro; Abel, Laurent; Puel, Anne; Cobat, Aurelie; Rice, Charles M.; Cadar, Daniel; Schmidt-Chanasit, Jonas; Scheid, Johannes F.; Lemieux, Jacob E.; Rosenberg, Eric S.; Agudelo, Marianna; Tangye, Stuart G.; Borghesi, Alessandro; Durand, Guillaume Andre; Duburcq-Gury, Emilie; Valencia, Braulio M.; Lloyd, Andrew R.; Nagy, Anna; MacDonald, Margaret M.; Simonin, Yannick; Zhang, Shen-Ying; Casanova, Jean-Laurent Share Save
Incontinentia pigmenti underlies thymic dysplasia, autoantibodies to type I IFNs, and viral diseases Rosain, Jeremie; Le Voyer, Tom; Liu, Xian; Gervais, Adrian; Polivka, Laura; Cederholm, Axel; Berteloot, Laureline; Parent, Audrey V.; Pescatore, Alessandra; Spinosa, Ezia; Minic, Snezana; Kiszewski, Ana Elisa; Tsumura, Miyuki; Thibault, Chloe; Azcoiti, Maria Esnaola; Martinovic, Jelena; Philippot, Quentin; Khan, Taushif; Marchal, Astrid; Charmeteau-De Muylder, Benedicte; Bizien, Lucy; Deswarte, Caroline; Hadjem, Lillia; Fauvarque, Marie-Odile; Dorgham, Karim; Eriksson, Daniel; Falcone, Emilia Liana; Puel, Mathilde; Uenal, Sinem; Geraldo, Amyrath; Le Floc'h, Corentin; Li, Hailun; Rheault, Sylvie; Muti, Christine; Bobrie-Moyrand, Claire; Welfringer-Morin, Anne; Fuleihan, Ramsay L.; Levy, Romain; Roelens, Marie; Gao, Liwei; Materna, Marie; Pellegrini, Silvia; Piemonti, Lorenzo; Catherinot, Emilie; Goffard, Jean-Christophe; Fekkar, Arnaud; Sacko-Sow, Aissata; Soudee, Camille; Boucherit, Soraya; Neehus, Anna-Lena; Has, Cristina; Huebner, Stefanie; Blanchard-Rohner, Geraldine; Amador-Borrero, Blanca; Utsumi, Takanori; Taniguchi, Maki; Tani, Hiroo; Izawa, Kazushi; Yasumi, Takahiro; Kanai, Sotaro; Migaud, Melanie; Aubart, Melodie; Lambert, Nathalie; Gorochov, Guy; Picard, Capucine; Soudais, Claire; L'Honneur, Anne-Sophie; Rozenberg, Flore; Milner, Joshua D.; Zhang, Shen-Ying; Vabres, Pierre; Trpinac, Dusan; Marr, Nico; Boddaert, Nathalie; Desguerre, Isabelle; Pasparakis, Manolis; Miller, Corey N.; Poziomczyk, Claudia S.; Abel, Laurent; Okada, Satoshi; Jouanguy, Emmanuelle; Cheynier, Remi; Zhang, Qian; Cobat, Aurelie; Beziat, Vivien; Boisson, Bertrand; Steffann, Julie; Fusco, Francesca; Ursini, Matilde Valeria; Hadj-Rabia, Smail; Bodemer, Christine; Bustamante, Jacinta; Luche, Herve; Puel, Anne; Courtois, Gilles; Bastard, Paul; Landegren, Nils; Anderson, Mark S.; Casanova, Jean-Laurent Share Save
Autoantibodies neutralizing type I IFNs underlie severe tick-borne encephalitis in ∼10% of patients Gervais, Adrian; Marchal, Astrid; Fortova, Andrea; Berankova, Michaela; Krbkova, Lenka; Pychova, Martina; Salat, Jiri; Zhao, Shuxiang; Kerrouche, Nacim; Le Voyer, Tom; Stiasny, Karin; Raffl, Simon; Schieber Pachart, Anne; Fafi-Kremer, Samira; Gravier, Simon; Robbiani, Davide F.; Abel, Laurent; MacDonald, Margaret R.; Rice, Charles M.; Weissmann, Gaia; Kamal Eldin, Tarek; Robatscher, Eva; Erne, Elke Maria; Pagani, Elisabetta; Borghesi, Alessandro; Puel, Anne; Bastard, Paul; Velay, Aurelie; Martinot, Martin; Hansmann, Yves; Aberle, Judith H.; Ruzek, Daniel; Cobat, Aurelie; Zhang, Shen-Ying; Casanova, Jean-Laurent Share Save
A Novel Case of IFNAR1 Deficiency Identified a Common Canonical Splice Site Variant in DOCK8 in Western Polynesia: The Importance of Validating Variants of Unknown Significance in Under-Represented Ancestries (vol 44, 170, 2024) Huynh, Aimee; Gray, Paul; Sullivan, Anna; Mackie, Joseph; Guerin, Antoine; Rao, Geetha; Pathmanandavel, Karrnan; Della Mina, Erika; Hollway, Georgina; Hobbs, Matthew; Enthoven, Karen; O'Young, Patrick; Mcmanus, Sam; Wainwright, Luke H.; Higgins, Megan; Noon, Fallon; Wong, Melanie; Bastard, Paul; Zhang, Qian; Casanova, Jean-Laurent; Hsiao, Kuang-Chih; Pinzon-Charry, Alberto; Ma, Cindy; Tangye, Stuart G. Share Save
Innate immune response in acute critical illness: a narrative review Stiel, Laure; Gaudet, Alexandre; Thietart, Sara; Vallet, Helene; Bastard, Paul; Voiriot, Guillaume; Oualha, Mehdi; Sarton, Benjamine; Kallel, Hatem; Brechot, Nicolas; Kreitmann, Louis; Benghanem, Sarah; Joffre, Jeremie; Jouan, Youenn Share Save
IgG4-related disease and B-cell malignancy due to an IKZF1 gain-of-function variant Garcia-Solis, Blanca; Tapia-Torres, Maria; Garcia-Soidan, Ana; Hernandez-Brito, Elisa; Martinez-Saavedra, Maria Teresa; Lorenzo-Salazar, Jose M.; Garcia-Hernandez, Sonia; Van Den Rym, Ana; Mayani, Karan; Govantes-Rodriguez, Jose Vicente; Gervais, Adrian; Bastard, Paul; Puel, Anne; Casanova, Jean-Laurent; Flores, Carlos; de Diego, Rebeca Perez; Rodriguez-Gallego, Carlos Share Save
A Novel Case of IFNAR1 Deficiency Identified a Common Canonical Splice Site Variant in DOCK8 in Western Polynesia: The Importance of Validating Variants of Unknown Significance in Under-Represented Ancestries Huynh, Aimee; Gray, Paul E.; Sullivan, Anna; Mackie, Joseph; Guerin, Antoine; Rao, Geetha; Pathmanandavel, Karrnan; Della Mina, Erika; Hollway, Georgina; Hobbs, Matthew; Enthoven, Karen; O'Young, Patrick; McManus, Sam; Wainwright, Luke H.; Higgins, Megan; Noon, Fallon; Wong, Melanie; Bastard, Paul; Zhang, Qian; Casanova, Jean-Laurent; Hsiao, Kuang-Chih; Pinzon-Charry, Alberto; Ma, Cindy S.; Tangye, Stuart G. Share Save
Severe West Nile Virus and Severe Acute Respiratory Syndrome Coronavirus 2 Infections in a Patient With Thymoma and Anti-Type I Interferon Antibodies Barzaghi, Federica; Visconti, Camilla; Pipitone, Giovanni Battista; Bondesan, Simone; Molli, Giulia; Giannelli, Stefania; Sartirana, Claudia; Lampasona, Vito; Bazzigaluppi, Elena; Brigatti, Cristina; Gervais, Adrian; Bastard, Paul; Din, Chiara Tassan; Molinari, Chiara; Piemonti, Lorenzo; Casanova, Jean-Laurent; Carrera, Paola; Casari, Giorgio; Aiuti, Alessandro Share Save
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Neutralizing IFN-γ autoantibodies are rare and in HLA-DRB1*15:02 or 16:02 individuals Peel, Jessica N.; Yang, Rui; Le Voyer, Tom; Gervais, Adrian; Rosain, Jeremie; Bastard, Paul; Behere, Anish; Cederholm, Axel; Bodansky, Aaron; Seeleuthner, Yoann; Conil, Clement; Ding, Jing-Ya; Lei, Wei-Te; Bizien, Lucy; Soudee, Camille; Migaud, Melanie; Ogishi, Masato; Yatim, Ahmad; Lee, Danyel; Bohlen, Jonathan; Perpoint, Thomas; Perez, Laura; Messina, Fernando; Genet, Roxana; Karkowski, Ludovic; Blot, Mathieu; Lafont, Emmanuel; Toullec, Laurie; Goulvestre, Claire; Mehlal-Sedkaoui, Souad; Sallette, Jerome; Martin, Fernando; Puel, Anne; Jouanguy, Emmanuelle; Anderson, Mark S.; Landegren, Nils; Tiberghien, Pierre; Abel, Laurent; Boisson-Dupuis, Stephanie; Bustamante, Jacinta; Ku, Cheng-Lung; Casanova, Jean-Laurent Share Save
Human autoantibodies neutralizing type I IFNs: From 1981 to 2023 Bastard, Paul; Gervais, Adrian; Le Voyer, Tom; Philippot, Quentin; Cobat, Aurelie; Rosain, Jeremie; Jouanguy, Emmanuelle; Abel, Laurent; Zhang, Shen-Ying; Zhang, Qian; Puel, Anne; Casanova, Jean-Laurent Share Save
Unraveling the Immune Signature of Herpes Zoster: Insights Into the Pathophysiology and Human Leukocyte Antigen Risk Profile Vandoren, Romi; Boeren, Marlies; Schippers, Jolien; Bartholomeus, Esther; Mullan, Kerry; Michels, Nele; Aerts, Olivier; Leysen, Julie; Bervoets, An; Lambert, Julien; Leuridan, Elke; Wens, Johan; Peeters, Karin; Emonds, Marie-Paule; Jansens, Hilde; Casanova, Jean-Laurent; Bastard, Paul; Suls, Arvid; Van Tendeloo, Viggo; Ponsaerts, Peter; Delputte, Peter; Ogunjimi, Benson; Laukens, Kris; Meysman, Pieter Share Save