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Bruno Crestani

université parís cité

83H-index
925Paper Count
2.8WCitation Count
Published Papers 337
Publication Date
Epithelial PCSK6 Promotes Proliferation and Decreases Collagen Deposition by Fibroblasts Potentially via MMP Activation
err2026-06-04
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errOAAI
errQian Tian; Annemiek Dijkhuis; Ester B. M. Remmerswaal; Hella Aberson; Bruno Crestani; Tom van der Poll; C. Arnold Spek; Jan Willem Duitman
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Pulmonary Fibrosis Beyond the Lung: Adipose Tissue as a Systemic Modifier of Fibrotic Remodeling
err2026-05-19
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errOAAI
errPanagiota Tsiri; Bruno Crestani; Arnaud Mailleux; Argyrios Tzouvelekis
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The pleuroparenchymal fibroelastosis atlas reveals aberrant cell states and their zonation as an alternate roadmap to lung fibrosis
err2026-05-08
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errOAAI
errJannik Ruwisch; Aurélie Cazes; Lena M. Leiber; Raphaël Borie; Lavinia Neubert; Leonard Christian; Vincent Thomas de Montpréville; Adam Szmul; Farah Moussa; Stijn E. Verleden; Svenja Gaedcke; Jan Hegermann; Jan Fuge; Matthias Ballmaier; Jan C. Kamp; Mark Greer; Peter Braubach; Christopher Werlein; Fabius Ius; Theresa Graalmann; Kalil Aburahma; Laurens J. De Sadeleer; Ryoko Egashira; Maximilian Ackermann; Daisuke Yamada; Marius M. Hoeper; Christine Falk; Jens Gottlieb; Herbert B. Schiller; Bart Vanaudenaerde; Benjamin Seeliger; Marie-Pierre Debray; Jean Francois Bernaudin; Lars Knudsen; Emmanuel Bergot; Joseph Jacob; Hervé Mal; Danny Jonigk; Sabine Dettmer; Pierre Mordant; Antje Prasse; Elie Fadel; Wim A. Wuyts; Bruno Crestani; Naftali Kaminski; Aurélien Justet; Jonas C. Schupp
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Adult male patients with DKC1 mutations present early-onset pulmonary fibrosis and severe prognosis
err2026-01-19
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PREAI
errEvrard, Ophelie; Philippot, Quentin; Kannengiesser, Caroline; Debray, Marie Pierre; Guyard, Alice; Fattori, Antonin; Schuller, Armelle; Nunes, Hilario; Montani, David; Bours, Vincent; Cottin, Vincent; Traclet, Julie; Benattia, Amira; Berthoux, Emilie; Daniel, Adrien; Yan-Min, Xu; Lainey, Elodie; Saussereau, Julien; Viallon, Malika Chelbi; Oudin, Claire; Morel, Helene; Crestani, Bruno; Borie, Raphael; Ba, Ibrahima
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ERS/EULAR clinical practice guidelines for connective tissue disease-associated interstitial lung disease
err2026-01-01
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errOAAI
errAntoniou, Katerina M.; Distler, Oliver; Gheorghiu, Ana-Maria; Moor, Catharina C.; Vikse, Jens; Bizymi, Nikoleta; Galetti, Ilaria; Brown, Graham; Bargagli, Elena; Allanore, Yannick; Corte, Tamera J.; Dieude, Philippe; Cottin, Vincent; Fisher, Benjamin A.; Fabre, Aurelie; Giles, Jon T.; Kreuter, Michael; Lundberg, Ingrid E.; Poletti, Venerino; Maurer, Britta; Renzoni, Elisabetta A.; Muller-Ladner, Ulf; Strek, Mary E.; Sverzellati, Nicola; Studenic, Paul; Mohammed, Jibril; Nagavci, Blin; Stamm, Tanja; Tonia, Thomy; Crestani, Bruno; Hoffmann-Vold, Anna-Maria
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Short telomere length is associated with accelerated lung disease progression in rheumatoid arthritis-associated interstitial lung disease
err2025-12-01
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PREAI
errEl Husseini, Kinan; Lee, Joyce S.; Juge, Pierre-Antoine; Ebstein, Esther; Ottaviani, Sebastien; Borie, Raphael; Bancal, Catherine; Debray, Marie-Pierre; Kannengiesser, Caroline; Ba, Ibrahima; Marchand-Adam, Sylvain; Richez, Christophe; Nunes, Hilario; Avouac, Jerome; Flipo, Rene-Marc; Wemeau, Lidwine; Boissier, Marie-Christophe; Schaeverbeke, Thierry; Kermanac'h, Nathalie Saidenberg; Kawano-Dourado, Leticia; Cottin, Vincent; Wolters, Paul J.; Granger, Benjamin; Dieude, Philippe; Crestani, Bruno
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CT features of interstitial lung disease in systemic lupus erythematosus and overlap lupus-other connective tissue disease
err2025-11-19
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PREAI
errAurore Sajust de Bergues de Escalup; Arthur Mageau; Lou Deneuville; Karim Sacre; Antoine Khalil; Nathalie Costedoat-Chalumeau; Eric Hachulla; Yurdagul Uzunhan; Erwan Le Tallec; Jacques Cadranel; Sylvain Marchand-Adam; David Montani; Martine Reynaud-Gaubert; Grégoire Prévot; Guillaume Beltramo; Bruno Crestani; Vincent Cottin; Raphaël Borie; Marie-Pierre Debray
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A novel RTEL1 nonsense variant in a case of familial pulmonary fibrosis: clinical description and genetic implications
err2025-11-09
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errGiovanni Franco; Francesca Bertola; Filippo Aloisi; Samuele Promi; Umberto Zanini; Paola Faverio; Angela Bentivegna; Raphaël Borie; Bruno Crestani; Giovanni Cazzaniga; Fabrizio Luppi
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Nintedanib combined with pirfenidone in patients with idiopathic pulmonary fibrosis or progressive pulmonary fibrosis: a long-term retrospective multicentre study (Combi-PF)
err2025-10-10
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errCorentin Meersseman; Elisa Martínez Besteiro; Nicolas Romain-Scelle; Bruno Crestani; Sylvain Marchand-Adam; Hilario Nunes; Lidwine Wémeau-Stervinou; Raphael Borie; Rémi Diesler; Claudia Valenzuela; Vincent Cottin
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Characterization of human lung immune cells in the humanized BRGSF mouse model
err2025-10-01
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PREAI
errPokhreal, Deepak; Curioni, Anna, V; Creusat, Florent; Martin, Gaelle H.; Sonego, Fabiane; Thiam, Kader; Mordant, Pierre; Mal, Herve; Bellamri, Nessrine; Flament, Heloise; Crestani, Bruno; Helou, Doumet Georges
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Lysosomal Storage Disorders
err2025-10-01
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PREAI
errCefalo, Jacopo; Crestani, Bruno; Guyard, Alice; Pettazzoni, Magali; Mauhin, Wladimir; Debray, Marie-Pierre; Borie, Raphael
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Stratifying GAP Stages by MUC5B rs35705950 T-Allele Carriage Refines Survival Prediction in IPF
errLung
IF3.9
err2025-07-30
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PREAI
errJoanne J. van der Vis; Antje Prasse; Elisabetta A. Renzoni; Carmel J. W. Stock; Toby M. Maher; Francesco Bonella; Raphael Borie; Bruno Crestani; Wim A. Wuyts; Philip L. Molyneaux; Johannes C. Kelder; Jan C. Grutters; Coline H. M. van Moorsel
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Identification of FGFR4 as a regulator of myofibroblast differentiation in pulmonary fibrosis
err2024-12-01
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PREAI
errGhanem, Mada; Justet, Aurelien; Jaillet, Madeleine; Vasarmidi, Eirini; Boghanim, Tiara; Hachem, Mouna; Vadel, Aurelie; Joannes, Audrey; Mordant, Pierre; Balayev, Agshin; Adams, Taylor; Mal, Herve; Cazes, Aurelie; Pote, Nicolas; Mailleux, Arnaud; Crestani, Bruno
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Rare genetic interstitial lung diseases: a pictorial essay
err2024-11-13
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errBorie, Raphael; Berteloot, Laureline; Kannengiesser, Caroline; Griese, Matthias; Cazes, Aurelie; Crestani, Bruno; Hadchouel, Alice; Debray, Marie Pierre
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Lucile Sese1⇈Isabella Annesi-Maesano2Pierre Antoine Juge3Sophie Mayer4Johanna Sigaux5Bruno Crestani6Lucas Semerano5Boris Dessimond2Raphaël Borie6Marie-Pierre Debray7Bernard Combe8Pierre-Yves Brillet9Yurdagul Uzunhan10Philippe Dieudé3Hilario Nunes10
err2024-10-30
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PREAI
errSese, Lucile; Annesi-Maesano, Isabella; Juge, Pierre Antoine; Mayer, Sophie; Sigaux, Johanna; Crestani, Bruno; Semerano, Lucas; Dessimond, Boris; Borie, Raphael; Debray, Marie-Pierre; Combe, Bernard; Brillet, Pierre-Yves; Uzunhan, Yurdagul; Dieude, Philippe; Nunes, Hilario
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Analysis of transcriptional profile of lung fibroblasts derived from patients with progressive pulmonary fibrosis (PPF)
err2024-10-30
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PREAI
errVoisin, Tom; Morzadec, Claudie; Lettelier, Alice; Le Naoures, Cecile; De Latour, Bertrand Richard; Crestan, Bruno; Jouneau, Stephane; Vernhet, Laurent; Joannes, Audrey
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BERYSARC: a multicentric control case study comparing chronic beryllium disease to pulmonary sarcoidosis
err2024-10-30
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PREAI
errRotenberg, Cecile; Ba, Stephane Tran; Marchand-Adam, Sylvain; Andujar, Pascal; Crestani, Bruno; Bravais, Juliette; Brauner, Michel; Brillet, Pierre-Yves; Cadranel, Jacques; Borie, Raphael; Cottin, Vincent; Leguen, Pierre; Maitre, Bernard; Nieves-Martinez, Ana; Nunes, Hilario; Reynaud-Gaubert, Martine; Salaun, Mathieu; Valeyre, Dominique; Jeny, Florence
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Impact of genetic multidisciplinaryteam discussion on lung fibrosis
err2024-10-30
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PREAI
errFranco, Giovanni; Kannengiesser, Caroline; Nathan, Nadia; Lassus, Albane; Guerin, Cecile; Ba, Ibrahima; Froidure, Antoine; Manali, Effrosyni; Brunel, Vincent; Bonniaud, Philippe; Bouvry, Diane; Debray, Marie Pierre; Juge, Pierre Antoine; Epaud, Ralph; De Becdelievre, Alix; Louvrie, Camille; Plessier, Aurelie; De Fontbrune, Flore Sicre; Wemeau-Stervinou, Lidwine; Adam, Sylvain Marchand; Chabrol, Alexandre; Maurac, Arnaud; Savale, Laurent; Montani, David; Crestani, Bruno; Cottin, Vincent; Borie, Raphael
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Short telomere length is associated with disease progression in rheumatoid arthritis- associated interstitial lung disease
err2024-10-30
err0
PREAI
errEl Husseini, Kinan; Juge, Pierre-Antoine; Ebstein, Esther; Ottaviani, Sebastien; Borie, Raphael; Kannengiesser, Caroline; Marchand-Adam, Sylvain; Richez, Christophe; Nunes, Hilario; Avouac, Jerome; Flipo, Rene-Marc; Boissier, Marie-Christophe; Schaeverbeke, Thierry; Saidenberg-Kermanac'H, Nathalie; Lee, Joyce; Kawanodourado, Leticia; Granger, Benjamin; Dieude, Philippe; Crestani, Bruno
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