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Benjamin L. Shneider

university of michigan system

77H-index
404Paper Count
1.8WCitation Count
Published Papers 150
Publication Date
Prospective Multicenter Longitudinal Measurement of Liver Stiffness in School-Age Children With Cholestatic Liver Disease
err2025-10-01
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errShneider, Benjamin L.; Goodrich, Nathan P.; Ye, Wen; Molleston, Jean P.; Leung, Daniel H.; Sokol, Ronald J.; Cavallo, Laurel; Wang, Kasper; Valentino, Pamela L.; Teckman, Jeffery H.; Squires, James E.; Sundaram, Shikha S.; Rosenthal, Philip; Romero, Rene; Miethke, Alexander G.; Loomes, Kathleen M.; Kohli, Rohit; Karpen, Saul J.; Kamath, Binita M.; Jensen, M. Kyle; Bezerra, Jorge A.; Bass, Lee M.; Magee, John C.
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Plasma proteome correlations with liver stiffness in pediatric cholestasis implicate epithelial to mesenchymal transition
err2025-09-29
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errShneider, Benjamin L.; Kanchi, Rupa S.; Grimm, Sandra L.; Devaraj, Sridevi; Emamaullee, Juliet; Schraw, Jeremy; Lupo, Philip J.; Bezerra, Jorge A.; Loomes, Kathleen M.; Magee, John C.; Sokol, Ronald J.; Wang, Kasper S.; Kriegmeier, Alyssa; Hsu, Evelyn; Molleston, Jean P.; Rosenthal, Philip; Kohli, Rohit; Karpen, Saul J.; Horslen, Simon P.; Jensen, M. Kyle; Barbetta, Arianna; Coarfa, Cristian; on behalf of the Childhood Liver Disease Research Network
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Prevalence of fibrosis in hepatic explants and biopsies from individuals with urea cycle disorders
err2025-06-13
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PREAI
errSaima Ali; Aisha Nisar; Anqing Zhang; Sandesh Nagamani; Nathalie M. Aceves-Ewing; Brandy Rawls; Thu Quan; Greg Enns; John Goss; Daniel H. Leung; Benjamin L. Shneider; Shilpa Jain; Florette K. Hazard; Deborah Schady; Lindsay C. Burrage
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High prevalence of hepatic fibrosis in liver tissue from individuals with argininosuccinate lyase deficiency
err2024-04-01
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PREAI
errBurrage, Lindsay; Ali, Saima; Nisar, Aisha; Quan, Thu; Aceves, Nathalie; Shneider, Benjamin; Leung, Daniel; Nagamani, Sandesh; Enns, Gregory; Jain, Shilpa; Goss, John; Hazard, Florette; Schady, Deborah
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Diagnostic accuracy of serum matrix metalloproteinase-7 as a biomarker of biliary atresia in a large North American cohort
err2024-03-06
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errPandurangi, Sindhu; Mourya, Reena; Nalluri, Shreya; Fei, Lin; Dong, Shun; Harpavat, Sanjiv; Guthery, Stephen L.; Molleston, Jean P.; Rosenthal, Philip; Sokol, Ronald J.; Wang, Kasper S.; Ng, Vicky; Alonso, Estella M.; Hsu, Evelyn K.; Karpen, Saul J.; Loomes, Kathleen M.; Magee, John C.; Shneider, Benjamin L.; Horslen, Simon P.; Teckman, Jeffrey H.; Bezerra, Jorge A.
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Neonatal cholestasis in children with Alpha-1-AT deficiency is a risk for earlier severe liver disease with male predominance
err2023-12-01
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errTeckman, Jeffrey; Rosenthal, Philip; Ignacio, Rosalinda V.; Spino, Cathie; Bass, Lee M.; Horslen, Simon; Wang, Kasper; Magee, John C.; Karpen, Saul; Asai, Akihiro; Molleston, Jean P.; Squires, Robert H.; Kamath, Binita M.; Guthery, Stephen L.; Loomes, Kathleen M.; Shneider, Benjamin L.; Sokol, Ronald J.
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Sarcopenia is associated with osteopenia and impaired quality of life in children with genetic intrahepatic cholestatic liver disease
err2023-11-01
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errBoster, Julia M.; Goodrich, Nathan P.; Spino, Cathie; Loomes, Kathleen M.; Alonso, Estella M.; Kamath, Binita M.; Sokol, Ronald J.; Karpen, Saul; Miethke, Alexander; Shneider, Benjamin L.; Molleston, Jean P.; Kohli, Rohit; Horslen, Simon P.; Rosenthal, Philip; Valentino, Pamela L.; Teckman, Jeffrey H.; Hangartner, Thomas N.; Sundaram, Shikha S.
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Serum bile acids as a prognostic biomarker in biliary atresia following Kasai portoenterostomy
err2023-02-17
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errHarpavat, Sanjiv; Hawthorne, Kieran; Setchell, Kenneth D. R.; Rivas, Monica Narvaez; Henn, Lisa; Beil, Charlotte A.; Karpen, Saul J.; Ng, Vicky L.; Alonso, Estella M.; Bezerra, Jorge A.; Guthery, Stephen L.; Horslen, Simon; Loomes, Kathy M.; McKiernan, Patrick; Magee, John C.; Merion, Robert M.; Molleston, Jean P.; Rosenthal, Philip; Thompson, Richard J.; Wang, Kasper S.; Sokol, Ronald J.; Shneider, Benjamin L.
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Genotype-phenotype relationships of truncating mutations, p.E297G and p.D482G in bile salt export pump deficiency
err2023-02-01
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errFelzen, Antonia; van Wessel, Daan B. E.; Gonzales, Emmanuel; Thompson, Richard J.; Jankowska, Irena; Shneider, Benjamin L.; Sokal, Etienne; Grammatikopoulos, Tassos; Kadaristiana, Agustina; Jacquemin, Emmanuel; Spraul, Anne; Lipinski, Patryk; Czubkowski, Piotr; Rock, Nathalie; Shagrani, Mohammad; Broering, Dieter; Nicastro, Emanuele; Kelly, Deirdre; Nebbia, Gabriella; Arnell, Henrik; Fischler, Bjoern; Hulscher, Jan B. F.; Serranti, Daniele; Arikan, Cigdem; Polat, Esra; Debray, Dominique; Lacaille, Florence; Goncalves, Cristina; Hierro, Loreto; Bartolo, Gema Munoz; Mozer-Glassberg, Yael; Azaz, Amer; Brecelj, Jernej; Dezsofi, Antal; Calvo, Pier Luigi; Grabhorn, Enke; Hartleif, Steffen; van der Woerd, Wendy J.; Kamath, Binita M.; Wang, Jian-She; Li, Liting; Durmaz, Ozlem; Kerkar, Nanda; Jorgensen, Marianne Horby; Fischer, Ryan; Jimenez-Rivera, Carolina; Alam, Seema; Cananzi, Mara; Laverdure, Noemie; Ferreira, Cristina Targa; Guerrero, Felipe Ordonez; Wang, Heng; Sency, Valerie; Kim, Kyung Mo; Chen, Huey-Ling; de Carvalho, Elisa; Fabre, Alexandre; Bernabeu, Jesus Quintero; Zellos, Aglaia; Alonso, Estella M.; Sokol, Ronald J.; Suchy, Frederick J.; Loomes, Kathleen M.; McKiernan, Patrick J.; Rosenthal, Philip; Turmelle, Yumirle; Horslen, Simon; Schwarz, Kathleen; Bezerra, Jorge A.; Wang, Kasper; Hansen, Bettina E.; Verkade, Henkjan J.
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Innate immune cell dysfunction and systemic inflammation in children with chronic liver diseases undergoing transplantation
err2023-01-01
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errMysore, Krupa R.; Kannanganat, Sunil; Schraw, Jeremy M.; Lupo, Philip J.; Goss, John A.; Setchell, Kenneth D. R.; Kheradmand, Farrah; Li, Xian C.; Shneider, Benjamin L.
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Serum biomarkers correlated with liver stiffness assessed in a multicenter study of pediatric cholestatic liver disease
err2022-11-03
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errLeung, Daniel H.; Devaraj, Sridevi; Goodrich, Nathan P.; Chen, Xinpu; Rajapakshe, Deepthi; Ye, Wen; Andreev, Victor; Minard, Charles G.; Guffey, Danielle; Molleston, Jean P.; Bass, Lee M.; Karpen, Saul J.; Kamath, Binita M.; Wang, Kasper S.; Sundaram, Shikha S.; Rosenthal, Philip; McKiernan, Patrick; Loomes, Kathleen M.; Jensen, M. Kyle; Horslen, Simon P.; Bezerra, Jorge A.; Magee, John C.; Merion, Robert M.; Sokol, Ronald J.; Shneider, Benjamin L.
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Assessment of telemedicine versus in-person care in managing abdominal pain in children during the COVID-19 pandemic
err2022-10-05
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errJazayeri, Amir; Dinh, Julie, V; Eseonu, Debra; Hollier, John M.; Shneider, Benjamin L.
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The Epidemiology of Biliary Atresia: Exploring the Role of Developmental Factors on Birth Prevalence
err2022-07-01
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errCavallo, Laurel; Kovar, Erin M.; Aqul, Amal; McLoughlin, Lucille; Mittal, Naveen K.; Rodriguez-Baez, Norberto; Shneider, Benjamin L.; Zwiener, Robert J.; Chambers, Tiffany M.; Langlois, Peter H.; Canfield, Mark A.; Agopian, A. J.; Lupo, Philip J.; Harpavat, Sanjiv
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Impact of long-term administration of maralixibat on children with cholestasis secondary to Alagille syndrome
err2022-06-07
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errShneider, Benjamin L.; Spino, Catherine A.; Kamath, Binita M.; Magee, John C.; Ignacio, Rosalinda, V; Huang, Suiyuan; Horslen, Simon P.; Molleston, Jean P.; Miethke, Alexander G.; Kohli, Rohit; Leung, Daniel H.; Jensen, M. Kyle; Loomes, Kathleen M.; Karpen, Saul J.; Mack, Cara; Rosenthal, Philip; Squires, Robert H.; Baker, Alastair; Rajwal, Sanjay; Kelly, Deirdre; Sokol, Ronald J.; Thompson, Richard J.
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Use of funded multicenter prospective longitudinal databases to inform clinical trials in rare diseases-Examination of cholestatic liver disease in Alagille syndrome
err2022-05-04
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errShneider, Benjamin L.; Kamath, Binita M.; Magee, John C.; Goodrich, Nathan P.; Loomes, Kathleen M.; Ye, Wen; Spino, Cathie; Alonso, Estella M.; Molleston, Jean P.; Bezerra, Jorge A.; Wang, Kasper S.; Karpen, Saul J.; Horslen, Simon P.; Guthery, Stephen L.; Rosenthal, Philip; Squires, Robert H.; Sokol, Ronald J.
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Risk of variceal hemorrhage and pretransplant mortality in children with biliary atresia
err2022-04-18
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errBass, Lee M.; Ye, Wen; Hawthorne, Kieran; Leung, Daniel H.; Murray, Karen F.; Molleston, Jean P.; Romero, Rene; Karpen, Saul; Rosenthal, Philip; Loomes, Kathleen M.; Wang, Kasper S.; Squires, Robert H.; Miethke, Alexander; Ng, Vicky L.; Horslen, Simon; Jensen, M. Kyle; Sokol, Ronald J.; Magee, John C.; Shneider, Benjamin L.
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Impact of Genotype, Serum Bile Acids, and Surgical Biliary Diversion on Native Liver Survival in FIC1 Deficiency
err2021-07-13
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errvan Wessel, Daan B. E.; Thompson, Richard J.; Gonzales, Emmanuel; Jankowska, Irena; Shneider, Benjamin L.; Sokal, Etienne; Grammatikopoulos, Tassos; Kadaristiana, Agustina; Jacquemin, Emmanuel; Spraul, Anne; Lipinski, Patryk; Czubkowski, Piotr; Rock, Nathalie; Shagrani, Mohammad; Broering, Dieter; Algoufi, Talal; Mazhar, Nejat; Nicastro, Emanuele; Kelly, Deirdre; Nebbia, Gabriella; Arnell, Henrik; Fischler, Bjorn; Hulscher, Jan B. F.; Serranti, Daniele; Arikan, Cigdem; Debray, Dominique; Lacaille, Florence; Goncalves, Cristina; Hierro, Loreto; Bartolo, Gema Munoz; Mozer-Glassberg, Yael; Azaz, Amer; Brecelj, Jernej; Dezsofi, Antal; Calvo, Pier Luigi; Krebs-Schmitt, Dorothee; Hartleif, Steffen; van der Woerd, Wendy L.; Wang, Jian-She; Li, Li-Ting; Durmaz, Ozlem; Kerkar, Nanda; Jorgensen, Marianne Horby; Fischer, Ryan; Jimenez-Rivera, Carolina; Alam, Seema; Cananzi, Mara; Laverdure, Noemie; Ferreira, Cristina Targa; Ordonez, Felipe; Wang, Heng; Sency, Valerie; Kim, Kyung Mo; Chen, Huey-Ling; Carvalho, Elisa; Fabre, Alexandre; Bernabeu, Jesus Quintero; Alonso, Estella M.; Sokol, Ronald J.; Suchy, Frederick J.; Loomes, Kathleen M.; McKiernan, Patrick J.; Rosenthal, Philip; Turmelle, Yumirle; Rao, Girish S.; Horslen, Simon; Kamath, Binita M.; Rogalidou, Maria; Karnsakul, Wikrom W.; Hansen, Bettina; Verkade, Henkjan J.
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Biomarkers for liver disease in urea cycle disorders
err2021-06-01
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errNagamani, Sandesh C. S.; Ali, Saima; Izem, Rima; Schady, Deborah; Masand, Prakash; Shneider, Benjamin L.; Leung, Daniel H.; Burrage, Lindsay C.
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Constitutive activation of mitogen-activated protein kinase kinase (MEK1) in ileal enterocytes leads to dysplasia and a predisposition to cancer
err2021-03-01
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errShneider, Benjamin L.; Cortes-Santiago, Nahir; Schady, Deborah A.; Krishnamoorthy, Swapna; Thevananther, Sundararajah; Rajapakshe, Kimal; Perera, Dimuthu; Huang, Shixia; Coarfa, Cristian
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