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Amyloid-Journal of Protein Folding Disorders

IF7.4
论文数2525
被引数2448
期刊论文 2525
发表时间
Prevalence and prognostic impact of valvular heart disease in transthyretin cardiac amyloidosistransthyretin心脏淀粉样变性中瓣膜性心脏病的患病率及预后影响
delete2026-10-29
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deleteCamille Sarrazyn; Philippe Debonnaire; Mathias Claeys; Francesca Graziani; Maria Chiara Meucci; Erwan Donal; Madelien Regeer; Fausto Jose Pinto; Steven Droogmans; Nico Van de Veire; Philippe Bertrand; Ching Hui Sia; Arnold Ng; Ruxandra Jurcut; Robert Adam; Kensuke Hirasawa; Takeru Nabeta; Caroline Van De Heyning; Nicole Sturkenboom; Jeroen J. Bax; Nina Ajmone Marsan
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Ixazomib maintenance for the treatment of light chain AL amyloidosis伊沙佐米维持治疗轻链型AL淀粉样变性
delete2026-10-29
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PREAI
deleteCaitlin Sarubbi; Hani Hassoun; Grace Gallagher; Mithat Gonen; Eugene Brailovski; Jessica Chapman-Lim; Sham Mailankody; Maya Levinson; Raymond Comenzo; Theresa Fogaren; Heather Landau
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Quality standards for the diagnosis and management of ATTR and AL amyloidosis: a nominal group technique studyATTR和AL淀粉样变性诊断与管理的质量标准:一项名义小组技术研究
delete2026-10-21
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deleteLaura Obici; Thibaud Damy; Lucia Galan; William Moody; João Agostinho; Carys Barton; Catarina Campos; Giovanni D’Alessio; Keith Dares; Maike F. Dohrn; Nowell Fine; David Gregory; Emmanuel Jammes; Katharine McIntosh; Tomas Ripoll-Vera; Ali Yilmaz; Isabel Ritchie; Giovanni Palladini
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Multiple musculoskeletal procedures over time and the risk of amyloidosis: a Danish nationwide cohort study多次肌肉骨骼手术与淀粉样变性风险:一项丹麦全国性队列研究
delete2026-10-20
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PREAI
deleteNavid Noory; Peter L. Graversen; Eva Havers-Borgersen; Oscar Westin; Mathew S. Maurer; Kasper Rossing; Lars Køber; Finn Gustafsson; Emil Fosbøl
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Cryo-EM reveals untwisted and non-periodic twist fibrils in ex vivo type B ATTRv-V30M fibrils冷冻电镜揭示了体外B型ATTRv-V30M原纤维中未扭转和非周期性扭转原纤维
delete2026-09-30
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PREAI
deleteShumaila  Afrin; Maria del Carmen Fernandez-Ramirez; Binh An Nguyen; Saylor Schreiber; Barbara Kluve-Beckerman; Lorena Saelices
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Frailty is a mortality risk factor in tafamidis-treated patients with transthyretin cardiac amyloidosis衰弱是接受tafamidis治疗的转甲状腺素蛋白心脏淀粉样变性患者的死亡风险因素
delete2026-09-10
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deleteAmaury Broussier; Amira Zaroui; Mounira Kharoubi; Silvia Oghina; Charlotte Lafont; Marie Laurent; Nina Liu; Nathalie Marie-Nelly; Jean-Philippe David; Emmanuel Teiger; Sylvie Bastuji Garin; Thibaud Damy
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Sodium-glucose cotransporter-2 inhibitor therapy and body composition analysis in transthyretin amyloid cardiomyopathy: a prospective, feasibility pilot study钠-葡萄糖协同转运蛋白-2抑制剂疗法与转甲状腺素蛋白淀粉样变性心肌病的体成分分析:一项前瞻性、可行性初步研究
delete2026-09-08
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PREAI
deleteAni Nalbandian; Sergio Teruya; Dia Smiley; Stephen Helmke; Hirad Yarmohammadi; Margaret Cuomo; Jeffeny De Los Santos; Kimberly Mateo Collado; Maxine Ashby-Thompson; Wen W. Yu; Alfonsina Mirabal Santos; Carlos Rodriguez; Denisse Santana Del Rosario; Elissa Driggin; Helene Maltz; Utpal Pajvani; Jai Radhakrishnan; Jonathan Barasch; Dympna Gallagher; Mathew S. Maurer
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Liver stiffness in AL amyloidosis: interest in diagnosis and prognosisAL淀粉样变性中的肝硬度:其在诊断和预后中的意义
delete2026-09-06
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PREAI
deletePaul Carrier; Véronique Loustaud-Ratti; Jean-François Cadranel; Céline Rigaud; Bienvenue Randrianarivo; David Lavergne; Laurent Alric; Aurore Baron; Eric Nguyen Khac; Arnaud Pauwels; Louis Bettan; Xavier Causse; Honoré Zougmoure; Abdelali El Kharrazi; Marilyne Debette-Gratien; Anne Cypierre; Murielle Roussel; Arnaud Jaccard
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Susceptibility and screening approaches in systemic amyloidosis: expert perspectives from the International Society of Amyloidosis (ISA)系统性淀粉样变性中的易感性和筛查方法:国际淀粉样变性学会(ISA)专家观点
delete2026-09-04
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PREAI
deleteTaxiarchis Kourelis; Raymond Comenzo; Andrea Cortese; Justin L. Grodin; Martha Grogan; Paolo Milani; Frederick L. Ruberg; Yoshiki Sekijima; Lukas D. Weberling; Efstathios Kastritis; Kevin M. Alexander
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Gastric amyloid pathology and mucosal denervation in ATTRv amyloidosis: insights from patients, mice, and gut microenvironment profilesATTRv淀粉样变性中的胃淀粉样病变和黏膜去神经支配:来自患者、小鼠和肠道微环境谱的见解
delete2026-08-29
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PREAI
deleteHsueh-Wen Hsueh; Ping-Hao Yang; Ping-Huei Tseng; Ti-Yen Yeh; Hao-Chia Hsu; Chieh‐Chang Chen; Chia-Lang Hsu; Ya‐Yin Cheng; Tsai-Wei Ting; Cheng-Chen Lin; Hui-Fang Ke; Ching-Hua Kuo; Chi‐Chao Chao; Koping Chang; Sung‐Tsang Hsieh
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Diagnostic utility of deep excisional skin biopsy including abdominal fat for transthyretin cardiac amyloidosis
delete2026-07-30
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PREAI
deleteKohei Honda; Ikoi Omatsu; Tetsuhiro Yamano; Hironobu Naiki; Ayano Maruyama; Yukiko Morinaga; Noriyuki Tanaka; Aya Miyagawa-Hayashino
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Guidelines for the management of hereditary ATTR amyloidosis 20262026年遗传性ATTR淀粉样变性管理指南
delete2026-07-09
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PREAI
deleteYoshiki Sekijima; Mitsuharu Ueda; John L. Berk; Laura Obici; Ronald M. Witteles; Violaine Planté-Bordeneuve; Markus Weiler; Marianna Fontana; Márcia Waddington Cruz; Teresa Coelho; Bo-Göran Ericzon; Pablo Garcia-Pavia; João Beirão; Jonas Wixner; Luísa Lobato; Yukio Ando; Giampaolo Merlini; Mathew S. Maurer
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Hepatic multimodal phenotyping in AL amyloidosis with cardiac involvement: the D-Amy-LIPHE studyAL淀粉样变性伴心脏受累的肝脏多模态表型研究:D-Amy-LIPHE研究
delete2026-07-06
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PREAI
deleteAnna Sessa; Amira Zaroui; Margaux Charles; Stefano Caruso; Julien Calderaro; Jeremy Augustin; Mounira Kharoubi; François Lemonnier; Karim Belhadj; Xue Shaodian; Sébastien Mulé; Emmanuel Itti; Thibaud Damy; Vincent Leroy
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